HDAC6

UniProt ID: Q9UBN7
Organism: Homo sapiens
Review Status: COMPLETE
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Gene Description

HDAC6 is a class IIb cytoplasmic protein deacetylase with unique dual catalytic domains (CD1/CD2) and a C-terminal ZnF-UBP ubiquitin-binding domain. It primarily deacetylates non-histone substrates in the cytoplasm, most notably alpha-tubulin (K40), HSP90, and cortactin. HDAC6 plays a central role in microtubule-dependent cell motility, cilium disassembly, and the aggresome-autophagy pathway for clearing misfolded protein aggregates. The SE14 repeat region mediates cytoplasmic retention, while the ZnF-UBP domain enables binding to polyubiquitinated misfolded proteins and their transport via dynein motors to aggresomes for autophagic clearance.

Existing Annotations Review

GO Term Evidence Action Reason
GO:0005737 cytoplasm
IBA
GO_REF:0000033
ACCEPT
Summary: HDAC6 is predominantly cytoplasmic, where it associates with microtubules and carries out its primary deacetylase functions on tubulin, HSP90, and cortactin [PMID:12024216]. The SE14 repeat region mediates cytoplasmic retention.
Reason: Core localization. HDAC6 is established as a predominantly cytoplasmic deacetylase, distinct from nuclear HDACs. This is supported by extensive experimental evidence [PMID:12024216, UniProt Q9UBN7].
Supporting Evidence:
PMID:12024216
HDAC6 is localized exclusively in the cytoplasm, where it associates with microtubules
file:human/HDAC6/HDAC6-deep-research-falcon.md
model: Edison Scientific Literature
GO:0019213 deacetylase activity
IBA
GO_REF:0000033
ACCEPT
Summary: HDAC6 is a Zn2+-dependent deacetylase with two catalytic domains. It deacetylates non-histone substrates including alpha-tubulin, HSP90, cortactin, peroxiredoxins, and other proteins.
Reason: Core molecular function. HDAC6 is a bona fide protein deacetylase. The term is appropriately general as a parent term to more specific deacetylase activities.
Supporting Evidence:
PMID:12024216
HDAC6, functions as a tubulin deacetylase
GO:0005829 cytosol
IBA
GO_REF:0000033
ACCEPT
Summary: HDAC6 localizes to the cytosol where it carries out its deacetylase functions.
Reason: Core localization. Cytosol is an appropriate more specific term than cytoplasm. HDAC6 is found in the soluble cytosolic fraction as well as associated with microtubules.
Supporting Evidence:
PMID:12024216
HDAC6 is localized exclusively in the cytoplasm
GO:0090042 tubulin deacetylation
IBA
GO_REF:0000033
ACCEPT
Summary: HDAC6 deacetylates alpha-tubulin at K40, regulating microtubule stability and dynamics. This is one of the primary functions of HDAC6 [PMID:12024216].
Reason: Core biological process. Tubulin deacetylation is one of the best-characterized and most important functions of HDAC6. Multiple studies demonstrate this activity both in vitro and in vivo.
Supporting Evidence:
PMID:12024216
In vivo, the overexpression of HDAC6 leads to a global deacetylation of alpha-tubulin, whereas a decrease in HDAC6 increases alpha-tubulin acetylation. In vitro, purified HDAC6 potently deacetylates alpha-tubulin in assembled microtubules.
GO:1904115 axon cytoplasm
IEA
GO_REF:0000108
KEEP AS NON CORE
Summary: HDAC6 localizes to axons and regulates axonal transport via tubulin deacetylation.
Reason: While HDAC6 does localize to axons (by sequence similarity), this is a specialized neuronal localization rather than a core function across all cell types. Its axonal role relates to regulating microtubule dynamics and transport.
GO:0000118 histone deacetylase complex
IEA
GO_REF:0000117
MARK AS OVER ANNOTATED
Summary: HDAC6 can interact with other HDACs (e.g., HDAC11) but primarily functions as a cytoplasmic non-histone deacetylase, not as part of classical histone deacetylase complexes.
Reason: HDAC6 is predominantly cytoplasmic and deacetylates non-histone substrates. While it can interact with other HDACs, it does not primarily function in canonical nuclear histone deacetylase complexes. This annotation may be misleading about HDAC6's actual role.
GO:0003779 actin binding
IEA
GO_REF:0000043
KEEP AS NON CORE
Summary: HDAC6 interacts with cortactin (an actin-binding protein) and F-actin. It deacetylates cortactin to regulate actin dynamics.
Reason: HDAC6 does interact with actin cytoskeleton components, but the primary functional relationship is through cortactin deacetylation rather than direct actin binding as a core function.
GO:0005634 nucleus
IEA
GO_REF:0000120
KEEP AS NON CORE
Summary: HDAC6 can shuttle to the nucleus under certain conditions (valine deprivation, DNA damage, differentiation) but is predominantly cytoplasmic.
Reason: While HDAC6 can translocate to the nucleus, its primary localization and function is cytoplasmic. Nuclear localization is context-dependent and represents a specialized rather than core localization.
Supporting Evidence:
UniProt:Q9UBN7
Can shuttle between the cytoplasm and the nucleus (PubMed:39567688). Retained in the cytoplasm by binding to valine via the primate-specific SE14 repeat region
GO:0005737 cytoplasm
IEA
GO_REF:0000120
ACCEPT
Summary: Duplicate annotation for cytoplasm localization.
Reason: Core localization. Same as IBA annotation - HDAC6 is predominantly cytoplasmic.
GO:0005813 centrosome
IEA
GO_REF:0000044
ACCEPT
Summary: HDAC6 localizes to the centrosome where it participates in cilium disassembly.
Reason: Core localization for cilium-related function. HDAC6 localizes to the centrosome/ ciliary basal body and is required for cilium disassembly via deacetylation of alpha-tubulin [PMID:17604723, PMID:26246421].
Supporting Evidence:
PMID:17604723
interactions between the prometastatic scaffolding protein HEF1/Cas-L/NEDD9 and the oncogenic Aurora A (AurA) kinase at the basal body of cilia causes phosphorylation and activation of HDAC6, a tubulin deacetylase, promoting ciliary disassembly
GO:0005856 cytoskeleton
IEA
GO_REF:0000044
ACCEPT
Summary: HDAC6 associates with the cytoskeleton, particularly microtubules.
Reason: Core localization. HDAC6 associates with microtubules and the cytoskeleton as part of its role in regulating microtubule dynamics.
Supporting Evidence:
PMID:12024216
HDAC6 is localized exclusively in the cytoplasm, where it associates with microtubules
IEA
GO_REF:0000044
ACCEPT
Summary: HDAC6 localizes to cilia where it promotes ciliary disassembly via tubulin deacetylation.
Reason: HDAC6 localizes to cilia/ciliary basal body and has a direct role in cilium disassembly through deacetylation of alpha-tubulin [PMID:17604723].
Supporting Evidence:
PMID:17604723
Aurora A (AurA) kinase at the basal body of cilia causes phosphorylation and activation of HDAC6, a tubulin deacetylase, promoting ciliary disassembly
GO:0006325 chromatin organization
IEA
GO_REF:0000043
MARK AS OVER ANNOTATED
Summary: Despite being named a histone deacetylase, HDAC6 primarily functions on non-histone substrates in the cytoplasm.
Reason: HDAC6 is predominantly cytoplasmic and deacetylates non-histone substrates. Its role in chromatin organization is minimal compared to nuclear HDACs. UniProt explicitly notes it was "originally thought to be a histone deacetylase" but subsequent work showed it primarily deacetylates non-histone substrates.
GO:0006914 autophagy
IEA
GO_REF:0000043
ACCEPT
Summary: HDAC6 plays a genuine role in autophagy, particularly aggrephagy. It binds polyubiquitinated misfolded proteins via its ZnF-UBP domain and transports them to aggresomes for autophagic clearance [PMID:14675537, PMID:16192271].
Reason: Core function. HDAC6's role in autophagy/aggrephagy is well-established and represents a key non-deacetylase function mediated by its ZnF-UBP domain and dynein binding.
Supporting Evidence:
PMID:14675537
HDAC6 has the capacity to bind both polyubiquitinated misfolded proteins and dynein motors, thereby acting to recruit misfolded protein cargo to dynein motors for transport to aggresomes
PMID:16192271
HDAC6-dependent retrograde transport on microtubules is used by cells to increase the efficiency and selectivity of autophagic degradation
GO:0006950 response to stress
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HDAC6 participates in cellular stress responses, particularly misfolded protein stress and heat stress responses.
Reason: HDAC6 does participate in stress responses (misfolded protein stress, heat shock response), but this is a very broad term. The specific mechanisms (aggresome formation, HSP90 regulation) are more informative annotations.
GO:0008270 zinc ion binding
IEA
GO_REF:0000120
ACCEPT
Summary: HDAC6 is a Zn2+-dependent deacetylase that binds 3 Zn2+ ions per subunit.
Reason: Core molecular function. Zinc binding is essential for HDAC6's deacetylase activity and for the ZnF-UBP domain function.
Supporting Evidence:
UniProt:Q9UBN7
Binds 3 Zn(2+) ions per subunit
GO:0016236 macroautophagy
IEA
GO_REF:0000117
ACCEPT
Summary: HDAC6 regulates macroautophagy through multiple mechanisms including aggresome formation and cortactin deacetylation promoting autophagosome-lysosome fusion.
Reason: Core function. HDAC6's role in autophagy is well-established through its aggresome function and regulation of autophagosome-lysosome fusion.
Supporting Evidence:
PMID:16192271
HDAC6 and microtubules are required for autophagic degradation of aggregated huntingtin
GO:0016740 transferase activity
IEA
GO_REF:0000043
KEEP AS NON CORE
Summary: HDAC6 has E3 ubiquitin-protein ligase activity (transferase activity transferring ubiquitin), in addition to its deacetylase function.
