SAMM50

UniProt ID: Q9Y512
Organism: Homo sapiens
Review Status: COMPLETE
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Gene Description

SAMM50 encodes the human Sam50/SAM50 Omp85-family beta-barrel subunit of the mitochondrial sorting and assembly machinery (SAM) complex. It is an outer mitochondrial membrane insertase for beta-barrel proteins such as TOM40 and VDACs and also participates in SAM-MICOS/MIB contact sites that link outer-membrane beta-barrel biogenesis to cristae organization.

Existing Annotations Review

GO Term Evidence Action Reason
GO:0001401 SAM complex
IBA
GO_REF:0000033
ACCEPT
Summary: SAMM50 is the conserved core beta-barrel subunit of the mitochondrial SAM complex.
Reason: SAM complex membership is a core cellular component annotation for SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
GO:0045040 protein insertion into mitochondrial outer membrane
IBA
GO_REF:0000033
ACCEPT
Summary: SAMM50/SAM inserts and assembles mitochondrial outer-membrane beta-barrel proteins such as TOM40 and VDAC.
Reason: Protein insertion into the mitochondrial outer membrane captures the central biological process of SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
file:human/SAMM50/SAMM50-deep-research-falcon.md
**Primary function:** SAMM50 is the core insertase/chaperone of the SAM complex that assembles **mitochondrial outer membrane β-barrel proteins** (including **Tom40** and **VDACs**) in an **energy-independent** manner. (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005737 cytoplasm
IEA
GO_REF:0000044
REMOVE
Summary: SAMM50 is an outer mitochondrial membrane beta-barrel protein, not a cytoplasmic protein.
Reason: The cytoplasm annotation conflicts with the curated outer mitochondrial membrane localization and likely reflects a broad or transferred location call.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005739 mitochondrion
IEA
GO_REF:0000044
MODIFY
Summary: SAMM50 is mitochondrial, but the literature supports the more specific outer mitochondrial membrane localization.
Reason: Use mitochondrial outer membrane rather than the broad parent term mitochondrion.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005741 mitochondrial outer membrane
IEA
GO_REF:0000044
ACCEPT
Summary: SAMM50 is an outer mitochondrial membrane Omp85-family beta-barrel protein.
Reason: Outer mitochondrial membrane localization is central to SAMM50 topology and function.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0019867 outer membrane
IEA
GO_REF:0000002
MODIFY
Summary: SAMM50 is in an outer membrane, specifically the mitochondrial outer membrane.
Reason: The taxon/gene-specific evidence supports mitochondrial outer membrane as the precise location.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005515 protein binding
IPI
PMID:25416956
A proteome-scale map of the human interactome network.
MARK AS OVER ANNOTATED
Summary: SAMM50 has many physical partners in SAM, TOM, MICOS/MIB, and contact-site assemblies, but generic protein binding is less informative than its insertase and complex annotations.
Reason: Retain specific SAM complex, MIB/contact-site, and membrane insertase annotations rather than broad protein binding.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0005515 protein binding
IPI
PMID:27059175
SAMM50 Affects Mitochondrial Morphology through the Associat...
MARK AS OVER ANNOTATED
Summary: SAMM50 has many physical partners in SAM, TOM, MICOS/MIB, and contact-site assemblies, but generic protein binding is less informative than its insertase and complex annotations.
Reason: Retain specific SAM complex, MIB/contact-site, and membrane insertase annotations rather than broad protein binding.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0005515 protein binding
IPI
PMID:32296183
A reference map of the human binary protein interactome.
MARK AS OVER ANNOTATED
Summary: SAMM50 has many physical partners in SAM, TOM, MICOS/MIB, and contact-site assemblies, but generic protein binding is less informative than its insertase and complex annotations.
Reason: Retain specific SAM complex, MIB/contact-site, and membrane insertase annotations rather than broad protein binding.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0005515 protein binding
IPI
PMID:33961781
Dual proteome-scale networks reveal cell-specific remodeling...
MARK AS OVER ANNOTATED
Summary: SAMM50 has many physical partners in SAM, TOM, MICOS/MIB, and contact-site assemblies, but generic protein binding is less informative than its insertase and complex annotations.
Reason: Retain specific SAM complex, MIB/contact-site, and membrane insertase annotations rather than broad protein binding.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0005739 mitochondrion
IDA
GO_REF:0000052
MODIFY
Summary: SAMM50 is mitochondrial, but the literature supports the more specific outer mitochondrial membrane localization.
Reason: Use mitochondrial outer membrane rather than the broad parent term mitochondrion.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005737 cytoplasm
ISS
GO_REF:0000024
REMOVE
Summary: SAMM50 is an outer mitochondrial membrane beta-barrel protein, not a cytoplasmic protein.
