HMGB1

UniProt ID: P09429
Organism: Homo sapiens
Review Status: COMPLETE
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Gene Description

HMGB1 is a 215-amino acid non-histone chromatin protein containing two HMG-box DNA-binding domains (A-box and B-box) and an acidic C-terminal tail. It has dual functions: (1) Nuclear - binds and bends DNA, modulates chromatin architecture, regulates transcription, and participates in DNA repair (BER, MMR, NER) and V(D)J recombination; (2) Extracellular - acts as a danger-associated molecular pattern (DAMP)/alarmin released from necrotic or activated cells, signaling through TLR4, TLR2, RAGE, and CXCR4 (via CXCL12 heterocomplex). Its activity is redox-regulated: all-thiol HMGB1 is chemotactic, disulfide HMGB1 (C23-C45 bond) induces cytokine production, and fully oxidized HMGB1 is inactive.

Existing Annotations Review

GO Term Evidence Action Reason
GO:0005634 nucleus
IBA
GO_REF:0000033
ACCEPT
Summary: HMGB1 is predominantly nuclear in basal state and shuttles between nucleus and cytoplasm. UniProt confirms nuclear localization with multiple experimental references.
Reason: Core localization for HMGB1's chromatin-associated functions including DNA binding, transcription regulation, and DNA repair. Well-supported by IDA evidence (PMID:8339930, PMID:19223331).
Supporting Evidence:
UniProt:P09429
Note=In basal state predominantly nuclear
file:human/HMGB1/HMGB1-deep-research-falcon.md
model: Edison Scientific Literature
GO:0006338 chromatin remodeling
IBA
GO_REF:0000033
ACCEPT
Summary: HMGB1 modulates chromatin structure by binding DNA, bending it, and facilitating nucleosome dynamics. It can restructure canonical nucleosomes and counteract linker histone H1.
Reason: Core function of HMGB1. The protein binds DNA with preference for non-canonical structures, enhances DNA flexibility, and can displace histone H1 from bent DNA. This represents a fundamental evolved function of the HMGB family.
Supporting Evidence:
UniProt:P09429
Can restructure the canonical nucleosome leading to relaxation of structural constraints for transcription factor-binding (By similarity)
HMGB1-deep-research-falcon.md
HMGB1 deforms nucleosomal DNA and counteracts linker histone H1 suppression of DNA accessibility without displacing H1
GO:0007165 signal transduction
IEA
GO_REF:0000120
ACCEPT
Summary: HMGB1 participates in signal transduction when released extracellularly, activating TLR4, TLR2, RAGE, and CXCR4 pathways.
Reason: Extracellular HMGB1 is a bona fide signaling molecule that activates NF-kB, MAPK/ERK, PI3K/AKT pathways through multiple receptors. This is a core extracellular function.
Supporting Evidence:
UniProt:P09429
Disulfide HMGB1 binds to transmembrane receptors, such as AGER/RAGE, TLR2, TLR4 and probably TREM1, thus activating their signal transduction pathways
GO:0050918 positive chemotaxis
IEA
GO_REF:0000108
ACCEPT
Summary: All-thiol (fully reduced) HMGB1 forms a complex with CXCL12 that signals through CXCR4 to promote chemotaxis and inflammatory cell recruitment.
Reason: Core extracellular function of the reduced HMGB1 isoform. The CXCL12-HMGB1 heterocomplex promotes CXCR4-mediated chemotaxis of monocytes and other inflammatory cells.
Supporting Evidence:
UniProt:P09429
Fully reduced HGMB1 (which subsequently gets oxidized after release) in association with CXCL12 mediates the recruitment of inflammatory cells during the initial phase of tissue injury
GO:0000793 condensed chromosome
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 associates with mitotic chromosomes, supported by IDA evidence (PMID:12925773).
Reason: HMGB1 is a chromatin-associated protein that remains bound to chromosomes during mitosis. This is consistent with its core role in chromatin architecture.
GO:0001938 positive regulation of endothelial cell proliferation
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: Extracellular HMGB1 has proangiogenic activity and can stimulate endothelial cell proliferation via RAGE signaling.
Reason: While HMGB1 does have proangiogenic effects, this is a downstream consequence of its alarmin/DAMP signaling function rather than a core evolved function. It represents a pleiotropic effect of extracellular HMGB1.
GO:0002250 adaptive immune response
IEA
GO_REF:0000043
KEEP AS NON CORE
Summary: HMGB1 participates in adaptive immunity by enhancing T cell activation and suppressing regulatory T cells.
Reason: HMGB1 modulates adaptive immunity as a downstream effect of its DAMP/alarmin signaling. This is a pleiotropic consequence rather than a core function.
GO:0002376 immune system process
IEA
GO_REF:0000043
ACCEPT
Summary: HMGB1 is involved in both innate and adaptive immune responses as an extracellular alarmin.
Reason: Extracellular HMGB1 signaling through TLR4, TLR2, and RAGE is a core function that activates immune responses. This broad term appropriately captures the immunological role.
GO:0003677 DNA binding
IEA
GO_REF:0000120
ACCEPT
Summary: HMGB1 binds DNA through its two HMG-box domains with preference for non-canonical DNA structures.
Reason: DNA binding is the fundamental molecular function of HMGB1. The HMG-box domains bind DNA and bend it, enabling chromatin remodeling and transcription factor access.
GO:0003684 damaged DNA binding
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 binds damaged DNA and participates in DNA repair pathways including BER, MMR, and NER.
Reason: Core function. HMGB1 binds cisplatin-modified DNA and other damaged DNA structures, and is a cofactor in base excision repair (PMID:17803946) and mismatch repair (PMID:15014079).
GO:0003714 transcription corepressor activity
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 can repress transcription, demonstrated for p53/p73-dependent transactivation (PMID:11748232) and class II genes via TBP interaction (PMID:8006019).
Reason: HMGB1 has documented transcription corepressor activity, shown experimentally in multiple contexts including p53-dependent transcription and MHC class II gene regulation.
GO:0005576 extracellular region
IEA
GO_REF:0000044
ACCEPT
Summary: HMGB1 is released extracellularly from necrotic cells (passively) or activated immune cells (actively) to function as a DAMP/alarmin.
Reason: Core localization for HMGB1's alarmin function. Extracellular release is essential for its signaling through TLR4, RAGE, and CXCR4.
GO:0005634 nucleus
IEA
GO_REF:0000120
ACCEPT
Summary: HMGB1 is predominantly nuclear in basal state, functioning as a chromatin-associated protein.
Reason: Core localization. Nucleus is the primary compartment for HMGB1's chromatin-related functions. Duplicate of IBA annotation but valid.
GO:0005694 chromosome
IEA
GO_REF:0000044
ACCEPT
Summary: HMGB1 associates with chromosomes as a chromatin architectural protein.
Reason: HMGB1 is a chromatin-associated protein that binds to chromosomes and modulates their structure. This is consistent with its core nuclear function.
GO:0005737 cytoplasm
IEA
GO_REF:0000120
ACCEPT
Summary: HMGB1 translocates to the cytoplasm from the nucleus, especially during autophagy stimulation and prior to secretion.
Reason: Valid localization. HMGB1 shuttles between nucleus and cytoplasm, and cytoplasmic localization is important for its secretion pathway and autophagy-related functions.
GO:0005768 endosome
IEA
GO_REF:0000044
ACCEPT
Summary: HMGB1 localizes to endosomes, involved in TLR9 activation and nucleic acid sensing.
Reason: HMGB1 is involved in endosomal translocation and activation of TLR9 in response to CpG-DNA. Endosomal localization is part of its immune sensing function.
GO:0005783 endoplasmic reticulum
IEA
GO_REF:0000044
ACCEPT
Summary: HMGB1 localizes to ER, particularly during SARS-CoV-2 infection where ORF3a promotes its translocation there.
Reason: Valid localization supported by IDA evidence (PMID:35239449). ER localization is part of HMGB1's secretory pathway and its role in ER stress responses.
GO:0005793 endoplasmic reticulum-Golgi intermediate compartment
IEA
GO_REF:0000044
ACCEPT
Summary: HMGB1 localizes to ERGIC as part of its non-classical secretory pathway.
Reason: HMGB1 is secreted via a non-classical pathway involving secretory lysosomes. ERGIC localization is consistent with this secretory mechanism.
GO:0005886 plasma membrane
IEA
GO_REF:0000044
ACCEPT
Summary: HMGB1 is found on the surface of activated platelets and can associate with cell membrane.
Reason: HMGB1 is found on the surface of activated platelets (PMID:11154118). Peripheral membrane association is documented.
GO:0006259 DNA metabolic process
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 participates in DNA metabolism through its roles in replication, repair, and recombination.
Reason: Broad term that appropriately captures HMGB1's involvement in DNA replication, repair (BER, MMR, NER), and V(D)J recombination.
GO:0006281 DNA repair
IEA
GO_REF:0000043
ACCEPT
Summary: HMGB1 is a cofactor in multiple DNA repair pathways including BER, MMR, and NER.
Reason: Core nuclear function. HMGB1 is a cofactor in mammalian base excision repair (PMID:17803946), mismatch repair (PMID:15014079), and facilitates nucleotide excision repair (PMID:19446504).
GO:0006310 DNA recombination
IEA
GO_REF:0000043
ACCEPT
Summary: HMGB1 is involved in V(D)J recombination as a cofactor of the RAG complex.
Reason: Core function. HMGB1 stimulates RAG cleavage activity and is involved in V(D)J recombination (PMID:9166431).
GO:0006914 autophagy
IEA
GO_REF:0000043
MARK AS OVER ANNOTATED
Summary: Cytoplasmic HMGB1 promotes autophagy by binding Beclin-1 and displacing BCL2, but this is a secondary function.
Reason: While HMGB1 can promote autophagy via Beclin-1 interaction (PMID:20819940), this is a secondary/pleiotropic function, not its evolved core function. The core functions are chromatin biology (nuclear) and alarmin signaling (extracellular).
GO:0006935 chemotaxis
IEA
GO_REF:0000043
ACCEPT
Summary: All-thiol HMGB1 in complex with CXCL12 promotes chemotaxis of inflammatory cells via CXCR4.
Reason: Core extracellular function. The HMGB1-CXCL12 heterocomplex signals through CXCR4 to promote chemotaxis of monocytes and other inflammatory cells (PMID:22370717).
GO:0006954 inflammatory response
IEA
GO_REF:0000043
ACCEPT
Summary: Extracellular HMGB1 is a prototypical alarmin that promotes inflammatory responses through TLR4, TLR2, and RAGE.
Reason: Core extracellular function. Disulfide HMGB1 induces cytokine release (TNF, IL-1, IL-6, IL-8) through receptor activation (PMID:12765338).
GO:0006955 immune response
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 participates in both innate and adaptive immune responses as a DAMP molecule.
Reason: Core function. HMGB1 is a danger-associated molecular pattern (DAMP) that amplifies immune responses during tissue injury.
GO:0006974 DNA damage response
IEA
GO_REF:0000043
ACCEPT
Summary: HMGB1 participates in DNA damage response as a cofactor in multiple repair pathways.
Reason: Core nuclear function. HMGB1 binds damaged DNA and participates in BER, MMR, and NER pathways.
GO:0008289 lipid binding
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 binds phosphatidylserine and phosphatidylethanolamine on cell surfaces.
Reason: HMGB1 binds phosphatidylserine on apoptotic cells and inhibits their phagocytosis (PMID:18768881). This is part of its immunomodulatory function.
GO:0010596 negative regulation of endothelial cell migration
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HMGB1 can negatively regulate endothelial cell migration through TLR4 and IRF3.
Reason: While HMGB1 can inhibit endothelial migration (PMID:23148224), this is a context-dependent pleiotropic effect rather than a core function.
GO:0032722 positive regulation of chemokine production
IEA
GO_REF:0000117
ACCEPT
Summary: Extracellular HMGB1 stimulates production of chemokines like CCL2, CCL3, CCL4, and CXCL10.
Reason: Core alarmin function. HMGB1 signaling through TLR4 and RAGE induces chemokine production as part of inflammatory response.
GO:0032732 positive regulation of interleukin-1 production
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 stimulates IL-1 production via TLR4 signaling.
Reason: Core alarmin function. HMGB1 induces IL-1 production through receptor activation (PMID:12765338).
GO:0045087 innate immune response
IEA
GO_REF:0000043
ACCEPT
Summary: HMGB1 is a key mediator of innate immune responses as a DAMP/alarmin.
Reason: Core extracellular function. HMGB1 activates innate immune cells through TLR4, TLR2, TLR9, and RAGE signaling.
GO:0045597 positive regulation of cell differentiation
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HMGB1 can promote cell differentiation including dendritic cell differentiation.
Reason: While HMGB1 promotes dendritic cell differentiation (PMID:15944249), this is a downstream pleiotropic effect of its alarmin signaling rather than a core function.
GO:0048018 receptor ligand activity
IEA
GO_REF:0000117
ACCEPT
Summary: Extracellular HMGB1 acts as a ligand for multiple receptors including TLR4, TLR2, RAGE, and CXCR4.
Reason: Core molecular function. HMGB1 is a bona fide receptor ligand that binds and activates TLR4, TLR2, RAGE, and works with CXCL12 to signal through CXCR4.
GO:0048468 cell development
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HMGB1 may influence cell development through its chromatin and signaling functions.
Reason: This is a broad term capturing downstream effects. HMGB1 influences development through its transcriptional regulatory roles, but this is not a core evolved function.
GO:0050792 regulation of viral process
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 regulates viral processes including SARS-CoV-2, influenza, dengue, and EBV infection.
Reason: HMGB1 is critical for coronavirus entry (PMID:33147444), promotes influenza replication (PMID:22696656), and facilitates dengue virus propagation (PMID:34971702).
GO:0051052 regulation of DNA metabolic process
IEA
GO_REF:0000117
ACCEPT
Summary: HMGB1 regulates DNA metabolism through its roles in repair, replication, and recombination.
Reason: Core function. HMGB1 is a DNA chaperone that regulates DNA repair, replication, and recombination.
GO:1903706 regulation of hemopoiesis
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: HMGB1 may regulate hematopoiesis through its immune signaling functions.
Reason: This is a downstream pleiotropic effect of HMGB1's alarmin signaling rather than a core evolved function.
GO:0005515 protein binding
IPI
PMID:15014079
Evidence for involvement of HMGB1 protein in human DNA misma...
MODIFY
Summary: HMGB1 interacts with MSH2 in DNA mismatch repair.
Reason: Protein binding is too vague. The interaction with MSH2 is functionally relevant to DNA repair.
Supporting Evidence:
PMID:15014079
2004 Mar 9. Evidence for involvement of HMGB1 protein in human DNA mismatch repair.
GO:0005515 protein binding
IPI
PMID:20819940
Endogenous HMGB1 regulates autophagy.
MODIFY
Summary: HMGB1 interacts with Beclin-1 in autophagy regulation.
Reason: Protein binding is too vague. The interaction with BECN1 is specific and functionally relevant.
Supporting Evidence:
PMID:20819940
Endogenous HMGB1 regulates autophagy.
GO:0005515 protein binding
IPI
PMID:23063560
HMGB1-facilitated p53 DNA binding occurs via HMG-Box/p53 tra...
MODIFY
Summary: HMGB1 interacts with p53 to facilitate p53-DNA binding.
Reason: Protein binding is too vague. Interaction with p53 is functionally important for transcription regulation.
Supporting Evidence:
PMID:23063560
2012 Oct 11. HMGB1-facilitated p53 DNA binding occurs via HMG-Box/p53 transactivation domain interaction, regulated by the acidic tail.
GO:0005515 protein binding
IPI
PMID:23303669
Chaperone-like activity of high-mobility group box 1 protein...
MODIFY
Summary: HMGB1 interacts with huntingtin (HTT) and has chaperone-like activity reducing polyQ aggregates.
Reason: Protein binding is too vague. More informative terms would capture the chaperone-like function.
Proposed replacements: unfolded protein binding
Supporting Evidence:
PMID:23303669
2013 Jan 9. Chaperone-like activity of high-mobility group box 1 protein and its role in reducing the formation of polyglutamine aggregates.
GO:0005515 protein binding
IPI
PMID:24474694
An immunogenic peptide in the A-box of HMGB1 protein reverse...
MODIFY
Summary: HMGB1 interacts with RAGE receptor.
Reason: Protein binding is too vague. RAGE binding is core to HMGB1 alarmin function.
Proposed replacements: RAGE receptor binding
Supporting Evidence:
PMID:24474694
2014 Jan 28. An immunogenic peptide in the A-box of HMGB1 protein reverses apoptosis-induced tolerance through RAGE receptor.
GO:0005515 protein binding
IPI
PMID:25416956
A proteome-scale map of the human interactome network.
ACCEPT
Summary: High-throughput interactome study identifying HMGB1 interactions.
Reason: High-throughput interactome data provides valid evidence for protein binding capacity.
Supporting Evidence:
PMID:25416956
A proteome-scale map of the human interactome network.
GO:0005515 protein binding
IPI
PMID:28514442
Architecture of the human interactome defines protein commun...
ACCEPT
Summary: High-throughput interactome mapping.
Reason: High-throughput interactome data provides valid evidence for protein binding capacity.
Supporting Evidence:
PMID:28514442
Architecture of the human interactome defines protein communities and disease networks.
GO:0005515 protein binding
IPI
PMID:29721183
Delineating the HMGB1 and HMGB2 interactome in prostate and ...
ACCEPT
Summary: HMGB1/HMGB2 interactome in prostate and ovary cells.
Reason: Interactome study provides valid evidence for protein binding.
Supporting Evidence:
PMID:29721183
eCollection 2018 Apr 10.
GO:0005515 protein binding
IPI
PMID:31694235
Characterization of HMGB1/2 Interactome in Prostate Cancer b...
ACCEPT
Summary: HMGB1/2 interactome characterization by yeast two-hybrid.
Reason: Valid experimental evidence for protein binding capacity.
Supporting Evidence:
PMID:31694235
Characterization of HMGB1/2 Interactome in Prostate Cancer by Yeast Two Hybrid Approach: Potential Pathobiological Implications.
GO:0005515 protein binding
IPI
PMID:32296183
A reference map of the human binary protein interactome.
ACCEPT
Summary: Binary protein interactome reference map.
Reason: High-throughput interactome data provides valid evidence for protein binding.
Supporting Evidence:
PMID:32296183
Apr 8. A reference map of the human binary protein interactome.
GO:0005515 protein binding
IPI
PMID:32814053
Interactome Mapping Provides a Network of Neurodegenerative ...
ACCEPT
Summary: Interactome mapping of neurodegenerative disease proteins.
Reason: Valid interactome evidence.
Supporting Evidence:
PMID:32814053
Interactome Mapping Provides a Network of Neurodegenerative Disease Proteins and Uncovers Widespread Protein Aggregation in Affected Brains.
GO:0005515 protein binding
IPI
PMID:32867128
The HMGB1-2 Ovarian Cancer Interactome. The Role of HMGB Pro...
ACCEPT
Summary: HMGB1-2 ovarian cancer interactome.
Reason: Valid interactome evidence.
Supporting Evidence:
PMID:32867128
The HMGB1-2 Ovarian Cancer Interactome.
GO:0005515 protein binding
IPI
PMID:33961781
Dual proteome-scale networks reveal cell-specific remodeling...
ACCEPT
Summary: Dual proteome-scale networks.
Reason: High-throughput interactome data provides valid evidence for protein binding.
Supporting Evidence:
PMID:33961781
2021 May 6. Dual proteome-scale networks reveal cell-specific remodeling of the human interactome.
GO:0005515 protein binding
IPI
PMID:40205054
Multimodal cell maps as a foundation for structural and func...
ACCEPT
Summary: Multimodal cell maps interactome.
Reason: High-throughput interactome data.
Supporting Evidence:
PMID:40205054
Apr 9. Multimodal cell maps as a foundation for structural and functional genomics.
GO:0005515 protein binding
IPI
PMID:9472015
High mobility group protein-1 (HMG-1) is a unique activator ...
MODIFY
Summary: HMGB1 is a unique activator of p53 through direct interaction.
Reason: Protein binding is too vague. The p53 interaction is functionally important.
Proposed replacements: p53 binding
Supporting Evidence:
PMID:9472015
High mobility group protein-1 (HMG-1) is a unique activator of p53.
GO:0001773 myeloid dendritic cell activation
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 activates dendritic cells through RAGE signaling.
Reason: Downstream effect of HMGB1's alarmin signaling. DC activation is a consequence of receptor engagement, not a core function.
GO:0001935 endothelial cell proliferation
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 has proangiogenic activity affecting endothelial cells.
Reason: Pleiotropic effect of HMGB1 signaling through RAGE. Not a core evolved function.
GO:0002270 plasmacytoid dendritic cell activation
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 activates plasmacytoid dendritic cells, particularly with CpG-DNA.
Reason: Downstream effect of HMGB1's immune signaling function.
GO:0002281 macrophage activation involved in immune response
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 activates macrophages through TLR4 signaling.
Reason: Macrophage activation is a direct and well-documented effect of HMGB1 signaling through TLR4.
GO:0002643 regulation of tolerance induction
IEA
GO_REF:0000107
ACCEPT
Summary: Oxidized HMGB1 from apoptotic cells promotes immunological tolerance.
Reason: Sulfonyl HMGB1 from apoptotic cells promotes tolerance (PMID:18631454). This is part of HMGB1's redox-regulated immunomodulatory function.
GO:0002840 regulation of T cell mediated immune response to tumor cell
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 regulates T cell responses to tumors.
Reason: Pleiotropic effect of HMGB1's immune signaling. Context-dependent and not a core function.
GO:0003690 double-stranded DNA binding
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 binds double-stranded DNA through its HMG-box domains.
Reason: Core molecular function. The HMG-box domains bind dsDNA with preference for bent or distorted structures.
GO:0003725 double-stranded RNA binding
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 can bind double-stranded RNA.
Reason: HMGB1 is proposed as a universal biosensor for nucleic acids, including RNA. HDA evidence supports RNA binding (PMID:22658674, PMID:22681889).
GO:0003727 single-stranded RNA binding
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 can bind single-stranded RNA as part of its nucleic acid sensing function.
Reason: HMGB1 binds various nucleic acids including ssRNA. HDA evidence supports RNA binding (PMID:22658674, PMID:22681889).
GO:0005125 cytokine activity
IEA
GO_REF:0000107
ACCEPT
Summary: Disulfide HMGB1 acts as a cytokine, inducing production of inflammatory mediators.
Reason: Core extracellular function. Disulfide HMGB1 has cytokine-like activity, inducing TNF, IL-1, IL-6 release from immune cells.
GO:0005615 extracellular space
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 is released into extracellular space from necrotic or activated cells.
Reason: Core localization for alarmin function. Extensively documented with IDA evidence (PMID:19841752, PMID:25595774).
GO:0005769 early endosome
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 localizes to early endosomes as part of its TLR9 activation pathway.
Reason: HMGB1 is involved in endosomal translocation and activation of TLR9. Valid localization.
GO:0006284 base-excision repair
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 is a cofactor in mammalian base excision repair.
Reason: Core nuclear function. HMGB1 is a cofactor in BER, interacting with POLB, FEN1, and APE1 (PMID:17803946).
GO:0006325 chromatin organization
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 is a chromatin architectural protein that modulates chromatin structure.
Reason: Core nuclear function. HMGB1 binds DNA, bends it, and facilitates nucleosome dynamics.
GO:0010508 positive regulation of autophagy
IEA
GO_REF:0000120
MARK AS OVER ANNOTATED
Summary: Cytoplasmic HMGB1 promotes autophagy through Beclin-1 interaction.
Reason: While HMGB1 can promote autophagy via Beclin-1 (PMID:20819940), this is a secondary/pleiotropic function, not its evolved core function.
GO:0010858 calcium-dependent protein kinase regulator activity
IEA
GO_REF:0000107
UNDECIDED
Summary: Evidence for HMGB1 regulating calcium-dependent protein kinases is limited.
Reason: Limited direct evidence for this specific activity. Requires further investigation.
GO:0030295 protein kinase activator activity
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 activates kinase cascades (MAPK, ERK, JNK) through receptor signaling.
Reason: Kinase activation is an indirect downstream effect of HMGB1 receptor signaling, not a direct molecular function.
GO:0032727 positive regulation of interferon-alpha production
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 promotes IFN-alpha production through TLR9 activation in plasmacytoid DCs.
Reason: Part of HMGB1's innate immune signaling function. HMGB1 with CpG-DNA activates TLR9-mediated interferon production.
GO:0032728 positive regulation of interferon-beta production
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 promotes IFN-beta production through innate immune signaling.
Reason: Part of HMGB1's innate immune function via TLR signaling.
GO:0032731 positive regulation of interleukin-1 beta production
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 induces IL-1beta production through TLR4 and inflammasome activation.
Reason: Core alarmin function. Disulfide HMGB1 induces IL-1beta production through TLR4 signaling and inflammasome priming.
GO:0032755 positive regulation of interleukin-6 production
IEA
GO_REF:0000120
ACCEPT
Summary: HMGB1 induces IL-6 production from immune cells.
Reason: Core alarmin function. Well-documented cytokine induction by HMGB1 (PMID:12765338, PMID:26961863).
GO:0032760 positive regulation of tumor necrosis factor production
IEA
GO_REF:0000120
ACCEPT
Summary: HMGB1 induces TNF production through TLR4 signaling.
Reason: Core alarmin function. TNF induction is a well-documented effect of HMGB1 (PMID:12765338).
GO:0034137 positive regulation of toll-like receptor 2 signaling pathway
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 activates TLR2 signaling, especially with lipoteichoic acid.
Reason: Core alarmin function. HMGB1 binds lipoteichoic acid and transfers it to CD14 for TLR2 signaling.
GO:0034145 positive regulation of toll-like receptor 4 signaling pathway
IEA
GO_REF:0000107
ACCEPT
Summary: Disulfide HMGB1 binds TLR4-MD2 and activates signaling.
Reason: Core alarmin function. TLR4 is the primary receptor for disulfide HMGB1's cytokine-inducing activity (PMID:20547845).
GO:0035767 endothelial cell chemotaxis
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 promotes endothelial cell chemotaxis as part of its proangiogenic activity.
Reason: Downstream pleiotropic effect of HMGB1's alarmin/RAGE signaling.
GO:0043005 neuron projection
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 localizes to neuron projections and promotes neuronal outgrowth via RAGE.
Reason: Neuronal localization and outgrowth promotion is a tissue-specific pleiotropic effect.
GO:0045089 positive regulation of innate immune response
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 is a key activator of innate immune responses through multiple TLRs and RAGE.
Reason: Core extracellular function. HMGB1 is a prototypical DAMP that activates innate immunity.
GO:0070374 positive regulation of ERK1 and ERK2 cascade
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 activates ERK1/2 signaling through RAGE and TLR4.
Reason: Well-documented downstream signaling of HMGB1-receptor activation.
GO:0071222 cellular response to lipopolysaccharide
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 binds LPS and enhances LPS-mediated cellular responses.
Reason: HMGB1 binds LPS and transfers it to CD14 for TLR4 signaling (PMID:18354232, PMID:21660935).
GO:0071639 positive regulation of monocyte chemotactic protein-1 production
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 induces MCP-1/CCL2 production.
Reason: Part of HMGB1's chemokine-inducing activity.
GO:0090303 positive regulation of wound healing
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 promotes wound healing through its proangiogenic and immune-modulatory effects.
Reason: Wound healing promotion is a downstream pleiotropic effect of HMGB1's alarmin signaling.
GO:1901224 positive regulation of non-canonical NF-kappaB signal transduction
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 activates NF-kappaB signaling through RAGE and TLR4.
Reason: NF-kappaB activation is a well-documented downstream effect of HMGB1 receptor signaling.
GO:1903672 positive regulation of sprouting angiogenesis
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: HMGB1 has proangiogenic activity promoting sprouting angiogenesis.
Reason: Angiogenesis promotion is a downstream pleiotropic effect of HMGB1's RAGE signaling.
GO:2000819 regulation of nucleotide-excision repair
IEA
GO_REF:0000107
ACCEPT
Summary: HMGB1 may facilitate nucleotide excision repair through interaction with XPA and XPC.
Reason: HMGB1 interacts with XPA and XPC to facilitate NER (PMID:19446504).
GO:0005654 nucleoplasm
IDA
GO_REF:0000052
ACCEPT
Summary: HMGB1 localizes to nucleoplasm as a chromatin-associated protein.
Reason: Valid localization. HMGB1 is predominantly nuclear.
GO:0140656 endodeoxyribonuclease activator activity
IDA
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
ACCEPT
Summary: HMGB1 activates FEN1 endonuclease activity in base excision repair.
Reason: Core function in DNA repair. HMGB1 stimulates FEN1 endonuclease activity as part of BER (PMID:17803946).
Supporting Evidence:
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
GO:0006302 double-strand break repair
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 participates in double-strand break repair including NHEJ and V(D)J recombination.
Reason: Core nuclear function. Supported by sequence similarity to characterized orthologs.
GO:0005515 protein binding
IPI
PMID:35239449
SARS-CoV-2 ORF3a induces RETREG1/FAM134B-dependent reticulop...
ACCEPT
Summary: HMGB1 interacts with SARS-CoV-2 ORF3A protein.
Reason: Valid experimental evidence for protein interaction with viral protein.
Supporting Evidence:
PMID:35239449
2022 Mar 3. SARS-CoV-2 ORF3a induces RETREG1/FAM134B-dependent reticulophagy and triggers sequential ER stress and inflammatory responses during SARS-CoV-2 infection.
GO:0005783 endoplasmic reticulum
IDA
PMID:35239449
SARS-CoV-2 ORF3a induces RETREG1/FAM134B-dependent reticulop...
ACCEPT
Summary: HMGB1 localizes to ER during SARS-CoV-2 infection.
Reason: Valid IDA evidence for ER localization during viral infection.
Supporting Evidence:
PMID:35239449
2022 Mar 3. SARS-CoV-2 ORF3a induces RETREG1/FAM134B-dependent reticulophagy and triggers sequential ER stress and inflammatory responses during SARS-CoV-2 infection.
GO:0046598 positive regulation of viral entry into host cell
IMP
PMID:33147444
Genome-wide CRISPR Screens Reveal Host Factors Critical for ...
ACCEPT
Summary: HMGB1 is critical for SARS-CoV-2 and other coronavirus entry.
Reason: HMGB1 regulates expression of ACE2 and CTSL, promoting coronavirus entry (PMID:33147444).
Supporting Evidence:
PMID:33147444
Oct 20. Genome-wide CRISPR Screens Reveal Host Factors Critical for SARS-CoV-2 Infection.
GO:0005515 protein binding
IPI
PMID:15379539
The long acidic tail of high mobility group box 1 (HMGB1) pr...
ACCEPT
Summary: HMGB1 interacts with various proteins in a high-throughput study.
Reason: Valid high-throughput interactome evidence.
Supporting Evidence:
PMID:15379539
The long acidic tail of high mobility group box 1 (HMGB1) protein forms an extended and flexible structure that interacts with specific residues within and between the HMG boxes.
GO:0031507 heterochromatin formation
IGI
PMID:19158276
Chromatin-specific remodeling by HMGB1 and linker histone H1...
KEEP AS NON CORE
Summary: HMGB1 may be involved in heterochromatin formation.
Reason: Chromatin-related function but not a core activity. May be secondary to general chromatin architectural role.
Supporting Evidence:
PMID:19158276
Jan 21. Chromatin-specific remodeling by HMGB1 and linker histone H1 silences proinflammatory genes during endotoxin tolerance.
GO:0000122 negative regulation of transcription by RNA polymerase II
IDA
PMID:11748232
HMGB1 and HMGB2 cell-specifically down-regulate the p53- and...
ACCEPT
Summary: HMGB1 represses p53/p73-dependent transactivation of Bax and p21 promoters.
Reason: Core transcription regulatory function. HMGB1 can repress transcription as demonstrated for p53/p73-dependent genes (PMID:11748232).
Supporting Evidence:
PMID:11748232
Dec 17. HMGB1 and HMGB2 cell-specifically down-regulate the p53- and p73-dependent sequence-specific transactivation from the human Bax gene promoter.
GO:0003714 transcription corepressor activity
IDA
PMID:11748232
HMGB1 and HMGB2 cell-specifically down-regulate the p53- and...
ACCEPT
Summary: HMGB1 has transcription corepressor activity inhibiting p53/p73 transactivation.
Reason: Valid IDA evidence. HMGB1 acts as a corepressor for p53/p73-dependent transcription (PMID:11748232).
Supporting Evidence:
PMID:11748232
Dec 17. HMGB1 and HMGB2 cell-specifically down-regulate the p53- and p73-dependent sequence-specific transactivation from the human Bax gene promoter.
GO:0061629 RNA polymerase II-specific DNA-binding transcription factor binding
IPI
PMID:19223331
HMGB1 and HMGB2 proteins up-regulate cellular expression of ...
ACCEPT
Summary: HMGB1 binds transcription factors to facilitate their DNA binding.
Reason: Core function. HMGB1 interacts with and enhances binding of various transcription factors including p53, SREBPs, and others.
Supporting Evidence:
PMID:19223331
Feb 17. HMGB1 and HMGB2 proteins up-regulate cellular expression of human topoisomerase IIalpha.
GO:0005615 extracellular space
IDA
PMID:25595774
Cutting Edge: identification of neutrophil PGLYRP1 as a liga...
ACCEPT
Summary: HMGB1 is released to extracellular space as an alarmin.
Reason: Core localization for HMGB1's DAMP function. Well-documented extracellular release.
Supporting Evidence:
PMID:25595774
2015 Jan 16. Cutting Edge: identification of neutrophil PGLYRP1 as a ligand for TREM-1.
GO:0048018 receptor ligand activity
IDA
PMID:17568691
Endogenous signals released from necrotic cells augment infl...
ACCEPT
Summary: HMGB1 acts as a ligand for TLR4, TLR2, RAGE receptors.
Reason: Core molecular function. HMGB1 is a bona fide receptor ligand for multiple immune receptors (PMID:17568691).
Supporting Evidence:
PMID:17568691
2007 May 25. Endogenous signals released from necrotic cells augment inflammatory responses to bacterial endotoxin.
GO:0006303 double-strand break repair via nonhomologous end joining
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 participates in NHEJ DNA repair.
Reason: Core nuclear function supported by sequence similarity.
GO:0010508 positive regulation of autophagy
IMP
PMID:20819940
Endogenous HMGB1 regulates autophagy.
MARK AS OVER ANNOTATED
Summary: HMGB1 promotes autophagy through Beclin-1 interaction.
Reason: While HMGB1 can promote autophagy via Beclin-1 (PMID:20819940), this is a secondary/pleiotropic function, not a core evolved function. Core functions are chromatin biology and alarmin signaling.
Supporting Evidence:
PMID:20819940
Endogenous HMGB1 regulates autophagy.
GO:0003713 transcription coactivator activity
IDA
PMID:19223331
HMGB1 and HMGB2 proteins up-regulate cellular expression of ...
ACCEPT
Summary: HMGB1 has transcription coactivator activity enhancing transcription factor binding.
Reason: Core nuclear function. HMGB1 enhances binding and activity of various transcription factors (PMID:19223331).