Reason: While HDAC6 does have ubiquitin ligase activity (mediates ubiquitination of MSH2), this is a more specialized function. The term is very broad and the more specific ubiquitin protein ligase activity term is more informative.
GO:0016787 hydrolase activity
IEA
GO_REF:0000043
ACCEPT
Summary: HDAC6 is a hydrolase that cleaves acetyl groups from lysine residues.
Reason: Core molecular function. Deacetylation is a hydrolysis reaction, so this parent term is accurate though very general.
IEA
GO_REF:0000120
KEEP AS NON CORE
Summary: HDAC6 localizes to axons where it regulates microtubule dynamics and axonal transport.
Reason: Specialized neuronal localization. While HDAC6 is present in axons, this is cell-type specific rather than a core localization across all cell types.
GO:0030425 dendrite
IEA
GO_REF:0000120
KEEP AS NON CORE
Summary: HDAC6 localizes to dendrites in neurons.
Reason: Specialized neuronal localization rather than core localization.
GO:0032886 regulation of microtubule-based process
IEA
GO_REF:0000117
ACCEPT
Summary: HDAC6 regulates microtubule-based processes through deacetylation of alpha-tubulin, affecting microtubule stability, dynamics, and dependent processes.
Reason: Core function. This accurately captures HDAC6's role in regulating microtubule dynamics through tubulin deacetylation.
Supporting Evidence:
PMID:12024216
overexpression of HDAC6 promotes chemotactic cell movement, supporting the idea that HDAC6-mediated deacetylation regulates microtubule-dependent cell motility
GO:0043204 perikaryon
IEA
GO_REF:0000120
KEEP AS NON CORE
Summary: HDAC6 localizes to the perikaryon (cell body) of neurons.
Reason: Specialized neuronal localization rather than core localization across all cell types.
GO:0046872 metal ion binding
IEA
GO_REF:0000043
ACCEPT
Summary: HDAC6 binds zinc ions which are required for its deacetylase activity.
Reason: Core molecular function. Metal (zinc) binding is essential for HDAC6 catalytic activity.
GO:0051129 negative regulation of cellular component organization
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HDAC6 can negatively regulate cellular component organization through effects on microtubule stability and cilium disassembly.
Reason: Very broad term. The specific effects (microtubule dynamics, cilium disassembly) are more informative annotations.
GO:0051130 positive regulation of cellular component organization
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HDAC6 can positively regulate cellular component organization through aggresome formation.
Reason: Very broad term. More specific terms like aggresome assembly are more informative.
GO:0098732 macromolecule deacylation
IEA
GO_REF:0000117
ACCEPT
Summary: HDAC6 catalyzes deacetylation (a type of deacylation) of proteins.
Reason: Core function. Deacetylation is the primary enzymatic activity of HDAC6.
GO:0120025 plasma membrane bounded cell projection
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HDAC6 localizes to cell projections including cilia, axons, and dendrites.
Reason: Very broad parent term. More specific terms (cilium, axon, dendrite) are more informative.
GO:0005515 protein binding
IPI
PMID:12024216
HDAC6 is a microtubule-associated deacetylase.
MODIFY
Summary: Generic protein binding annotation from the study that identified HDAC6 as a tubulin deacetylase.
Reason: 'Protein binding' is uninformative. This study showed HDAC6 binds tubulin, which should be captured by more specific terms like alpha-tubulin binding or microtubule binding.
Proposed replacements: alpha-tubulin binding
Supporting Evidence:
PMID:12024216
HDAC6 is a microtubule-associated deacetylase.
GO:0005515 protein binding
IPI
PMID:12354939
Histone deacetylase 6 binds polyubiquitin through its zinc f...
MODIFY
Summary: This study showed HDAC6 binds polyubiquitin through its zinc finger (PAZ/BUZ) domain.
Reason: 'Protein binding' is uninformative. This study demonstrated ubiquitin binding which is captured by GO:0043130 (ubiquitin binding).
Proposed replacements: ubiquitin binding
Supporting Evidence:
PMID:12354939
Histone deacetylase 6 binds polyubiquitin through its zinc finger (PAZ domain) and copurifies with deubiquitinating enzymes.
GO:0005515 protein binding
IPI
PMID:16919237
Breast cancer metastasis suppressor 1 (BRMS1) is stabilized ...
MODIFY
Summary: Study showing HDAC6 interaction (via HSP90 pathway).
Reason: 'Protein binding' is uninformative. Should be captured by more specific binding terms.
Proposed replacements: Hsp90 protein binding
Supporting Evidence:
PMID:16919237
Breast cancer metastasis suppressor 1 (BRMS1) is stabilized by the Hsp90 chaperone.
GO:0005515 protein binding
IPI
PMID:18356165
HDAC6 is required for epidermal growth factor-induced beta-c...
MODIFY
Summary: Study showing HDAC6 interactions with beta-catenin and EGFR pathway components.
Reason: 'Protein binding' is uninformative. More specific terms available.
Proposed replacements: beta-catenin binding
Supporting Evidence:
PMID:18356165
2008 Mar 20. HDAC6 is required for epidermal growth factor-induced beta-catenin nuclear localization.
GO:0005515 protein binding
IPI
PMID:19036992
Direct binding with histone deacetylase 6 mediates the rever...
KEEP AS NON CORE
Summary: Study showing direct binding of HDAC6 with parkin at the centrosome.
Reason: While 'protein binding' is uninformative, the parkin interaction relates to HDAC6's role in the autophagy/mitophagy pathway.
Supporting Evidence:
PMID:19036992
Direct binding with histone deacetylase 6 mediates the reversible recruitment of parkin to the centrosome.
GO:0005515 protein binding
IPI
PMID:19167333
A centrosomal Cdc20-APC pathway controls dendrite morphogene...
KEEP AS NON CORE
Summary: Study on centrosomal Cdc20-APC pathway in dendrite morphogenesis.
Reason: Interaction related to neuronal development, not core HDAC6 function.
Supporting Evidence:
PMID:19167333
A centrosomal Cdc20-APC pathway controls dendrite morphogenesis in postmitotic neurons.
GO:0005515 protein binding
IPI
PMID:19893491
CYLD negatively regulates cell-cycle progression by inactiva...
KEEP AS NON CORE
Summary: Study showing CYLD negatively regulates HDAC6 and tubulin acetylation.
Reason: CYLD-HDAC6 interaction is a regulatory mechanism, not a core function.
Supporting Evidence:
PMID:19893491
CYLD negatively regulates cell-cycle progression by inactivating HDAC6 and increasing the levels of acetylated tubulin.
GO:0005515 protein binding
IPI
PMID:20029029
Regulation of epidermal growth factor receptor trafficking b...
KEEP AS NON CORE
Summary: Study on HDAC6 regulation of EGFR trafficking.
Reason: EGFR interaction may be indirect through HDAC6's effects on microtubule dynamics.
Supporting Evidence:
PMID:20029029
Regulation of epidermal growth factor receptor trafficking by lysine deacetylase HDAC6.
GO:0005515 protein binding
IPI
PMID:21220424
Regulation of Tat acetylation and transactivation activity b...
KEEP AS NON CORE
Summary: Study on HDAC6 regulation of HIV Tat acetylation.
Reason: Viral protein interaction, specialized context.
Supporting Evidence:
PMID:21220424
2011 Jan 10. Regulation of Tat acetylation and transactivation activity by the microtubule-associated deacetylase HDAC6.
GO:0005515 protein binding
IPI
PMID:21532619
The HTLV-1 Tax protein inhibits formation of stress granules...
KEEP AS NON CORE
Summary: Study showing HTLV-1 Tax protein interacts with HDAC6.
Reason: Viral protein interaction, specialized context.
Supporting Evidence:
PMID:21532619
The HTLV-1 Tax protein inhibits formation of stress granules by interacting with histone deacetylase 6.
GO:0005515 protein binding
IPI
PMID:21847094
Class IIb HDAC6 regulates endothelial cell migration and ang...
MODIFY
Summary: Study showing HDAC6 deacetylates cortactin affecting angiogenesis.
Reason: 'Protein binding' is uninformative. Cortactin is a known HDAC6 substrate.
Proposed replacements: actin binding
Supporting Evidence:
PMID:21847094
Class IIb HDAC6 regulates endothelial cell migration and angiogenesis by deacetylation of cortactin.
GO:0005515 protein binding
IPI
PMID:21952047
PKC alpha regulates Sendai virus-mediated interferon inducti...
KEEP AS NON CORE
Summary: Study on PKC alpha regulation of interferon induction via HDAC6.
Reason: Signaling pathway interaction, downstream effect.
Supporting Evidence:
PMID:21952047
PKC alpha regulates Sendai virus-mediated interferon induction through HDAC6 and Ξ²-catenin.
GO:0005515 protein binding
IPI
PMID:22193721
A novel GRK2/HDAC6 interaction modulates cell spreading and ...
KEEP AS NON CORE
Summary: Study showing GRK2/HDAC6 interaction modulates cell spreading and motility.
Reason: Regulatory interaction affecting cell motility.
Supporting Evidence:
PMID:22193721
A novel GRK2/HDAC6 interaction modulates cell spreading and motility.
GO:0005515 protein binding
IPI
PMID:22645275
Identification of novel ATP13A2 interactors and their role i...
KEEP AS NON CORE
Summary: Study on ATP13A2 interactors including HDAC6 in alpha-synuclein misfolding.
Reason: Interaction relevant to protein quality control pathway.
Supporting Evidence:
PMID:22645275
May 29. Identification of novel ATP13A2 interactors and their role in Ξ±-synuclein misfolding and toxicity.
GO:0005515 protein binding
IPI
PMID:23084749
Regulation of CD133 by HDAC6 promotes Ξ²-catenin signaling to...
KEEP AS NON CORE
Summary: Study on HDAC6 regulation of CD133 and beta-catenin signaling.
Reason: Cancer signaling context, downstream effect.
Supporting Evidence:
PMID:23084749
2012 Oct 19. Regulation of CD133 by HDAC6 promotes Ξ²-catenin signaling to suppress cancer cell differentiation.
GO:0005515 protein binding
IPI
PMID:24658140
