krz

UniProt ID: Q9V393
Organism: Drosophila melanogaster
Review Status: DRAFT
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Gene Description

Kurtz (Krz) is the single non-visual (beta-)arrestin of Drosophila melanogaster, a cytoplasmic member of the arrestin family with two arrestin domains. As a canonical arrestin, it binds activated/phosphorylated G-protein-coupled receptors and receptor-family proteins and acts as an adaptor that promotes their clathrin-mediated internalization, desensitization and downregulation; conserved residues required for GPCR targeting to clathrin-coated pits and for clathrin binding are functionally important. Krz is essential for viability and neural function and, because it is the only non-visual arrestin in the fly, has broad pleiotropic roles as an attenuator of multiple developmental and immune signalling pathways. It limits receptor-tyrosine-kinase/MAPK (ERK) signalling by directly binding and sequestering inactive ERK away from its activating kinase MEK, thereby restraining the Torso pathway in the early embryo; it limits Toll/NF-kappaB (Dorsal) signalling in part by binding and stabilizing the IkappaB orthologue Cactus and, in larvae, through a functional interaction with the SUMO protease Ulp1; it can promote internalization and proteasomal degradation of the GPCR-family receptor Smoothened (antagonizing Hedgehog signalling when over-expressed) and facilitates Smoothened desumoylation via Ulp1; and it forms a Notch-Deltex-Kurtz complex that drives ubiquitination-dependent degradation of the Notch receptor. In the adult nervous system Krz is required for exploratory locomotor behaviour. The protein is predominantly cytoplasmic/cytosolic, acting transiently at the plasma membrane and endocytic compartments during receptor internalization.