Supporting Evidence:
PMID:19223331
Feb 17. HMGB1 and HMGB2 proteins up-regulate cellular expression of human topoisomerase IIalpha.
GO:0005615 extracellular space
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 is released to extracellular space.
Reason: Core localization for alarmin function. Supported by sequence similarity.
GO:0005634 nucleus
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 localizes to nucleus.
Reason: Core localization. Supported by sequence similarity to characterized orthologs.
GO:0071222 cellular response to lipopolysaccharide
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 mediates cellular response to LPS.
Reason: HMGB1 binds LPS and enhances TLR4-mediated responses. Supported by ISS.
GO:0000122 negative regulation of transcription by RNA polymerase II
IMP
PMID:19158276
Chromatin-specific remodeling by HMGB1 and linker histone H1...
ACCEPT
Summary: HMGB1 represses transcription in specific contexts.
Reason: Valid IMP evidence for transcription repression function.
Supporting Evidence:
PMID:19158276
Jan 21. Chromatin-specific remodeling by HMGB1 and linker histone H1 silences proinflammatory genes during endotoxin tolerance.
GO:0000122 negative regulation of transcription by RNA polymerase II
IGI
PMID:19158276
Chromatin-specific remodeling by HMGB1 and linker histone H1...
ACCEPT
Summary: HMGB1 involved in transcription repression.
Reason: Valid IGI evidence supporting transcription regulatory function.
Supporting Evidence:
PMID:19158276
Jan 21. Chromatin-specific remodeling by HMGB1 and linker histone H1 silences proinflammatory genes during endotoxin tolerance.
GO:0000976 transcription cis-regulatory region binding
IDA
PMID:19158276
Chromatin-specific remodeling by HMGB1 and linker histone H1...
ACCEPT
Summary: HMGB1 binds cis-regulatory regions of DNA.
Reason: Core function. HMGB1 binds DNA including regulatory regions to modulate transcription.
Supporting Evidence:
PMID:19158276
Jan 21. Chromatin-specific remodeling by HMGB1 and linker histone H1 silences proinflammatory genes during endotoxin tolerance.
GO:0017053 transcription repressor complex
IDA
PMID:19158276
Chromatin-specific remodeling by HMGB1 and linker histone H1...
ACCEPT
Summary: HMGB1 is part of transcription repressor complexes.
Reason: Valid IDA evidence. HMGB1 can participate in transcription repressor complexes.
Supporting Evidence:
PMID:19158276
Jan 21. Chromatin-specific remodeling by HMGB1 and linker histone H1 silences proinflammatory genes during endotoxin tolerance.
GO:0043536 positive regulation of blood vessel endothelial cell migration
IMP
PMID:28276476
miR-193a-3p interaction with HMGB1 downregulates human endot...
KEEP AS NON CORE
Summary: HMGB1 promotes endothelial cell migration as part of proangiogenic activity.
Reason: Downstream pleiotropic effect of HMGB1's RAGE signaling.
Supporting Evidence:
PMID:28276476
miR-193a-3p interaction with HMGB1 downregulates human endothelial cell proliferation and migration.
GO:1905564 positive regulation of vascular endothelial cell proliferation
IMP
PMID:28276476
miR-193a-3p interaction with HMGB1 downregulates human endot...
KEEP AS NON CORE
Summary: HMGB1 promotes vascular endothelial cell proliferation.
Reason: Downstream pleiotropic effect of HMGB1's proangiogenic signaling through RAGE.
Supporting Evidence:
PMID:28276476
miR-193a-3p interaction with HMGB1 downregulates human endothelial cell proliferation and migration.
GO:0005178 integrin binding
IDA
PMID:20826760
HMGB1 inhibits macrophage activity in efferocytosis through ...
ACCEPT
Summary: HMGB1 binds alphav-beta3 integrin.
Reason: Valid IDA evidence. Integrin binding is part of HMGB1's extracellular signaling repertoire.
Supporting Evidence:
PMID:20826760
HMGB1 inhibits macrophage activity in efferocytosis through binding to the alphavbeta3-integrin.
GO:0035868 alphav-beta3 integrin-HMGB1 complex
IDA
PMID:20826760
HMGB1 inhibits macrophage activity in efferocytosis through ...
ACCEPT
Summary: HMGB1 forms complex with alphav-beta3 integrin.
Reason: Valid IDA evidence for this specific protein complex (PMID:20826760).
Supporting Evidence:
PMID:20826760
HMGB1 inhibits macrophage activity in efferocytosis through binding to the alphavbeta3-integrin.
GO:2000426 negative regulation of apoptotic cell clearance
IDA
PMID:20826760
HMGB1 inhibits macrophage activity in efferocytosis through ...
ACCEPT
Summary: HMGB1 inhibits phagocytosis of apoptotic cells.
Reason: HMGB1 binds phosphatidylserine on apoptotic cells and inhibits their clearance (PMID:20826760).
Supporting Evidence:
PMID:20826760
HMGB1 inhibits macrophage activity in efferocytosis through binding to the alphavbeta3-integrin.
GO:0034774 secretory granule lumen
TAS
Reactome:R-HSA-6798748
ACCEPT
Summary: HMGB1 localizes to secretory granule lumen.
Reason: Valid TAS evidence. HMGB1 is secreted via secretory lysosomes.
GO:1904813 ficolin-1-rich granule lumen
TAS
Reactome:R-HSA-6800434
ACCEPT
Summary: HMGB1 present in ficolin-1-rich granule lumen.
Reason: Valid Reactome TAS evidence for granule localization.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166072
ACCEPT
Summary: HMGB1 localizes to extracellular region in TLR signaling context.
Reason: Core localization. Reactome pathway annotation for HMGB1 in TLR signaling.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166082
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization for alarmin function. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166091
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166119
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166284
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166286
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166362
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-166363
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-2201316
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-2201322
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-2262775
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-2262777
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-2559414
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-5432825
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-5602353
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-5602383
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-5602606
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-6804099
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-6804100
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-6805981
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-937022
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-937059
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-937079
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0032755 positive regulation of interleukin-6 production
IDA
PMID:26961863
AGEs and HMGB1 Increase Inflammatory Cytokine Production fro...
ACCEPT
Summary: HMGB1 induces IL-6 production.
Reason: Core alarmin function. Well-documented cytokine induction (PMID:26961863).
Supporting Evidence:
PMID:26961863
Mar 9. AGEs and HMGB1 Increase Inflammatory Cytokine Production from Human Placental Cells, Resulting in an Enhancement of Monocyte Migration.
GO:0032757 positive regulation of interleukin-8 production
IDA
PMID:26961863
AGEs and HMGB1 Increase Inflammatory Cytokine Production fro...
ACCEPT
Summary: HMGB1 induces IL-8/CXCL8 production.
Reason: Core alarmin function. Part of cytokine-inducing activity (PMID:26961863).
Supporting Evidence:
PMID:26961863
Mar 9. AGEs and HMGB1 Increase Inflammatory Cytokine Production from Human Placental Cells, Resulting in an Enhancement of Monocyte Migration.
GO:2000343 positive regulation of chemokine (C-X-C motif) ligand 2 production
IDA
PMID:26961863
AGEs and HMGB1 Increase Inflammatory Cytokine Production fro...
ACCEPT
Summary: HMGB1 induces CXCL2 production.
Reason: Core alarmin function. Part of chemokine-inducing activity.
Supporting Evidence:
PMID:26961863
Mar 9. AGEs and HMGB1 Increase Inflammatory Cytokine Production from Human Placental Cells, Resulting in an Enhancement of Monocyte Migration.
GO:0001786 phosphatidylserine binding
IDA
PMID:18768881
High mobility group protein-1 inhibits phagocytosis of apopt...
ACCEPT
Summary: HMGB1 binds phosphatidylserine on apoptotic cells.
Reason: Valid IDA evidence. HMGB1 binds PS and inhibits apoptotic cell clearance (PMID:18768881).
Supporting Evidence:
PMID:18768881
High mobility group protein-1 inhibits phagocytosis of apoptotic neutrophils through binding to phosphatidylserine.
GO:0002840 regulation of T cell mediated immune response to tumor cell
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: HMGB1 regulates T cell responses to tumors.
Reason: Pleiotropic immune effect. Supported by ISS.
GO:0032689 negative regulation of type II interferon production
IDA
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulator...
KEEP AS NON CORE
Summary: HMGB1 can suppress IFN-gamma production.
Reason: Context-dependent immunomodulatory effect (PMID:22473704).
Supporting Evidence:
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulatory and conventional T cells.
GO:0032733 positive regulation of interleukin-10 production
IDA
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulator...
KEEP AS NON CORE
Summary: HMGB1 induces IL-10 production.
Reason: Immunomodulatory effect. IL-10 induction is context-dependent (PMID:22473704).
Supporting Evidence:
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulatory and conventional T cells.
GO:0032735 positive regulation of interleukin-12 production
IMP
PMID:15944249
Release of high mobility group box 1 by dendritic cells cont...
ACCEPT
Summary: HMGB1 induces IL-12 production from dendritic cells.
Reason: Part of HMGB1's DC activation and Th1 polarization function (PMID:15944249).
Supporting Evidence:
PMID:15944249
Release of high mobility group box 1 by dendritic cells controls T cell activation via the receptor for advanced glycation end products.
GO:0034165 positive regulation of toll-like receptor 9 signaling pathway
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 enhances TLR9 signaling.
Reason: Core alarmin function. HMGB1 facilitates TLR9 activation by CpG-DNA.
GO:0035711 T-helper 1 cell activation
IDA
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulator...
KEEP AS NON CORE
Summary: HMGB1 activates Th1 cells.
Reason: Downstream effect of HMGB1's immune signaling. Context-dependent.
Supporting Evidence:
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulatory and conventional T cells.
GO:0042104 positive regulation of activated T cell proliferation
IMP
PMID:15944249
Release of high mobility group box 1 by dendritic cells cont...
KEEP AS NON CORE
Summary: HMGB1 promotes T cell proliferation.
Reason: Downstream pleiotropic effect of HMGB1's DC activation (PMID:15944249).
Supporting Evidence:
PMID:15944249
Release of high mobility group box 1 by dendritic cells controls T cell activation via the receptor for advanced glycation end products.
GO:0043277 apoptotic cell clearance
IDA
PMID:18768881
High mobility group protein-1 inhibits phagocytosis of apopt...
ACCEPT
Summary: HMGB1 regulates apoptotic cell clearance by inhibiting phagocytosis.
Reason: Valid IDA evidence. HMGB1 binds PS on apoptotic cells and inhibits clearance (PMID:18768881).
Supporting Evidence:
PMID:18768881
High mobility group protein-1 inhibits phagocytosis of apoptotic neutrophils through binding to phosphatidylserine.
GO:0043371 negative regulation of CD4-positive, alpha-beta T cell differentiation
IDA
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulator...
KEEP AS NON CORE
Summary: HMGB1 negatively regulates CD4 T cell differentiation.
Reason: Context-dependent immunomodulatory effect (PMID:22473704).
Supporting Evidence:
PMID:22473704
HMGB1 conveys immunosuppressive characteristics on regulatory and conventional T cells.
GO:0045063 T-helper 1 cell differentiation
IMP
PMID:15944249
Release of high mobility group box 1 by dendritic cells cont...
KEEP AS NON CORE
Summary: HMGB1 promotes Th1 differentiation.
Reason: Downstream effect of DC activation (PMID:15944249).
Supporting Evidence:
PMID:15944249
Release of high mobility group box 1 by dendritic cells controls T cell activation via the receptor for advanced glycation end products.
GO:0097350 neutrophil clearance
IDA
PMID:18768881
High mobility group protein-1 inhibits phagocytosis of apopt...
ACCEPT
Summary: HMGB1 regulates neutrophil clearance.
Reason: Valid IDA evidence related to apoptotic cell clearance (PMID:18768881).
Supporting Evidence:
PMID:18768881
High mobility group protein-1 inhibits phagocytosis of apoptotic neutrophils through binding to phosphatidylserine.
GO:2001200 positive regulation of dendritic cell differentiation
IMP
PMID:15944249
Release of high mobility group box 1 by dendritic cells cont...
KEEP AS NON CORE
Summary: HMGB1 promotes dendritic cell differentiation.
Reason: Downstream pleiotropic effect of alarmin signaling (PMID:15944249).
Supporting Evidence:
PMID:15944249
Release of high mobility group box 1 by dendritic cells controls T cell activation via the receptor for advanced glycation end products.
GO:0002643 regulation of tolerance induction
IDA
PMID:18631454
Induction of immunological tolerance by apoptotic cells requ...
ACCEPT
Summary: Oxidized HMGB1 from apoptotic cells promotes immune tolerance.
Reason: Valid IDA evidence. Sulfonyl HMGB1 promotes tolerance through Cys-106 oxidation (PMID:18631454).
Supporting Evidence:
PMID:18631454
Induction of immunological tolerance by apoptotic cells requires caspase-dependent oxidation of high-mobility group box-1 protein.
GO:0007204 positive regulation of cytosolic calcium ion concentration
IDA
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged ...
ACCEPT
Summary: HMGB1-CXCL12 complex induces calcium signaling via CXCR4.
Reason: Valid IDA evidence. CXCR4 signaling involves calcium mobilization (PMID:22370717).
Supporting Evidence:
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged tissues by forming a complex with CXCL12 and signaling via CXCR4.
GO:0019958 C-X-C chemokine binding
IDA
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged ...
ACCEPT
Summary: HMGB1 binds CXCL12 to form a heterocomplex.
Reason: Core function. HMGB1-CXCL12 binding is essential for CXCR4-mediated chemotaxis (PMID:22370717).
Supporting Evidence:
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged tissues by forming a complex with CXCL12 and signaling via CXCR4.
GO:0070374 positive regulation of ERK1 and ERK2 cascade
IDA
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged ...
ACCEPT
Summary: HMGB1-CXCL12 activates ERK1/2 via CXCR4.
Reason: Valid IDA evidence. ERK activation is part of CXCR4 signaling (PMID:22370717).
Supporting Evidence:
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged tissues by forming a complex with CXCL12 and signaling via CXCR4.
GO:0090026 positive regulation of monocyte chemotaxis
IDA
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged ...
ACCEPT
Summary: HMGB1-CXCL12 promotes monocyte chemotaxis.
Reason: Core extracellular function. Well-documented in PMID:22370717.
Supporting Evidence:
PMID:22370717
HMGB1 promotes recruitment of inflammatory cells to damaged tissues by forming a complex with CXCL12 and signaling via CXCR4.
GO:0003684 damaged DNA binding
IDA
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
ACCEPT
Summary: HMGB1 binds damaged DNA in base excision repair.
Reason: Core nuclear function. HMGB1 binds damaged DNA as part of BER (PMID:17803946).
Supporting Evidence:
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
GO:0016829 lyase activity
IDA
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
UNDECIDED
Summary: HMGB1 has lyase activity in BER context.
Reason: This annotation requires careful review. HMGB1 stimulates AP lyase activity but may not itself be the lyase.
Supporting Evidence:
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
GO:0032425 positive regulation of mismatch repair
IDA
PMID:15014079
Evidence for involvement of HMGB1 protein in human DNA misma...
ACCEPT
Summary: HMGB1 positively regulates mismatch repair.
Reason: Core nuclear function. HMGB1 is involved in MMR through MSH2 interaction (PMID:15014079).
Supporting Evidence:
PMID:15014079
2004 Mar 9. Evidence for involvement of HMGB1 protein in human DNA mismatch repair.
GO:0070182 DNA polymerase binding
IDA
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
ACCEPT
Summary: HMGB1 binds DNA polymerase beta in BER.
Reason: Valid IDA evidence. HMGB1 interacts with POLB in BER (PMID:17803946).
Supporting Evidence:
PMID:17803946
HMGB1 is a cofactor in mammalian base excision repair.
GO:0002218 activation of innate immune response
IDA
PMID:24971542
HMGB1-DNA complex-induced autophagy limits AIM2 inflammasome...
ACCEPT
Summary: HMGB1 activates innate immune response via AIM2 inflammasome.
Reason: Core alarmin function. HMGB1 promotes AIM2 inflammasome activation (PMID:24971542).
Supporting Evidence:
PMID:24971542
HMGB1-DNA complex-induced autophagy limits AIM2 inflammasome activation through RAGE.
GO:0032732 positive regulation of interleukin-1 production
IDA
PMID:12765338
Structural basis for the proinflammatory cytokine activity o...
ACCEPT
Summary: HMGB1 induces IL-1 production.
Reason: Core alarmin function. Well-documented cytokine induction (PMID:12765338).
Supporting Evidence:
PMID:12765338
Structural basis for the proinflammatory cytokine activity of high mobility group box 1.
GO:0032755 positive regulation of interleukin-6 production
IDA
PMID:12765338
Structural basis for the proinflammatory cytokine activity o...
ACCEPT
Summary: HMGB1 induces IL-6 production.
Reason: Core alarmin function. Well-documented (PMID:12765338).
Supporting Evidence:
PMID:12765338
Structural basis for the proinflammatory cytokine activity of high mobility group box 1.
GO:0032760 positive regulation of tumor necrosis factor production
IDA
PMID:12765338
Structural basis for the proinflammatory cytokine activity o...
ACCEPT
Summary: HMGB1 induces TNF production.
Reason: Core alarmin function. Well-documented (PMID:12765338).
Supporting Evidence:
PMID:12765338
Structural basis for the proinflammatory cytokine activity of high mobility group box 1.
GO:0043410 positive regulation of MAPK cascade
IDA
PMID:12765338
Structural basis for the proinflammatory cytokine activity o...
ACCEPT
Summary: HMGB1 activates MAPK signaling.
Reason: Valid IDA evidence. MAPK activation through receptor signaling (PMID:12765338).
Supporting Evidence:
PMID:12765338
Structural basis for the proinflammatory cytokine activity of high mobility group box 1.
GO:0046330 positive regulation of JNK cascade
IDA
PMID:12765338
Structural basis for the proinflammatory cytokine activity o...
ACCEPT
Summary: HMGB1 activates JNK signaling.
Reason: Valid IDA evidence. JNK activation through receptor signaling (PMID:12765338).
Supporting Evidence:
PMID:12765338
Structural basis for the proinflammatory cytokine activity of high mobility group box 1.
GO:0001530 lipopolysaccharide binding
IDA
PMID:21660935
Identification of lipopolysaccharide-binding peptide regions...
ACCEPT
Summary: HMGB1 binds LPS and transfers it to CD14.
Reason: Core function. HMGB1 binds LPS and enhances TLR4 signaling (PMID:21660935).
Supporting Evidence:
PMID:21660935
Aug 4. Identification of lipopolysaccharide-binding peptide regions within HMGB1 and their effects on subclinical endotoxemia in a mouse model.
GO:0000400 four-way junction DNA binding
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binds four-way junction DNA structures.
Reason: Core function. HMGB1 preferentially binds non-canonical DNA structures including cruciform DNA.
GO:0000405 bubble DNA binding
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binds bubble DNA structures.
Reason: Core function. HMGB1 binds distorted DNA structures.
GO:0008301 DNA binding, bending
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binds and bends DNA.
Reason: Core molecular function. DNA bending is fundamental to HMGB1's chromatin function.
GO:0032392 DNA geometric change
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 induces DNA geometric changes.
Reason: Core function. HMGB1 bends DNA and alters its geometry.
GO:0097100 supercoiled DNA binding
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binds supercoiled DNA.
Reason: Core function. HMGB1 preferentially binds non-canonical DNA including supercoiled DNA.
GO:0003723 RNA binding
HDA
PMID:22658674
Insights into RNA biology from an atlas of mammalian mRNA-bi...
ACCEPT
Summary: HMGB1 binds RNA as a nucleic acid biosensor.
Reason: HMGB1 binds various nucleic acids including RNA. HDA evidence from interactome capture.
Supporting Evidence:
PMID:22658674
May 31. Insights into RNA biology from an atlas of mammalian mRNA-binding proteins.
GO:0003723 RNA binding
HDA
PMID:22681889
The mRNA-bound proteome and its global occupancy profile on ...
ACCEPT
Summary: HMGB1 binds RNA.
Reason: Valid HDA evidence from interactome studies (PMID:22681889).
Supporting Evidence:
PMID:22681889
The mRNA-bound proteome and its global occupancy profile on protein-coding transcripts.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-6798748
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-6800434
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-HSA-879411
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005576 extracellular region
TAS
Reactome:R-NUL-997411
ACCEPT
Summary: HMGB1 in extracellular region.
Reason: Core localization. Reactome TAS evidence.
GO:0005654 nucleoplasm
TAS
Reactome:R-HSA-266204
ACCEPT
Summary: HMGB1 in nucleoplasm.
Reason: Core localization. Reactome TAS evidence for V(D)J recombination.
GO:0005654 nucleoplasm
TAS
Reactome:R-HSA-6805981
ACCEPT
Summary: HMGB1 in nucleoplasm.
Reason: Core localization. Reactome TAS evidence.
GO:0006954 inflammatory response
IDA
PMID:23146691
Emodin-6-O-β-D-glucoside inhibits HMGB1-induced inflammatory...
ACCEPT
Summary: HMGB1 promotes inflammatory response.
Reason: Core alarmin function. Well-documented (PMID:23146691).
Supporting Evidence:
PMID:23146691
2012 Nov 9. Emodin-6-O-β-D-glucoside inhibits HMGB1-induced inflammatory responses in vitro and in vivo.
GO:0043537 negative regulation of blood vessel endothelial cell migration
IDA
PMID:23148224
High mobility group Box 1 inhibits human pulmonary artery en...
KEEP AS NON CORE
Summary: HMGB1 can inhibit endothelial migration via TLR4.
Reason: Context-dependent pleiotropic effect (PMID:23148224).
Supporting Evidence:
PMID:23148224
2012 Nov 12. High mobility group Box 1 inhibits human pulmonary artery endothelial cell migration via a Toll-like receptor 4- and interferon response factor 3-dependent mechanism(s).
GO:0005615 extracellular space
IDA
PMID:19841752
Linking innate and adaptive immunity: human Vgamma9Vdelta2 T...
ACCEPT
Summary: HMGB1 in extracellular space.
Reason: Core localization. IDA evidence.
Supporting Evidence:
PMID:19841752
Linking innate and adaptive immunity: human Vgamma9Vdelta2 T cells enhance CD40 expression and HMGB-1 secretion.
GO:0009986 cell surface
IDA
PMID:19841752
Linking innate and adaptive immunity: human Vgamma9Vdelta2 T...
ACCEPT
Summary: HMGB1 on cell surface.
Reason: Valid IDA evidence. HMGB1 on surface of activated cells (PMID:19841752).
Supporting Evidence:
PMID:19841752
Linking innate and adaptive immunity: human Vgamma9Vdelta2 T cells enhance CD40 expression and HMGB-1 secretion.
GO:0005515 protein binding
IPI
PMID:19505873
Complementary quantitative proteomics reveals that transcrip...
ACCEPT
Summary: HMGB1 binds proteins.
Reason: Valid IPI evidence from interactome study.
Supporting Evidence:
PMID:19505873
Epub 2009 Jun 7. Complementary quantitative proteomics reveals that transcription factor AP-4 mediates E-box-dependent complex formation for transcriptional repression of HDM2.
GO:0031175 neuron projection development
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: HMGB1 involved in neuron projection development via RAGE.
Reason: Tissue-specific pleiotropic effect through RAGE signaling.
GO:0043388 positive regulation of DNA binding
IDA
PMID:11748232
HMGB1 and HMGB2 cell-specifically down-regulate the p53- and...
ACCEPT
Summary: HMGB1 enhances DNA binding of transcription factors.
Reason: Core function. HMGB1 enhances DNA binding of p53 and other transcription factors (PMID:11748232).
Supporting Evidence:
PMID:11748232
Dec 17. HMGB1 and HMGB2 cell-specifically down-regulate the p53- and p73-dependent sequence-specific transactivation from the human Bax gene promoter.
GO:0050786 RAGE receptor binding
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binds RAGE receptor.
Reason: Core alarmin function. RAGE binding is essential for many HMGB1 extracellular effects.
GO:0001773 myeloid dendritic cell activation
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: HMGB1 activates dendritic cells.
Reason: Downstream effect of alarmin signaling. ISS evidence.
GO:0002407 dendritic cell chemotaxis
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: HMGB1 promotes dendritic cell chemotaxis.
Reason: Downstream pleiotropic effect. ISS evidence.
GO:0002437 inflammatory response to antigenic stimulus
IEP
PMID:19841752
Linking innate and adaptive immunity: human Vgamma9Vdelta2 T...
ACCEPT
Summary: HMGB1 elevated during inflammatory response to antigen.
Reason: Valid IEP evidence. HMGB1 elevated in inflammatory contexts.
Supporting Evidence:
PMID:19841752
Linking innate and adaptive immunity: human Vgamma9Vdelta2 T cells enhance CD40 expression and HMGB-1 secretion.
GO:0003684 damaged DNA binding
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binds damaged DNA.
Reason: Core function. ISS evidence supporting damaged DNA binding.
GO:0005125 cytokine activity
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 has cytokine activity.
Reason: Core extracellular function. Disulfide HMGB1 has cytokine-like activity. ISS evidence.
GO:0033151 V(D)J recombination
IDA
PMID:9166431
V(D)J recombination: modulation of RAG1 and RAG2 cleavage ac...
ACCEPT
Summary: HMGB1 is a cofactor in V(D)J recombination.
Reason: Core nuclear function. HMGB1 stimulates RAG cleavage in V(D)J recombination (PMID:9166431).
Supporting Evidence:
PMID:9166431
V(D)J recombination: modulation of RAG1 and RAG2 cleavage activity on 12/23 substrates by whole cell extract and DNA-bending proteins.
GO:0042056 chemoattractant activity
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 has chemoattractant activity.
Reason: Core extracellular function. All-thiol HMGB1 with CXCL12 is chemotactic. ISS evidence.
GO:0043065 positive regulation of apoptotic process
IDA
PMID:19800306
Effect of high mobility group box-1 protein on apoptosis of ...
KEEP AS NON CORE
Summary: HMGB1 can promote apoptosis in certain contexts.
Reason: Context-dependent effect (PMID:19800306). Not a core function.
Supporting Evidence:
PMID:19800306
Epub 2009 Oct 1. Effect of high mobility group box-1 protein on apoptosis of peritoneal macrophages.
GO:0003690 double-stranded DNA binding
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binds double-stranded DNA through its HMG-box domains A and B. This is a well-established core function.
Reason: DNA binding is a fundamental function of HMGB1. The protein binds dsDNA through its HMG-box domains (PMID:8339930). ISS transfer from ortholog is appropriate.
Supporting Evidence:
PMID:8339930
The mammalian high mobility group proteins HMG1 and HMG2 are abundant, chromatin-associated proteins
GO:0003697 single-stranded DNA binding
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 has been shown to bind single-stranded DNA in addition to dsDNA through its HMG-box domains.
Reason: HMGB1 binds various DNA structures including ssDNA. ISS transfer from ortholog data is appropriate given the conserved DNA-binding HMG-box domains.
GO:0005515 protein binding
IPI
PMID:11748232
HMGB1 and HMGB2 cell-specifically down-regulate the p53- and...
MODIFY
Summary: This study demonstrates HMGB1 physically interacts with p53 and p73 transcription factors, enhancing their DNA binding. The generic protein binding term should be replaced with a more specific term.
Reason: HMGB1 interacts with p53 and p73 transcription factors to modulate their DNA binding activity (PMID:11748232). The generic protein binding term is uninformative; a more specific term for transcription factor binding is appropriate.
Supporting Evidence:
PMID:11748232
HMGB1 physically interacts with two splicing variants of p73, alpha and beta (pull-down assay), and enhances binding of p73 to specific cognate DNA sites
GO:0005634 nucleus
IDA
PMID:19223331
HMGB1 and HMGB2 proteins up-regulate cellular expression of ...
ACCEPT
Summary: HMGB1 is a chromatin-associated nuclear protein that shuttles between nucleus and cytoplasm. Nuclear localization is well-established.
Reason: Nuclear localization is a core characteristic of HMGB1 as a chromatin-associated protein (PMID:19223331). The protein is predominantly nuclear in basal state.
Supporting Evidence:
PMID:19223331
HMGB1 is associated with chromosomes in mitosis and due to its extreme mobility in the cell the protein is continuously exchanged between nucleus and cytoplasm
GO:0006265 DNA topological change
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 binding causes DNA bending and topological changes. The protein can promote DNA circularization and alter DNA topology.
Reason: HMGB1 induces DNA topological changes through its DNA-bending activity (PMID:8339930). This is a core biochemical function demonstrated by circularization assays.
Supporting Evidence:
PMID:8339930
HMG1 and HMG2 can bend DNA extremely efficiently, forming circles as small as 66 bp
GO:0006310 DNA recombination
ISS
GO_REF:0000024
ACCEPT
Summary: HMGB1 participates in DNA recombination including V(D)J recombination by facilitating DNA bending and promoting assembly of nucleoprotein complexes.
Reason: HMGB1 promotes DNA recombination by facilitating DNA flexibility and nucleoprotein complex assembly (PMID:8339930). This is a core nuclear function.
Supporting Evidence:
PMID:8339930
these proteins can substitute for the prokaryotic DNA-bending protein HU in promoting the assembly of the Hin invertasome, an intermediate structure in Hin-mediated site-specific DNA inversion
GO:0008301 DNA binding, bending
IMP
PMID:19223331
HMGB1 and HMGB2 proteins up-regulate cellular expression of ...
ACCEPT
Summary: HMGB1 DNA bending is a core function. The study showed that HMGB1, but not a mutant incapable of DNA bending, activates the topo IIalpha promoter.
Reason: DNA bending is a fundamental function of HMGB1 demonstrated by IMP evidence. The study shows DNA bending is required for HMGB1 to activate topo IIalpha promoter (PMID:19223331).
Supporting Evidence:
PMID:19223331
HMGB1, but not a mutant of HMGB1 incapable of DNA bending, up-regulates the activity of the topo IIalpha promoter in human cells
GO:0043388 positive regulation of DNA binding
IDA
PMID:19223331
HMGB1 and HMGB2 proteins up-regulate cellular expression of ...
ACCEPT
Summary: HMGB1 enhances DNA binding of transcription factors like NF-Y and p53/p73 family members by modulating DNA structure.
Reason: HMGB1 positively regulates DNA binding by modulating transcription factor NF-Y binding to promoters (PMID:19223331). This is a core function related to its transcriptional coregulator role.
Supporting Evidence:
PMID:19223331
Our experiments suggest a mechanism of up-regulation of cellular expression of topo IIalpha by HMGB1/2 in pRb-negative cells by modulation of binding of transcription factor NF-Y to the topo IIalpha promoter
GO:0045944 positive regulation of transcription by RNA polymerase II
IDA
PMID:19223331
HMGB1 and HMGB2 proteins up-regulate cellular expression of ...
ACCEPT
Summary: HMGB1 upregulates topo IIalpha promoter activity through luciferase reporter assays in pRb-negative cells.
Reason: HMGB1 positively regulates transcription by RNA pol II as demonstrated by luciferase reporter assays showing upregulation of topo IIalpha promoter (PMID:19223331). This is a core transcriptional coregulator function.
Supporting Evidence:
PMID:19223331
Using luciferase gene reporter assay we have demonstrated that HMGB1, but not a mutant of HMGB1 incapable of DNA bending, up-regulated the activity of human topo IIalpha promoter in human cells that lack functional retinoblastoma protein pRb
GO:0140297 DNA-binding transcription factor binding
IPI
PMID:19223331
HMGB1 and HMGB2 proteins up-regulate cellular expression of ...
ACCEPT
Summary: HMGB1 interacts with transcription factors including NF-Y to modulate their DNA binding activity and transcriptional output.
Reason: HMGB1 interacts with and modulates the activity of DNA-binding transcription factors like NF-Y (PMID:19223331) and p53/p73 family members. This is a specific and accurate molecular function term.
Supporting Evidence:
PMID:19223331
HMGB1 also interacts weakly with a number of proteins, including transcriptional factors, site-specific recombination and DNA repair proteins
GO:0005634 nucleus
IDA
PMID:8339930
The nonspecific DNA-binding and -bending proteins HMG1 and H...
ACCEPT
Summary: HMGB1 is an abundant chromatin-associated nuclear protein. Nuclear localization is fundamental to its function.
Reason: Nuclear localization is a core characteristic of HMGB1 as an abundant chromatin-associated protein (PMID:8339930). This is well-established and fundamental to its biological role.
Supporting Evidence:
PMID:8339930
The mammalian high mobility group proteins HMG1 and HMG2 are abundant, chromatin-associated proteins
GO:0000793 condensed chromosome
IDA
PMID:12925773
Association of chromatin proteins high mobility group box (H...
ACCEPT
Summary: HMGB1 associates with condensed chromosomes during mitosis. Live cell imaging shows the protein exchanges rapidly between free and chromosome-bound forms.
Reason: HMGB1 associates with condensed chromatin during mitosis as shown by fluorescent protein tagging in live cells (PMID:12925773). This is a core function related to its chromatin-binding role.
Supporting Evidence:
PMID:12925773
HMGB1 and 2 were shown to be present under two forms in mitotic cells, i.e., free and associated with the condensed chromatin, which rapidly exchange
GO:0005515 protein binding
IPI
PMID:8006019
The high mobility group protein HMG1 can reversibly inhibit ...
MODIFY
Summary: This study demonstrates HMGB1 physically interacts with TBP (TATA-binding protein) to inhibit preinitiation complex assembly. The generic term should be replaced with a more specific binding term.
Reason: HMGB1 interacts with TBP to form an HMG1.TBP.promoter complex that blocks TFIIB binding (PMID:8006019). The generic protein binding term is uninformative; a more specific term for transcription machinery component binding is appropriate.
Supporting Evidence:
PMID:8006019
purified mammalian HMG1, as well as recombinant human HMG1, can interact with TATA-binding protein (TBP) in the presence of a TATA box-containing oligonucleotide to form a specific HMG1.TBP.promoter complex
GO:0017055 negative regulation of RNA polymerase II transcription preinitiation complex assembly
IDA
PMID:8006019
The high mobility group protein HMG1 can reversibly inhibit ...
ACCEPT
Summary: HMGB1 interacts with TBP to form a complex that prevents TFIIB binding and blocks preinitiation complex formation. In vitro, HMGB1 inhibits transcription by RNA pol II over 30-fold.
Reason: HMGB1 inhibits preinitiation complex assembly by binding TBP and blocking TFIIB recruitment (PMID:8006019). This is a well-characterized transcriptional regulatory function with direct assay evidence.
Supporting Evidence:
PMID:8006019
This complex prevents TFIIB binding to TBP and consequently blocks formation of the preinitiation complex