The mammalian-membrane two-hybrid assay (MaMTH) for probing ...
KEEP AS NON CORE
Summary: Mammalian membrane two-hybrid assay identifying protein interactions.
Reason: High-throughput interaction data, context unclear.
Supporting Evidence:
PMID:24658140
The mammalian-membrane two-hybrid assay (MaMTH) for probing membrane-protein interactions in human cells.
GO:0005515 protein binding
IPI
PMID:29281743
HDAC6 controls innate immune and autophagy responses to TLR-...
KEEP AS NON CORE
Summary: Study on HDAC6 in innate immune and autophagy responses to Listeria infection.
Reason: Infection context, relates to autophagy function.
Supporting Evidence:
PMID:29281743
eCollection 2017 Dec.
GO:0005515 protein binding
IPI
PMID:31980649
Extensive rewiring of the EGFR network in colorectal cancer ...
KEEP AS NON CORE
Summary: Large-scale interactome study in EGFR network.
Reason: High-throughput data, not specific to core function.
Supporting Evidence:
PMID:31980649
Extensive rewiring of the EGFR network in colorectal cancer cells expressing transforming levels of KRAS(G13D).
GO:0005515 protein binding
IPI
PMID:32814053
Interactome Mapping Provides a Network of Neurodegenerative ...
KEEP AS NON CORE
Summary: Interactome mapping of neurodegenerative disease proteins.
Reason: High-throughput data related to protein aggregation.
Supporting Evidence:
PMID:32814053
Interactome Mapping Provides a Network of Neurodegenerative Disease Proteins and Uncovers Widespread Protein Aggregation in Affected Brains.
GO:0005515 protein binding
IPI
PMID:33961781
Dual proteome-scale networks reveal cell-specific remodeling...
KEEP AS NON CORE
Summary: Dual proteome-scale interactome study.
Reason: High-throughput data, not specific to core function.
Supporting Evidence:
PMID:33961781
2021 May 6. Dual proteome-scale networks reveal cell-specific remodeling of the human interactome.
GO:0000153 cytoplasmic ubiquitin ligase complex
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 has E3 ubiquitin ligase activity and can ubiquitinate substrates like MSH2.
Reason: While HDAC6 has ubiquitin ligase activity, this is not its primary function. The deacetylase activity is the core function.
GO:0004407 histone deacetylase activity
IEA
GO_REF:0000120
MARK AS OVER ANNOTATED
Summary: HDAC6 was originally named for histone deacetylase activity but primarily deacetylates non-histone cytoplasmic substrates.
Reason: UniProt explicitly notes that HDAC6 "was originally thought to be a histone deacetylase. However, subsequent work has shown that it is predominantly cytoplasmic and deacetylates a range of non-histone substrates." The more appropriate term is protein lysine deacetylase activity.
GO:0005829 cytosol
IEA
GO_REF:0000107
ACCEPT
Summary: Duplicate cytosol annotation.
Reason: Core localization, consistent with other cytosol annotations.
GO:0008017 microtubule binding
IEA
GO_REF:0000107
ACCEPT
Summary: HDAC6 associates with microtubules where it deacetylates alpha-tubulin.
Reason: Core molecular function. HDAC6 binds microtubules as part of its tubulin deacetylase function [PMID:12024216].
Supporting Evidence:
PMID:12024216
HDAC6 is localized exclusively in the cytoplasm, where it associates with microtubules
GO:0015630 microtubule cytoskeleton
IEA
GO_REF:0000120
ACCEPT
Summary: HDAC6 localizes to the microtubule cytoskeleton.
Reason: Core localization. HDAC6 associates with microtubules [PMID:12024216].
GO:0031648 protein destabilization
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 can promote protein destabilization through deacetylation and ubiquitination.
Reason: Downstream effect of HDAC6 activity on specific substrates (e.g., MSH2).
GO:0032461 positive regulation of protein oligomerization
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 can affect protein oligomerization through its deacetylase activity.
Reason: Downstream effect, context-specific (e.g., tau aggregation).
GO:0032991 protein-containing complex
IEA
GO_REF:0000107
ACCEPT
Summary: Very generic term indicating HDAC6 is part of protein complexes.
Reason: True but very general. HDAC6 participates in multiple protein complexes.
GO:0033558 protein lysine deacetylase activity
IEA
GO_REF:0000120
ACCEPT
Summary: HDAC6 is a protein lysine deacetylase that removes acetyl groups from lysine residues of non-histone substrates.
Reason: Core molecular function. This is the most accurate term for HDAC6's primary enzymatic activity.
GO:0042903 tubulin deacetylase activity
IEA
GO_REF:0000107
ACCEPT
Summary: HDAC6 deacetylates alpha-tubulin at K40.
Reason: Core molecular function [PMID:12024216].
Supporting Evidence:
PMID:12024216
HDAC6, functions as a tubulin deacetylase
GO:0043005 neuron projection
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 localizes to neuron projections (axons, dendrites).
Reason: Specialized neuronal localization.
GO:0043130 ubiquitin binding
IEA
GO_REF:0000107
ACCEPT
Summary: HDAC6 binds ubiquitin via its C-terminal ZnF-UBP domain.
Reason: Core molecular function. The ZnF-UBP domain binds polyubiquitinated proteins and is essential for HDAC6's role in aggresome formation [PMID:14675537].
Supporting Evidence:
PMID:14675537
HDAC6 has the capacity to bind both polyubiquitinated misfolded proteins and dynein motors
GO:0044297 cell body
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 localizes to the cell body.
Reason: Very general localization term.
GO:0048156 tau protein binding
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 interacts with tau protein. Tau can inhibit HDAC6 deacetylase activity [PMID:19457097].
Reason: Tau is a regulatory interactor of HDAC6 rather than a core functional binding partner.
Supporting Evidence:
PMID:19457097
tau binds to the tubulin-deacetylase, histone deacetylase 6 (HDAC6), decreasing its activity with a consequent increase in tubulin acetylation
GO:0048487 beta-tubulin binding
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 binds tubulin including beta-tubulin as part of microtubule binding.
Reason: The primary substrate is alpha-tubulin K40. Beta-tubulin binding is likely incidental to microtubule association.
GO:0051646 mitochondrion localization
IEA
GO_REF:0000120
KEEP AS NON CORE
Summary: HDAC6 can affect mitochondrial localization/transport through its effects on microtubule dynamics and axonal transport.
Reason: Downstream effect of HDAC6's role in microtubule regulation rather than direct mitochondrial localization function.
GO:0061630 ubiquitin protein ligase activity
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 has E3 ubiquitin ligase activity mediated by its histone deacetylase domain 1.
Reason: While HDAC6 does have ubiquitin ligase activity (for MSH2), this is a secondary function. The deacetylase activity is the primary enzymatic function.
GO:1905091 positive regulation of type 2 mitophagy
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HDAC6 participates in parkin-mediated mitophagy through its ubiquitin-binding function.
Reason: Specialized autophagy function related to HDAC6's broader role in aggrephagy/autophagy.
GO:0005813 centrosome
IDA
GO_REF:0000052
ACCEPT
Summary: HDAC6 localizes to the centrosome based on immunofluorescence data.
Reason: Core localization for cilium-related function [PMID:26246421].
GO:0005829 cytosol
IDA
GO_REF:0000052
ACCEPT
Summary: HDAC6 localizes to cytosol based on immunofluorescence data.
Reason: Core localization.
GO:0036064 ciliary basal body
IDA
GO_REF:0000052
ACCEPT
Summary: HDAC6 localizes to the ciliary basal body based on immunofluorescence data.
Reason: Core localization for cilium disassembly function [PMID:17604723, PMID:26246421].
GO:0034605 cellular response to heat
TAS
Reactome:R-HSA-3371511
KEEP AS NON CORE
Summary: HDAC6 participates in heat shock response through HSF1 activation pathway.
Reason: HDAC6's role in heat shock response is related to its HSP90 deacetylation function. The heat shock response is a downstream process.
GO:0060271 cilium assembly
TAS
Reactome:R-HSA-5620920
MODIFY
Summary: HDAC6 affects cilium assembly through its role in cilium disassembly via tubulin deacetylation.
Reason: HDAC6 promotes cilium DISassembly rather than assembly. The term should be cilium disassembly.
Proposed replacements: cilium disassembly
GO:0042903 tubulin deacetylase activity
IMP
PMID:19457097
Tau--an inhibitor of deacetylase HDAC6 function.
ACCEPT
Summary: Study showing tau inhibits HDAC6 tubulin deacetylase activity.
Reason: Core molecular function. Supports HDAC6's role as a tubulin deacetylase.
Supporting Evidence:
PMID:19457097
tau binds to the tubulin-deacetylase, histone deacetylase 6 (HDAC6), decreasing its activity
GO:0060632 regulation of microtubule-based movement
IDA
PMID:19228685
The protein farnesyltransferase regulates HDAC6 activity in ...
ACCEPT
Summary: HDAC6 regulates microtubule-based movement through tubulin deacetylation.
Reason: Core function directly related to tubulin deacetylation.
Supporting Evidence:
PMID:19228685
2009 Feb 18. The protein farnesyltransferase regulates HDAC6 activity in a microtubule-dependent manner.
GO:0007173 epidermal growth factor receptor signaling pathway
IMP
PMID:18356165
HDAC6 is required for epidermal growth factor-induced beta-c...
KEEP AS NON CORE
Summary: HDAC6 participates in EGFR signaling.
Reason: Downstream signaling effect, not a core function of HDAC6.
Supporting Evidence:
PMID:18356165
2008 Mar 20. HDAC6 is required for epidermal growth factor-induced beta-catenin nuclear localization.
GO:0010727 negative regulation of hydrogen peroxide metabolic process
IMP
PMID:18606987
HDAC6 is a specific deacetylase of peroxiredoxins and is inv...