Existing Annotations Review

GO Term Evidence Action Reason
GO:0007600 sensory perception
IBA
GO_REF:0000033
KEEP AS NON CORE
Summary: Phylogenetic (IBA) annotation reflecting the arrestin family's conserved role in sensory/GPCR signalling; Krz controls Drosophila olfaction and other sensory GPCR responses. A real but distal, pleiotropic role rather than the gene's core biochemical function.
Reason: Consistent with Krz functioning as a GPCR regulator that controls sensory responses such as olfaction, but this is a downstream physiological outcome of the core arrestin activity rather than the molecular function itself; kept as non-core.
Supporting Evidence:
PMID:20802461
controls Drosophila olfaction, behaviour, sensitivity to osmotic stress
GO:0001664 G protein-coupled receptor binding
IBA
GO_REF:0000033
ACCEPT
Summary: Core, evolutionarily conserved molecular function of a non-visual arrestin: binding activated/phosphorylated GPCRs (and GPCR-family receptors such as Smoothened) to desensitize them and drive their internalization.
Reason: Well supported both by the canonical arrestin mechanism and by direct experimental demonstration in Drosophila that Krz binds the GPCR-family receptor Smoothened. This is a central, defining molecular function of Krz and is retained as core.
Supporting Evidence:
PMID:21437272
Krz binds to Smo and internalizes it via clathrin-coated vesicles
PMID:20802461
promote internalization of GPCRs on receptor activation
GO:0005737 cytoplasm
IBA
GO_REF:0000033
ACCEPT
Summary: Krz is predominantly a cytoplasmic protein, consistent with the non-visual arrestins being cytosolic proteins that act on receptors at/near the plasma membrane.
Reason: Directly observed by antibody staining in both embryos and imaginal discs, matching the IBA phylogenetic assignment.
Supporting Evidence:
PMID:20802461
the Krz protein is expressed throughout the blastoderm embryo and is predominantly cytoplasmic
PMID:21437272
the protein is localized in the cytoplasm of imaginal cells
GO:0002031 G protein-coupled receptor internalization
IBA
GO_REF:0000033
ACCEPT
Summary: Core arrestin function: Krz promotes clathrin-mediated internalization of activated GPCRs/GPCR-family receptors, shown directly for Smoothened and reported for other GPCRs on activation.
Reason: Canonical, conserved arrestin activity supported experimentally in Drosophila (Smo internalization via clathrin-coated vesicles; promotion of GPCR internalization on receptor activation). Retained as core.
Supporting Evidence:
PMID:21437272
promote Smoothened internalization and degradation in a clathrin- and proteosomal-dependent manner
PMID:20802461
promote internalization of GPCRs on receptor activation
GO:0007165 signal transduction
IEA
GO_REF:0000002
ACCEPT
Summary: Very general InterPro-based (IEA) annotation reflecting that arrestins participate in signal transduction. Not wrong but uninformative relative to the specific regulatory roles captured elsewhere.
Reason: A broad IEA that is biologically correct (Krz is a regulator of multiple signalling pathways); acceptable as a high-level term even though more specific process terms are also annotated.
Supporting Evidence:
PMID:21437272
participate in a variety of signalling events
GO:0005515 protein binding
IPI
PMID:20802461
Ξ²-arrestin Kurtz inhibits MAPK and Toll signalling in Drosop...
MODIFY
Summary: Bare 'protein binding' from the interaction between Krz and ERK (rolled), the WITH/FROM = UniProtKB:P40417 row of this IPI pair. Uninformative as annotated; the specific, experimentally supported activity is binding of the MAP kinase ERK, which Krz sequesters in its inactive form. The second partner from the same reference (UniProtKB:Q03017, Cactus) is adjudicated in the entry below.
Reason: 'protein binding' conveys no functional information. The IPI evidence (Krz directly binds ERK/rolled; IntAct NbExp=12) supports the more informative molecular function 'mitogen-activated protein kinase binding' (GO:0051019).
Supporting Evidence:
PMID:20802461
Krz can directly bind and sequester an inactive form of ERK, thus preventing its activation by the upstream kinase, MEK
GO:0005515 protein binding
IPI
PMID:20802461
Ξ²-arrestin Kurtz inhibits MAPK and Toll signalling in Drosop...
KEEP AS NON CORE
Summary: The second IPI row from the same reference, WITH/FROM = UniProtKB:Q03017 (Cactus, the Drosophila IkappaB orthologue). Co-immunoprecipitation from S2 cells and an in vitro translated-protein assay support a direct Krz-Cactus interaction; Krz stabilizes Cactus and thereby limits Toll/Dorsal signalling. Unlike the ERK interaction, Cactus binding is insensitive to the 'pre-activated' Krz-R209E conformation.
Reason: The interaction itself is well supported - co-immunoprecipitation from S2 cells plus an in vitro translated-protein assay - so the term is not an over-annotation; it is simply uninformative, and the Cactus interaction is peripheral to Krz's core GPCR-binding adaptor function, so it is retained as non-core. Unlike the ERK partner, there is no specific GO molecular-function term for binding an IkappaB/Cactus-family inhibitor (GO has no 'I-kappaB binding' MF; GO:0051059 NF-kappaB binding is the wrong target, since Cactus is the inhibitor, not the Rel factor), so no replacement term is proposed rather than forcing an inaccurate one. The biology this interaction supports is already captured by the GO:0045751 negative regulation of Toll signaling pathway annotation, which cites the same experiments.
Supporting Evidence:
PMID:20802461
We detected an interaction using co-immunoprecipitation from S2 cells ( Figure 7J ), as well as using in vitro translated proteins ( Supplementary Figure S7 ), suggesting a direct binding.
PMID:20802461
We observed that Krz can directly bind to the Drosophila orthologue of IΞΊBΞ±, Cactus
GO:0045751 negative regulation of Toll signaling pathway
IMP
PMID:24077307
Regulation of Toll signaling and inflammation by Ξ²-arrestin ...
KEEP AS NON CORE
Summary: Krz limits Toll/NF-kappaB signalling in larvae/immunity, acting together with the SUMO protease Ulp1; loss of krz produces an inflammatory phenotype with nuclear accumulation of Toll effectors Dorsal and Dif.
Reason: Experimentally supported inhibitory role in Toll signalling and inflammation, but a pleiotropic downstream regulatory role rather than the core arrestin biochemical function.
Supporting Evidence:
PMID:24077307
Loss of function of krz or Ulp1 in Drosophila larvae results in a similar inflammatory phenotype
GO:0120177 negative regulation of torso signaling pathway
IMP
PMID:20802461
Ξ²-arrestin Kurtz inhibits MAPK and Toll signalling in Drosop...
KEEP AS NON CORE
Summary: Krz restrains the Torso RTK pathway in the early embryo by limiting ERK activity; maternal loss of krz expands and intensifies dpERK and Torso target-gene expression.
Reason: Directly supported by maternal krz mutant analysis (increased/expanded dpERK; upregulated tll/hkb). A specific developmental-signalling role downstream of the core ERK-binding activity; kept as non-core.
Supporting Evidence:
PMID:20802461
the normal function of Krz is to limit the activity of ERK, and hence the Torso pathway, in the early embryo
GO:0005829 cytosol
IDA
PMID:21437272
Role of the Drosophila non-visual ß-arrestin kurtz in hedgeh...
ACCEPT
Summary: Direct antibody localization of Krz to the cytoplasm/cytosol of imaginal cells.
Reason: IDA-quality localization data; consistent with the cytosolic nature of non-visual arrestins and with the cytoplasm (IBA) and Reactome (TAS) cytosol annotations.
Supporting Evidence:
PMID:21437272