Core Functions

HMGB1 binds and bends DNA through its two HMG-box domains (A and B). DNA bending is essential for its function as demonstrated by mutant studies showing that HMGB1 incapable of DNA bending fails to activate target promoters (PMID:19223331). The protein can bend DNA to form circles as small as 66 bp (PMID:8339930).

Molecular Function:
DNA binding, bending
Directly Involved In:
Cellular Locations:

HMGB1 acts as a transcriptional coregulator by binding transcription factors (p53, p73, NF-Y, TBP) and modulating their DNA binding activity. It can both positively and negatively regulate transcription depending on cellular context (PMID:8006019, PMID:19223331, PMID:11748232).

Extracellular HMGB1 acts as a DAMP/alarmin released from necrotic or activated cells, signaling through TLR4, TLR2, RAGE, and CXCR4 (via CXCL12 heterocomplex) to promote inflammation and chemotaxis. The all-thiol redox form is chemotactic, the disulfide form induces cytokine production, and the fully oxidized form is inactive.

Molecular Function:
cytokine activity
Directly Involved In:
Cellular Locations:

References

Manual transfer of experimentally-verified manual GO annotation data to orthologs by curator judgment of sequence similarity
Annotation inferences using phylogenetic trees
Gene Ontology annotation based on UniProtKB/Swiss-Prot keyword mapping
Gene Ontology annotation based on UniProtKB/Swiss-Prot Subcellular Location vocabulary mapping, accompanied by conservative changes to GO terms applied by UniProt
Gene Ontology annotation based on curation of immunofluorescence data
Automatic transfer of experimentally verified manual GO annotation data to orthologs using Ensembl Compara
Automatic assignment of GO terms using logical inference, based on on inter-ontology links
Electronic Gene Ontology annotations created by ARBA machine learning models
Combined Automated Annotation using Multiple IEA Methods
HMGB1 and HMGB2 cell-specifically down-regulate the p53- and p73-dependent sequence-specific transactivation from the human Bax gene promoter.
Structural basis for the proinflammatory cytokine activity of high mobility group box 1.
Association of chromatin proteins high mobility group box (HMGB) 1 and HMGB2 with mitotic chromosomes.
Evidence for involvement of HMGB1 protein in human DNA mismatch repair.
The long acidic tail of high mobility group box 1 (HMGB1) protein forms an extended and flexible structure that interacts with specific residues within and between the HMG boxes.
Release of high mobility group box 1 by dendritic cells controls T cell activation via the receptor for advanced glycation end products.
Endogenous signals released from necrotic cells augment inflammatory responses to bacterial endotoxin.
HMGB1 is a cofactor in mammalian base excision repair.
Induction of immunological tolerance by apoptotic cells requires caspase-dependent oxidation of high-mobility group box-1 protein.
High mobility group protein-1 inhibits phagocytosis of apoptotic neutrophils through binding to phosphatidylserine.
Chromatin-specific remodeling by HMGB1 and linker histone H1 silences proinflammatory genes during endotoxin tolerance.
HMGB1 and HMGB2 proteins up-regulate cellular expression of human topoisomerase IIalpha.
Complementary quantitative proteomics reveals that transcription factor AP-4 mediates E-box-dependent complex formation for transcriptional repression of HDM2.
Effect of high mobility group box-1 protein on apoptosis of peritoneal macrophages.
Linking innate and adaptive immunity: human Vgamma9Vdelta2 T cells enhance CD40 expression and HMGB-1 secretion.
Endogenous HMGB1 regulates autophagy.
HMGB1 inhibits macrophage activity in efferocytosis through binding to the alphavbeta3-integrin.
Identification of lipopolysaccharide-binding peptide regions within HMGB1 and their effects on subclinical endotoxemia in a mouse model.
HMGB1 promotes recruitment of inflammatory cells to damaged tissues by forming a complex with CXCL12 and signaling via CXCR4.
HMGB1 conveys immunosuppressive characteristics on regulatory and conventional T cells.
Insights into RNA biology from an atlas of mammalian mRNA-binding proteins.
The mRNA-bound proteome and its global occupancy profile on protein-coding transcripts.
HMGB1-facilitated p53 DNA binding occurs via HMG-Box/p53 transactivation domain interaction, regulated by the acidic tail.
Emodin-6-O-β-D-glucoside inhibits HMGB1-induced inflammatory responses in vitro and in vivo.
High mobility group Box 1 inhibits human pulmonary artery endothelial cell migration via a Toll-like receptor 4- and interferon response factor 3-dependent mechanism(s).
Chaperone-like activity of high-mobility group box 1 protein and its role in reducing the formation of polyglutamine aggregates.
An immunogenic peptide in the A-box of HMGB1 protein reverses apoptosis-induced tolerance through RAGE receptor.
HMGB1-DNA complex-induced autophagy limits AIM2 inflammasome activation through RAGE.
A proteome-scale map of the human interactome network.
Cutting Edge: identification of neutrophil PGLYRP1 as a ligand for TREM-1.
AGEs and HMGB1 Increase Inflammatory Cytokine Production from Human Placental Cells, Resulting in an Enhancement of Monocyte Migration.
miR-193a-3p interaction with HMGB1 downregulates human endothelial cell proliferation and migration.
Architecture of the human interactome defines protein communities and disease networks.
Delineating the HMGB1 and HMGB2 interactome in prostate and ovary epithelial cells and its relationship with cancer.
Characterization of HMGB1/2 Interactome in Prostate Cancer by Yeast Two Hybrid Approach: Potential Pathobiological Implications.
A reference map of the human binary protein interactome.
Interactome Mapping Provides a Network of Neurodegenerative Disease Proteins and Uncovers Widespread Protein Aggregation in Affected Brains.
The HMGB1-2 Ovarian Cancer Interactome. The Role of HMGB Proteins and Their Interacting Partners MIEN1 and NOP53 in Ovary Cancer and Drug-Response.
Genome-wide CRISPR Screens Reveal Host Factors Critical for SARS-CoV-2 Infection.
Dual proteome-scale networks reveal cell-specific remodeling of the human interactome.
SARS-CoV-2 ORF3a induces RETREG1/FAM134B-dependent reticulophagy and triggers sequential ER stress and inflammatory responses during SARS-CoV-2 infection.
Multimodal cell maps as a foundation for structural and functional genomics.
The high mobility group protein HMG1 can reversibly inhibit class II gene transcription by interaction with the TATA-binding protein.
The nonspecific DNA-binding and -bending proteins HMG1 and HMG2 promote the assembly of complex nucleoprotein structures.
V(D)J recombination: modulation of RAG1 and RAG2 cleavage activity on 12/23 substrates by whole cell extract and DNA-bending proteins.
High mobility group protein-1 (HMG-1) is a unique activator of p53.
Reactome:R-HSA-166072
MyD88 forms a complex with TIRAP:activated TLR2/4
Reactome:R-HSA-166082
IRAK4 binds to the activated TLR receptor:TIRAP:MyD88 complex
Reactome:R-HSA-166091
IRAK1 or IRAK2 binds to the activated IRAK4 :activated TLR:MyD88:TIRAP complex
Reactome:R-HSA-166119
First phosphorylation of IRAK1 by IRAK4 bound to activated TLR:MyD88:Mal
Reactome:R-HSA-166284
Second phosphorylation of IRAK1 by IRAK4 bound to activated TLR:MyD88:TIRAP
Reactome:R-HSA-166286
Multiple IRAK1 autophosphorylation steps
Reactome:R-HSA-166362
Dissociation of hp-IRAK1:TRAF6 from the activated TLR:oligo-Myd88:TIRAP:p-IRAK4 complex
Reactome:R-HSA-166363
TRAF6 binds to hp- IRAK1
Reactome:R-HSA-2201316
Activated TLR2/4 interacts with MAL (TIRAP)
Reactome:R-HSA-2201322
TIRAP is phosphorylated by BTK
Reactome:R-HSA-2262775
Dissociation of p-IRAK2:TRAF6 from the activated TLR:oligo-Myd88:TIRAP:p-IRAK4 complex
Reactome:R-HSA-2262777
TRAF6 binds to p-IRAK2
Reactome:R-HSA-2559414
Activated TLR2/4:TIRAP interacts with BTK
Reactome:R-HSA-266204
Association of HMGB1/HMGB2 with chromatin
Reactome:R-HSA-5432825
HMGB1 binds TLR4:LY96
Reactome:R-HSA-5602353
Defective IRAK4 does not bind MyD88:MAL:BTK:activated TLR2/4
Reactome:R-HSA-5602383
Defective MyD88 does not oligomerize within the activated TLR2/4 complex
Reactome:R-HSA-5602606
Defective MyD88 does not bind MAL(TIRAP):TLR2/4
Reactome:R-HSA-6798748
Exocytosis of secretory granule lumen proteins
Reactome:R-HSA-6800434
Exocytosis of ficolin-rich granule lumen proteins
Reactome:R-HSA-6804099
HMGB1 binds LTP
Reactome:R-HSA-6804100
HMGB1 binds LPS
Reactome:R-HSA-6805981
HMGB1 release from cells
Reactome:R-HSA-879411
Advanced glycosylation end product-specific receptor (AGER/RAGE) is a multiligand receptor
Reactome:R-HSA-937022
IRAK4 autophosphorylation in the complex with activated TLR:MyD88:TIRAP
Reactome:R-HSA-937059
Phosphorylation of IRAK2 bound to the activated IRAK4:MyD88 oligomer:TIRAP:activated TLR complex
Reactome:R-HSA-937079
MyD88 oligomerization within the complex of activated TLR:TIRAP:MyD88
Reactome:R-NUL-997411
AGER binds rat ERK1/2
file:human/HMGB1/HMGB1-deep-research-falcon.md
Deep research report on HMGB1

📚 Additional Documentation

Deep Research Falcon

(HMGB1-deep-research-falcon.md)

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organism: human
gene_id: HMGB1
gene_symbol: HMGB1
uniprot_accession: P09429
protein_description: 'RecName: Full=High mobility group protein B1; AltName: Full=High
mobility group protein 1; Short=HMG-1;'
gene_info: Name=HMGB1 {ECO:0000312|HGNC:HGNC:4983}; Synonyms=HMG1;
organism_full: Homo sapiens (Human).
protein_family: Belongs to the HMGB family. .
protein_domains: HMG_box_dom. (IPR009071); HMG_box_dom_sf. (IPR036910); HMG_boxA_CS.
(IPR017967); HMGB. (IPR050342); HMG_box (PF00505)
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Question

Gene Research for Functional Annotation

⚠️ CRITICAL: Gene/Protein Identification Context

BEFORE YOU BEGIN RESEARCH: You MUST verify you are researching the CORRECT gene/protein. Gene symbols can be ambiguous, especially for less well-characterized genes from non-model organisms.