KEEP AS NON CORE
Summary: HDAC6 deacetylates peroxiredoxins, affecting their H2O2 reducing activity.
Reason: Downstream effect of peroxiredoxin deacetylation rather than core function.
Supporting Evidence:
PMID:18606987
HDAC6 is a specific deacetylase of peroxiredoxins and is involved in redox regulation
GO:0019899 enzyme binding
IPI
PMID:19228685
The protein farnesyltransferase regulates HDAC6 activity in ...
KEEP AS NON CORE
Summary: HDAC6 binds enzymes including farnesyltransferase.
Reason: Generic binding term, context-specific regulatory interaction.
Supporting Evidence:
PMID:19228685
2009 Feb 18. The protein farnesyltransferase regulates HDAC6 activity in a microtubule-dependent manner.
GO:0033148 positive regulation of intracellular estrogen receptor signaling pathway
IMP
PMID:18316616
Selective inhibition of histone deacetylase 2 silences proge...
KEEP AS NON CORE
Summary: HDAC6 affects estrogen receptor signaling.
Reason: Downstream signaling effect through HSP90 deacetylation or other mechanisms.
Supporting Evidence:
PMID:18316616
Selective inhibition of histone deacetylase 2 silences progesterone receptor-mediated signaling.
GO:0033558 protein lysine deacetylase activity
IMP
PMID:18356165
HDAC6 is required for epidermal growth factor-induced beta-c...
ACCEPT
Summary: Experimental evidence for protein lysine deacetylase activity.
Reason: Core molecular function.
Supporting Evidence:
PMID:18356165
2008 Mar 20. HDAC6 is required for epidermal growth factor-induced beta-catenin nuclear localization.
GO:0033558 protein lysine deacetylase activity
TAS
PMID:28386764
Roles of tau protein in health and disease.
ACCEPT
Summary: Review article supporting protein lysine deacetylase activity.
Reason: Core molecular function.
Supporting Evidence:
PMID:28386764
Epub 2017 Apr 6. Roles of tau protein in health and disease.
GO:0036479 peroxidase inhibitor activity
IMP
PMID:18606987
HDAC6 is a specific deacetylase of peroxiredoxins and is inv...
KEEP AS NON CORE
Summary: HDAC6 deacetylates peroxiredoxins, decreasing their peroxidase activity.
Reason: Downstream effect of peroxiredoxin deacetylation. HDAC6 is not itself an inhibitor but deacetylates peroxiredoxins which modulates their activity.
Supporting Evidence:
PMID:18606987
Acetylation of Prx increases its reducing activity... Thus, HDAC6 and Prx are targets for modulating intracellular redox status
GO:0042030 ATPase inhibitor activity
IMP
PMID:15916966
HDAC6 regulates Hsp90 acetylation and chaperone-dependent ac...
KEEP AS NON CORE
Summary: HDAC6 deacetylates HSP90, affecting its ATPase-dependent chaperone activity.
Reason: Indirect effect through HSP90 deacetylation. HDAC6 modulates HSP90 function but is not itself an ATPase inhibitor.
Supporting Evidence:
PMID:15916966
HDAC6 functions as an Hsp90 deacetylase. Inactivation of HDAC6 leads to Hsp90 hyperacetylation, its dissociation from an essential cochaperone, p23, and a loss of chaperone activity
GO:0032461 positive regulation of protein oligomerization
IMP
PMID:23962722
Acetylation of the KXGS motifs in tau is a critical determin...
KEEP AS NON CORE
Summary: HDAC6 affects tau aggregation/oligomerization through deacetylation of KXGS motifs.
Reason: Context-specific effect on tau aggregation in neurodegeneration.
Supporting Evidence:
PMID:23962722
Acetylation of the KXGS motifs in tau is a critical determinant in modulation of tau aggregation and clearance.
GO:0033558 protein lysine deacetylase activity
IMP
PMID:23962722
Acetylation of the KXGS motifs in tau is a critical determin...
ACCEPT
Summary: HDAC6 deacetylates tau protein at KXGS motifs.
Reason: Core molecular function.
Supporting Evidence:
PMID:23962722
Acetylation of the KXGS motifs in tau is a critical determinant in modulation of tau aggregation and clearance.
GO:0033558 protein lysine deacetylase activity
IDA
PMID:31857589
Requirement for p62 acetylation in the aggregation of ubiqui...
ACCEPT
Summary: HDAC6 deacetylates p62/SQSTM1.
Reason: Core molecular function. Demonstrates HDAC6 deacetylates p62 which regulates autophagy.
Supporting Evidence:
PMID:31857589
Requirement for p62 acetylation in the aggregation of ubiquitylated proteins under nutrient stress.
GO:1905336 negative regulation of aggrephagy
IDA
PMID:31857589
Requirement for p62 acetylation in the aggregation of ubiqui...
MODIFY
Summary: HDAC6 deacetylation of p62 regulates aggrephagy.
Reason: HDAC6 actually promotes aggrephagy through aggresome formation. The p62 deacetylation may have complex regulatory effects but HDAC6's overall role is to promote aggrephagy.
Supporting Evidence:
PMID:31857589
Requirement for p62 acetylation in the aggregation of ubiquitylated proteins under nutrient stress.
GO:0005737 cytoplasm
IDA
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDA...
ACCEPT
Summary: Direct experimental evidence for cytoplasmic localization.
Reason: Core localization.
Supporting Evidence:
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDAC6 to trigger ciliary disassembly.
GO:0005813 centrosome
IDA
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDA...
ACCEPT
Summary: Direct experimental evidence for centrosome localization.
Reason: Core localization for cilium function.
Supporting Evidence:
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDAC6 to trigger ciliary disassembly.
GO:0036064 ciliary basal body
IDA
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDA...
ACCEPT
Summary: Direct experimental evidence for ciliary basal body localization.
Reason: Core localization for cilium disassembly function.
Supporting Evidence:
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDAC6 to trigger ciliary disassembly.
GO:0061523 cilium disassembly
IDA
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDA...
ACCEPT
Summary: HDAC6 promotes cilium disassembly via deacetylation of alpha-tubulin and cortactin.
Reason: Core biological process. HDAC6-mediated tubulin deacetylation is required for cilium disassembly [PMID:17604723, PMID:26246421].
Supporting Evidence:
PMID:17604723
phosphorylation and activation of HDAC6, a tubulin deacetylase, promoting ciliary disassembly
PMID:26246421
Deacetylation of Ξ±-tubulin and cortactin is required for HDAC6 to trigger ciliary disassembly.
GO:0045814 negative regulation of gene expression, epigenetic
IMP
PMID:24413532
Differential regulation of estrogen receptor Ξ± expression in...
KEEP AS NON CORE
Summary: HDAC6 involved in MTA1-mediated epigenetic regulation of ESR1.
Reason: Context-specific effect in breast cancer, not a core function.
Supporting Evidence:
PMID:24413532
2014 Jan 10. Differential regulation of estrogen receptor Ξ± expression in breast cancer cells by metastasis-associated protein 1.
GO:0005515 protein binding
IPI
PMID:17604723
HEF1-dependent Aurora A activation induces disassembly of th...
MODIFY
Summary: HDAC6 interacts with Aurora A and HEF1 at the ciliary basal body.
Reason: 'Protein binding' is uninformative. The specific interaction with Aurora A kinase is more informative.
Proposed replacements: phosphoprotein binding
Supporting Evidence:
PMID:17604723
HEF1-dependent Aurora A activation induces disassembly of the primary cilium.
GO:0036064 ciliary basal body
IDA
PMID:17604723
HEF1-dependent Aurora A activation induces disassembly of th...
ACCEPT
Summary: HDAC6 localizes to ciliary basal body.
Reason: Core localization for cilium function [PMID:17604723].
Supporting Evidence:
PMID:17604723
Aurora A (AurA) kinase at the basal body of cilia causes phosphorylation and activation of HDAC6
GO:0061523 cilium disassembly
IMP
PMID:17604723
HEF1-dependent Aurora A activation induces disassembly of th...
ACCEPT
Summary: HDAC6 is required for cilium disassembly.
Reason: Core biological process [PMID:17604723].
Supporting Evidence:
PMID:17604723
this pathway is both necessary and sufficient for ciliary resorption
GO:0051787 misfolded protein binding
EXP
PMID:17785525
HDAC6 controls major cell response pathways to cytotoxic acc...
ACCEPT
Summary: HDAC6 binds misfolded proteins through its ZnF-UBP domain recognizing polyubiquitin chains.
Reason: Core molecular function. Essential for HDAC6's role in aggresome formation [PMID:14675537].
Supporting Evidence:
PMID:14675537
HDAC6 has the capacity to bind both polyubiquitinated misfolded proteins and dynein motors
PMID:17785525
HDAC6 controls major cell response pathways to cytotoxic accumulation of protein aggregates.
GO:0019896 axonal transport of mitochondrion
IGI
PMID:28105056
HDAC6 Inhibitors Rescued the Defective Axonal Mitochondrial ...
KEEP AS NON CORE
Summary: HDAC6 affects axonal mitochondrial transport through effects on microtubule acetylation.
Reason: Specialized neuronal function related to microtubule regulation.
Supporting Evidence:
PMID:28105056
HDAC6 Inhibitors Rescued the Defective Axonal Mitochondrial Movement in Motor Neurons Derived from the Induced Pluripotent Stem Cells of Peripheral Neuropathy Patients with HSPB1 Mutation.
GO:0001222 transcription corepressor binding
IPI
PMID:12535528
Ligand-dependent nuclear receptor corepressor LCoR functions...
KEEP AS NON CORE
Summary: HDAC6 interacts with LCoR transcription corepressor.
Reason: Context-specific interaction in transcriptional regulation, not a core function.
Supporting Evidence:
PMID:12535528
Ligand-dependent nuclear receptor corepressor LCoR functions by histone deacetylase-dependent and -independent mechanisms.
GO:0042903 tubulin deacetylase activity
EXP
PMID:12024216
HDAC6 is a microtubule-associated deacetylase.
ACCEPT
Summary: Original discovery of HDAC6 as a tubulin deacetylase.