the protein is localized in the cytoplasm of imaginal cells
GO:0031648 protein destabilization
IMP
PMID:21437272
Role of the Drosophila non-visual ß-arrestin kurtz in hedgeh...
KEEP AS NON CORE
Summary: Over-expressed Krz reduces steady-state Smoothened levels by promoting its proteasomal degradation (destabilization), an outcome of Krz-driven Smo internalization.
Reason: Supported by S2-cell and imaginal-disc data showing Krz enhances Smo turnover via the proteasome. This destabilizing activity is a consequence of the core internalization/adaptor function acting on a specific receptor; retained as non-core.
Supporting Evidence:
PMID:21437272
Krz enhances Smo degradation via the proteosomal pathway
GO:0045879 negative regulation of smoothened signaling pathway
IMP
PMID:21437272
Role of the Drosophila non-visual ß-arrestin kurtz in hedgeh...
KEEP AS NON CORE
Summary: Over-expression of Krz phenocopies loss of Hedgehog signalling and reduces Hh target-gene expression (Ptc, En) by promoting Smoothened internalization and degradation. Note the effect is seen only on over-expression; krz loss-of-function has no Smo phenotype.
Reason: Experimentally supported antagonism of Smoothened/Hh signalling, but manifested only upon Krz over-expression and dispensable in loss-of-function, so a conditional, non-core regulatory role.
Supporting Evidence:
PMID:21437272
Krz has the potential to antagonize Hh signalling, although this antagonism is only observed upon its over-expression
GO:0045879 negative regulation of smoothened signaling pathway
IMP
PMID:28195188
SUMO regulates the activity of Smoothened and Costal-2 in Dr...
KEEP AS NON CORE
Summary: Excess Krz inhibits Smoothened sumoylation and prevents Smoothened accumulation, thereby down-regulating Hedgehog/Smoothened signalling; the effect maps to the Krz regulatory domain.
Reason: Independent experimental support (a second lab) for Krz antagonizing Smoothened signalling, here via the SUMO axis. A specific, non-core regulatory role.
Supporting Evidence:
PMID:28195188
inhibits Smo sumoylation and prevents Smo accumulation through Krz regulatory domain
GO:0060189 positive regulation of protein desumoylation
IMP
PMID:28195188
SUMO regulates the activity of Smoothened and Costal-2 in Dr...
KEEP AS NON CORE
Summary: Krz bridges Smoothened to the SUMO protease Ulp1, promoting Smo desumoylation; RNAi knockdown of Krz weakens the Smo-Ulp1 interaction.
Reason: Supported by the demonstration that Krz facilitates the Smo-Ulp1 interaction that drives desumoylation. A specialized adaptor/scaffolding role in the SUMO pathway; non-core.
Supporting Evidence:
PMID:28195188
Krz likely facilitates the interaction between Smo and Ulp1 because knockdown of Krz by RNAi attenuates Smo-Ulp1 interaction
GO:0045746 negative regulation of Notch signaling pathway
IGI
PMID:16284625
Regulation of Notch signalling by non-visual beta-arrestin.
KEEP AS NON CORE
Summary: Krz forms a trimeric Notch-Deltex-Kurtz complex that promotes ubiquitination-dependent degradation of the Notch receptor, thereby down-regulating Notch signalling. GOA carries this term as two IGI rows from the same reference, one per genetic-interaction partner (WITH/FROM = FB:FBgn0000524 and FB:FBgn0004647, the other two members of that complex); both rows are adjudicated together by this single entry.
Reason: Supported by the paper's own abstract (identification of the Notch-Deltex-Krz complex and ubiquitination-dependent Notch degradation), consistent with the arrestin adaptor role in receptor downregulation; a specific developmental-signalling role kept as non-core.
Supporting Evidence:
PMID:16284625
This complex mediates the degradation of the Notch receptor through a ubiquitination-dependent pathway.
GO:0045751 negative regulation of Toll signaling pathway
IMP
PMID:20802461
Ξ²-arrestin Kurtz inhibits MAPK and Toll signalling in Drosop...
KEEP AS NON CORE
Summary: In the early embryo Krz limits Toll signalling: maternal loss of krz expands the Dorsal nuclear gradient and Toll target-gene (twi, rho) domains; Krz binds and stabilizes the IkappaB orthologue Cactus.
Reason: Directly supported by maternal krz mutant analysis and Krz-Cactus interaction. A specific developmental-signalling role (distinct paper/context from the larval Toll annotation); non-core.
Supporting Evidence:
PMID:20802461
Krz functions during normal development to limit the activity of Toll
GO:0043409 negative regulation of MAPK cascade
IMP
PMID:20802461
Ξ²-arrestin Kurtz inhibits MAPK and Toll signalling in Drosop...
KEEP AS NON CORE
Summary: Krz negatively regulates the ERK/MAPK cascade by directly binding and sequestering inactive ERK (rolled), preventing its activation by MEK; loss of krz increases overall ERK activity.
Reason: Strongly supported mechanistically (direct ERK binding plus increased dpERK in krz mutants). The underlying molecular activity (MAP kinase binding) is captured in core_functions; this process-level inhibitory role across multiple RTKs is a pleiotropic regulatory function kept as non-core.
Supporting Evidence:
PMID:20802461
loss of krz function results in an overall increase in ERK activity
GO:0048260 positive regulation of receptor-mediated endocytosis
IMP
PMID:19850026
Regulation of smoothened by Drosophila G-protein-coupled rec...
ACCEPT
Summary: Over-expression of the beta-arrestin Krz reduces Smoothened levels, the first evidence that arrestins promote receptor (Smo) internalization/endocytosis in flies - a manifestation of the canonical arrestin adaptor-for-endocytosis function.
Reason: Captures the core, conserved arrestin activity of promoting clathrin/receptor-mediated endocytosis; supported by Krz over-expression reducing Smo. Retained as core (canonical arrestin adaptor role).
Supporting Evidence:
PMID:19850026
This is the first evidence that arrestins participate in Smo regulation in flies
PMID:21437272
Krz binds to Smo and internalizes it via clathrin-coated vesicles
GO:0005829 cytosol
TAS
Reactome:R-DME-2071846
ACCEPT
Summary: Reactome (TAS) cytosol localization for the "Deltex recruits Kurtz arrestin to Notch" step, consistent with the cytoplasmic/cytosolic localization of Krz.
Reason: Agrees with direct antibody localization of Krz to the cytoplasm/cytosol; a correct and well-supported cellular-component annotation.
Supporting Evidence:
PMID:21437272
the protein is localized in the cytoplasm of imaginal cells
GO:0005829 cytosol
TAS
Reactome:R-NUL-2071858
ACCEPT
Summary: Reactome (TAS) cytosol localization for the "Kurtz promotes ubiquitination of Notch" step, consistent with the cytoplasmic/cytosolic localization of Krz.
Reason: Duplicate cytosol localization from a related Reactome reaction; agrees with the IDA/IBA cytoplasm/cytosol evidence. Retained.
Supporting Evidence:
PMID:21437272
the protein is localized in the cytoplasm of imaginal cells
GO:0035641 locomotory exploration behavior
IMP
PMID:17151232
Exploratory activity in Drosophila requires the kurtz nonvis...
KEEP AS NON CORE
Summary: Krz is specifically required in the nervous system for exploratory locomotor activity evoked by a novel arena and for mechanically stimulated activity; it is not required for spontaneous activity.
Reason: Experimentally supported organismal behavioural phenotype, a distal physiological consequence of Krz's neuronal GPCR-regulatory activity rather than its core molecular function; non-core.
Supporting Evidence:
PMID:17151232
There is a specific requirement for the kurtz nonvisual arrestin in the nervous system for both the exploration stimulated by the novel arena and the mechanically stimulated activity.