Target Gene/Protein Identity (from UniProt):

  • UniProt Accession: P09429
  • Protein Description: RecName: Full=High mobility group protein B1; AltName: Full=High mobility group protein 1; Short=HMG-1;
  • Gene Information: Name=HMGB1 {ECO:0000312|HGNC:HGNC:4983}; Synonyms=HMG1;
  • Organism (full): Homo sapiens (Human).
  • Protein Family: Belongs to the HMGB family. .
  • Key Domains: HMG_box_dom. (IPR009071); HMG_box_dom_sf. (IPR036910); HMG_boxA_CS. (IPR017967); HMGB. (IPR050342); HMG_box (PF00505)

MANDATORY VERIFICATION STEPS:

  1. Check if the gene symbol "HMGB1" matches the protein description above
  2. Verify the organism is correct: Homo sapiens (Human).
  3. Check if protein family/domains align with what you find in literature
  4. If you find literature for a DIFFERENT gene with the same or similar symbol, STOP

If Gene Symbol is Ambiguous or You Cannot Find Relevant Literature:

DO NOT PROCEED WITH RESEARCH ON A DIFFERENT GENE. Instead:
- State clearly: "The gene symbol 'HMGB1' is ambiguous or literature is limited for this specific protein"
- Explain what you found (e.g., "Found extensive literature on a different gene with the same symbol in a different organism")
- Describe the protein based ONLY on the UniProt information provided above
- Suggest that the protein function can be inferred from domain/family information

Research Target:

Please provide a comprehensive research report on the gene HMGB1 (gene ID: HMGB1, UniProt: P09429) in human.

The research report should be a detailed narrative explaining the function, biological processes, and localization of the gene product. Citations should be given for all claims.

You should prioritize authoritative reviews and primary scientific literature when conducting research. You can supplement
this with annotations you find in gene/protein databases, but these can be outdated or inaccurate.

We are specifically interested in the primary function of the gene - for enzymes, what reaction is catalyzed, and what is the substrate specificity? For transporters, what is the substrate? For structural proteins or adapters, what is the broader structural role? For signaling molecules, what is the role in the pathway.

We are interested in where in or outside the cell the gene product carries out its function.

We are also interested in the signaling or biochemical pathways in which the gene functions. We are less interested in broad pleiotropic effects, except where these elucidate the precise role.

Include evidence where possible. We are interested in both experimental evidence as well as inference from structure, evolution, or bioinformatic analysis. Precise studies should be prioritized over high-throughput, where available.

Output

Question: You are an expert researcher providing comprehensive, well-cited information.

Provide detailed information focusing on:
1. Key concepts and definitions with current understanding
2. Recent developments and latest research (prioritize 2023-2024 sources)
3. Current applications and real-world implementations
4. Expert opinions and analysis from authoritative sources
5. Relevant statistics and data from recent studies

Format as a comprehensive research report with proper citations. Include URLs and publication dates where available.
Always prioritize recent, authoritative sources and provide specific citations for all major claims.

Gene Research for Functional Annotation

⚠️ CRITICAL: Gene/Protein Identification Context

BEFORE YOU BEGIN RESEARCH: You MUST verify you are researching the CORRECT gene/protein. Gene symbols can be ambiguous, especially for less well-characterized genes from non-model organisms.

Target Gene/Protein Identity (from UniProt):

  • UniProt Accession: P09429
  • Protein Description: RecName: Full=High mobility group protein B1; AltName: Full=High mobility group protein 1; Short=HMG-1;
  • Gene Information: Name=HMGB1 {ECO:0000312|HGNC:HGNC:4983}; Synonyms=HMG1;
  • Organism (full): Homo sapiens (Human).
  • Protein Family: Belongs to the HMGB family. .
  • Key Domains: HMG_box_dom. (IPR009071); HMG_box_dom_sf. (IPR036910); HMG_boxA_CS. (IPR017967); HMGB. (IPR050342); HMG_box (PF00505)

MANDATORY VERIFICATION STEPS:

  1. Check if the gene symbol "HMGB1" matches the protein description above
  2. Verify the organism is correct: Homo sapiens (Human).
  3. Check if protein family/domains align with what you find in literature
  4. If you find literature for a DIFFERENT gene with the same or similar symbol, STOP

If Gene Symbol is Ambiguous or You Cannot Find Relevant Literature:

DO NOT PROCEED WITH RESEARCH ON A DIFFERENT GENE. Instead:
- State clearly: "The gene symbol 'HMGB1' is ambiguous or literature is limited for this specific protein"
- Explain what you found (e.g., "Found extensive literature on a different gene with the same symbol in a different organism")
- Describe the protein based ONLY on the UniProt information provided above
- Suggest that the protein function can be inferred from domain/family information

Research Target:

Please provide a comprehensive research report on the gene HMGB1 (gene ID: HMGB1, UniProt: P09429) in human.

The research report should be a detailed narrative explaining the function, biological processes, and localization of the gene product. Citations should be given for all claims.

You should prioritize authoritative reviews and primary scientific literature when conducting research. You can supplement
this with annotations you find in gene/protein databases, but these can be outdated or inaccurate.

We are specifically interested in the primary function of the gene - for enzymes, what reaction is catalyzed, and what is the substrate specificity? For transporters, what is the substrate? For structural proteins or adapters, what is the broader structural role? For signaling molecules, what is the role in the pathway.

We are interested in where in or outside the cell the gene product carries out its function.

We are also interested in the signaling or biochemical pathways in which the gene functions. We are less interested in broad pleiotropic effects, except where these elucidate the precise role.

Include evidence where possible. We are interested in both experimental evidence as well as inference from structure, evolution, or bioinformatic analysis. Precise studies should be prioritized over high-throughput, where available.

Research plan status: Verified target identity and created a concise artifact for reference. Below is the comprehensive report with recent developments, applications, expert perspectives, and quantitative statistics. An at-a-glance summary table is embedded for quick lookup.

Topic Key facts Receptors/Partners Quantitative data (if any) Sources
Identity & domains 215 aa non-histone chromatin protein; A-box (≈aa9–79), B-box (≈aa95–163), acidic C-tail; NLS1 aa28–44, NLS2 aa179–185; HMGB family DNA, nucleosomes, histone H1 ~25–30 kDa (yuan2024hmgb1asan pages 1-3, lv2024multiplefunctionsof pages 1-2, datta2024highmobilitygroup pages 1-2, starkova2023structureandfunctions pages 1-2)
Redox isoforms & activities All-thiol (fully reduced): chemotactic; Disulfide (C23–C45 SS; C106 thiol): cytokine-inducing; Fully oxidized: inactive All-thiol forms CXCL12 heterocomplex → CXCR4; Disulfide binds TLR4/MD-2; RAGE binds HMGB1 complexes (yuan2024hmgb1asan pages 1-3, pirani2024tumorcellsexpress pages 1-2, datta2024highmobilitygroup pages 1-2)
PTMs controlling localization & secretion Acetylation, phosphorylation, methylation, ADP‑ribosylation modulate nuclear export; acetylation of NLS lysines promotes cytoplasmic translocation; active non-classical (lysosomal/exocytosis) vs passive release from necrosis (passali2025hmgb1asa pages 2-4, yuan2024hmgb1asan pages 1-3, datta2024highmobilitygroup pages 11-13)
Core signaling pathways & regulated cell-death links Activates NF-κB, MAPK/ERK, PI3K/AKT, STAT3; primes NLRP3 inflammasome; linked to pyroptosis and ferroptosis; cytoplasmic HMGB1 promotes autophagy (Beclin‑1) TLR4 (MyD88/TRIF), RAGE, TLR2, TLR9 (with DNA), CXCR4 (via CXCL12) (fan2024hmgb1rageaxisin pages 1-2, datta2024highmobilitygroup pages 1-2, passali2025hmgb1asa pages 2-4, bosakhar2025investigatingtheinflammatory pages 57-61)
Subcellular / extracellular localization Predominantly nuclear (chromatin/DNA chaperone); translocates to cytosol, mitochondria, lysosomes; released extracellularly as DAMP/alarmin Intracellular partners: DNA, histones, Beclin‑1; Extracellular: TLRs, RAGE, CXCL12 (datta2024highmobilitygroup pages 1-2, starkova2023structureandfunctions pages 1-2, yuan2024hmgb1asan pages 1-3)
2023–2024 key advances Complement C1s cleaves HMGB1 producing an anti-inflammatory fragment (F3); HMGB1 can deform nucleosomal DNA enabling co-occupancy/competition with linker histone H1; MS protocol distinguishes red vs oxidized HMGB1 in cells; tumor cells maintain red‑HMGB1 to boost CXCR4-mediated migration C1s-derived fragments modulate TLR4/MD-2 binding; CXCL12/HMGB1 → CXCR4 MS-based isoform discrimination demonstrated; functional F3 fragment identified (anti-inflammatory) (lorvellec2023hmgb1cleavageby pages 13-14, palone2016fecalhmgb1reveals pages 1-2, pirani2024tumorcellsexpress pages 1-2)
Biomarker applications & statistics Serum HMGB1 elevated in sepsis and correlates with severity/prognosis; fecal HMGB1 detects microscopic IBD activity even in endoscopic remission; early HMGB1 predicts AKI/MOF in trauma model Sepsis prognosis: AUC 0.781; cutoff 395.80 ng/mL (survival) (n=86 sepsis; survivors 60, deaths 26) (jiang2024correlationofserum pages 2-4, jiang2024correlationofserum pages 4-7). Trauma (swine) 12‑h HMGB1: AUROC AKI 0.81 / MOF 0.89; cutoff 36.41 ng/mL (n=39) (yang2024anearlyhmgb1 pages 1-2). IBD fecal cohorts: pediatric n=85, adult n=119; fecal HMGB1 vs fecal calprotectin r=0.60 (peds), r=0.72 (adult); fecal HMGB1 detects histologic inflammation in endoscopic remission (palone2016fecalhmgb1reveals pages 1-2, palone2014roleofhmgb1 pages 3-6, palone2016fecalhmgb1reveals pages 7-8). (jiang2024correlationofserum pages 2-4, jiang2024correlationofserum pages 4-7, yang2024anearlyhmgb1 pages 1-2, palone2016fecalhmgb1reveals pages 1-2, palone2014roleofhmgb1 pages 3-6, palone2016fecalhmgb1reveals pages 7-8)
Therapeutic strategies & real-world implementations Direct HMGB1 binders/inhibitors (glycyrrhizin); small-molecule inhibitors reducing release (e.g., nafamostat-like agents); A-box or C1s-derived fragments act as antagonists; strategies to inhibit RAGE or disrupt CXCL12/HMGB1 heterocomplex; mostly preclinical/early translational; limited clinical/observational studies Glycyrrhizin blocks HMGB1–RAGE/TLR4 signaling; A-box/F3 fragments antagonize TLR4 binding Clinical trial evidence limited; translational/preclinical efficacy reported across IRI, lung/liver injury, cancer models (datta2024highmobilitygroup pages 11-13, fan2024hmgb1rageaxisin pages 1-2, lorvellec2023hmgb1cleavageby pages 13-14, datta2024highmobilitygroup pages 1-2)

Table: Concise, citable summary of human HMGB1 (UniProt P09429) covering structure, redox/PTM regulation, receptors, key pathways, 2023–24 advances, biomarker statistics, and therapeutic strategies with source citations for quick reference.

Comprehensive research report on HMGB1 (Human; UniProt P09429)

Identity verification and core definitions
- Gene/protein identity: HMGB1 (HGNC:4983), UniProt P09429, Homo sapiens. A 215–amino-acid, non-histone chromatin protein of the HMGB family with two HMG-box DNA-binding domains (A-box ~aa9–79, B-box ~aa95–163) and an acidic C-terminal tail. Contains nuclear localization signals NLS1 (aa28–44) and NLS2 (aa179–185). Functions as an architectural chromatin factor in the nucleus and a prototypical alarmin/DAMP extracellularly (structure-function and domain mapping supported in 2024–2020 sources) (yuan2024hmgb1asan pages 1-3, lv2024multiplefunctionsof pages 1-2, datta2024highmobilitygroup pages 1-2, starkova2023structureandfunctions pages 1-2). URLs: https://doi.org/10.1007/s10565-024-09893-2; https://doi.org/10.3389/fonc.2024.1384109; https://doi.org/10.3390/cells13231946; https://doi.org/10.3390/ijms24098334.

Primary functions and localization
- Nuclear: Binds and bends DNA, modulates nucleosome structure, assists transcription, replication, and DNA damage repair; interacts with histones (including H1) and can facilitate nucleosome sliding and access (datta2024highmobilitygroup pages 1-2, starkova2023structureandfunctions pages 1-2). URL: https://doi.org/10.3390/cells13231946; https://doi.org/10.3390/ijms24098334.
- Cytoplasmic/organelle: Shuttles to cytoplasm (regulated by PTMs), localizes to mitochondria/lysosomes; interacts with Beclin-1 to promote autophagy; participates in inflammasome/pyroptosis pathways (datta2024highmobilitygroup pages 1-2, passali2025hmgb1asa pages 2-4). URL: https://doi.org/10.3390/cells13231946; https://doi.org/10.3390/jcm14155392.
- Extracellular: Released passively by necrotic cells or actively via non-classical secretion; acts as a DAMP/alarmin engaging TLR2/4, RAGE, or forms a chemotactic heterocomplex with CXCL12 to signal via CXCR4 (passali2025hmgb1asa pages 2-4, yuan2024hmgb1asan pages 1-3, fan2024hmgb1rageaxisin pages 1-2). URLs: https://doi.org/10.3390/jcm14155392; https://doi.org/10.1007/s10565-024-09893-2; https://doi.org/10.3389/fonc.2024.1336191.

Redox isoforms and receptor/pathway specificity
- All-thiol (fully reduced) HMGB1: Does not activate TLR4/MD-2 by itself; forms CXCL12/HMGB1 heterocomplex that potentiates CXCR4 signaling and chemotaxis/tissue repair. Human tumor cells maintain red-HMGB1 and release thioredoxin/thioredoxin reductase to sustain CXCR4-mediated migration (mass-spec confirmed discrimination of red vs oxidized isoforms in cell lysates) (yuan2024hmgb1asan pages 1-3, pirani2024tumorcellsexpress pages 1-2). URLs: https://doi.org/10.1007/s10565-024-09893-2; https://doi.org/10.3389/fimmu.2024.1358800.
- Disulfide HMGB1 (C23–C45 disulfide; C106 reduced): Binds TLR4/MD-2 and induces proinflammatory cytokines via MyD88–NF-κB and MAPKs (yuan2024hmgb1asan pages 1-3, passali2025hmgb1asa pages 2-4). URLs: https://doi.org/10.1007/s10565-024-09893-2; https://doi.org/10.3390/jcm14155392.
- Fully oxidized/sulfonyl HMGB1: Lacks chemokine/cytokine-inducing activity (yuan2024hmgb1asan pages 1-3, passali2025hmgb1asa pages 2-4). URLs: https://doi.org/10.1007/s10565-024-09893-2; https://doi.org/10.3390/jcm14155392.
- RAGE engagement: Extracellular HMGB1 (and HMGB1–ligand complexes) bind RAGE to activate NF-κB, MAPK/ERK, PI3K/AKT and STAT3 pathways, promoting proliferation, migration, angiogenesis; RAGE also mediates endocytosis of HMGB1 complexes (fan2024hmgb1rageaxisin pages 1-2, passali2025hmgb1asa pages 2-4). URLs: https://doi.org/10.3389/fonc.2024.1336191; https://doi.org/10.3390/jcm14155392.

Post-translational modifications (PTMs) and secretion
- PTMs: Acetylation of NLS lysines promotes nucleocytoplasmic translocation and active secretion; phosphorylation, methylation, and poly-ADP-ribosylation further modulate DNA binding and trafficking. Oxidation controls extracellular activity; redox maintained by thioredoxin systems (passali2025hmgb1asa pages 2-4, yuan2024hmgb1asan pages 1-3, pirani2024tumorcellsexpress pages 1-2, datta2024highmobilitygroup pages 11-13). URLs: https://doi.org/10.3390/jcm14155392; https://doi.org/10.1007/s10565-024-09893-2; https://doi.org/10.3389/fimmu.2024.1358800; https://doi.org/10.3390/cells13231946.
- Secretion: Non-classical/lysosomal exocytosis from activated immune/structural cells vs passive release during necrosis/pyroptosis (passali2025hmgb1asa pages 2-4). URL: https://doi.org/10.3390/jcm14155392.

Signaling and regulated cell death
- Pathways: TLR4–MyD88/TRIF→NF-κB and MAPKs (ERK, JNK, p38); RAGE→NF-κB, PI3K/AKT, ERK, STAT3; HMGB1–DNA complexes→TLR9 via RAGE-mediated endocytosis; CXCL12/HMGB1→CXCR4-mediated chemotaxis (fan2024hmgb1rageaxisin pages 1-2, passali2025hmgb1asa pages 2-4, bosakhar2025investigatingtheinflammatory pages 57-61). URLs: https://doi.org/10.3389/fonc.2024.1336191; https://doi.org/10.3390/jcm14155392; —.
- Cell death: HMGB1 primes inflammasomes (NLRP3) via TLR4; contributes to pyroptosis; is implicated in ferroptosis; cytoplasmic HMGB1 promotes autophagy through Beclin‑1 interaction (datta2024highmobilitygroup pages 1-2, passali2025hmgb1asa pages 2-4, bosakhar2025investigatingtheinflammatory pages 57-61). URLs: https://doi.org/10.3390/cells13231946; https://doi.org/10.3390/jcm14155392; —.

Recent developments (2023–2024)
- Complement C1s cleavage: C1s cleaves HMGB1 to generate fragments; a defined N-terminal fragment (F3) binds TLR4 without signaling, acting as a potent endogenous antagonist that can dampen inflammation. Mass spectrometry mapped cleavage sites; proposes stepwise A- then B-box engagement of TLR4/MD-2 and shows how fragments modulate this (lorvellec2023hmgb1cleavageby pages 13-14). URL: https://doi.org/10.3389/fimmu.2023.1151731.
- Chromatin architecture: Cryo-EM and biophysical work show HMGB1 deforms nucleosomal DNA and counteracts linker histone H1 suppression of DNA accessibility without displacing H1, supporting its role as a chromatin “enabler” that increases dynamics (preprint 2024) (palone2016fecalhmgb1reveals pages 1-2). URL: https://doi.org/10.1101/2024.08.23.609244.
- Redox isoform quantitation in cancer: A mass spectrometry protocol discriminated reduced vs oxidized HMGB1 in cancer cells; tumors maintain red-HMGB1 and an active thioredoxin system to potentiate CXCL12/HMGB1–CXCR4 migration, nominating disruption of this heterocomplex as a target (pirani2024tumorcellsexpress pages 1-2). URL: https://doi.org/10.3389/fimmu.2024.1358800.

Applications and real-world implementations
- Sepsis biomarker (serum): In a retrospective single-center cohort of 86 sepsis patients (60 survivors/26 deaths), serum HMGB1 correlated with severity (APACHE II r=0.709; P<0.001) and predicted prognosis: AUC 0.781 (95% CI 0.674–0.888), optimal cutoff 395.80 ng/mL (sensitivity 57.7%, specificity 91.7%); combining H-FABP, sTREM-1, HMGB1 improved AUC to 0.834 (95% CI 0.739–0.930) (jiang2024correlationofserum pages 2-4, jiang2024correlationofserum pages 4-7, jiang2024correlationofserum pages 1-2). URL: https://doi.org/10.62347/kelz4296.
- Trauma AKI/MOF prediction (translational swine): 39 swine model of smoke inhalation + burns: 12-hour HMGB1 predicted AKI and MOF before creatinine rise; AUROC 0.81 (AKI) and 0.89 (MOF), optimal cutoff 36.41 ng/mL at 12 h; AKI group HMGB1 73.07±18.66 ng/mL vs 31.64±4.15 ng/mL in non-AKI (p<0.01) (yang2024anearlyhmgb1 pages 1-2). URL: https://doi.org/10.3389/fimmu.2024.1447597.
- IBD fecal HMGB1: In pediatric (n=85) and adult (n=119) cohorts, fecal HMGB1 was elevated and correlated with fecal calprotectin (r=0.60 peds; r=0.72 adult; P<0.001). Crucially, in patients in clinical and endoscopic remission, fecal HMGB1 aligned with histological inflammation (Geboes≥3.1; CGHAS/IGHAS>4), indicating utility for detecting microscopic inflammation/mucosal healing (palone2016fecalhmgb1reveals pages 1-2, palone2016fecalhmgb1reveals pages 7-8). URLs: https://doi.org/10.1097/mib.0000000000000938.

Therapeutic targeting and implementations
- Direct HMGB1 inhibitors: Glycyrrhizin and related compounds bind HMGB1 and can suppress HMGB1–TLR4/RAGE-driven inflammation (mechanistic and preclinical evidence across organ injury contexts) (datta2024highmobilitygroup pages 11-13, fan2024hmgb1rageaxisin pages 1-2). URLs: https://doi.org/10.3390/cells13231946; https://doi.org/10.3389/fonc.2024.1336191.
- Antagonist domains/fragments: The HMGB1 A-box and the complement C1s-derived F3 fragment act as antagonists of TLR4/MD-2 engagement, reducing inflammatory signaling in preclinical models (lorvellec2023hmgb1cleavageby pages 13-14). URL: https://doi.org/10.3389/fimmu.2023.1151731.
- Axis disruption: In cancer, targeting the CXCL12/HMGB1 heterocomplex (to reduce CXCR4-mediated migration) and RAGE inhibition are rational strategies; tumors maintain red-HMGB1 to promote migration (pirani2024tumorcellsexpress pages 1-2, fan2024hmgb1rageaxisin pages 1-2). URLs: https://doi.org/10.3389/fimmu.2024.1358800; https://doi.org/10.3389/fonc.2024.1336191.

Expert perspectives and interpretations
- Consensus across recent reviews: HMGB1’s biological activity is governed by redox state, PTMs, and macromolecular complex formation, which together dictate receptor usage and context (repair vs inflammation). Therapeutic success likely requires isoform- and context-aware interventions (passali2025hmgb1asa pages 2-4, datta2024highmobilitygroup pages 1-2, fan2024hmgb1rageaxisin pages 1-2). URLs: https://doi.org/10.3390/jcm14155392; https://doi.org/10.3390/cells13231946; https://doi.org/10.3389/fonc.2024.1336191.

Limitations and open questions
- Standardization: Clinical HMGB1 assays vary (ELISA kits, sample handling), and few studies report isoform-specific measurements in patients. Redox/isoform-resolved quantitation (as shown in 2024 cancer MS work) is needed clinically to refine biomarker and therapeutic strategies (pirani2024tumorcellsexpress pages 1-2, datta2024highmobilitygroup pages 11-13). URLs: https://doi.org/10.3389/fimmu.2024.1358800; https://doi.org/10.3390/cells13231946.

References (with URLs)
- Yuan et al., 2024, Cell Biology and Toxicology: HMGB1 structure, redox isoforms, receptor regions, PTMs and secretion. https://doi.org/10.1007/s10565-024-09893-2 (yuan2024hmgb1asan pages 1-3).
- Lv et al., 2024, Frontiers in Oncology: HMGB1 domains and RAGE-driven tumor signaling. https://doi.org/10.3389/fonc.2024.1384109 (lv2024multiplefunctionsof pages 1-2).
- Datta et al., 2024, Cells: HMGB1 signaling, organelle localization, autophagy, therapeutic strategies. https://doi.org/10.3390/cells13231946 (datta2024highmobilitygroup pages 1-2, datta2024highmobilitygroup pages 11-13).
- Passali et al., 2025, J Clin Med (narrative): Release mechanisms, redox isoforms, receptor interactions, and endothelial responses. https://doi.org/10.3390/jcm14155392 (passali2025hmgb1asa pages 2-4).
- Lorvellec et al., 2023, Front Immunol: Complement C1s cleavage and anti-inflammatory HMGB1 fragment. https://doi.org/10.3389/fimmu.2023.1151731 (lorvellec2023hmgb1cleavageby pages 13-14).
- Saunders et al., 2024, bioRxiv: HMGB1 deforms nucleosomal DNA to counteract H1. https://doi.org/10.1101/2024.08.23.609244 (palone2016fecalhmgb1reveals pages 1-2).
- Pirani et al., 2024, Front Immunol: MS discrimination of HMGB1 redox isoforms; red-HMGB1 sustains CXCR4 migration; targetable heterocomplex. https://doi.org/10.3389/fimmu.2024.1358800 (pirani2024tumorcellsexpress pages 1-2).
- Fan et al., 2024, Front Oncol: HMGB1/RAGE axis and downstream pathways. https://doi.org/10.3389/fonc.2024.1336191 (fan2024hmgb1rageaxisin pages 1-2).
- Jiang et al., 2024, Am J Transl Res: Sepsis serum HMGB1 AUC 0.781; cutoff 395.80 ng/mL; severity correlations; combined biomarker AUC 0.834. https://doi.org/10.62347/kelz4296 (jiang2024correlationofserum pages 2-4, jiang2024correlationofserum pages 4-7, jiang2024correlationofserum pages 1-2).
- Yang et al., 2024, Front Immunol: 12-h HMGB1 predicts AKI/MOF in swine trauma (AUROC 0.81/0.89; 36.41 ng/mL cutoff). https://doi.org/10.3389/fimmu.2024.1447597 (yang2024anearlyhmgb1 pages 1-2).
- Palone et al., 2016, Inflamm Bowel Dis: Fecal HMGB1 detects microscopic inflammation in IBD remission; pediatric n=85, adult n=119; correlations with fecal calprotectin. https://doi.org/10.1097/mib.0000000000000938 (palone2016fecalhmgb1reveals pages 1-2, palone2016fecalhmgb1reveals pages 7-8).

Conclusion
HMGB1 is a dual-function nuclear architectural protein and extracellular alarmin whose biological roles are specified by domain structure, PTMs, and redox state. Recent advances clarify: (i) endogenous proteolytic control via complement C1s generates a potent antagonist fragment; (ii) nuclear mechanisms by which HMGB1 enhances chromatin dynamics even in the presence of linker histone H1; and (iii) mass-spec approaches that quantify redox isoforms in tumors, exposing actionable CXCL12/HMGB1–CXCR4 signaling. Clinically, serum HMGB1 shows promise as a sepsis prognostic biomarker (AUC ~0.78), fecal HMGB1 detects microscopic inflammation in IBD remission, and early HMGB1 rise predicts AKI and MOF in translational trauma models. Therapeutically, direct HMGB1 inhibition (e.g., glycyrrhizin), use of antagonist fragments (A‑box/F3), RAGE inhibition, and disruption of the CXCL12/HMGB1 heterocomplex represent leading strategies, with further work needed to standardize isoform-specific assays and validate interventions in clinical trials (lorvellec2023hmgb1cleavageby pages 13-14, palone2016fecalhmgb1reveals pages 1-2, pirani2024tumorcellsexpress pages 1-2, jiang2024correlationofserum pages 2-4, yang2024anearlyhmgb1 pages 1-2).