Reason: The cytoplasm annotation conflicts with the curated outer mitochondrial membrane localization and likely reflects a broad or transferred location call.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0001401 SAM complex
IPI
PMID:17510655
Conserved roles of Sam50 and metaxins in VDAC biogenesis.
ACCEPT
Summary: SAMM50 is the conserved core beta-barrel subunit of the mitochondrial SAM complex.
Reason: SAM complex membership is a core cellular component annotation for SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
GO:0005741 mitochondrial outer membrane
NAS
PMID:31387448
Mitochondria-hubs for regulating cellular biochemistry: emer...
ACCEPT
Summary: SAMM50 is an outer mitochondrial membrane Omp85-family beta-barrel protein.
Reason: Outer mitochondrial membrane localization is central to SAMM50 topology and function.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0045040 protein insertion into mitochondrial outer membrane
NAS
PMID:31387448
Mitochondria-hubs for regulating cellular biochemistry: emer...
ACCEPT
Summary: SAMM50/SAM inserts and assembles mitochondrial outer-membrane beta-barrel proteins such as TOM40 and VDAC.
Reason: Protein insertion into the mitochondrial outer membrane captures the central biological process of SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
file:human/SAMM50/SAMM50-deep-research-falcon.md
**Primary function:** SAMM50 is the core insertase/chaperone of the SAM complex that assembles **mitochondrial outer membrane β-barrel proteins** (including **Tom40** and **VDACs**) in an **energy-independent** manner. (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0030150 protein import into mitochondrial matrix
IDA
PMID:15644312
Dissection of the mitochondrial import and assembly pathway ...
MODIFY
Summary: SAMM50 handles outer-membrane beta-barrel substrates after TOM translocation, not matrix-targeted presequence import through TIM23.
Reason: The original Tom40 pathway evidence is better captured by protein insertion into mitochondrial outer membrane.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
file:human/SAMM50/SAMM50-deep-research-falcon.md
**Primary function:** SAMM50 is the core insertase/chaperone of the SAM complex that assembles **mitochondrial outer membrane β-barrel proteins** (including **Tom40** and **VDACs**) in an **energy-independent** manner. (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005739 mitochondrion
HTP
PMID:34800366
Quantitative high-confidence human mitochondrial proteome an...
MODIFY
Summary: SAMM50 is mitochondrial, but the literature supports the more specific outer mitochondrial membrane localization.
Reason: Use mitochondrial outer membrane rather than the broad parent term mitochondrion.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005515 protein binding
IPI
PMID:31644573
Armadillo repeat-containing protein 1 is a dual localization...
MARK AS OVER ANNOTATED
Summary: SAMM50 has many physical partners in SAM, TOM, MICOS/MIB, and contact-site assemblies, but generic protein binding is less informative than its insertase and complex annotations.
Reason: Retain specific SAM complex, MIB/contact-site, and membrane insertase annotations rather than broad protein binding.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0001401 SAM complex
HDA
PMID:26477565
Evolution and structural organization of the mitochondrial c...
ACCEPT
Summary: SAMM50 is the conserved core beta-barrel subunit of the mitochondrial SAM complex.
Reason: SAM complex membership is a core cellular component annotation for SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
GO:0007007 inner mitochondrial membrane organization
IC
PMID:26477565
Evolution and structural organization of the mitochondrial c...
KEEP AS NON CORE
Summary: SAMM50 contributes to inner-membrane/cristae architecture through SAM-MICOS/MIB contact sites, but this is secondary to its core SAM insertase role.
Reason: The annotation is supported as a downstream organizational role of the MIB/SAM-MICOS axis rather than the primary evolved molecular function.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0140275 MIB complex
HDA
PMID:26477565
Evolution and structural organization of the mitochondrial c...
KEEP AS NON CORE
Summary: SAMM50 participates in the mitochondrial intermembrane-space bridging (MIB) complex/contact-site axis with MICOS components.
Reason: MIB complex association is supported but is treated as a contact-site/architecture role secondary to SAM beta-barrel insertion.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0005739 mitochondrion
IDA
PMID:25781180
Detailed analysis of the human mitochondrial contact site co...
MODIFY
Summary: SAMM50 is mitochondrial, but the literature supports the more specific outer mitochondrial membrane localization.
Reason: Use mitochondrial outer membrane rather than the broad parent term mitochondrion.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0042407 cristae formation
IMP
PMID:22252321
Sam50 functions in mitochondrial intermembrane space bridgin...
KEEP AS NON CORE
Summary: SAMM50 perturbation affects cristae organization through SAM-MICOS/MIB contact sites.
Reason: Cristae formation is a supported cellular architecture consequence, but the core SAMM50 function remains outer-membrane beta-barrel insertion.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0042407 cristae formation