Reason: Core molecular function. This is the seminal paper establishing HDAC6 as the tubulin deacetylase.
Supporting Evidence:
PMID:12024216
HDAC6, functions as a tubulin deacetylase... In vitro, purified HDAC6 potently deacetylates alpha-tubulin in assembled microtubules
GO:0005515 protein binding
IPI
PMID:20308065
TPPP/p25 promotes tubulin acetylation by inhibiting histone ...
KEEP AS NON CORE
Summary: HDAC6 interacts with TPPP/p25 which inhibits its tubulin deacetylase activity.
Reason: 'Protein binding' is uninformative. TPPP is a regulatory interactor.
Supporting Evidence:
PMID:20308065
2010 Mar 22. TPPP/p25 promotes tubulin acetylation by inhibiting histone deacetylase 6.
GO:0042903 tubulin deacetylase activity
IDA
PMID:20308065
TPPP/p25 promotes tubulin acetylation by inhibiting histone ...
ACCEPT
Summary: Direct demonstration of HDAC6 tubulin deacetylase activity.
Reason: Core molecular function.
Supporting Evidence:
PMID:20308065
2010 Mar 22. TPPP/p25 promotes tubulin acetylation by inhibiting histone deacetylase 6.
GO:0090042 tubulin deacetylation
IDA
PMID:20308065
TPPP/p25 promotes tubulin acetylation by inhibiting histone ...
ACCEPT
Summary: Direct demonstration of HDAC6-mediated tubulin deacetylation.
Reason: Core biological process.
Supporting Evidence:
PMID:20308065
2010 Mar 22. TPPP/p25 promotes tubulin acetylation by inhibiting histone deacetylase 6.
GO:0090042 tubulin deacetylation
IDA
PMID:23093407
Rho-associated coiled-coil kinase (ROCK) protein controls mi...
ACCEPT
Summary: ROCK signaling pathway regulates HDAC6-mediated tubulin deacetylation.
Reason: Core biological process.
Supporting Evidence:
PMID:23093407
2012 Oct 23. Rho-associated coiled-coil kinase (ROCK) protein controls microtubule dynamics in a novel signaling pathway that regulates cell migration.
GO:0031333 negative regulation of protein-containing complex assembly
IMP
PMID:23962722
Acetylation of the KXGS motifs in tau is a critical determin...
KEEP AS NON CORE
Summary: HDAC6 affects protein complex assembly through deacetylation.
Reason: Context-specific effect, likely related to tau aggregation studies.
Supporting Evidence:
PMID:23962722
Acetylation of the KXGS motifs in tau is a critical determinant in modulation of tau aggregation and clearance.
GO:0006476 protein deacetylation
IDA
PMID:28516954
Histone deacetylase 10 structure and molecular function as a...
UNDECIDED
Summary: Note: PMID:28516954 is about HDAC10, not HDAC6. This may be an error.
Reason: Need to verify this annotation - the PMID is about HDAC10 structure and polyamine deacetylation, which may have been mis-annotated to HDAC6.
Supporting Evidence:
PMID:28516954
Histone deacetylase 10 structure and molecular function as a polyamine deacetylase.
GO:0033558 protein lysine deacetylase activity
IDA
PMID:28516954
Histone deacetylase 10 structure and molecular function as a...
UNDECIDED
Summary: Note: PMID:28516954 is about HDAC10, not HDAC6.
Reason: Need to verify - may be annotation error as this paper is about HDAC10.
Supporting Evidence:
PMID:28516954
Histone deacetylase 10 structure and molecular function as a polyamine deacetylase.
GO:0047611 acetylspermidine deacetylase activity
IDA NOT
PMID:28516954
Histone deacetylase 10 structure and molecular function as a...
ACCEPT
Summary: This is a NOT annotation. PMID:28516954 demonstrated that HDAC6 does NOT have acetylspermidine deacetylase activity - this activity is specific to HDAC10.
Reason: This is correctly a NOT annotation. The paper PMID:28516954 established that polyamine deacetylation is a function of HDAC10, not HDAC6. The negative annotation correctly reflects that HDAC6 lacks this activity.
Supporting Evidence:
PMID:28516954
Histone deacetylase 10 structure and molecular function as a polyamine deacetylase.
GO:0106047 polyamine deacetylation
IDA NOT
PMID:28516954
Histone deacetylase 10 structure and molecular function as a...
ACCEPT
Summary: This is a NOT annotation. PMID:28516954 demonstrated that HDAC6 is NOT involved in polyamine deacetylation - this activity is specific to HDAC10.
Reason: This is correctly a NOT annotation. The paper PMID:28516954 established that polyamine deacetylation is a function of HDAC10, not HDAC6.
Supporting Evidence:
PMID:28516954
Histone deacetylase 10 structure and molecular function as a polyamine deacetylase.
GO:0106048 spermidine deacetylation
IDA NOT
PMID:28516954
Histone deacetylase 10 structure and molecular function as a...
ACCEPT
Summary: This is a NOT annotation. PMID:28516954 demonstrated that HDAC6 is NOT involved in spermidine deacetylation - this activity is specific to HDAC10.
Reason: This is correctly a NOT annotation. The paper PMID:28516954 established that spermidine deacetylation is a function of HDAC10, not HDAC6.
Supporting Evidence:
PMID:28516954
Histone deacetylase 10 structure and molecular function as a polyamine deacetylase.
GO:0048156 tau protein binding
NAS
PMID:28386764
Roles of tau protein in health and disease.
KEEP AS NON CORE
Summary: Review article discussing tau-HDAC6 interaction.
Reason: Tau is a regulatory interactor rather than core functional partner.
Supporting Evidence:
PMID:28386764
Epub 2017 Apr 6. Roles of tau protein in health and disease.
GO:0000978 RNA polymerase II cis-regulatory region sequence-specific DNA binding
IDA
PMID:24413532
Differential regulation of estrogen receptor Ξ± expression in...
MARK AS OVER ANNOTATED
Summary: HDAC6 involvement in transcriptional regulation of ESR1.
Reason: HDAC6 is primarily a cytoplasmic deacetylase. Direct DNA binding is not a core function. This may reflect an indirect effect or context-specific nuclear function.
Supporting Evidence:
PMID:24413532
2014 Jan 10. Differential regulation of estrogen receptor Ξ± expression in breast cancer cells by metastasis-associated protein 1.
GO:0005737 cytoplasm
TAS
PMID:19457097
Tau--an inhibitor of deacetylase HDAC6 function.
ACCEPT
Summary: Cytoplasmic localization noted in tau-HDAC6 interaction study.
Reason: Core localization. HDAC6 is well-established as a cytoplasmic protein.
Supporting Evidence:
PMID:19457097
Epub 2009 May 7. Tau--an inhibitor of deacetylase HDAC6 function.
GO:0016235 aggresome
TAS
PMID:19457097
Tau--an inhibitor of deacetylase HDAC6 function.
ACCEPT
Summary: HDAC6 localizes to aggresomes.
Reason: Core localization. HDAC6 is a component of the aggresome [PMID:14675537].
Supporting Evidence:
PMID:14675537
HDAC6, a microtubule-associated deacetylase, is a component of the aggresome
PMID:19457097
Epub 2009 May 7. Tau--an inhibitor of deacetylase HDAC6 function.
GO:0048156 tau protein binding
ISS
PMID:19457097
Tau--an inhibitor of deacetylase HDAC6 function.
KEEP AS NON CORE
Summary: Tau binds and inhibits HDAC6.
Reason: Tau is a regulatory interactor.
Supporting Evidence:
PMID:19457097
tau binds to the tubulin-deacetylase, histone deacetylase 6 (HDAC6), decreasing its activity
GO:0048156 tau protein binding
TAS
PMID:19457097
Tau--an inhibitor of deacetylase HDAC6 function.
KEEP AS NON CORE
Summary: Tau binds HDAC6.
Reason: Duplicate - tau is a regulatory interactor.
Supporting Evidence:
PMID:19457097
Epub 2009 May 7. Tau--an inhibitor of deacetylase HDAC6 function.
GO:0005515 protein binding
IPI
PMID:25422469
Disruption of FAT10-MAD2 binding inhibits tumor progression.
KEEP AS NON CORE
Summary: HDAC6 interacts with UBD/FAT10.
Reason: UBD is a ubiquitin-like modifier; interaction related to ubiquitin binding function.
Supporting Evidence:
PMID:25422469
Disruption of FAT10-MAD2 binding inhibits tumor progression.
GO:0005515 protein binding
IPI
PMID:24687993
Fam65b is important for formation of the HDAC6-dysferlin pro...
KEEP AS NON CORE
Summary: HDAC6 interacts with FAM65B and dysferlin during myogenesis.
Reason: Context-specific interaction during myogenic differentiation.
Supporting Evidence:
PMID:24687993
Fam65b is important for formation of the HDAC6-dysferlin protein complex during myogenic cell differentiation.
GO:0005515 protein binding
IPI
PMID:27556504
FAM65B controls the proliferation of transformed and primary...
KEEP AS NON CORE
Summary: FAM65B interaction with HDAC6 in T cell proliferation.
Reason: Context-specific interaction in immune cells.
Supporting Evidence:
PMID:27556504
FAM65B controls the proliferation of transformed and primary T cells.
GO:0005737 cytoplasm
IDA
PMID:24687993
Fam65b is important for formation of the HDAC6-dysferlin pro...
ACCEPT
Summary: Cytoplasmic localization during myogenic differentiation.
Reason: Core localization.
Supporting Evidence:
PMID:24687993
Fam65b is important for formation of the HDAC6-dysferlin protein complex during myogenic cell differentiation.
GO:0016241 regulation of macroautophagy
IMP
PMID:16192271
HDAC6 and microtubules are required for autophagic degradati...
ACCEPT
Summary: HDAC6 regulates macroautophagy of aggregated proteins.
Reason: Core function. HDAC6 is required for autophagic degradation of aggregated proteins [PMID:16192271].
Supporting Evidence:
PMID:16192271
HDAC6-dependent retrograde transport on microtubules is used by cells to increase the efficiency and selectivity of autophagic degradation
GO:0061734 type 2 mitophagy
IGI
PMID:20457763
Disease-causing mutations in parkin impair mitochondrial ubi...
KEEP AS NON CORE
Summary: HDAC6 participates in parkin-mediated mitophagy.
Reason: Specialized autophagy function related to parkin pathway.
Supporting Evidence:
PMID:20457763
May 10. Disease-causing mutations in parkin impair mitochondrial ubiquitination, aggregation, and HDAC6-dependent mitophagy.
GO:0005771 multivesicular body
TAS
PMID:25548531