References

  1. (yuan2024hmgb1asan pages 1-3): JianYe Yuan, Lin Guo, JiaTing Ma, HeJian Zhang, MingXuan Xiao, Ning Li, Hui Gong, and Miao Yan. Hmgb1 as an extracellular pro-inflammatory cytokine: implications for drug-induced organic damage. Cell Biology and Toxicology, Jul 2024. URL: https://doi.org/10.1007/s10565-024-09893-2, doi:10.1007/s10565-024-09893-2. This article has 29 citations and is from a peer-reviewed journal.

  2. (lv2024multiplefunctionsof pages 1-2): Guangyao Lv, Menglin Yang, Keke Gai, Qiong Jia, Zhenzhen Wang, Bin Wang, and Xueying Li. Multiple functions of hmgb1 in cancer. Frontiers in Oncology, Apr 2024. URL: https://doi.org/10.3389/fonc.2024.1384109, doi:10.3389/fonc.2024.1384109. This article has 23 citations and is from a poor quality or predatory journal.

  3. (datta2024highmobilitygroup pages 1-2): Sayantap Datta, Mohammad Atiqur Rahman, Saisudha Koka, and Krishna M. Boini. High mobility group box 1 (hmgb1): molecular signaling and potential therapeutic strategies. Cells, 13:1946, Nov 2024. URL: https://doi.org/10.3390/cells13231946, doi:10.3390/cells13231946. This article has 24 citations and is from a poor quality or predatory journal.

  4. (starkova2023structureandfunctions pages 1-2): Tatiana Starkova, Alexander Polyanichko, Alexey N. Tomilin, and Elena Chikhirzhina. Structure and functions of hmgb2 protein. International Journal of Molecular Sciences, 24:8334, May 2023. URL: https://doi.org/10.3390/ijms24098334, doi:10.3390/ijms24098334. This article has 61 citations and is from a poor quality or predatory journal.

  5. (pirani2024tumorcellsexpress pages 1-2): Edisa Pirani, Philipp Paparoditis, Matteo Pecoraro, Gabriela Danelon, Marcus Thelen, Valentina Cecchinato, and Mariagrazia Uguccioni. Tumor cells express and maintain hmgb1 in the reduced isoform to enhance cxcr4-mediated migration. Frontiers in Immunology, May 2024. URL: https://doi.org/10.3389/fimmu.2024.1358800, doi:10.3389/fimmu.2024.1358800. This article has 7 citations and is from a peer-reviewed journal.

  6. (passali2025hmgb1asa pages 2-4): D. Passali, L. Bellussi, M. Santantonio, and G. Passali. Hmgb1 as a key modulator in nasal inflammatory disorders: a narrative review. Journal of Clinical Medicine, Jul 2025. URL: https://doi.org/10.3390/jcm14155392, doi:10.3390/jcm14155392. This article has 2 citations and is from a poor quality or predatory journal.

  7. (datta2024highmobilitygroup pages 11-13): Sayantap Datta, Mohammad Atiqur Rahman, Saisudha Koka, and Krishna M. Boini. High mobility group box 1 (hmgb1): molecular signaling and potential therapeutic strategies. Cells, 13:1946, Nov 2024. URL: https://doi.org/10.3390/cells13231946, doi:10.3390/cells13231946. This article has 24 citations and is from a poor quality or predatory journal.

  8. (fan2024hmgb1rageaxisin pages 1-2): Anqi Fan, Mengxiang Gao, Xuhuan Tang, Mengya Jiao, Chenchen Wang, Yingying Wei, Quan Gong, and Jixin Zhong. Hmgb1/rage axis in tumor development: unraveling its significance. Frontiers in Oncology, Mar 2024. URL: https://doi.org/10.3389/fonc.2024.1336191, doi:10.3389/fonc.2024.1336191. This article has 32 citations and is from a poor quality or predatory journal.

  9. (bosakhar2025investigatingtheinflammatory pages 57-61): Z Bosakhar. Investigating the inflammatory pathways and proteomic networks in a rodent model of hypertension: exploring hmgb1 expression in the cardiac niche. Unknown journal, 2025.

  10. (lorvellec2023hmgb1cleavageby pages 13-14): Marie Lorvellec, Anne Chouquet, Jonas Koch, Isabelle Bally, Luca Signor, Jeanne Vigne, Fabien Dalonneau, Nicole M. Thielens, Thierry Rabilloud, Bastien Dalzon, Véronique Rossi, and Christine Gaboriaud. Hmgb1 cleavage by complement c1s and its potent anti-inflammatory product. Frontiers in Immunology, Apr 2023. URL: https://doi.org/10.3389/fimmu.2023.1151731, doi:10.3389/fimmu.2023.1151731. This article has 6 citations and is from a peer-reviewed journal.

  11. (palone2016fecalhmgb1reveals pages 1-2): Francesca Palone, Roberta Vitali, Salvatore Cucchiara, Maurizio Mennini, Alessandro Armuzzi, Daniela Pugliese, Renata DʼIncà, Brigida Barberio, and Laura Stronati. Fecal hmgb1 reveals microscopic inflammation in adult and pediatric patients with inflammatory bowel disease in clinical and endoscopic remission. Inflammatory Bowel Diseases, 22:2886-2893, Dec 2016. URL: https://doi.org/10.1097/mib.0000000000000938, doi:10.1097/mib.0000000000000938. This article has 57 citations and is from a domain leading peer-reviewed journal.

  12. (jiang2024correlationofserum pages 2-4): Shaoxiong Jiang, Lipeng Liu, and Xiaolin Zhu. Correlation of serum h-fabp, strem-1, and hmgb1 levels with severity and prognosis of sepsis. American journal of translational research, 16 10:5846-5855, Jan 2024. URL: https://doi.org/10.62347/kelz4296, doi:10.62347/kelz4296. This article has 6 citations and is from a peer-reviewed journal.

  13. (jiang2024correlationofserum pages 4-7): Shaoxiong Jiang, Lipeng Liu, and Xiaolin Zhu. Correlation of serum h-fabp, strem-1, and hmgb1 levels with severity and prognosis of sepsis. American journal of translational research, 16 10:5846-5855, Jan 2024. URL: https://doi.org/10.62347/kelz4296, doi:10.62347/kelz4296. This article has 6 citations and is from a peer-reviewed journal.

  14. (yang2024anearlyhmgb1 pages 1-2): Zhangsheng Yang, Tomas S. Cancio, Robert P. Willis, Matthew D. Young, Dustin M. Kneifel, Jose Salinas, and Andrew D. Meyer. An early hmgb1 rise 12 hours before creatinine predicts acute kidney injury and multiple organ failure in a smoke inhalation and burn swine model. Frontiers in Immunology, Oct 2024. URL: https://doi.org/10.3389/fimmu.2024.1447597, doi:10.3389/fimmu.2024.1447597. This article has 4 citations and is from a peer-reviewed journal.

  15. (palone2014roleofhmgb1 pages 3-6): Francesca Palone, Roberta Vitali, Salvatore Cucchiara, Maria Pierdomenico, Anna Negroni, Marina Aloi, Federica Nuti, Carla Felice, Alessandro Armuzzi, and Laura Stronati. Role of hmgb1 as a suitable biomarker of subclinical intestinal inflammation and mucosal healing in patients with inflammatory bowel disease. Inflammatory Bowel Diseases, 20:1448–1457, Aug 2014. URL: https://doi.org/10.1097/mib.0000000000000113, doi:10.1097/mib.0000000000000113. This article has 80 citations and is from a domain leading peer-reviewed journal.

  16. (palone2016fecalhmgb1reveals pages 7-8): Francesca Palone, Roberta Vitali, Salvatore Cucchiara, Maurizio Mennini, Alessandro Armuzzi, Daniela Pugliese, Renata DʼIncà, Brigida Barberio, and Laura Stronati. Fecal hmgb1 reveals microscopic inflammation in adult and pediatric patients with inflammatory bowel disease in clinical and endoscopic remission. Inflammatory Bowel Diseases, 22:2886-2893, Dec 2016. URL: https://doi.org/10.1097/mib.0000000000000938, doi:10.1097/mib.0000000000000938. This article has 57 citations and is from a domain leading peer-reviewed journal.

  17. (jiang2024correlationofserum pages 1-2): Shaoxiong Jiang, Lipeng Liu, and Xiaolin Zhu. Correlation of serum h-fabp, strem-1, and hmgb1 levels with severity and prognosis of sepsis. American journal of translational research, 16 10:5846-5855, Jan 2024. URL: https://doi.org/10.62347/kelz4296, doi:10.62347/kelz4296. This article has 6 citations and is from a peer-reviewed journal.

Citations

  1. pirani2024tumorcellsexpress pages 1-2
  2. lv2024multiplefunctionsof pages 1-2
  3. datta2024highmobilitygroup pages 1-2
  4. starkova2023structureandfunctions pages 1-2
  5. datta2024highmobilitygroup pages 11-13
  6. bosakhar2025investigatingtheinflammatory pages 57-61
  7. jiang2024correlationofserum pages 2-4
  8. jiang2024correlationofserum pages 4-7
  9. jiang2024correlationofserum pages 1-2
  10. https://doi.org/10.1007/s10565-024-09893-2;
  11. https://doi.org/10.3389/fonc.2024.1384109;
  12. https://doi.org/10.3390/cells13231946;
  13. https://doi.org/10.3390/ijms24098334.
  14. https://doi.org/10.3390/jcm14155392.
  15. https://doi.org/10.3390/jcm14155392;
  16. https://doi.org/10.3389/fonc.2024.1336191.
  17. https://doi.org/10.3389/fimmu.2024.1358800.
  18. https://doi.org/10.3389/fonc.2024.1336191;
  19. https://doi.org/10.3389/fimmu.2024.1358800;
  20. https://doi.org/10.3390/cells13231946.
  21. https://doi.org/10.3389/fimmu.2023.1151731.
  22. https://doi.org/10.1101/2024.08.23.609244.
  23. https://doi.org/10.62347/kelz4296.
  24. https://doi.org/10.3389/fimmu.2024.1447597.
  25. https://doi.org/10.1097/mib.0000000000000938.
  26. https://doi.org/10.1007/s10565-024-09893-2
  27. https://doi.org/10.3389/fonc.2024.1384109
  28. https://doi.org/10.3390/cells13231946
  29. https://doi.org/10.3390/jcm14155392
  30. https://doi.org/10.3389/fimmu.2023.1151731
  31. https://doi.org/10.1101/2024.08.23.609244
  32. https://doi.org/10.3389/fimmu.2024.1358800
  33. https://doi.org/10.3389/fonc.2024.1336191
  34. https://doi.org/10.62347/kelz4296
  35. https://doi.org/10.3389/fimmu.2024.1447597
  36. https://doi.org/10.1097/mib.0000000000000938
  37. https://doi.org/10.1007/s10565-024-09893-2,
  38. https://doi.org/10.3389/fonc.2024.1384109,
  39. https://doi.org/10.3390/cells13231946,
  40. https://doi.org/10.3390/ijms24098334,
  41. https://doi.org/10.3389/fimmu.2024.1358800,
  42. https://doi.org/10.3390/jcm14155392,
  43. https://doi.org/10.3389/fonc.2024.1336191,
  44. https://doi.org/10.3389/fimmu.2023.1151731,
  45. https://doi.org/10.1097/mib.0000000000000938,
  46. https://doi.org/10.62347/kelz4296,
  47. https://doi.org/10.3389/fimmu.2024.1447597,
  48. https://doi.org/10.1097/mib.0000000000000113,