IMP
PMID:25781180
Detailed analysis of the human mitochondrial contact site co...
KEEP AS NON CORE
Summary: SAMM50 perturbation affects cristae organization through SAM-MICOS/MIB contact sites.
Reason: Cristae formation is a supported cellular architecture consequence, but the core SAMM50 function remains outer-membrane beta-barrel insertion.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0005739 mitochondrion
HDA
PMID:20833797
Phosphoproteome analysis of functional mitochondria isolated...
MODIFY
Summary: SAMM50 is mitochondrial, but the literature supports the more specific outer mitochondrial membrane localization.
Reason: Use mitochondrial outer membrane rather than the broad parent term mitochondrion.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0070062 extracellular exosome
HDA
PMID:19056867
Large-scale proteomics and phosphoproteomics of urinary exos...
REMOVE
Summary: The curated literature supports mitochondrial outer membrane localization and SAM complex function, not extracellular exosome localization.
Reason: This high-throughput exosome annotation is not supported by gene-specific functional evidence for SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0016020 membrane
IDA
PMID:15644312
Dissection of the mitochondrial import and assembly pathway ...
MODIFY
Summary: SAMM50 is a membrane protein, specifically a mitochondrial outer membrane beta-barrel protein.
Reason: Use mitochondrial outer membrane rather than generic membrane.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005515 protein binding
IPI
PMID:21081504
ChChd3, an inner mitochondrial membrane protein, is essentia...
MARK AS OVER ANNOTATED
Summary: SAMM50 has many physical partners in SAM, TOM, MICOS/MIB, and contact-site assemblies, but generic protein binding is less informative than its insertase and complex annotations.
Reason: Retain specific SAM complex, MIB/contact-site, and membrane insertase annotations rather than broad protein binding.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
**SAM–MICOS contact site / MIB axis (cristae junction biology):** SAM is also described as an interaction hub forming a defined **outer–inner membrane contact** with **MICOS**, notably via interaction between Sam50 and MICOS subunits (e.g., Mic60/Mic19), thereby linking β-barrel biogenesis to **cristae organization** and mitochondrial architecture. (ravi2025mitochondrialsortingand pages 8-10, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)
GO:0001401 SAM complex
IMP
PMID:15644312
Dissection of the mitochondrial import and assembly pathway ...
ACCEPT
Summary: SAMM50 is the conserved core beta-barrel subunit of the mitochondrial SAM complex.
Reason: SAM complex membership is a core cellular component annotation for SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
GO:0005739 mitochondrion
IDA
PMID:15644312
Dissection of the mitochondrial import and assembly pathway ...
MODIFY
Summary: SAMM50 is mitochondrial, but the literature supports the more specific outer mitochondrial membrane localization.
Reason: Use mitochondrial outer membrane rather than the broad parent term mitochondrion.
Proposed replacements: mitochondrial outer membrane
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0005741 mitochondrial outer membrane
IDA
PMID:15644312
Dissection of the mitochondrial import and assembly pathway ...
ACCEPT
Summary: SAMM50 is an outer mitochondrial membrane Omp85-family beta-barrel protein.
Reason: Outer mitochondrial membrane localization is central to SAMM50 topology and function.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The target in this report is **human SAMM50** (UniProt **Q9Y512**), annotated as **Sorting and assembly machinery component 50 homolog** (also called **SAM50**; synonym **TRG-3 / transformation-related gene 3**) and belonging to the **SAM50/Omp85** family that mediates mitochondrial outer-membrane β-barrel biogenesis. The literature summarized below consistently describes **Sam50/SAMM50** as the **core β-barrel subunit of the mitochondrial Sorting and Assembly Machinery (SAM) complex**, localized to the **mitochondrial outer membrane (OMM)** and functionally homologous to bacterial **BamA** (Omp85 family). (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
GO:0032977 membrane insertase activity
NAS
file:human/SAMM50/SAMM50-deep-research-falcon.md
NEW
Summary: SAMM50 is the core Sam50/SAM50 membrane insertase subunit that inserts and assembles mitochondrial outer-membrane beta-barrel proteins.
Reason: The current GOA captures the biological process and complex but lacks the precise molecular function membrane insertase activity for SAMM50.
Supporting Evidence:
file:human/SAMM50/SAMM50-deep-research-falcon.md
The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
file:human/SAMM50/SAMM50-deep-research-falcon.md
**Primary function:** SAMM50 is the core insertase/chaperone of the SAM complex that assembles **mitochondrial outer membrane β-barrel proteins** (including **Tom40** and **VDACs**) in an **energy-independent** manner. (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
file:human/SAMM50/SAMM50-deep-research-falcon.md
SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)