ATP13A2 and Alpha-synuclein: a Metal Taste in Autophagy.
KEEP AS NON CORE
Summary: HDAC6 involved in autophagy-related membrane trafficking.
Reason: Related to autophagy function but not core localization.
Supporting Evidence:
PMID:25548531
Dec 12. ATP13A2 and Alpha-synuclein: a Metal Taste in Autophagy.
GO:0010506 regulation of autophagy
TAS
PMID:25548531
ATP13A2 and Alpha-synuclein: a Metal Taste in Autophagy.
ACCEPT
Summary: HDAC6 regulates autophagy.
Reason: Core function - autophagy regulation is a key HDAC6 function.
Supporting Evidence:
PMID:25548531
Dec 12. ATP13A2 and Alpha-synuclein: a Metal Taste in Autophagy.
GO:1903146 regulation of autophagy of mitochondrion
TAS
PMID:25548531
ATP13A2 and Alpha-synuclein: a Metal Taste in Autophagy.
KEEP AS NON CORE
Summary: HDAC6 involved in mitophagy regulation.
Reason: Specialized autophagy function.
Supporting Evidence:
PMID:25548531
Dec 12. ATP13A2 and Alpha-synuclein: a Metal Taste in Autophagy.
GO:0031647 regulation of protein stability
IMP
PMID:23580651
HDAC6 regulates mutant SOD1 aggregation through two SMIR mot...
KEEP AS NON CORE
Summary: HDAC6 regulates mutant SOD1 aggregation through tubulin acetylation.
Reason: Context-specific effect in neurodegeneration models.
Supporting Evidence:
PMID:23580651
2013 Apr 11. HDAC6 regulates mutant SOD1 aggregation through two SMIR motifs and tubulin acetylation.
GO:0031625 ubiquitin protein ligase binding
IPI
PMID:21753002
Parkin interacts with Ambra1 to induce mitophagy.
KEEP AS NON CORE
Summary: HDAC6 interacts with Ambra1 and ubiquitin ligases in mitophagy.
Reason: Interaction related to autophagy pathway.
Supporting Evidence:
PMID:21753002
Parkin interacts with Ambra1 to induce mitophagy.
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: HDAC6 localizes to axons based on sequence similarity.
Reason: Specialized neuronal localization.
GO:0030425 dendrite
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: HDAC6 localizes to dendrites based on sequence similarity.
Reason: Specialized neuronal localization.
GO:0043204 perikaryon
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: HDAC6 localizes to perikaryon based on sequence similarity.
Reason: Specialized neuronal localization.
GO:0005829 cytosol
TAS
Reactome:R-HSA-5324632
ACCEPT
Summary: Cytosol localization in HSF1 activation pathway.
Reason: Core localization.
GO:0005829 cytosol
TAS
Reactome:R-HSA-5618331
ACCEPT
Summary: Cytosol localization in microtubule deacetylation pathway.
Reason: Core localization.
GO:0005829 cytosol
TAS
Reactome:R-HSA-9646348
ACCEPT
Summary: Cytosol localization in aggrephagy pathway.
Reason: Core localization.
GO:0005829 cytosol
TAS
Reactome:R-HSA-9646679
ACCEPT
Summary: Cytosol localization in aggresome formation pathway.
Reason: Core localization.
GO:0005829 cytosol
TAS
Reactome:R-HSA-9646685
ACCEPT
Summary: Cytosol localization in aggresome pathway.
Reason: Core localization.
GO:0004407 histone deacetylase activity
IMP
PMID:23322205
A novel small molecule hydroxamate preferentially inhibits H...
MODIFY
Summary: Study testing HDAC6 inhibitors.
Reason: HDAC6 is more accurately described as a protein lysine deacetylase. It primarily deacetylates non-histone substrates.
Supporting Evidence:
PMID:23322205
Jan 15. A novel small molecule hydroxamate preferentially inhibits HDAC6 activity and tumour growth.
GO:0005515 protein binding
IPI
PMID:17872950
Critical and functional regulation of CHOP (C/EBP homologous...
KEEP AS NON CORE
Summary: HDAC6 interacts with CHOP/DDIT3.
Reason: Context-specific interaction in ER stress response.
Supporting Evidence:
PMID:17872950
2007 Sep 14. Critical and functional regulation of CHOP (C/EBP homologous protein) through the N-terminal portion.
GO:0035967 cellular response to topologically incorrect protein
IMP
PMID:16192271
HDAC6 and microtubules are required for autophagic degradati...
ACCEPT
Summary: HDAC6 mediates response to misfolded proteins by facilitating aggresome formation.
Reason: Core function. HDAC6 is essential for cellular response to misfolded protein accumulation [PMID:14675537, PMID:16192271].
Supporting Evidence:
PMID:14675537
cells deficient in HDAC6 fail to clear misfolded protein aggregates from the cytoplasm, cannot form aggresomes properly, and are hypersensitive to the accumulation of misfolded proteins
PMID:16192271
2005 Sep 28. HDAC6 and microtubules are required for autophagic degradation of aggregated huntingtin.
GO:0005515 protein binding
IPI
PMID:19081074
A BBSome subunit links ciliogenesis, microtubule stability, ...
KEEP AS NON CORE
Summary: HDAC6 interacts with BBIP1, a BBSome subunit, affecting ciliogenesis.
Reason: Interaction related to cilium function.
Supporting Evidence:
PMID:19081074
A BBSome subunit links ciliogenesis, microtubule stability, and acetylation.
GO:0005634 nucleus
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: Nuclear localization based on sequence similarity.
Reason: HDAC6 is predominantly cytoplasmic but can shuttle to nucleus under specific conditions.
GO:0005829 cytosol
ISS
GO_REF:0000024
ACCEPT
Summary: Cytosol localization based on sequence similarity.
Reason: Core localization.
GO:0008017 microtubule binding
ISS
GO_REF:0000024
ACCEPT
Summary: Microtubule binding based on sequence similarity.
Reason: Core molecular function.
GO:0042903 tubulin deacetylase activity
ISS
GO_REF:0000024
ACCEPT
Summary: Tubulin deacetylase activity based on sequence similarity.
Reason: Core molecular function.
GO:0090042 tubulin deacetylation
ISS
GO_REF:0000024
ACCEPT
Summary: Tubulin deacetylation based on sequence similarity.
Reason: Core biological process.
GO:0005515 protein binding
IPI
PMID:19033385
The ubiquitin-like modifier FAT10 interacts with HDAC6 and l...
KEEP AS NON CORE
Summary: HDAC6 interacts with FAT10/UBD under proteasome inhibition.
Reason: Interaction related to ubiquitin-like modifier system.
Supporting Evidence:
PMID:19033385
Nov 25. The ubiquitin-like modifier FAT10 interacts with HDAC6 and localizes to aggresomes under proteasome inhibition.
GO:0004407 histone deacetylase activity
IDA
PMID:10220385
Three proteins define a class of human histone deacetylases ...
MODIFY
Summary: Original identification of HDAC6 as a histone deacetylase family member.
Reason: While HDAC6 was originally identified as an HDAC, subsequent work has shown it primarily deacetylates non-histone substrates. Should be protein lysine deacetylase activity.
Supporting Evidence:
PMID:10220385
Three proteins define a class of human histone deacetylases related to yeast Hda1p.
GO:0070840 dynein complex binding
IDA
PMID:14675537
The deacetylase HDAC6 regulates aggresome formation and cell...
ACCEPT
Summary: HDAC6 binds dynein motors to transport misfolded proteins to aggresomes.
Reason: Core molecular function. Dynein binding is essential for HDAC6's role in aggresome formation [PMID:14675537].
Supporting Evidence:
PMID:14675537
HDAC6 has the capacity to bind both polyubiquitinated misfolded proteins and dynein motors, thereby acting to recruit misfolded protein cargo to dynein motors for transport to aggresomes
GO:0070842 aggresome assembly
IMP
PMID:14675537
The deacetylase HDAC6 regulates aggresome formation and cell...
ACCEPT
Summary: HDAC6 is required for aggresome assembly.
Reason: Core biological process [PMID:14675537].
Supporting Evidence:
PMID:14675537
cells deficient in HDAC6 fail to clear misfolded protein aggregates from the cytoplasm, cannot form aggresomes properly
GO:0070845 polyubiquitinated misfolded protein transport
IMP
PMID:14675537
The deacetylase HDAC6 regulates aggresome formation and cell...
ACCEPT
Summary: HDAC6 mediates transport of polyubiquitinated misfolded proteins to aggresomes.
Reason: Core biological process [PMID:14675537].
Supporting Evidence:
PMID:14675537
HDAC6 has the capacity to bind both polyubiquitinated misfolded proteins and dynein motors, thereby acting to recruit misfolded protein cargo to dynein motors for transport to aggresomes
GO:0006515 protein quality control for misfolded or incompletely synthesized proteins
IMP
PMID:14675537
The deacetylase HDAC6 regulates aggresome formation and cell...
ACCEPT
Summary: HDAC6 is essential for cellular protein quality control by facilitating aggresome formation and autophagic clearance of misfolded proteins.
Reason: Core biological process [PMID:14675537].
Supporting Evidence:
PMID:14675537
These findings identify HDAC6 as a crucial player in the cellular management of misfolded protein-induced stress
GO:0016235 aggresome
IDA
PMID:14675537
The deacetylase HDAC6 regulates aggresome formation and cell...
ACCEPT
Summary: HDAC6 localizes to aggresomes.
Reason: Core localization [PMID:14675537].
Supporting Evidence:
PMID:14675537
HDAC6, a microtubule-associated deacetylase, is a component of the aggresome
GO:0031593 polyubiquitin modification-dependent protein binding
IDA
PMID:14675537
The deacetylase HDAC6 regulates aggresome formation and cell...
ACCEPT
Summary: HDAC6 binds polyubiquitinated proteins via its ZnF-UBP domain.
Reason: Core molecular function [PMID:14675537].
Supporting Evidence:
PMID:14675537
HDAC6 has the capacity to bind both polyubiquitinated misfolded proteins and dynein motors
GO:0048156 tau protein binding
IDA
PMID:18636984
Histone deacetylase 6 interacts with the microtubule-associa...
KEEP AS NON CORE
Summary: HDAC6 binds tau protein.
Reason: Tau is a regulatory interactor.
Supporting Evidence:
PMID:18636984
Epub 2008 Jul 12. Histone deacetylase 6 interacts with the microtubule-associated protein tau.
GO:0051788 response to misfolded protein
IMP
PMID:14675537
The deacetylase HDAC6 regulates aggresome formation and cell...