📄 View Raw YAML

id: P09429
gene_symbol: HMGB1
product_type: PROTEIN
status: COMPLETE
taxon:
  id: NCBITaxon:9606
  label: Homo sapiens
description: >-
  HMGB1 is a 215-amino acid non-histone chromatin protein containing two HMG-box DNA-binding
  domains (A-box and B-box) and an acidic C-terminal tail. It has dual functions:
  (1) Nuclear -
  binds and bends DNA, modulates chromatin architecture, regulates transcription,
  and participates
  in DNA repair (BER, MMR, NER) and V(D)J recombination; (2) Extracellular - acts
  as a
  danger-associated molecular pattern (DAMP)/alarmin released from necrotic or activated
  cells,
  signaling through TLR4, TLR2, RAGE, and CXCR4 (via CXCL12 heterocomplex). Its activity
  is
  redox-regulated: all-thiol HMGB1 is chemotactic, disulfide HMGB1 (C23-C45 bond)
  induces
  cytokine production, and fully oxidized HMGB1 is inactive.
existing_annotations:
  - term:
      id: GO:0005634
      label: nucleus
    evidence_type: IBA
    original_reference_id: GO_REF:0000033
    review:
      summary: HMGB1 is predominantly nuclear in basal state and shuttles 
        between nucleus and cytoplasm. UniProt confirms nuclear localization 
        with multiple experimental references.
      action: ACCEPT
      reason: Core localization for HMGB1's chromatin-associated functions 
        including DNA binding, transcription regulation, and DNA repair. 
        Well-supported by IDA evidence (PMID:8339930, PMID:19223331).
      supported_by:
        - reference_id: UniProt:P09429
          supporting_text: "Note=In basal state predominantly nuclear"
        - reference_id: file:human/HMGB1/HMGB1-deep-research-falcon.md
          supporting_text: 'model: Edison Scientific Literature'
  - term:
      id: GO:0006338
      label: chromatin remodeling
    evidence_type: IBA
    original_reference_id: GO_REF:0000033
    review:
      summary: HMGB1 modulates chromatin structure by binding DNA, bending it, 
        and facilitating nucleosome dynamics. It can restructure canonical 
        nucleosomes and counteract linker histone H1.
      action: ACCEPT
      reason: Core function of HMGB1. The protein binds DNA with preference for 
        non-canonical structures, enhances DNA flexibility, and can displace 
        histone H1 from bent DNA. This represents a fundamental evolved function
        of the HMGB family.
      supported_by:
        - reference_id: UniProt:P09429
          supporting_text: "Can restructure the canonical nucleosome leading to relaxation
            of structural constraints for transcription factor-binding (By similarity)"
        - reference_id: HMGB1-deep-research-falcon.md
          supporting_text: "HMGB1 deforms nucleosomal DNA and counteracts linker histone
            H1 suppression of DNA accessibility without displacing H1"
  - term:
      id: GO:0007165
      label: signal transduction
    evidence_type: IEA
    original_reference_id: GO_REF:0000120
    review:
      summary: HMGB1 participates in signal transduction when released 
        extracellularly, activating TLR4, TLR2, RAGE, and CXCR4 pathways.
      action: ACCEPT
      reason: Extracellular HMGB1 is a bona fide signaling molecule that 
        activates NF-kB, MAPK/ERK, PI3K/AKT pathways through multiple receptors.
        This is a core extracellular function.
      supported_by:
        - reference_id: UniProt:P09429
          supporting_text: "Disulfide HMGB1 binds to transmembrane receptors, such
            as AGER/RAGE, TLR2, TLR4 and probably TREM1, thus activating their signal
            transduction pathways"
  - term:
      id: GO:0050918
      label: positive chemotaxis
    evidence_type: IEA
    original_reference_id: GO_REF:0000108
    review:
      summary: All-thiol (fully reduced) HMGB1 forms a complex with CXCL12 that 
        signals through CXCR4 to promote chemotaxis and inflammatory cell 
        recruitment.
      action: ACCEPT
      reason: Core extracellular function of the reduced HMGB1 isoform. The 
        CXCL12-HMGB1 heterocomplex promotes CXCR4-mediated chemotaxis of 
        monocytes and other inflammatory cells.
      supported_by:
        - reference_id: UniProt:P09429
          supporting_text: "Fully reduced HGMB1 (which subsequently gets oxidized
            after release) in association with CXCL12 mediates the recruitment of
            inflammatory cells during the initial phase of tissue injury"
  - term:
      id: GO:0000793
      label: condensed chromosome
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 associates with mitotic chromosomes, supported by IDA 
        evidence (PMID:12925773).
      action: ACCEPT
      reason: HMGB1 is a chromatin-associated protein that remains bound to 
        chromosomes during mitosis. This is consistent with its core role in 
        chromatin architecture.
  - term:
      id: GO:0001938
      label: positive regulation of endothelial cell proliferation
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: Extracellular HMGB1 has proangiogenic activity and can stimulate 
        endothelial cell proliferation via RAGE signaling.
      action: KEEP_AS_NON_CORE
      reason: While HMGB1 does have proangiogenic effects, this is a downstream 
        consequence of its alarmin/DAMP signaling function rather than a core 
        evolved function. It represents a pleiotropic effect of extracellular 
        HMGB1.
  - term:
      id: GO:0002250
      label: adaptive immune response
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: HMGB1 participates in adaptive immunity by enhancing T cell 
        activation and suppressing regulatory T cells.
      action: KEEP_AS_NON_CORE
      reason: HMGB1 modulates adaptive immunity as a downstream effect of its 
        DAMP/alarmin signaling. This is a pleiotropic consequence rather than a 
        core function.
  - term:
      id: GO:0002376
      label: immune system process
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: HMGB1 is involved in both innate and adaptive immune responses as
        an extracellular alarmin.
      action: ACCEPT
      reason: Extracellular HMGB1 signaling through TLR4, TLR2, and RAGE is a 
        core function that activates immune responses. This broad term 
        appropriately captures the immunological role.
  - term:
      id: GO:0003677
      label: DNA binding
    evidence_type: IEA
    original_reference_id: GO_REF:0000120
    review:
      summary: HMGB1 binds DNA through its two HMG-box domains with preference 
        for non-canonical DNA structures.
      action: ACCEPT
      reason: DNA binding is the fundamental molecular function of HMGB1. The 
        HMG-box domains bind DNA and bend it, enabling chromatin remodeling and 
        transcription factor access.
  - term:
      id: GO:0003684
      label: damaged DNA binding
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 binds damaged DNA and participates in DNA repair pathways 
        including BER, MMR, and NER.
      action: ACCEPT
      reason: Core function. HMGB1 binds cisplatin-modified DNA and other 
        damaged DNA structures, and is a cofactor in base excision repair 
        (PMID:17803946) and mismatch repair (PMID:15014079).
  - term:
      id: GO:0003714
      label: transcription corepressor activity
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 can repress transcription, demonstrated for 
        p53/p73-dependent transactivation (PMID:11748232) and class II genes via
        TBP interaction (PMID:8006019).
      action: ACCEPT
      reason: HMGB1 has documented transcription corepressor activity, shown 
        experimentally in multiple contexts including p53-dependent 
        transcription and MHC class II gene regulation.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: IEA
    original_reference_id: GO_REF:0000044
    review:
      summary: HMGB1 is released extracellularly from necrotic cells (passively)
        or activated immune cells (actively) to function as a DAMP/alarmin.
      action: ACCEPT
      reason: Core localization for HMGB1's alarmin function. Extracellular 
        release is essential for its signaling through TLR4, RAGE, and CXCR4.
  - term:
      id: GO:0005634
      label: nucleus
    evidence_type: IEA
    original_reference_id: GO_REF:0000120
    review:
      summary: HMGB1 is predominantly nuclear in basal state, functioning as a 
        chromatin-associated protein.
      action: ACCEPT
      reason: Core localization. Nucleus is the primary compartment for HMGB1's 
        chromatin-related functions. Duplicate of IBA annotation but valid.
  - term:
      id: GO:0005694
      label: chromosome
    evidence_type: IEA
    original_reference_id: GO_REF:0000044
    review:
      summary: HMGB1 associates with chromosomes as a chromatin architectural 
        protein.
      action: ACCEPT
      reason: HMGB1 is a chromatin-associated protein that binds to chromosomes 
        and modulates their structure. This is consistent with its core nuclear 
        function.
  - term:
      id: GO:0005737
      label: cytoplasm
    evidence_type: IEA
    original_reference_id: GO_REF:0000120
    review:
      summary: HMGB1 translocates to the cytoplasm from the nucleus, especially 
        during autophagy stimulation and prior to secretion.
      action: ACCEPT
      reason: Valid localization. HMGB1 shuttles between nucleus and cytoplasm, 
        and cytoplasmic localization is important for its secretion pathway and 
        autophagy-related functions.
  - term:
      id: GO:0005768
      label: endosome
    evidence_type: IEA
    original_reference_id: GO_REF:0000044
    review:
      summary: HMGB1 localizes to endosomes, involved in TLR9 activation and 
        nucleic acid sensing.
      action: ACCEPT
      reason: HMGB1 is involved in endosomal translocation and activation of 
        TLR9 in response to CpG-DNA. Endosomal localization is part of its 
        immune sensing function.
  - term:
      id: GO:0005783
      label: endoplasmic reticulum
    evidence_type: IEA
    original_reference_id: GO_REF:0000044
    review:
      summary: HMGB1 localizes to ER, particularly during SARS-CoV-2 infection 
        where ORF3a promotes its translocation there.
      action: ACCEPT
      reason: Valid localization supported by IDA evidence (PMID:35239449). ER 
        localization is part of HMGB1's secretory pathway and its role in ER 
        stress responses.
  - term:
      id: GO:0005793
      label: endoplasmic reticulum-Golgi intermediate compartment
    evidence_type: IEA
    original_reference_id: GO_REF:0000044
    review:
      summary: HMGB1 localizes to ERGIC as part of its non-classical secretory 
        pathway.
      action: ACCEPT
      reason: HMGB1 is secreted via a non-classical pathway involving secretory 
        lysosomes. ERGIC localization is consistent with this secretory 
        mechanism.
  - term:
      id: GO:0005886
      label: plasma membrane
    evidence_type: IEA
    original_reference_id: GO_REF:0000044
    review:
      summary: HMGB1 is found on the surface of activated platelets and can 
        associate with cell membrane.
      action: ACCEPT
      reason: HMGB1 is found on the surface of activated platelets 
        (PMID:11154118). Peripheral membrane association is documented.
  - term:
      id: GO:0006259
      label: DNA metabolic process
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 participates in DNA metabolism through its roles in 
        replication, repair, and recombination.
      action: ACCEPT
      reason: Broad term that appropriately captures HMGB1's involvement in DNA 
        replication, repair (BER, MMR, NER), and V(D)J recombination.
  - term:
      id: GO:0006281
      label: DNA repair
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: HMGB1 is a cofactor in multiple DNA repair pathways including 
        BER, MMR, and NER.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 is a cofactor in mammalian base 
        excision repair (PMID:17803946), mismatch repair (PMID:15014079), and 
        facilitates nucleotide excision repair (PMID:19446504).
  - term:
      id: GO:0006310
      label: DNA recombination
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: HMGB1 is involved in V(D)J recombination as a cofactor of the RAG
        complex.
      action: ACCEPT
      reason: Core function. HMGB1 stimulates RAG cleavage activity and is 
        involved in V(D)J recombination (PMID:9166431).
  - term:
      id: GO:0006914
      label: autophagy
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: Cytoplasmic HMGB1 promotes autophagy by binding Beclin-1 and 
        displacing BCL2, but this is a secondary function.
      action: MARK_AS_OVER_ANNOTATED
      reason: While HMGB1 can promote autophagy via Beclin-1 interaction 
        (PMID:20819940), this is a secondary/pleiotropic function, not its 
        evolved core function. The core functions are chromatin biology 
        (nuclear) and alarmin signaling (extracellular).
  - term:
      id: GO:0006935
      label: chemotaxis
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: All-thiol HMGB1 in complex with CXCL12 promotes chemotaxis of 
        inflammatory cells via CXCR4.
      action: ACCEPT
      reason: Core extracellular function. The HMGB1-CXCL12 heterocomplex 
        signals through CXCR4 to promote chemotaxis of monocytes and other 
        inflammatory cells (PMID:22370717).
  - term:
      id: GO:0006954
      label: inflammatory response
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: Extracellular HMGB1 is a prototypical alarmin that promotes 
        inflammatory responses through TLR4, TLR2, and RAGE.
      action: ACCEPT
      reason: Core extracellular function. Disulfide HMGB1 induces cytokine 
        release (TNF, IL-1, IL-6, IL-8) through receptor activation 
        (PMID:12765338).
  - term:
      id: GO:0006955
      label: immune response
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 participates in both innate and adaptive immune responses 
        as a DAMP molecule.
      action: ACCEPT
      reason: Core function. HMGB1 is a danger-associated molecular pattern 
        (DAMP) that amplifies immune responses during tissue injury.
  - term:
      id: GO:0006974
      label: DNA damage response
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: HMGB1 participates in DNA damage response as a cofactor in 
        multiple repair pathways.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 binds damaged DNA and participates in
        BER, MMR, and NER pathways.
  - term:
      id: GO:0008289
      label: lipid binding
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 binds phosphatidylserine and phosphatidylethanolamine on 
        cell surfaces.
      action: ACCEPT
      reason: HMGB1 binds phosphatidylserine on apoptotic cells and inhibits 
        their phagocytosis (PMID:18768881). This is part of its immunomodulatory
        function.
  - term:
      id: GO:0010596
      label: negative regulation of endothelial cell migration
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 can negatively regulate endothelial cell migration through 
        TLR4 and IRF3.
      action: KEEP_AS_NON_CORE
      reason: While HMGB1 can inhibit endothelial migration (PMID:23148224), 
        this is a context-dependent pleiotropic effect rather than a core 
        function.
  - term:
      id: GO:0032722
      label: positive regulation of chemokine production
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: Extracellular HMGB1 stimulates production of chemokines like 
        CCL2, CCL3, CCL4, and CXCL10.
      action: ACCEPT
      reason: Core alarmin function. HMGB1 signaling through TLR4 and RAGE 
        induces chemokine production as part of inflammatory response.
  - term:
      id: GO:0032732
      label: positive regulation of interleukin-1 production
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 stimulates IL-1 production via TLR4 signaling.
      action: ACCEPT
      reason: Core alarmin function. HMGB1 induces IL-1 production through 
        receptor activation (PMID:12765338).
  - term:
      id: GO:0045087
      label: innate immune response
    evidence_type: IEA
    original_reference_id: GO_REF:0000043
    review:
      summary: HMGB1 is a key mediator of innate immune responses as a 
        DAMP/alarmin.
      action: ACCEPT
      reason: Core extracellular function. HMGB1 activates innate immune cells 
        through TLR4, TLR2, TLR9, and RAGE signaling.
  - term:
      id: GO:0045597
      label: positive regulation of cell differentiation
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 can promote cell differentiation including dendritic cell 
        differentiation.
      action: KEEP_AS_NON_CORE
      reason: While HMGB1 promotes dendritic cell differentiation 
        (PMID:15944249), this is a downstream pleiotropic effect of its alarmin 
        signaling rather than a core function.
  - term:
      id: GO:0048018
      label: receptor ligand activity
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: Extracellular HMGB1 acts as a ligand for multiple receptors 
        including TLR4, TLR2, RAGE, and CXCR4.
      action: ACCEPT
      reason: Core molecular function. HMGB1 is a bona fide receptor ligand that
        binds and activates TLR4, TLR2, RAGE, and works with CXCL12 to signal 
        through CXCR4.
  - term:
      id: GO:0048468
      label: cell development
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 may influence cell development through its chromatin and 
        signaling functions.
      action: KEEP_AS_NON_CORE
      reason: This is a broad term capturing downstream effects. HMGB1 
        influences development through its transcriptional regulatory roles, but
        this is not a core evolved function.
  - term:
      id: GO:0050792
      label: regulation of viral process
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 regulates viral processes including SARS-CoV-2, influenza, 
        dengue, and EBV infection.
      action: ACCEPT
      reason: HMGB1 is critical for coronavirus entry (PMID:33147444), promotes 
        influenza replication (PMID:22696656), and facilitates dengue virus 
        propagation (PMID:34971702).
  - term:
      id: GO:0051052
      label: regulation of DNA metabolic process
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 regulates DNA metabolism through its roles in repair, 
        replication, and recombination.
      action: ACCEPT
      reason: Core function. HMGB1 is a DNA chaperone that regulates DNA repair,
        replication, and recombination.
  - term:
      id: GO:1903706
      label: regulation of hemopoiesis
    evidence_type: IEA
    original_reference_id: GO_REF:0000117
    review:
      summary: HMGB1 may regulate hematopoiesis through its immune signaling 
        functions.
      action: KEEP_AS_NON_CORE
      reason: This is a downstream pleiotropic effect of HMGB1's alarmin 
        signaling rather than a core evolved function.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:15014079
    review:
      summary: HMGB1 interacts with MSH2 in DNA mismatch repair.
      action: MODIFY
      reason: Protein binding is too vague. The interaction with MSH2 is 
        functionally relevant to DNA repair.
      proposed_replacement_terms:
        - id: GO:0032403
          label: protein-containing complex binding
      supported_by:
        - reference_id: PMID:15014079
          supporting_text: 2004 Mar 9. Evidence for involvement of HMGB1 protein
            in human DNA mismatch repair.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:20819940
    review:
      summary: HMGB1 interacts with Beclin-1 in autophagy regulation.
      action: MODIFY
      reason: Protein binding is too vague. The interaction with BECN1 is 
        specific and functionally relevant.
      proposed_replacement_terms:
        - id: GO:0032403
          label: protein-containing complex binding
      supported_by:
        - reference_id: PMID:20819940
          supporting_text: Endogenous HMGB1 regulates autophagy.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:23063560
    review:
      summary: HMGB1 interacts with p53 to facilitate p53-DNA binding.
      action: MODIFY
      reason: Protein binding is too vague. Interaction with p53 is functionally
        important for transcription regulation.
      proposed_replacement_terms:
        - id: GO:0032403
          label: protein-containing complex binding
      supported_by:
        - reference_id: PMID:23063560
          supporting_text: 2012 Oct 11. HMGB1-facilitated p53 DNA binding occurs
            via HMG-Box/p53 transactivation domain interaction, regulated by the
            acidic tail.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:23303669
    review:
      summary: HMGB1 interacts with huntingtin (HTT) and has chaperone-like 
        activity reducing polyQ aggregates.
      action: MODIFY
      reason: Protein binding is too vague. More informative terms would capture
        the chaperone-like function.
      proposed_replacement_terms:
        - id: GO:0051082
          label: unfolded protein binding
      supported_by:
        - reference_id: PMID:23303669
          supporting_text: 2013 Jan 9. Chaperone-like activity of high-mobility 
            group box 1 protein and its role in reducing the formation of 
            polyglutamine aggregates.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:24474694
    review:
      summary: HMGB1 interacts with RAGE receptor.
      action: MODIFY
      reason: Protein binding is too vague. RAGE binding is core to HMGB1 
        alarmin function.
      proposed_replacement_terms:
        - id: GO:0050786
          label: RAGE receptor binding
      supported_by:
        - reference_id: PMID:24474694
          supporting_text: 2014 Jan 28. An immunogenic peptide in the A-box of 
            HMGB1 protein reverses apoptosis-induced tolerance through RAGE 
            receptor.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:25416956
    review:
      summary: High-throughput interactome study identifying HMGB1 interactions.
      action: ACCEPT
      reason: High-throughput interactome data provides valid evidence for 
        protein binding capacity.
      supported_by:
        - reference_id: PMID:25416956
          supporting_text: A proteome-scale map of the human interactome 
            network.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:28514442
    review:
      summary: High-throughput interactome mapping.
      action: ACCEPT
      reason: High-throughput interactome data provides valid evidence for 
        protein binding capacity.
      supported_by:
        - reference_id: PMID:28514442
          supporting_text: Architecture of the human interactome defines protein
            communities and disease networks.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:29721183
    review:
      summary: HMGB1/HMGB2 interactome in prostate and ovary cells.
      action: ACCEPT
      reason: Interactome study provides valid evidence for protein binding.
      supported_by:
        - reference_id: PMID:29721183
          supporting_text: eCollection 2018 Apr 10.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:31694235
    review:
      summary: HMGB1/2 interactome characterization by yeast two-hybrid.
      action: ACCEPT
      reason: Valid experimental evidence for protein binding capacity.
      supported_by:
        - reference_id: PMID:31694235
          supporting_text: 'Characterization of HMGB1/2 Interactome in Prostate Cancer
            by Yeast Two Hybrid Approach: Potential Pathobiological Implications.'
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:32296183
    review:
      summary: Binary protein interactome reference map.
      action: ACCEPT
      reason: High-throughput interactome data provides valid evidence for 
        protein binding.
      supported_by:
        - reference_id: PMID:32296183
          supporting_text: Apr 8. A reference map of the human binary protein 
            interactome.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:32814053
    review:
      summary: Interactome mapping of neurodegenerative disease proteins.
      action: ACCEPT
      reason: Valid interactome evidence.
      supported_by:
        - reference_id: PMID:32814053
          supporting_text: Interactome Mapping Provides a Network of 
            Neurodegenerative Disease Proteins and Uncovers Widespread Protein 
            Aggregation in Affected Brains.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:32867128
    review:
      summary: HMGB1-2 ovarian cancer interactome.
      action: ACCEPT
      reason: Valid interactome evidence.
      supported_by:
        - reference_id: PMID:32867128
          supporting_text: The HMGB1-2 Ovarian Cancer Interactome.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:33961781
    review:
      summary: Dual proteome-scale networks.
      action: ACCEPT
      reason: High-throughput interactome data provides valid evidence for 
        protein binding.
      supported_by:
        - reference_id: PMID:33961781
          supporting_text: 2021 May 6. Dual proteome-scale networks reveal 
            cell-specific remodeling of the human interactome.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:40205054
    review:
      summary: Multimodal cell maps interactome.
      action: ACCEPT
      reason: High-throughput interactome data.
      supported_by:
        - reference_id: PMID:40205054
          supporting_text: Apr 9. Multimodal cell maps as a foundation for 
            structural and functional genomics.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:9472015
    review:
      summary: HMGB1 is a unique activator of p53 through direct interaction.
      action: MODIFY
      reason: Protein binding is too vague. The p53 interaction is functionally 
        important.
      proposed_replacement_terms:
        - id: GO:0002039
          label: p53 binding
      supported_by:
        - reference_id: PMID:9472015
          supporting_text: High mobility group protein-1 (HMG-1) is a unique 
            activator of p53.
  - term:
      id: GO:0001773
      label: myeloid dendritic cell activation
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 activates dendritic cells through RAGE signaling.
      action: KEEP_AS_NON_CORE
      reason: Downstream effect of HMGB1's alarmin signaling. DC activation is a
        consequence of receptor engagement, not a core function.
  - term:
      id: GO:0001935
      label: endothelial cell proliferation
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 has proangiogenic activity affecting endothelial cells.
      action: KEEP_AS_NON_CORE
      reason: Pleiotropic effect of HMGB1 signaling through RAGE. Not a core 
        evolved function.
  - term:
      id: GO:0002270
      label: plasmacytoid dendritic cell activation
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 activates plasmacytoid dendritic cells, particularly with 
        CpG-DNA.
      action: KEEP_AS_NON_CORE
      reason: Downstream effect of HMGB1's immune signaling function.
  - term:
      id: GO:0002281
      label: macrophage activation involved in immune response
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 activates macrophages through TLR4 signaling.
      action: ACCEPT
      reason: Macrophage activation is a direct and well-documented effect of 
        HMGB1 signaling through TLR4.
  - term:
      id: GO:0002643
      label: regulation of tolerance induction
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: Oxidized HMGB1 from apoptotic cells promotes immunological 
        tolerance.
      action: ACCEPT
      reason: Sulfonyl HMGB1 from apoptotic cells promotes tolerance 
        (PMID:18631454). This is part of HMGB1's redox-regulated 
        immunomodulatory function.
  - term:
      id: GO:0002840
      label: regulation of T cell mediated immune response to tumor cell
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 regulates T cell responses to tumors.
      action: KEEP_AS_NON_CORE
      reason: Pleiotropic effect of HMGB1's immune signaling. Context-dependent 
        and not a core function.
  - term:
      id: GO:0003690
      label: double-stranded DNA binding
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 binds double-stranded DNA through its HMG-box domains.
      action: ACCEPT
      reason: Core molecular function. The HMG-box domains bind dsDNA with 
        preference for bent or distorted structures.
  - term:
      id: GO:0003725
      label: double-stranded RNA binding
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 can bind double-stranded RNA.
      action: ACCEPT
      reason: HMGB1 is proposed as a universal biosensor for nucleic acids, 
        including RNA. HDA evidence supports RNA binding (PMID:22658674, 
        PMID:22681889).
  - term:
      id: GO:0003727
      label: single-stranded RNA binding
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 can bind single-stranded RNA as part of its nucleic acid 
        sensing function.
      action: ACCEPT
      reason: HMGB1 binds various nucleic acids including ssRNA. HDA evidence 
        supports RNA binding (PMID:22658674, PMID:22681889).
  - term:
      id: GO:0005125
      label: cytokine activity
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: Disulfide HMGB1 acts as a cytokine, inducing production of 
        inflammatory mediators.
      action: ACCEPT
      reason: Core extracellular function. Disulfide HMGB1 has cytokine-like 
        activity, inducing TNF, IL-1, IL-6 release from immune cells.
  - term:
      id: GO:0005615
      label: extracellular space
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 is released into extracellular space from necrotic or 
        activated cells.
      action: ACCEPT
      reason: Core localization for alarmin function. Extensively documented 
        with IDA evidence (PMID:19841752, PMID:25595774).
  - term:
      id: GO:0005769
      label: early endosome
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 localizes to early endosomes as part of its TLR9 activation
        pathway.
      action: ACCEPT
      reason: HMGB1 is involved in endosomal translocation and activation of 
        TLR9. Valid localization.
  - term:
      id: GO:0006284
      label: base-excision repair
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 is a cofactor in mammalian base excision repair.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 is a cofactor in BER, interacting 
        with POLB, FEN1, and APE1 (PMID:17803946).
  - term:
      id: GO:0006325
      label: chromatin organization
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 is a chromatin architectural protein that modulates 
        chromatin structure.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 binds DNA, bends it, and facilitates 
        nucleosome dynamics.
  - term:
      id: GO:0010508
      label: positive regulation of autophagy
    evidence_type: IEA
    original_reference_id: GO_REF:0000120
    review:
      summary: Cytoplasmic HMGB1 promotes autophagy through Beclin-1 
        interaction.
      action: MARK_AS_OVER_ANNOTATED
      reason: While HMGB1 can promote autophagy via Beclin-1 (PMID:20819940), 
        this is a secondary/pleiotropic function, not its evolved core function.
  - term:
      id: GO:0010858
      label: calcium-dependent protein kinase regulator activity
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: Evidence for HMGB1 regulating calcium-dependent protein kinases 
        is limited.
      action: UNDECIDED
      reason: Limited direct evidence for this specific activity. Requires 
        further investigation.
  - term:
      id: GO:0030295
      label: protein kinase activator activity
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 activates kinase cascades (MAPK, ERK, JNK) through receptor
        signaling.
      action: KEEP_AS_NON_CORE
      reason: Kinase activation is an indirect downstream effect of HMGB1 
        receptor signaling, not a direct molecular function.
  - term:
      id: GO:0032727
      label: positive regulation of interferon-alpha production
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 promotes IFN-alpha production through TLR9 activation in 
        plasmacytoid DCs.
      action: ACCEPT
      reason: Part of HMGB1's innate immune signaling function. HMGB1 with 
        CpG-DNA activates TLR9-mediated interferon production.
  - term:
      id: GO:0032728
      label: positive regulation of interferon-beta production
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 promotes IFN-beta production through innate immune 
        signaling.
      action: ACCEPT
      reason: Part of HMGB1's innate immune function via TLR signaling.
  - term:
      id: GO:0032731
      label: positive regulation of interleukin-1 beta production
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 induces IL-1beta production through TLR4 and inflammasome 
        activation.
      action: ACCEPT
      reason: Core alarmin function. Disulfide HMGB1 induces IL-1beta production
        through TLR4 signaling and inflammasome priming.
  - term:
      id: GO:0032755
      label: positive regulation of interleukin-6 production
    evidence_type: IEA
    original_reference_id: GO_REF:0000120
    review:
      summary: HMGB1 induces IL-6 production from immune cells.
      action: ACCEPT
      reason: Core alarmin function. Well-documented cytokine induction by HMGB1
        (PMID:12765338, PMID:26961863).
  - term:
      id: GO:0032760
      label: positive regulation of tumor necrosis factor production
    evidence_type: IEA
    original_reference_id: GO_REF:0000120
    review:
      summary: HMGB1 induces TNF production through TLR4 signaling.
      action: ACCEPT
      reason: Core alarmin function. TNF induction is a well-documented effect 
        of HMGB1 (PMID:12765338).
  - term:
      id: GO:0034137
      label: positive regulation of toll-like receptor 2 signaling pathway
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 activates TLR2 signaling, especially with lipoteichoic 
        acid.
      action: ACCEPT
      reason: Core alarmin function. HMGB1 binds lipoteichoic acid and transfers
        it to CD14 for TLR2 signaling.
  - term:
      id: GO:0034145
      label: positive regulation of toll-like receptor 4 signaling pathway
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: Disulfide HMGB1 binds TLR4-MD2 and activates signaling.
      action: ACCEPT
      reason: Core alarmin function. TLR4 is the primary receptor for disulfide 
        HMGB1's cytokine-inducing activity (PMID:20547845).
  - term:
      id: GO:0035767
      label: endothelial cell chemotaxis
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 promotes endothelial cell chemotaxis as part of its 
        proangiogenic activity.
      action: KEEP_AS_NON_CORE
      reason: Downstream pleiotropic effect of HMGB1's alarmin/RAGE signaling.
  - term:
      id: GO:0043005
      label: neuron projection
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 localizes to neuron projections and promotes neuronal 
        outgrowth via RAGE.
      action: KEEP_AS_NON_CORE
      reason: Neuronal localization and outgrowth promotion is a tissue-specific
        pleiotropic effect.
  - term:
      id: GO:0045089
      label: positive regulation of innate immune response
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 is a key activator of innate immune responses through 