Core Functions

SAMM50 is the core Omp85-family membrane insertase of the mitochondrial SAM complex. It recognizes and assembles beta-barrel precursor proteins delivered by the TOM/IMS chaperone pathway and releases mature beta-barrels such as TOM40 and VDAC into the outer mitochondrial membrane.

Supporting Evidence:
  • file:human/SAMM50/SAMM50-deep-research-falcon.md
    The **Sorting and Assembly Machinery (SAM)** is the **mitochondrial outer-membrane insertase** required for insertion/assembly of **β-barrel proteins** into the OMM. Its core subunit **Sam50 (SAMM50 in humans)** is itself an Omp85-family β-barrel protein; yeast SAM includes additional subunits (e.g., Sam35/Sam37/Mdm10/Mco6), whereas in mammals the accessory subunits are functionally replaced by **metaxins**. (ganesan2024biogenesisofmitochondrial pages 1-2, ravi2025mitochondrialsortingand pages 1-3)
  • file:human/SAMM50/SAMM50-deep-research-falcon.md
    **Primary function:** SAMM50 is the core insertase/chaperone of the SAM complex that assembles **mitochondrial outer membrane β-barrel proteins** (including **Tom40** and **VDACs**) in an **energy-independent** manner. (ravi2025mitochondrialsortingand pages 1-3, ganesan2024biogenesisofmitochondrial pages 1-2)
  • file:human/SAMM50/SAMM50-deep-research-falcon.md
    SAMM50/Sam50 is an **outer mitochondrial membrane (OMM)** protein. It is described as a **16-stranded transmembrane β-barrel** with a single N-terminal **POTRA** domain. In mitochondria, the POTRA domain is positioned to participate in intermembrane-space (IMS) interactions and outer–inner membrane contacts (e.g., with MICOS). (ravi2025mitochondrialsortingand pages 20-24, ganesan2024biogenesisofmitochondrial pages 1-2)
  • file:human/SAMM50/SAMM50-deep-research-falcon.md
    SAMM50 (UniProt Q9Y512; SAM50/TRG-3) is a **mitochondrial outer membrane Omp85-family β-barrel insertase** and the **core subunit of the SAM complex**. Its primary, experimentally grounded role is the **assembly/insertion of OMM β-barrel proteins** (e.g., Tom40 and VDAC) delivered through the TOM→IMS chaperone→SAM pathway and assembled via **β-signal recognition**, **lateral gating**, and **β-barrel switching**. SAMM50 also serves as an organizational hub by forming **TOM–SAM** supercomplexes and participating in **SAM–MICOS** contact sites that connect outer-membrane protein biogenesis to **cristae junction organization**. In human populations, common SAMM50 variants show reproducible associations with **NAFLD risk** in some cohorts, supporting a role for mitochondrial membrane architecture pathways in metabolic liver disease susceptibility. (ganesan2024biogenesisofmitochondrial pages 1-2, zhao2023samm50rs2073082rs738491and pages 1-2)

References

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Suggested Questions for Experts

Q: Should human SAMM50 be annotated directly to membrane insertase activity in GOA, and should that annotation be made with a contributes_to qualifier for the SAM complex or as enabled by the Sam50 subunit itself?

Suggested Experiments

Experiment: Reconstitute the human SAMM50-MTX SAM complex with purified human TOM40 or VDAC beta-barrel precursors and assay insertion intermediates, lateral-gate mutants, and beta-signal dependence.

Hypothesis: Human SAMM50 provides the core membrane insertase activity for outer-membrane beta-barrel substrate assembly.

Deep Research

Falcon

(SAMM50-deep-research-falcon.md)

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