ACCEPT
Summary: HDAC6 mediates cellular response to misfolded proteins.
Reason: Core biological process [PMID:14675537].
Supporting Evidence:
PMID:14675537
These findings identify HDAC6 as a crucial player in the cellular management of misfolded protein-induced stress
GO:0060765 regulation of androgen receptor signaling pathway
TAS
PMID:18852123
Genistein down-regulates androgen receptor by modulating HDA...
KEEP AS NON CORE
Summary: HDAC6 affects androgen receptor signaling through HSP90.
Reason: Downstream effect of HSP90 deacetylation.
Supporting Evidence:
PMID:18852123
Genistein down-regulates androgen receptor by modulating HDAC6-Hsp90 chaperone function.
GO:0006886 intracellular protein transport
IMP
PMID:16192271
HDAC6 and microtubules are required for autophagic degradati...
ACCEPT
Summary: HDAC6 involved in transport of aggregated proteins via microtubules.
Reason: Core function - HDAC6 mediates retrograde transport of misfolded proteins to aggresomes [PMID:14675537, PMID:16192271].
Supporting Evidence:
PMID:16192271
HDAC6-dependent retrograde transport on microtubules is used by cells to increase the efficiency and selectivity of autophagic degradation
GO:0016234 inclusion body
IDA
PMID:16192271
HDAC6 and microtubules are required for autophagic degradati...
ACCEPT
Summary: HDAC6 localizes to inclusion bodies/aggresomes.
Reason: Core localization related to aggresome function.
Supporting Evidence:
PMID:16192271
2005 Sep 28. HDAC6 and microtubules are required for autophagic degradation of aggregated huntingtin.
GO:0032418 lysosome localization
IMP
PMID:16192271
HDAC6 and microtubules are required for autophagic degradati...
KEEP AS NON CORE
Summary: HDAC6 affects lysosome localization during autophagy.
Reason: Downstream effect of autophagy regulation.
Supporting Evidence:
PMID:16192271
2005 Sep 28. HDAC6 and microtubules are required for autophagic degradation of aggregated huntingtin.
GO:0070301 cellular response to hydrogen peroxide
IMP
PMID:18606987
HDAC6 is a specific deacetylase of peroxiredoxins and is inv...
KEEP AS NON CORE
Summary: HDAC6 affects cellular response to H2O2 through peroxiredoxin deacetylation.
Reason: Downstream effect of peroxiredoxin deacetylation.
Supporting Evidence:
PMID:18606987
HDAC6 is a specific deacetylase of peroxiredoxins and is involved in redox regulation.
GO:0005875 microtubule associated complex
IDA
PMID:19228685
The protein farnesyltransferase regulates HDAC6 activity in ...
ACCEPT
Summary: HDAC6 associates with microtubule complexes.
Reason: Core localization.
Supporting Evidence:
PMID:19228685
2009 Feb 18. The protein farnesyltransferase regulates HDAC6 activity in a microtubule-dependent manner.
GO:0005901 caveola
IDA
PMID:18356165
HDAC6 is required for epidermal growth factor-induced beta-c...
KEEP AS NON CORE
Summary: HDAC6 localizes to caveolae in EGFR signaling context.
Reason: Context-specific localization in EGFR signaling.
Supporting Evidence:
PMID:18356165
2008 Mar 20. HDAC6 is required for epidermal growth factor-induced beta-catenin nuclear localization.
GO:0008013 beta-catenin binding
IPI
PMID:18356165
HDAC6 is required for epidermal growth factor-induced beta-c...
KEEP AS NON CORE
Summary: HDAC6 binds beta-catenin.
Reason: Signaling pathway interaction.
Supporting Evidence:
PMID:18356165
2008 Mar 20. HDAC6 is required for epidermal growth factor-induced beta-catenin nuclear localization.
GO:0008017 microtubule binding
IDA
PMID:19228685
The protein farnesyltransferase regulates HDAC6 activity in ...
ACCEPT
Summary: Direct demonstration of HDAC6 microtubule binding.
Reason: Core molecular function.
Supporting Evidence:
PMID:19228685
2009 Feb 18. The protein farnesyltransferase regulates HDAC6 activity in a microtubule-dependent manner.
GO:0010634 positive regulation of epithelial cell migration
IMP
PMID:12024216
HDAC6 is a microtubule-associated deacetylase.
ACCEPT
Summary: HDAC6 promotes cell motility through tubulin deacetylation.
Reason: Core function - HDAC6 regulates cell motility through effects on microtubule dynamics [PMID:12024216].
Supporting Evidence:
PMID:12024216
overexpression of HDAC6 promotes chemotactic cell movement, supporting the idea that HDAC6-mediated deacetylation regulates microtubule-dependent cell motility
GO:0031252 cell leading edge
IDA
PMID:12024216
HDAC6 is a microtubule-associated deacetylase.
ACCEPT
Summary: HDAC6 localizes to cell leading edge.
Reason: Relevant to cell motility function [PMID:12024216].
Supporting Evidence:
PMID:12024216
Acetylated alpha-tubulin is most abundant in stable microtubules but is absent from dynamic cellular structures such as neuronal growth cones and the leading edges of fibroblasts
GO:0042903 tubulin deacetylase activity
IDA
PMID:19228685
The protein farnesyltransferase regulates HDAC6 activity in ...
ACCEPT
Summary: Direct demonstration of tubulin deacetylase activity.
Reason: Core molecular function.
Supporting Evidence:
PMID:19228685
2009 Feb 18. The protein farnesyltransferase regulates HDAC6 activity in a microtubule-dependent manner.
GO:0043014 alpha-tubulin binding
IDA
PMID:19228685
The protein farnesyltransferase regulates HDAC6 activity in ...
ACCEPT
Summary: HDAC6 binds alpha-tubulin, its primary substrate.
Reason: Core molecular function - alpha-tubulin is the primary substrate.
Supporting Evidence:
PMID:19228685
2009 Feb 18. The protein farnesyltransferase regulates HDAC6 activity in a microtubule-dependent manner.
GO:0043242 negative regulation of protein-containing complex disassembly
IMP
PMID:15916966
HDAC6 regulates Hsp90 acetylation and chaperone-dependent ac...
KEEP AS NON CORE
Summary: HDAC6 affects HSP90 complex stability through deacetylation.
Reason: Downstream effect of HSP90 deacetylation.
Supporting Evidence:
PMID:15916966
HDAC6 regulates Hsp90 acetylation and chaperone-dependent activation of glucocorticoid receptor.
GO:0045861 negative regulation of proteolysis
IMP
PMID:18356165
HDAC6 is required for epidermal growth factor-induced beta-c...
KEEP AS NON CORE
Summary: HDAC6 affects proteolysis in EGFR signaling context.
Reason: Context-specific effect.
Supporting Evidence:
PMID:18356165
2008 Mar 20. HDAC6 is required for epidermal growth factor-induced beta-catenin nuclear localization.
GO:0048471 perinuclear region of cytoplasm
IDA
PMID:12024216
HDAC6 is a microtubule-associated deacetylase.
ACCEPT
Summary: HDAC6 localizes to perinuclear region (MTOC/aggresome region).
Reason: Relevant to aggresome function - aggresomes form at the MTOC in the perinuclear region.
Supporting Evidence:
PMID:12024216
HDAC6 is a microtubule-associated deacetylase.
GO:0051879 Hsp90 protein binding
IDA
PMID:15916966
HDAC6 regulates Hsp90 acetylation and chaperone-dependent ac...
ACCEPT
Summary: HDAC6 binds and deacetylates HSP90.
Reason: Core molecular function - HSP90 is a major HDAC6 substrate [PMID:15916966].
Supporting Evidence:
PMID:15916966
HDAC6 functions as an Hsp90 deacetylase
GO:0005874 microtubule
IDA
PMID:12620231
The human Sir2 ortholog, SIRT2, is an NAD+-dependent tubulin...
ACCEPT
Summary: HDAC6 associates with microtubules (study on SIRT2-HDAC6 interaction).
Reason: Core localization.
Supporting Evidence:
PMID:12620231
SIRT2 colocalizes and interacts in vivo with HDAC6, another tubulin deacetylase
GO:0042903 tubulin deacetylase activity
IDA
PMID:12620231
The human Sir2 ortholog, SIRT2, is an NAD+-dependent tubulin...
ACCEPT
Summary: HDAC6 tubulin deacetylase activity (study on SIRT2-HDAC6 interaction).
Reason: Core molecular function.
Supporting Evidence:
PMID:12620231
HDAC6, another tubulin deacetylase
GO:0042826 histone deacetylase binding
IPI
PMID:12620231
The human Sir2 ortholog, SIRT2, is an NAD+-dependent tubulin...
KEEP AS NON CORE
Summary: HDAC6 interacts with SIRT2.
Reason: Interaction with another tubulin deacetylase (SIRT2) - regulatory relationship.
Supporting Evidence:
PMID:12620231
SIRT2 colocalizes and interacts in vivo with HDAC6
GO:0005737 cytoplasm
ISS
PMID:11861901
Identification of HDAC10, a novel class II human histone dea...
ACCEPT
Summary: Cytoplasmic localization by sequence similarity.
Reason: Core localization.
Supporting Evidence:
PMID:11861901
Identification of HDAC10, a novel class II human histone deacetylase containing a leucine-rich domain.
GO:0019899 enzyme binding
ISS
PMID:11861901
Identification of HDAC10, a novel class II human histone dea...
KEEP AS NON CORE
Summary: HDAC6 binds other enzymes.
Reason: Generic binding term.
Supporting Evidence:
PMID:11861901
Identification of HDAC10, a novel class II human histone deacetylase containing a leucine-rich domain.
GO:0045892 negative regulation of DNA-templated transcription
ISS
PMID:11861901
Identification of HDAC10, a novel class II human histone dea...
MARK AS OVER ANNOTATED
Summary: HDAC6 may affect transcription through deacetylase activity.
Reason: HDAC6 is predominantly cytoplasmic and deacetylates non-histone substrates. Its role in transcriptional regulation is indirect and not a core function.
Supporting Evidence:
PMID:11861901
Identification of HDAC10, a novel class II human histone deacetylase containing a leucine-rich domain.
GO:0000118 histone deacetylase complex
IDA
PMID:11948178
Cloning and functional characterization of HDAC11, a novel m...
KEEP AS NON CORE
Summary: HDAC6 interacts with HDAC11.
Reason: While HDAC6 can interact with other HDACs, it does not primarily function as part of nuclear HDAC complexes.
Supporting Evidence:
PMID:11948178
2002 Apr 10. Cloning and functional characterization of HDAC11, a novel member of the human histone deacetylase family.