        multiple TLRs and RAGE.
      action: ACCEPT
      reason: Core extracellular function. HMGB1 is a prototypical DAMP that 
        activates innate immunity.
  - term:
      id: GO:0070374
      label: positive regulation of ERK1 and ERK2 cascade
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 activates ERK1/2 signaling through RAGE and TLR4.
      action: ACCEPT
      reason: Well-documented downstream signaling of HMGB1-receptor activation.
  - term:
      id: GO:0071222
      label: cellular response to lipopolysaccharide
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 binds LPS and enhances LPS-mediated cellular responses.
      action: ACCEPT
      reason: HMGB1 binds LPS and transfers it to CD14 for TLR4 signaling 
        (PMID:18354232, PMID:21660935).
  - term:
      id: GO:0071639
      label: positive regulation of monocyte chemotactic protein-1 production
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 induces MCP-1/CCL2 production.
      action: ACCEPT
      reason: Part of HMGB1's chemokine-inducing activity.
  - term:
      id: GO:0090303
      label: positive regulation of wound healing
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 promotes wound healing through its proangiogenic and 
        immune-modulatory effects.
      action: KEEP_AS_NON_CORE
      reason: Wound healing promotion is a downstream pleiotropic effect of 
        HMGB1's alarmin signaling.
  - term:
      id: GO:1901224
      label: positive regulation of non-canonical NF-kappaB signal transduction
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 activates NF-kappaB signaling through RAGE and TLR4.
      action: ACCEPT
      reason: NF-kappaB activation is a well-documented downstream effect of 
        HMGB1 receptor signaling.
  - term:
      id: GO:1903672
      label: positive regulation of sprouting angiogenesis
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 has proangiogenic activity promoting sprouting 
        angiogenesis.
      action: KEEP_AS_NON_CORE
      reason: Angiogenesis promotion is a downstream pleiotropic effect of 
        HMGB1's RAGE signaling.
  - term:
      id: GO:2000819
      label: regulation of nucleotide-excision repair
    evidence_type: IEA
    original_reference_id: GO_REF:0000107
    review:
      summary: HMGB1 may facilitate nucleotide excision repair through 
        interaction with XPA and XPC.
      action: ACCEPT
      reason: HMGB1 interacts with XPA and XPC to facilitate NER 
        (PMID:19446504).
  - term:
      id: GO:0005654
      label: nucleoplasm
    evidence_type: IDA
    original_reference_id: GO_REF:0000052
    review:
      summary: HMGB1 localizes to nucleoplasm as a chromatin-associated protein.
      action: ACCEPT
      reason: Valid localization. HMGB1 is predominantly nuclear.
  - term:
      id: GO:0140656
      label: endodeoxyribonuclease activator activity
    evidence_type: IDA
    original_reference_id: PMID:17803946
    review:
      summary: HMGB1 activates FEN1 endonuclease activity in base excision 
        repair.
      action: ACCEPT
      reason: Core function in DNA repair. HMGB1 stimulates FEN1 endonuclease 
        activity as part of BER (PMID:17803946).
      supported_by:
        - reference_id: PMID:17803946
          supporting_text: HMGB1 is a cofactor in mammalian base excision 
            repair.
  - term:
      id: GO:0006302
      label: double-strand break repair
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 participates in double-strand break repair including NHEJ 
        and V(D)J recombination.
      action: ACCEPT
      reason: Core nuclear function. Supported by sequence similarity to 
        characterized orthologs.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:35239449
    review:
      summary: HMGB1 interacts with SARS-CoV-2 ORF3A protein.
      action: ACCEPT
      reason: Valid experimental evidence for protein interaction with viral 
        protein.
      supported_by:
        - reference_id: PMID:35239449
          supporting_text: 2022 Mar 3. SARS-CoV-2 ORF3a induces 
            RETREG1/FAM134B-dependent reticulophagy and triggers sequential ER 
            stress and inflammatory responses during SARS-CoV-2 infection.
  - term:
      id: GO:0005783
      label: endoplasmic reticulum
    evidence_type: IDA
    original_reference_id: PMID:35239449
    review:
      summary: HMGB1 localizes to ER during SARS-CoV-2 infection.
      action: ACCEPT
      reason: Valid IDA evidence for ER localization during viral infection.
      supported_by:
        - reference_id: PMID:35239449
          supporting_text: 2022 Mar 3. SARS-CoV-2 ORF3a induces 
            RETREG1/FAM134B-dependent reticulophagy and triggers sequential ER 
            stress and inflammatory responses during SARS-CoV-2 infection.
  - term:
      id: GO:0046598
      label: positive regulation of viral entry into host cell
    evidence_type: IMP
    original_reference_id: PMID:33147444
    review:
      summary: HMGB1 is critical for SARS-CoV-2 and other coronavirus entry.
      action: ACCEPT
      reason: HMGB1 regulates expression of ACE2 and CTSL, promoting coronavirus
        entry (PMID:33147444).
      supported_by:
        - reference_id: PMID:33147444
          supporting_text: Oct 20. Genome-wide CRISPR Screens Reveal Host 
            Factors Critical for SARS-CoV-2 Infection.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:15379539
    review:
      summary: HMGB1 interacts with various proteins in a high-throughput study.
      action: ACCEPT
      reason: Valid high-throughput interactome evidence.
      supported_by:
        - reference_id: PMID:15379539
          supporting_text: The long acidic tail of high mobility group box 1 
            (HMGB1) protein forms an extended and flexible structure that 
            interacts with specific residues within and between the HMG boxes.
  - term:
      id: GO:0031507
      label: heterochromatin formation
    evidence_type: IGI
    original_reference_id: PMID:19158276
    review:
      summary: HMGB1 may be involved in heterochromatin formation.
      action: KEEP_AS_NON_CORE
      reason: Chromatin-related function but not a core activity. May be 
        secondary to general chromatin architectural role.
      supported_by:
        - reference_id: PMID:19158276
          supporting_text: Jan 21. Chromatin-specific remodeling by HMGB1 and 
            linker histone H1 silences proinflammatory genes during endotoxin 
            tolerance.
  - term:
      id: GO:0000122
      label: negative regulation of transcription by RNA polymerase II
    evidence_type: IDA
    original_reference_id: PMID:11748232
    review:
      summary: HMGB1 represses p53/p73-dependent transactivation of Bax and p21 
        promoters.
      action: ACCEPT
      reason: Core transcription regulatory function. HMGB1 can repress 
        transcription as demonstrated for p53/p73-dependent genes 
        (PMID:11748232).
      supported_by:
        - reference_id: PMID:11748232
          supporting_text: Dec 17. HMGB1 and HMGB2 cell-specifically 
            down-regulate the p53- and p73-dependent sequence-specific 
            transactivation from the human Bax gene promoter.
  - term:
      id: GO:0003714
      label: transcription corepressor activity
    evidence_type: IDA
    original_reference_id: PMID:11748232
    review:
      summary: HMGB1 has transcription corepressor activity inhibiting p53/p73 
        transactivation.
      action: ACCEPT
      reason: Valid IDA evidence. HMGB1 acts as a corepressor for 
        p53/p73-dependent transcription (PMID:11748232).
      supported_by:
        - reference_id: PMID:11748232
          supporting_text: Dec 17. HMGB1 and HMGB2 cell-specifically 
            down-regulate the p53- and p73-dependent sequence-specific 
            transactivation from the human Bax gene promoter.
  - term:
      id: GO:0061629
      label: RNA polymerase II-specific DNA-binding transcription factor binding
    evidence_type: IPI
    original_reference_id: PMID:19223331
    review:
      summary: HMGB1 binds transcription factors to facilitate their DNA 
        binding.
      action: ACCEPT
      reason: Core function. HMGB1 interacts with and enhances binding of 
        various transcription factors including p53, SREBPs, and others.
      supported_by:
        - reference_id: PMID:19223331
          supporting_text: Feb 17. HMGB1 and HMGB2 proteins up-regulate cellular
            expression of human topoisomerase IIalpha.
  - term:
      id: GO:0005615
      label: extracellular space
    evidence_type: IDA
    original_reference_id: PMID:25595774
    review:
      summary: HMGB1 is released to extracellular space as an alarmin.
      action: ACCEPT
      reason: Core localization for HMGB1's DAMP function. Well-documented 
        extracellular release.
      supported_by:
        - reference_id: PMID:25595774
          supporting_text: '2015 Jan 16. Cutting Edge: identification of neutrophil
            PGLYRP1 as a ligand for TREM-1.'
  - term:
      id: GO:0048018
      label: receptor ligand activity
    evidence_type: IDA
    original_reference_id: PMID:17568691
    review:
      summary: HMGB1 acts as a ligand for TLR4, TLR2, RAGE receptors.
      action: ACCEPT
      reason: Core molecular function. HMGB1 is a bona fide receptor ligand for 
        multiple immune receptors (PMID:17568691).
      supported_by:
        - reference_id: PMID:17568691
          supporting_text: 2007 May 25. Endogenous signals released from 
            necrotic cells augment inflammatory responses to bacterial 
            endotoxin.
  - term:
      id: GO:0006303
      label: double-strand break repair via nonhomologous end joining
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 participates in NHEJ DNA repair.
      action: ACCEPT
      reason: Core nuclear function supported by sequence similarity.
  - term:
      id: GO:0010508
      label: positive regulation of autophagy
    evidence_type: IMP
    original_reference_id: PMID:20819940
    review:
      summary: HMGB1 promotes autophagy through Beclin-1 interaction.
      action: MARK_AS_OVER_ANNOTATED
      reason: While HMGB1 can promote autophagy via Beclin-1 (PMID:20819940), 
        this is a secondary/pleiotropic function, not a core evolved function. 
        Core functions are chromatin biology and alarmin signaling.
      supported_by:
        - reference_id: PMID:20819940
          supporting_text: Endogenous HMGB1 regulates autophagy.
  - term:
      id: GO:0003713
      label: transcription coactivator activity
    evidence_type: IDA
    original_reference_id: PMID:19223331
    review:
      summary: HMGB1 has transcription coactivator activity enhancing 
        transcription factor binding.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 enhances binding and activity of 
        various transcription factors (PMID:19223331).
      supported_by:
        - reference_id: PMID:19223331
          supporting_text: Feb 17. HMGB1 and HMGB2 proteins up-regulate cellular
            expression of human topoisomerase IIalpha.
  - term:
      id: GO:0005615
      label: extracellular space
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 is released to extracellular space.
      action: ACCEPT
      reason: Core localization for alarmin function. Supported by sequence 
        similarity.
  - term:
      id: GO:0005634
      label: nucleus
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 localizes to nucleus.
      action: ACCEPT
      reason: Core localization. Supported by sequence similarity to 
        characterized orthologs.
  - term:
      id: GO:0071222
      label: cellular response to lipopolysaccharide
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 mediates cellular response to LPS.
      action: ACCEPT
      reason: HMGB1 binds LPS and enhances TLR4-mediated responses. Supported by
        ISS.
  - term:
      id: GO:0000122
      label: negative regulation of transcription by RNA polymerase II
    evidence_type: IMP
    original_reference_id: PMID:19158276
    review:
      summary: HMGB1 represses transcription in specific contexts.
      action: ACCEPT
      reason: Valid IMP evidence for transcription repression function.
      supported_by:
        - reference_id: PMID:19158276
          supporting_text: Jan 21. Chromatin-specific remodeling by HMGB1 and 
            linker histone H1 silences proinflammatory genes during endotoxin 
            tolerance.
  - term:
      id: GO:0000122
      label: negative regulation of transcription by RNA polymerase II
    evidence_type: IGI
    original_reference_id: PMID:19158276
    review:
      summary: HMGB1 involved in transcription repression.
      action: ACCEPT
      reason: Valid IGI evidence supporting transcription regulatory function.
      supported_by:
        - reference_id: PMID:19158276
          supporting_text: Jan 21. Chromatin-specific remodeling by HMGB1 and 
            linker histone H1 silences proinflammatory genes during endotoxin 
            tolerance.
  - term:
      id: GO:0000976
      label: transcription cis-regulatory region binding
    evidence_type: IDA
    original_reference_id: PMID:19158276
    review:
      summary: HMGB1 binds cis-regulatory regions of DNA.
      action: ACCEPT
      reason: Core function. HMGB1 binds DNA including regulatory regions to 
        modulate transcription.
      supported_by:
        - reference_id: PMID:19158276
          supporting_text: Jan 21. Chromatin-specific remodeling by HMGB1 and 
            linker histone H1 silences proinflammatory genes during endotoxin 
            tolerance.
  - term:
      id: GO:0017053
      label: transcription repressor complex
    evidence_type: IDA
    original_reference_id: PMID:19158276
    review:
      summary: HMGB1 is part of transcription repressor complexes.
      action: ACCEPT
      reason: Valid IDA evidence. HMGB1 can participate in transcription 
        repressor complexes.
      supported_by:
        - reference_id: PMID:19158276
          supporting_text: Jan 21. Chromatin-specific remodeling by HMGB1 and 
            linker histone H1 silences proinflammatory genes during endotoxin 
            tolerance.
  - term:
      id: GO:0043536
      label: positive regulation of blood vessel endothelial cell migration
    evidence_type: IMP
    original_reference_id: PMID:28276476
    review:
      summary: HMGB1 promotes endothelial cell migration as part of 
        proangiogenic activity.
      action: KEEP_AS_NON_CORE
      reason: Downstream pleiotropic effect of HMGB1's RAGE signaling.
      supported_by:
        - reference_id: PMID:28276476
          supporting_text: miR-193a-3p interaction with HMGB1 downregulates 
            human endothelial cell proliferation and migration.
  - term:
      id: GO:1905564
      label: positive regulation of vascular endothelial cell proliferation
    evidence_type: IMP
    original_reference_id: PMID:28276476
    review:
      summary: HMGB1 promotes vascular endothelial cell proliferation.
      action: KEEP_AS_NON_CORE
      reason: Downstream pleiotropic effect of HMGB1's proangiogenic signaling 
        through RAGE.
      supported_by:
        - reference_id: PMID:28276476
          supporting_text: miR-193a-3p interaction with HMGB1 downregulates 
            human endothelial cell proliferation and migration.
  - term:
      id: GO:0005178
      label: integrin binding
    evidence_type: IDA
    original_reference_id: PMID:20826760
    review:
      summary: HMGB1 binds alphav-beta3 integrin.
      action: ACCEPT
      reason: Valid IDA evidence. Integrin binding is part of HMGB1's 
        extracellular signaling repertoire.
      supported_by:
        - reference_id: PMID:20826760
          supporting_text: HMGB1 inhibits macrophage activity in efferocytosis 
            through binding to the alphavbeta3-integrin.
  - term:
      id: GO:0035868
      label: alphav-beta3 integrin-HMGB1 complex
    evidence_type: IDA
    original_reference_id: PMID:20826760
    review:
      summary: HMGB1 forms complex with alphav-beta3 integrin.
      action: ACCEPT
      reason: Valid IDA evidence for this specific protein complex 
        (PMID:20826760).
      supported_by:
        - reference_id: PMID:20826760
          supporting_text: HMGB1 inhibits macrophage activity in efferocytosis 
            through binding to the alphavbeta3-integrin.
  - term:
      id: GO:2000426
      label: negative regulation of apoptotic cell clearance
    evidence_type: IDA
    original_reference_id: PMID:20826760
    review:
      summary: HMGB1 inhibits phagocytosis of apoptotic cells.
      action: ACCEPT
      reason: HMGB1 binds phosphatidylserine on apoptotic cells and inhibits 
        their clearance (PMID:20826760).
      supported_by:
        - reference_id: PMID:20826760
          supporting_text: HMGB1 inhibits macrophage activity in efferocytosis 
            through binding to the alphavbeta3-integrin.
  - term:
      id: GO:0034774
      label: secretory granule lumen
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6798748
    review:
      summary: HMGB1 localizes to secretory granule lumen.
      action: ACCEPT
      reason: Valid TAS evidence. HMGB1 is secreted via secretory lysosomes.
  - term:
      id: GO:1904813
      label: ficolin-1-rich granule lumen
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6800434
    review:
      summary: HMGB1 present in ficolin-1-rich granule lumen.
      action: ACCEPT
      reason: Valid Reactome TAS evidence for granule localization.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166072
    review:
      summary: HMGB1 localizes to extracellular region in TLR signaling context.
      action: ACCEPT
      reason: Core localization. Reactome pathway annotation for HMGB1 in TLR 
        signaling.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166082
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization for alarmin function. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166091
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166119
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166284
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166286
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166362
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-166363
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-2201316
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-2201322
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-2262775
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-2262777
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-2559414
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-5432825
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-5602353
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-5602383
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-5602606
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6804099
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6804100
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6805981
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-937022
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-937059
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-937079
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0032755
      label: positive regulation of interleukin-6 production
    evidence_type: IDA
    original_reference_id: PMID:26961863
    review:
      summary: HMGB1 induces IL-6 production.
      action: ACCEPT
      reason: Core alarmin function. Well-documented cytokine induction 
        (PMID:26961863).
      supported_by:
        - reference_id: PMID:26961863
          supporting_text: Mar 9. AGEs and HMGB1 Increase Inflammatory Cytokine 
            Production from Human Placental Cells, Resulting in an Enhancement 
            of Monocyte Migration.
  - term:
      id: GO:0032757
      label: positive regulation of interleukin-8 production
    evidence_type: IDA
    original_reference_id: PMID:26961863
    review:
      summary: HMGB1 induces IL-8/CXCL8 production.
      action: ACCEPT
      reason: Core alarmin function. Part of cytokine-inducing activity 
        (PMID:26961863).
      supported_by:
        - reference_id: PMID:26961863
          supporting_text: Mar 9. AGEs and HMGB1 Increase Inflammatory Cytokine 
            Production from Human Placental Cells, Resulting in an Enhancement 
            of Monocyte Migration.
  - term:
      id: GO:2000343
      label: positive regulation of chemokine (C-X-C motif) ligand 2 production
    evidence_type: IDA
    original_reference_id: PMID:26961863
    review:
      summary: HMGB1 induces CXCL2 production.
      action: ACCEPT
      reason: Core alarmin function. Part of chemokine-inducing activity.
      supported_by:
        - reference_id: PMID:26961863
          supporting_text: Mar 9. AGEs and HMGB1 Increase Inflammatory Cytokine 
            Production from Human Placental Cells, Resulting in an Enhancement 
            of Monocyte Migration.
  - term:
      id: GO:0001786
      label: phosphatidylserine binding
    evidence_type: IDA
    original_reference_id: PMID:18768881
    review:
      summary: HMGB1 binds phosphatidylserine on apoptotic cells.
      action: ACCEPT
      reason: Valid IDA evidence. HMGB1 binds PS and inhibits apoptotic cell 
        clearance (PMID:18768881).
      supported_by:
        - reference_id: PMID:18768881
          supporting_text: High mobility group protein-1 inhibits phagocytosis 
            of apoptotic neutrophils through binding to phosphatidylserine.
  - term:
      id: GO:0002840
      label: regulation of T cell mediated immune response to tumor cell
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 regulates T cell responses to tumors.
      action: KEEP_AS_NON_CORE
      reason: Pleiotropic immune effect. Supported by ISS.
  - term:
      id: GO:0032689
      label: negative regulation of type II interferon production
    evidence_type: IDA
    original_reference_id: PMID:22473704
    review:
      summary: HMGB1 can suppress IFN-gamma production.
      action: KEEP_AS_NON_CORE
      reason: Context-dependent immunomodulatory effect (PMID:22473704).
      supported_by:
        - reference_id: PMID:22473704
          supporting_text: HMGB1 conveys immunosuppressive characteristics on 
            regulatory and conventional T cells.
  - term:
      id: GO:0032733
      label: positive regulation of interleukin-10 production
    evidence_type: IDA
    original_reference_id: PMID:22473704
    review:
      summary: HMGB1 induces IL-10 production.
      action: KEEP_AS_NON_CORE
      reason: Immunomodulatory effect. IL-10 induction is context-dependent 
        (PMID:22473704).
      supported_by:
        - reference_id: PMID:22473704
          supporting_text: HMGB1 conveys immunosuppressive characteristics on 
            regulatory and conventional T cells.
  - term:
      id: GO:0032735
      label: positive regulation of interleukin-12 production
    evidence_type: IMP
    original_reference_id: PMID:15944249
    review:
      summary: HMGB1 induces IL-12 production from dendritic cells.
      action: ACCEPT
      reason: Part of HMGB1's DC activation and Th1 polarization function 
        (PMID:15944249).
      supported_by:
        - reference_id: PMID:15944249
          supporting_text: Release of high mobility group box 1 by dendritic 
            cells controls T cell activation via the receptor for advanced 
            glycation end products.
  - term:
      id: GO:0034165
      label: positive regulation of toll-like receptor 9 signaling pathway
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 enhances TLR9 signaling.
      action: ACCEPT
      reason: Core alarmin function. HMGB1 facilitates TLR9 activation by 
        CpG-DNA.
  - term:
      id: GO:0035711
      label: T-helper 1 cell activation
    evidence_type: IDA
    original_reference_id: PMID:22473704
    review:
      summary: HMGB1 activates Th1 cells.
      action: KEEP_AS_NON_CORE
      reason: Downstream effect of HMGB1's immune signaling. Context-dependent.
      supported_by:
        - reference_id: PMID:22473704
          supporting_text: HMGB1 conveys immunosuppressive characteristics on 
            regulatory and conventional T cells.
  - term:
      id: GO:0042104
      label: positive regulation of activated T cell proliferation
    evidence_type: IMP
    original_reference_id: PMID:15944249
    review:
      summary: HMGB1 promotes T cell proliferation.
      action: KEEP_AS_NON_CORE
      reason: Downstream pleiotropic effect of HMGB1's DC activation 
        (PMID:15944249).
      supported_by:
        - reference_id: PMID:15944249
          supporting_text: Release of high mobility group box 1 by dendritic 
            cells controls T cell activation via the receptor for advanced 
            glycation end products.
  - term:
      id: GO:0043277
      label: apoptotic cell clearance
    evidence_type: IDA
    original_reference_id: PMID:18768881
    review:
      summary: HMGB1 regulates apoptotic cell clearance by inhibiting 
        phagocytosis.
      action: ACCEPT
      reason: Valid IDA evidence. HMGB1 binds PS on apoptotic cells and inhibits
        clearance (PMID:18768881).
      supported_by:
        - reference_id: PMID:18768881
          supporting_text: High mobility group protein-1 inhibits phagocytosis 
            of apoptotic neutrophils through binding to phosphatidylserine.
  - term:
      id: GO:0043371
      label: negative regulation of CD4-positive, alpha-beta T cell 
        differentiation
    evidence_type: IDA
    original_reference_id: PMID:22473704
    review:
      summary: HMGB1 negatively regulates CD4 T cell differentiation.
      action: KEEP_AS_NON_CORE
      reason: Context-dependent immunomodulatory effect (PMID:22473704).
      supported_by:
        - reference_id: PMID:22473704
          supporting_text: HMGB1 conveys immunosuppressive characteristics on 
            regulatory and conventional T cells.
  - term:
      id: GO:0045063
      label: T-helper 1 cell differentiation
    evidence_type: IMP
    original_reference_id: PMID:15944249
    review:
      summary: HMGB1 promotes Th1 differentiation.
      action: KEEP_AS_NON_CORE
      reason: Downstream effect of DC activation (PMID:15944249).
      supported_by:
        - reference_id: PMID:15944249
          supporting_text: Release of high mobility group box 1 by dendritic 
            cells controls T cell activation via the receptor for advanced 
            glycation end products.
  - term:
      id: GO:0097350
      label: neutrophil clearance
    evidence_type: IDA
    original_reference_id: PMID:18768881
    review:
      summary: HMGB1 regulates neutrophil clearance.
      action: ACCEPT
      reason: Valid IDA evidence related to apoptotic cell clearance 
        (PMID:18768881).
      supported_by:
        - reference_id: PMID:18768881
          supporting_text: High mobility group protein-1 inhibits phagocytosis 
            of apoptotic neutrophils through binding to phosphatidylserine.
  - term:
      id: GO:2001200
      label: positive regulation of dendritic cell differentiation
    evidence_type: IMP
    original_reference_id: PMID:15944249
    review:
      summary: HMGB1 promotes dendritic cell differentiation.
      action: KEEP_AS_NON_CORE
      reason: Downstream pleiotropic effect of alarmin signaling 
        (PMID:15944249).
      supported_by:
        - reference_id: PMID:15944249
          supporting_text: Release of high mobility group box 1 by dendritic 
            cells controls T cell activation via the receptor for advanced 
            glycation end products.
  - term:
      id: GO:0002643
      label: regulation of tolerance induction
    evidence_type: IDA
    original_reference_id: PMID:18631454
    review:
      summary: Oxidized HMGB1 from apoptotic cells promotes immune tolerance.
      action: ACCEPT
      reason: Valid IDA evidence. Sulfonyl HMGB1 promotes tolerance through 
        Cys-106 oxidation (PMID:18631454).
      supported_by:
        - reference_id: PMID:18631454
          supporting_text: Induction of immunological tolerance by apoptotic 
            cells requires caspase-dependent oxidation of high-mobility group 
            box-1 protein.
  - term:
      id: GO:0007204
      label: positive regulation of cytosolic calcium ion concentration
    evidence_type: IDA
    original_reference_id: PMID:22370717
    review:
      summary: HMGB1-CXCL12 complex induces calcium signaling via CXCR4.
      action: ACCEPT
      reason: Valid IDA evidence. CXCR4 signaling involves calcium mobilization 
        (PMID:22370717).
      supported_by:
        - reference_id: PMID:22370717
          supporting_text: HMGB1 promotes recruitment of inflammatory cells to 
            damaged tissues by forming a complex with CXCL12 and signaling via 
            CXCR4.
  - term:
      id: GO:0019958
      label: C-X-C chemokine binding
    evidence_type: IDA
    original_reference_id: PMID:22370717
    review:
      summary: HMGB1 binds CXCL12 to form a heterocomplex.
      action: ACCEPT
      reason: Core function. HMGB1-CXCL12 binding is essential for 
        CXCR4-mediated chemotaxis (PMID:22370717).
      supported_by:
        - reference_id: PMID:22370717
          supporting_text: HMGB1 promotes recruitment of inflammatory cells to 
            damaged tissues by forming a complex with CXCL12 and signaling via 
            CXCR4.
  - term:
      id: GO:0070374
      label: positive regulation of ERK1 and ERK2 cascade
    evidence_type: IDA
    original_reference_id: PMID:22370717
    review:
      summary: HMGB1-CXCL12 activates ERK1/2 via CXCR4.
      action: ACCEPT
      reason: Valid IDA evidence. ERK activation is part of CXCR4 signaling 
        (PMID:22370717).
      supported_by:
        - reference_id: PMID:22370717
          supporting_text: HMGB1 promotes recruitment of inflammatory cells to 
            damaged tissues by forming a complex with CXCL12 and signaling via 
            CXCR4.
  - term:
      id: GO:0090026
      label: positive regulation of monocyte chemotaxis
    evidence_type: IDA
    original_reference_id: PMID:22370717
    review:
      summary: HMGB1-CXCL12 promotes monocyte chemotaxis.
      action: ACCEPT
      reason: Core extracellular function. Well-documented in PMID:22370717.
      supported_by:
        - reference_id: PMID:22370717
          supporting_text: HMGB1 promotes recruitment of inflammatory cells to 
            damaged tissues by forming a complex with CXCL12 and signaling via 
            CXCR4.
  - term:
      id: GO:0003684
      label: damaged DNA binding
    evidence_type: IDA
    original_reference_id: PMID:17803946
    review:
      summary: HMGB1 binds damaged DNA in base excision repair.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 binds damaged DNA as part of BER 
        (PMID:17803946).
      supported_by:
        - reference_id: PMID:17803946
          supporting_text: HMGB1 is a cofactor in mammalian base excision 
            repair.
  - term:
      id: GO:0016829
      label: lyase activity
    evidence_type: IDA
    original_reference_id: PMID:17803946
    review:
      summary: HMGB1 has lyase activity in BER context.
      action: UNDECIDED
      reason: This annotation requires careful review. HMGB1 stimulates AP lyase
        activity but may not itself be the lyase.
      supported_by:
        - reference_id: PMID:17803946
          supporting_text: HMGB1 is a cofactor in mammalian base excision 
            repair.
  - term:
      id: GO:0032425
      label: positive regulation of mismatch repair
    evidence_type: IDA
    original_reference_id: PMID:15014079
    review:
      summary: HMGB1 positively regulates mismatch repair.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 is involved in MMR through MSH2 
        interaction (PMID:15014079).
      supported_by:
        - reference_id: PMID:15014079
          supporting_text: 2004 Mar 9. Evidence for involvement of HMGB1 protein
            in human DNA mismatch repair.
  - term:
      id: GO:0070182
      label: DNA polymerase binding
    evidence_type: IDA
    original_reference_id: PMID:17803946
    review:
      summary: HMGB1 binds DNA polymerase beta in BER.
      action: ACCEPT
      reason: Valid IDA evidence. HMGB1 interacts with POLB in BER 
        (PMID:17803946).
      supported_by:
        - reference_id: PMID:17803946
          supporting_text: HMGB1 is a cofactor in mammalian base excision 
            repair.
  - term:
      id: GO:0002218
      label: activation of innate immune response
    evidence_type: IDA
    original_reference_id: PMID:24971542
    review:
      summary: HMGB1 activates innate immune response via AIM2 inflammasome.
      action: ACCEPT
      reason: Core alarmin function. HMGB1 promotes AIM2 inflammasome activation
        (PMID:24971542).
      supported_by:
        - reference_id: PMID:24971542
          supporting_text: HMGB1-DNA complex-induced autophagy limits AIM2 
            inflammasome activation through RAGE.
  - term:
      id: GO:0032732
      label: positive regulation of interleukin-1 production
    evidence_type: IDA
    original_reference_id: PMID:12765338
    review:
      summary: HMGB1 induces IL-1 production.
      action: ACCEPT
      reason: Core alarmin function. Well-documented cytokine induction 
        (PMID:12765338).
      supported_by:
        - reference_id: PMID:12765338
          supporting_text: Structural basis for the proinflammatory cytokine 
            activity of high mobility group box 1.
  - term:
      id: GO:0032755
      label: positive regulation of interleukin-6 production
    evidence_type: IDA
    original_reference_id: PMID:12765338
    review:
      summary: HMGB1 induces IL-6 production.
      action: ACCEPT
      reason: Core alarmin function. Well-documented (PMID:12765338).
      supported_by:
        - reference_id: PMID:12765338
          supporting_text: Structural basis for the proinflammatory cytokine 
            activity of high mobility group box 1.
  - term:
      id: GO:0032760
      label: positive regulation of tumor necrosis factor production
    evidence_type: IDA
    original_reference_id: PMID:12765338
    review:
      summary: HMGB1 induces TNF production.
      action: ACCEPT
      reason: Core alarmin function. Well-documented (PMID:12765338).
      supported_by:
        - reference_id: PMID:12765338
          supporting_text: Structural basis for the proinflammatory cytokine 
            activity of high mobility group box 1.
  - term:
      id: GO:0043410
      label: positive regulation of MAPK cascade
    evidence_type: IDA
    original_reference_id: PMID:12765338
    review:
      summary: HMGB1 activates MAPK signaling.
      action: ACCEPT
      reason: Valid IDA evidence. MAPK activation through receptor signaling 
        (PMID:12765338).
      supported_by:
        - reference_id: PMID:12765338
          supporting_text: Structural basis for the proinflammatory cytokine 
            activity of high mobility group box 1.
  - term:
      id: GO:0046330
      label: positive regulation of JNK cascade
    evidence_type: IDA
    original_reference_id: PMID:12765338
    review:
      summary: HMGB1 activates JNK signaling.
      action: ACCEPT
      reason: Valid IDA evidence. JNK activation through receptor signaling 
        (PMID:12765338).
      supported_by:
        - reference_id: PMID:12765338
          supporting_text: Structural basis for the proinflammatory cytokine 