Core Functions

Non-visual arrestin adaptor that binds activated GPCRs / GPCR-family receptors and promotes their clathrin-mediated internalization and endocytic downregulation, acting from the cytoplasm.

Supporting Evidence:
  • PMID:21437272
    promote Smoothened internalization and degradation in a clathrin- and proteosomal-dependent manner
  • PMID:21437272
    Krz binds to Smo and internalizes it via clathrin-coated vesicles
  • PMID:20802461
    promote internalization of GPCRs on receptor activation

Directly binds the MAP kinase ERK (rolled), sequestering its inactive form and thereby limiting ERK/MAPK-cascade activation downstream of receptor tyrosine kinases.

Cellular Locations:
Supporting Evidence:
  • PMID:20802461
    Krz can directly bind and sequester an inactive form of ERK, thus preventing its activation by the upstream kinase, MEK
  • PMID:20802461
    loss of krz function results in an overall increase in ERK activity

References

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Suggested Questions for Experts

Q: Does Krz bind clathrin and/or the AP-2 adaptor directly in Drosophila (as predicted by the conserved Leu440/IsoLeu441/Leu443 clathrin-binding motif), and can a specific clathrin-binding or clathrin-adaptor molecular function be experimentally assigned?

Q: Which endogenous GPCRs (beyond Smoothened) are physiological Krz substrates in vivo, and is Krz's ERK-sequestration mechanism used downstream of GPCRs as well as RTKs?

Suggested Experiments

Experiment: Endogenous co-immunoprecipitation / proximity-labeling of Krz to identify its receptor and adaptor (clathrin, AP-2) interactome under basal versus receptor-activated conditions.

Experiment: Live imaging of tagged endogenous Krz to test transient recruitment to the plasma membrane and endosomes during agonist-induced receptor internalization.

πŸ“š Additional Documentation

Notes

(krz-notes.md)

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