Core Functions

HDAC6 deacetylates alpha-tubulin at K40, regulating microtubule stability and dynamics. This is one of the best-characterized functions of HDAC6.

Molecular Function:
tubulin deacetylase activity

HDAC6 is a Zn2+-dependent deacetylase that removes acetyl groups from lysine residues of various non-histone substrates including tubulin, HSP90, cortactin, peroxiredoxins, and other cytoplasmic proteins.

HDAC6 binds and deacetylates HSP90, regulating its chaperone activity. This affects client protein maturation including steroid hormone receptors.

Molecular Function:
Hsp90 protein binding

HDAC6 binds ubiquitin via its C-terminal ZnF-UBP domain. This is essential for recognizing polyubiquitinated misfolded proteins and transporting them to aggresomes.

Molecular Function:
ubiquitin binding

HDAC6 is essential for aggresome formation. It binds polyubiquitinated misfolded proteins via its ZnF-UBP domain and recruits dynein motors for retrograde transport to the MTOC.

Molecular Function:
dynein complex binding
Directly Involved In:

HDAC6 promotes cilium disassembly through deacetylation of alpha-tubulin and cortactin at the ciliary basal body. This is regulated by Aurora A phosphorylation.

Molecular Function:
tubulin deacetylase activity
Directly Involved In:

References

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Deep Research

Falcon

(HDAC6-deep-research-falcon.md)

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