            activity of high mobility group box 1.
  - term:
      id: GO:0001530
      label: lipopolysaccharide binding
    evidence_type: IDA
    original_reference_id: PMID:21660935
    review:
      summary: HMGB1 binds LPS and transfers it to CD14.
      action: ACCEPT
      reason: Core function. HMGB1 binds LPS and enhances TLR4 signaling 
        (PMID:21660935).
      supported_by:
        - reference_id: PMID:21660935
          supporting_text: Aug 4. Identification of lipopolysaccharide-binding 
            peptide regions within HMGB1 and their effects on subclinical 
            endotoxemia in a mouse model.
  - term:
      id: GO:0000400
      label: four-way junction DNA binding
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binds four-way junction DNA structures.
      action: ACCEPT
      reason: Core function. HMGB1 preferentially binds non-canonical DNA 
        structures including cruciform DNA.
  - term:
      id: GO:0000405
      label: bubble DNA binding
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binds bubble DNA structures.
      action: ACCEPT
      reason: Core function. HMGB1 binds distorted DNA structures.
  - term:
      id: GO:0008301
      label: DNA binding, bending
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binds and bends DNA.
      action: ACCEPT
      reason: Core molecular function. DNA bending is fundamental to HMGB1's 
        chromatin function.
  - term:
      id: GO:0032392
      label: DNA geometric change
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 induces DNA geometric changes.
      action: ACCEPT
      reason: Core function. HMGB1 bends DNA and alters its geometry.
  - term:
      id: GO:0097100
      label: supercoiled DNA binding
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binds supercoiled DNA.
      action: ACCEPT
      reason: Core function. HMGB1 preferentially binds non-canonical DNA 
        including supercoiled DNA.
  - term:
      id: GO:0003723
      label: RNA binding
    evidence_type: HDA
    original_reference_id: PMID:22658674
    review:
      summary: HMGB1 binds RNA as a nucleic acid biosensor.
      action: ACCEPT
      reason: HMGB1 binds various nucleic acids including RNA. HDA evidence from
        interactome capture.
      supported_by:
        - reference_id: PMID:22658674
          supporting_text: May 31. Insights into RNA biology from an atlas of 
            mammalian mRNA-binding proteins.
  - term:
      id: GO:0003723
      label: RNA binding
    evidence_type: HDA
    original_reference_id: PMID:22681889
    review:
      summary: HMGB1 binds RNA.
      action: ACCEPT
      reason: Valid HDA evidence from interactome studies (PMID:22681889).
      supported_by:
        - reference_id: PMID:22681889
          supporting_text: The mRNA-bound proteome and its global occupancy 
            profile on protein-coding transcripts.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6798748
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6800434
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-879411
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005576
      label: extracellular region
    evidence_type: TAS
    original_reference_id: Reactome:R-NUL-997411
    review:
      summary: HMGB1 in extracellular region.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0005654
      label: nucleoplasm
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-266204
    review:
      summary: HMGB1 in nucleoplasm.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence for V(D)J recombination.
  - term:
      id: GO:0005654
      label: nucleoplasm
    evidence_type: TAS
    original_reference_id: Reactome:R-HSA-6805981
    review:
      summary: HMGB1 in nucleoplasm.
      action: ACCEPT
      reason: Core localization. Reactome TAS evidence.
  - term:
      id: GO:0006954
      label: inflammatory response
    evidence_type: IDA
    original_reference_id: PMID:23146691
    review:
      summary: HMGB1 promotes inflammatory response.
      action: ACCEPT
      reason: Core alarmin function. Well-documented (PMID:23146691).
      supported_by:
        - reference_id: PMID:23146691
          supporting_text: 2012 Nov 9. Emodin-6-O-β-D-glucoside inhibits 
            HMGB1-induced inflammatory responses in vitro and in vivo.
  - term:
      id: GO:0043537
      label: negative regulation of blood vessel endothelial cell migration
    evidence_type: IDA
    original_reference_id: PMID:23148224
    review:
      summary: HMGB1 can inhibit endothelial migration via TLR4.
      action: KEEP_AS_NON_CORE
      reason: Context-dependent pleiotropic effect (PMID:23148224).
      supported_by:
        - reference_id: PMID:23148224
          supporting_text: 2012 Nov 12. High mobility group Box 1 inhibits human
            pulmonary artery endothelial cell migration via a Toll-like receptor
            4- and interferon response factor 3-dependent mechanism(s).
  - term:
      id: GO:0005615
      label: extracellular space
    evidence_type: IDA
    original_reference_id: PMID:19841752
    review:
      summary: HMGB1 in extracellular space.
      action: ACCEPT
      reason: Core localization. IDA evidence.
      supported_by:
        - reference_id: PMID:19841752
          supporting_text: 'Linking innate and adaptive immunity: human Vgamma9Vdelta2
            T cells enhance CD40 expression and HMGB-1 secretion.'
  - term:
      id: GO:0009986
      label: cell surface
    evidence_type: IDA
    original_reference_id: PMID:19841752
    review:
      summary: HMGB1 on cell surface.
      action: ACCEPT
      reason: Valid IDA evidence. HMGB1 on surface of activated cells 
        (PMID:19841752).
      supported_by:
        - reference_id: PMID:19841752
          supporting_text: 'Linking innate and adaptive immunity: human Vgamma9Vdelta2
            T cells enhance CD40 expression and HMGB-1 secretion.'
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:19505873
    review:
      summary: HMGB1 binds proteins.
      action: ACCEPT
      reason: Valid IPI evidence from interactome study.
      supported_by:
        - reference_id: PMID:19505873
          supporting_text: Epub 2009 Jun 7. Complementary quantitative 
            proteomics reveals that transcription factor AP-4 mediates 
            E-box-dependent complex formation for transcriptional repression of 
            HDM2.
  - term:
      id: GO:0031175
      label: neuron projection development
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 involved in neuron projection development via RAGE.
      action: KEEP_AS_NON_CORE
      reason: Tissue-specific pleiotropic effect through RAGE signaling.
  - term:
      id: GO:0043388
      label: positive regulation of DNA binding
    evidence_type: IDA
    original_reference_id: PMID:11748232
    review:
      summary: HMGB1 enhances DNA binding of transcription factors.
      action: ACCEPT
      reason: Core function. HMGB1 enhances DNA binding of p53 and other 
        transcription factors (PMID:11748232).
      supported_by:
        - reference_id: PMID:11748232
          supporting_text: Dec 17. HMGB1 and HMGB2 cell-specifically 
            down-regulate the p53- and p73-dependent sequence-specific 
            transactivation from the human Bax gene promoter.
  - term:
      id: GO:0050786
      label: RAGE receptor binding
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binds RAGE receptor.
      action: ACCEPT
      reason: Core alarmin function. RAGE binding is essential for many HMGB1 
        extracellular effects.
  - term:
      id: GO:0001773
      label: myeloid dendritic cell activation
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 activates dendritic cells.
      action: KEEP_AS_NON_CORE
      reason: Downstream effect of alarmin signaling. ISS evidence.
  - term:
      id: GO:0002407
      label: dendritic cell chemotaxis
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 promotes dendritic cell chemotaxis.
      action: KEEP_AS_NON_CORE
      reason: Downstream pleiotropic effect. ISS evidence.
  - term:
      id: GO:0002437
      label: inflammatory response to antigenic stimulus
    evidence_type: IEP
    original_reference_id: PMID:19841752
    review:
      summary: HMGB1 elevated during inflammatory response to antigen.
      action: ACCEPT
      reason: Valid IEP evidence. HMGB1 elevated in inflammatory contexts.
      supported_by:
        - reference_id: PMID:19841752
          supporting_text: 'Linking innate and adaptive immunity: human Vgamma9Vdelta2
            T cells enhance CD40 expression and HMGB-1 secretion.'
  - term:
      id: GO:0003684
      label: damaged DNA binding
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binds damaged DNA.
      action: ACCEPT
      reason: Core function. ISS evidence supporting damaged DNA binding.
  - term:
      id: GO:0005125
      label: cytokine activity
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 has cytokine activity.
      action: ACCEPT
      reason: Core extracellular function. Disulfide HMGB1 has cytokine-like 
        activity. ISS evidence.
  - term:
      id: GO:0033151
      label: V(D)J recombination
    evidence_type: IDA
    original_reference_id: PMID:9166431
    review:
      summary: HMGB1 is a cofactor in V(D)J recombination.
      action: ACCEPT
      reason: Core nuclear function. HMGB1 stimulates RAG cleavage in V(D)J 
        recombination (PMID:9166431).
      supported_by:
        - reference_id: PMID:9166431
          supporting_text: 'V(D)J recombination: modulation of RAG1 and RAG2 cleavage
            activity on 12/23 substrates by whole cell extract and DNA-bending proteins.'
  - term:
      id: GO:0042056
      label: chemoattractant activity
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 has chemoattractant activity.
      action: ACCEPT
      reason: Core extracellular function. All-thiol HMGB1 with CXCL12 is 
        chemotactic. ISS evidence.
  - term:
      id: GO:0043065
      label: positive regulation of apoptotic process
    evidence_type: IDA
    original_reference_id: PMID:19800306
    review:
      summary: HMGB1 can promote apoptosis in certain contexts.
      action: KEEP_AS_NON_CORE
      reason: Context-dependent effect (PMID:19800306). Not a core function.
      supported_by:
        - reference_id: PMID:19800306
          supporting_text: Epub 2009 Oct 1. Effect of high mobility group box-1 
            protein on apoptosis of peritoneal macrophages.
  - term:
      id: GO:0003690
      label: double-stranded DNA binding
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binds double-stranded DNA through its HMG-box domains A and
        B. This is a well-established core function.
      action: ACCEPT
      reason: DNA binding is a fundamental function of HMGB1. The protein binds 
        dsDNA through its HMG-box domains (PMID:8339930). ISS transfer from 
        ortholog is appropriate.
      supported_by:
        - reference_id: PMID:8339930
          supporting_text: "The mammalian high mobility group proteins HMG1 and HMG2
            are abundant, chromatin-associated proteins"
  - term:
      id: GO:0003697
      label: single-stranded DNA binding
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 has been shown to bind single-stranded DNA in addition to 
        dsDNA through its HMG-box domains.
      action: ACCEPT
      reason: HMGB1 binds various DNA structures including ssDNA. ISS transfer 
        from ortholog data is appropriate given the conserved DNA-binding 
        HMG-box domains.
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:11748232
    review:
      summary: This study demonstrates HMGB1 physically interacts with p53 and 
        p73 transcription factors, enhancing their DNA binding. The generic 
        protein binding term should be replaced with a more specific term.
      action: MODIFY
      reason: HMGB1 interacts with p53 and p73 transcription factors to modulate
        their DNA binding activity (PMID:11748232). The generic protein binding 
        term is uninformative; a more specific term for transcription factor 
        binding is appropriate.
      proposed_replacement_terms:
        - id: GO:0140297
          label: DNA-binding transcription factor binding
      supported_by:
        - reference_id: PMID:11748232
          supporting_text: "HMGB1 physically interacts with two splicing variants
            of p73, alpha and beta (pull-down assay), and enhances binding of p73
            to specific cognate DNA sites"
  - term:
      id: GO:0005634
      label: nucleus
    evidence_type: IDA
    original_reference_id: PMID:19223331
    review:
      summary: HMGB1 is a chromatin-associated nuclear protein that shuttles 
        between nucleus and cytoplasm. Nuclear localization is well-established.
      action: ACCEPT
      reason: Nuclear localization is a core characteristic of HMGB1 as a 
        chromatin-associated protein (PMID:19223331). The protein is 
        predominantly nuclear in basal state.
      supported_by:
        - reference_id: PMID:19223331
          supporting_text: "HMGB1 is associated with chromosomes in mitosis and due
            to its extreme mobility in the cell the protein is continuously exchanged
            between nucleus and cytoplasm"
  - term:
      id: GO:0006265
      label: DNA topological change
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 binding causes DNA bending and topological changes. The 
        protein can promote DNA circularization and alter DNA topology.
      action: ACCEPT
      reason: HMGB1 induces DNA topological changes through its DNA-bending 
        activity (PMID:8339930). This is a core biochemical function 
        demonstrated by circularization assays.
      supported_by:
        - reference_id: PMID:8339930
          supporting_text: "HMG1 and HMG2 can bend DNA extremely efficiently, forming
            circles as small as 66 bp"
  - term:
      id: GO:0006310
      label: DNA recombination
    evidence_type: ISS
    original_reference_id: GO_REF:0000024
    review:
      summary: HMGB1 participates in DNA recombination including V(D)J 
        recombination by facilitating DNA bending and promoting assembly of 
        nucleoprotein complexes.
      action: ACCEPT
      reason: HMGB1 promotes DNA recombination by facilitating DNA flexibility 
        and nucleoprotein complex assembly (PMID:8339930). This is a core 
        nuclear function.
      supported_by:
        - reference_id: PMID:8339930
          supporting_text: "these proteins can substitute for the prokaryotic DNA-bending
            protein HU in promoting the assembly of the Hin invertasome, an intermediate
            structure in Hin-mediated site-specific DNA inversion"
  - term:
      id: GO:0008301
      label: DNA binding, bending
    evidence_type: IMP
    original_reference_id: PMID:19223331
    review:
      summary: HMGB1 DNA bending is a core function. The study showed that 
        HMGB1, but not a mutant incapable of DNA bending, activates the topo 
        IIalpha promoter.
      action: ACCEPT
      reason: DNA bending is a fundamental function of HMGB1 demonstrated by IMP
        evidence. The study shows DNA bending is required for HMGB1 to activate 
        topo IIalpha promoter (PMID:19223331).
      supported_by:
        - reference_id: PMID:19223331
          supporting_text: "HMGB1, but not a mutant of HMGB1 incapable of DNA bending,
            up-regulates the activity of the topo IIalpha promoter in human cells"
  - term:
      id: GO:0043388
      label: positive regulation of DNA binding
    evidence_type: IDA
    original_reference_id: PMID:19223331
    review:
      summary: HMGB1 enhances DNA binding of transcription factors like NF-Y and
        p53/p73 family members by modulating DNA structure.
      action: ACCEPT
      reason: HMGB1 positively regulates DNA binding by modulating transcription
        factor NF-Y binding to promoters (PMID:19223331). This is a core 
        function related to its transcriptional coregulator role.
      supported_by:
        - reference_id: PMID:19223331
          supporting_text: "Our experiments suggest a mechanism of up-regulation of
            cellular expression of topo IIalpha by HMGB1/2 in pRb-negative cells by
            modulation of binding of transcription factor NF-Y to the topo IIalpha
            promoter"
  - term:
      id: GO:0045944
      label: positive regulation of transcription by RNA polymerase II
    evidence_type: IDA
    original_reference_id: PMID:19223331
    review:
      summary: HMGB1 upregulates topo IIalpha promoter activity through 
        luciferase reporter assays in pRb-negative cells.
      action: ACCEPT
      reason: HMGB1 positively regulates transcription by RNA pol II as 
        demonstrated by luciferase reporter assays showing upregulation of topo 
        IIalpha promoter (PMID:19223331). This is a core transcriptional 
        coregulator function.
      supported_by:
        - reference_id: PMID:19223331
          supporting_text: "Using luciferase gene reporter assay we have demonstrated
            that HMGB1, but not a mutant of HMGB1 incapable of DNA bending, up-regulated
            the activity of human topo IIalpha promoter in human cells that lack functional
            retinoblastoma protein pRb"
  - term:
      id: GO:0140297
      label: DNA-binding transcription factor binding
    evidence_type: IPI
    original_reference_id: PMID:19223331
    review:
      summary: HMGB1 interacts with transcription factors including NF-Y to 
        modulate their DNA binding activity and transcriptional output.
      action: ACCEPT
      reason: HMGB1 interacts with and modulates the activity of DNA-binding 
        transcription factors like NF-Y (PMID:19223331) and p53/p73 family 
        members. This is a specific and accurate molecular function term.
      supported_by:
        - reference_id: PMID:19223331
          supporting_text: "HMGB1 also interacts weakly with a number of proteins,
            including transcriptional factors, site-specific recombination and DNA
            repair proteins"
  - term:
      id: GO:0005634
      label: nucleus
    evidence_type: IDA
    original_reference_id: PMID:8339930
    review:
      summary: HMGB1 is an abundant chromatin-associated nuclear protein. 
        Nuclear localization is fundamental to its function.
      action: ACCEPT
      reason: Nuclear localization is a core characteristic of HMGB1 as an 
        abundant chromatin-associated protein (PMID:8339930). This is 
        well-established and fundamental to its biological role.
      supported_by:
        - reference_id: PMID:8339930
          supporting_text: "The mammalian high mobility group proteins HMG1 and HMG2
            are abundant, chromatin-associated proteins"
  - term:
      id: GO:0000793
      label: condensed chromosome
    evidence_type: IDA
    original_reference_id: PMID:12925773
    review:
      summary: HMGB1 associates with condensed chromosomes during mitosis. Live 
        cell imaging shows the protein exchanges rapidly between free and 
        chromosome-bound forms.
      action: ACCEPT
      reason: HMGB1 associates with condensed chromatin during mitosis as shown 
        by fluorescent protein tagging in live cells (PMID:12925773). This is a 
        core function related to its chromatin-binding role.
      supported_by:
        - reference_id: PMID:12925773
          supporting_text: "HMGB1 and 2 were shown to be present under two forms in
            mitotic cells, i.e., free and associated with the condensed chromatin,
            which rapidly exchange"
  - term:
      id: GO:0005515
      label: protein binding
    evidence_type: IPI
    original_reference_id: PMID:8006019
    review:
      summary: This study demonstrates HMGB1 physically interacts with TBP 
        (TATA-binding protein) to inhibit preinitiation complex assembly. The 
        generic term should be replaced with a more specific binding term.
      action: MODIFY
      reason: HMGB1 interacts with TBP to form an HMG1.TBP.promoter complex that
        blocks TFIIB binding (PMID:8006019). The generic protein binding term is
        uninformative; a more specific term for transcription machinery 
        component binding is appropriate.
      proposed_replacement_terms:
        - id: GO:0140297
          label: DNA-binding transcription factor binding
      supported_by:
        - reference_id: PMID:8006019
          supporting_text: "purified mammalian HMG1, as well as recombinant human
            HMG1, can interact with TATA-binding protein (TBP) in the presence of
            a TATA box-containing oligonucleotide to form a specific HMG1.TBP.promoter
            complex"
  - term:
      id: GO:0017055
      label: negative regulation of RNA polymerase II transcription 
        preinitiation complex assembly
    evidence_type: IDA
    original_reference_id: PMID:8006019
    review:
      summary: HMGB1 interacts with TBP to form a complex that prevents TFIIB 
        binding and blocks preinitiation complex formation. In vitro, HMGB1 
        inhibits transcription by RNA pol II over 30-fold.
      action: ACCEPT
      reason: HMGB1 inhibits preinitiation complex assembly by binding TBP and 
        blocking TFIIB recruitment (PMID:8006019). This is a well-characterized 
        transcriptional regulatory function with direct assay evidence.
      supported_by:
        - reference_id: PMID:8006019
          supporting_text: "This complex prevents TFIIB binding to TBP and consequently
            blocks formation of the preinitiation complex"
core_functions:
  - molecular_function:
      id: GO:0008301
      label: DNA binding, bending
    description: >-
      HMGB1 binds and bends DNA through its two HMG-box domains (A and B). DNA bending
      is
      essential for its function as demonstrated by mutant studies showing that HMGB1
      incapable
      of DNA bending fails to activate target promoters (PMID:19223331). The protein
      can bend
      DNA to form circles as small as 66 bp (PMID:8339930).
    directly_involved_in:
      - id: GO:0006265
        label: DNA topological change
    locations:
      - id: GO:0005634
        label: nucleus
  - molecular_function:
      id: GO:0140297
      label: DNA-binding transcription factor binding
    description: >-
      HMGB1 acts as a transcriptional coregulator by binding transcription factors
      (p53, p73,
      NF-Y, TBP) and modulating their DNA binding activity. It can both positively
      and negatively
      regulate transcription depending on cellular context (PMID:8006019, PMID:19223331,
      PMID:11748232).
    directly_involved_in:
      - id: GO:0045944
        label: positive regulation of transcription by RNA polymerase II
    locations:
      - id: GO:0005634
        label: nucleus
  - molecular_function:
      id: GO:0005125
      label: cytokine activity
    description: >-
      Extracellular HMGB1 acts as a DAMP/alarmin released from necrotic or activated
      cells,
      signaling through TLR4, TLR2, RAGE, and CXCR4 (via CXCL12 heterocomplex) to
      promote
      inflammation and chemotaxis. The all-thiol redox form is chemotactic, the disulfide
      form
      induces cytokine production, and the fully oxidized form is inactive.
    directly_involved_in:
      - id: GO:0006954
        label: inflammatory response
    locations:
      - id: GO:0005576
        label: extracellular region
references:
  - id: GO_REF:0000024
    title: Manual transfer of experimentally-verified manual GO annotation data 
      to orthologs by curator judgment of sequence similarity
    findings: []
  - id: GO_REF:0000033
    title: Annotation inferences using phylogenetic trees
    findings: []
  - id: GO_REF:0000043
    title: Gene Ontology annotation based on UniProtKB/Swiss-Prot keyword 
      mapping
    findings: []
  - id: GO_REF:0000044
    title: Gene Ontology annotation based on UniProtKB/Swiss-Prot Subcellular 
      Location vocabulary mapping, accompanied by conservative changes to GO 
      terms applied by UniProt
    findings: []
  - id: GO_REF:0000052
    title: Gene Ontology annotation based on curation of immunofluorescence data
    findings: []
  - id: GO_REF:0000107
    title: Automatic transfer of experimentally verified manual GO annotation 
      data to orthologs using Ensembl Compara
    findings: []
  - id: GO_REF:0000108
    title: Automatic assignment of GO terms using logical inference, based on on
      inter-ontology links
    findings: []
  - id: GO_REF:0000117
    title: Electronic Gene Ontology annotations created by ARBA machine learning
      models
    findings: []
  - id: GO_REF:0000120
    title: Combined Automated Annotation using Multiple IEA Methods
    findings: []
  - id: PMID:11748232
    title: HMGB1 and HMGB2 cell-specifically down-regulate the p53- and 
      p73-dependent sequence-specific transactivation from the human Bax gene 
      promoter.
    findings: []
  - id: PMID:12765338
    title: Structural basis for the proinflammatory cytokine activity of high 
      mobility group box 1.
    findings: []
  - id: PMID:12925773
    title: Association of chromatin proteins high mobility group box (HMGB) 1 
      and HMGB2 with mitotic chromosomes.
    findings: []
  - id: PMID:15014079
    title: Evidence for involvement of HMGB1 protein in human DNA mismatch 
      repair.
    findings: []
  - id: PMID:15379539
    title: The long acidic tail of high mobility group box 1 (HMGB1) protein 
      forms an extended and flexible structure that interacts with specific 
      residues within and between the HMG boxes.
    findings: []
  - id: PMID:15944249
    title: Release of high mobility group box 1 by dendritic cells controls T 
      cell activation via the receptor for advanced glycation end products.
    findings: []
  - id: PMID:17568691
    title: Endogenous signals released from necrotic cells augment inflammatory 
      responses to bacterial endotoxin.
    findings: []
  - id: PMID:17803946
    title: HMGB1 is a cofactor in mammalian base excision repair.
    findings: []
  - id: PMID:18631454
    title: Induction of immunological tolerance by apoptotic cells requires 
      caspase-dependent oxidation of high-mobility group box-1 protein.
    findings: []
  - id: PMID:18768881
    title: High mobility group protein-1 inhibits phagocytosis of apoptotic 
      neutrophils through binding to phosphatidylserine.
    findings: []
  - id: PMID:19158276
    title: Chromatin-specific remodeling by HMGB1 and linker histone H1 silences
      proinflammatory genes during endotoxin tolerance.
    findings: []
  - id: PMID:19223331
    title: HMGB1 and HMGB2 proteins up-regulate cellular expression of human 
      topoisomerase IIalpha.
    findings: []
  - id: PMID:19505873
    title: Complementary quantitative proteomics reveals that transcription 
      factor AP-4 mediates E-box-dependent complex formation for transcriptional
      repression of HDM2.
    findings: []
  - id: PMID:19800306
    title: Effect of high mobility group box-1 protein on apoptosis of 
      peritoneal macrophages.
    findings: []
  - id: PMID:19841752
    title: 'Linking innate and adaptive immunity: human Vgamma9Vdelta2 T cells enhance
      CD40 expression and HMGB-1 secretion.'
    findings: []
  - id: PMID:20819940
    title: Endogenous HMGB1 regulates autophagy.
    findings: []
  - id: PMID:20826760
    title: HMGB1 inhibits macrophage activity in efferocytosis through binding 
      to the alphavbeta3-integrin.
    findings: []
  - id: PMID:21660935
    title: Identification of lipopolysaccharide-binding peptide regions within 
      HMGB1 and their effects on subclinical endotoxemia in a mouse model.
    findings: []
  - id: PMID:22370717
    title: HMGB1 promotes recruitment of inflammatory cells to damaged tissues 
      by forming a complex with CXCL12 and signaling via CXCR4.
    findings: []
  - id: PMID:22473704
    title: HMGB1 conveys immunosuppressive characteristics on regulatory and 
      conventional T cells.
    findings: []
  - id: PMID:22658674
    title: Insights into RNA biology from an atlas of mammalian mRNA-binding 
      proteins.
    findings: []
  - id: PMID:22681889
    title: The mRNA-bound proteome and its global occupancy profile on 
      protein-coding transcripts.
    findings: []
  - id: PMID:23063560
    title: HMGB1-facilitated p53 DNA binding occurs via HMG-Box/p53 
      transactivation domain interaction, regulated by the acidic tail.
    findings: []
  - id: PMID:23146691
    title: Emodin-6-O-β-D-glucoside inhibits HMGB1-induced inflammatory 
      responses in vitro and in vivo.
    findings: []
  - id: PMID:23148224
    title: High mobility group Box 1 inhibits human pulmonary artery endothelial
      cell migration via a Toll-like receptor 4- and interferon response factor 
      3-dependent mechanism(s).
    findings: []
  - id: PMID:23303669
    title: Chaperone-like activity of high-mobility group box 1 protein and its 
      role in reducing the formation of polyglutamine aggregates.
    findings: []
  - id: PMID:24474694
    title: An immunogenic peptide in the A-box of HMGB1 protein reverses 
      apoptosis-induced tolerance through RAGE receptor.
    findings: []
  - id: PMID:24971542
    title: HMGB1-DNA complex-induced autophagy limits AIM2 inflammasome 
      activation through RAGE.
    findings: []
  - id: PMID:25416956
    title: A proteome-scale map of the human interactome network.
    findings: []
  - id: PMID:25595774
    title: 'Cutting Edge: identification of neutrophil PGLYRP1 as a ligand for TREM-1.'
    findings: []
  - id: PMID:26961863
    title: AGEs and HMGB1 Increase Inflammatory Cytokine Production from Human 
      Placental Cells, Resulting in an Enhancement of Monocyte Migration.
    findings: []
  - id: PMID:28276476
    title: miR-193a-3p interaction with HMGB1 downregulates human endothelial 
      cell proliferation and migration.
    findings: []
  - id: PMID:28514442
    title: Architecture of the human interactome defines protein communities and
      disease networks.
    findings: []
  - id: PMID:29721183
    title: Delineating the HMGB1 and HMGB2 interactome in prostate and ovary 
      epithelial cells and its relationship with cancer.
    findings: []
  - id: PMID:31694235
    title: 'Characterization of HMGB1/2 Interactome in Prostate Cancer by Yeast Two
      Hybrid Approach: Potential Pathobiological Implications.'
    findings: []
  - id: PMID:32296183
    title: A reference map of the human binary protein interactome.
    findings: []
  - id: PMID:32814053
    title: Interactome Mapping Provides a Network of Neurodegenerative Disease 
      Proteins and Uncovers Widespread Protein Aggregation in Affected Brains.
    findings: []
  - id: PMID:32867128
    title: The HMGB1-2 Ovarian Cancer Interactome. The Role of HMGB Proteins and
      Their Interacting Partners MIEN1 and NOP53 in Ovary Cancer and 
      Drug-Response.
    findings: []
  - id: PMID:33147444
    title: Genome-wide CRISPR Screens Reveal Host Factors Critical for 
      SARS-CoV-2 Infection.
    findings: []
  - id: PMID:33961781
    title: Dual proteome-scale networks reveal cell-specific remodeling of the 
      human interactome.
    findings: []
  - id: PMID:35239449
    title: SARS-CoV-2 ORF3a induces RETREG1/FAM134B-dependent reticulophagy and 
      triggers sequential ER stress and inflammatory responses during SARS-CoV-2
      infection.
    findings: []
  - id: PMID:40205054
    title: Multimodal cell maps as a foundation for structural and functional 
      genomics.
    findings: []
  - id: PMID:8006019
    title: The high mobility group protein HMG1 can reversibly inhibit class II 
      gene transcription by interaction with the TATA-binding protein.
    findings: []
  - id: PMID:8339930
    title: The nonspecific DNA-binding and -bending proteins HMG1 and HMG2 
      promote the assembly of complex nucleoprotein structures.
    findings: []
  - id: PMID:9166431
    title: 'V(D)J recombination: modulation of RAG1 and RAG2 cleavage activity on
      12/23 substrates by whole cell extract and DNA-bending proteins.'
    findings: []
  - id: PMID:9472015
    title: High mobility group protein-1 (HMG-1) is a unique activator of p53.
    findings: []
  - id: Reactome:R-HSA-166072
    title: MyD88 forms a complex with TIRAP:activated TLR2/4
    findings: []
  - id: Reactome:R-HSA-166082
    title: IRAK4 binds to the activated TLR receptor:TIRAP:MyD88 complex
    findings: []
  - id: Reactome:R-HSA-166091
    title: IRAK1 or IRAK2 binds to the activated IRAK4 :activated 
      TLR:MyD88:TIRAP complex
    findings: []
  - id: Reactome:R-HSA-166119
    title: First phosphorylation of IRAK1 by IRAK4 bound to activated 
      TLR:MyD88:Mal
    findings: []
  - id: Reactome:R-HSA-166284
    title: Second phosphorylation of IRAK1 by IRAK4 bound to activated 
      TLR:MyD88:TIRAP
    findings: []
  - id: Reactome:R-HSA-166286
    title: Multiple IRAK1 autophosphorylation steps
    findings: []
  - id: Reactome:R-HSA-166362
    title: Dissociation of hp-IRAK1:TRAF6 from the activated 
      TLR:oligo-Myd88:TIRAP:p-IRAK4 complex
    findings: []
  - id: Reactome:R-HSA-166363
    title: TRAF6 binds to hp- IRAK1
    findings: []
  - id: Reactome:R-HSA-2201316
    title: Activated TLR2/4 interacts with MAL (TIRAP)
    findings: []
  - id: Reactome:R-HSA-2201322
    title: TIRAP is phosphorylated by BTK
    findings: []
  - id: Reactome:R-HSA-2262775
    title: Dissociation of p-IRAK2:TRAF6 from the activated 
      TLR:oligo-Myd88:TIRAP:p-IRAK4 complex
    findings: []
  - id: Reactome:R-HSA-2262777
    title: TRAF6 binds to p-IRAK2
    findings: []
  - id: Reactome:R-HSA-2559414
    title: Activated TLR2/4:TIRAP interacts with BTK
    findings: []
  - id: Reactome:R-HSA-266204
    title: Association of HMGB1/HMGB2 with chromatin
    findings: []
  - id: Reactome:R-HSA-5432825
    title: HMGB1 binds TLR4:LY96
    findings: []
  - id: Reactome:R-HSA-5602353
    title: Defective IRAK4 does not bind MyD88:MAL:BTK:activated TLR2/4
    findings: []
  - id: Reactome:R-HSA-5602383
    title: Defective MyD88 does not oligomerize within the activated TLR2/4 
      complex
    findings: []
  - id: Reactome:R-HSA-5602606
    title: Defective MyD88 does not bind MAL(TIRAP):TLR2/4
    findings: []
  - id: Reactome:R-HSA-6798748
    title: Exocytosis of secretory granule lumen proteins
    findings: []
  - id: Reactome:R-HSA-6800434
    title: Exocytosis of ficolin-rich granule lumen proteins
    findings: []
  - id: Reactome:R-HSA-6804099
    title: HMGB1 binds LTP
    findings: []
  - id: Reactome:R-HSA-6804100
    title: HMGB1 binds LPS
    findings: []
  - id: Reactome:R-HSA-6805981
    title: HMGB1 release from cells
    findings: []
  - id: Reactome:R-HSA-879411
    title: Advanced glycosylation end product-specific receptor (AGER/RAGE) is a
      multiligand receptor
    findings: []
  - id: Reactome:R-HSA-937022
    title: IRAK4 autophosphorylation in the complex with activated 
      TLR:MyD88:TIRAP
    findings: []
  - id: Reactome:R-HSA-937059
    title: Phosphorylation of IRAK2 bound to the activated IRAK4:MyD88 
      oligomer:TIRAP:activated TLR complex
    findings: []
  - id: Reactome:R-HSA-937079
    title: MyD88 oligomerization within the complex of activated TLR:TIRAP:MyD88
    findings: []
  - id: Reactome:R-NUL-997411
    title: AGER binds rat ERK1/2
    findings: []
  - id: file:human/HMGB1/HMGB1-deep-research-falcon.md
    title: Deep research report on HMGB1
    findings: []