Nf1

UniProt ID: Q04690
Organism: Mus musculus
Review Status: COMPLETE
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Gene Description

Nf1 encodes neurofibromin, a large Ras GTPase-activating protein and tumor suppressor. Its core activity is stimulation of Ras GTP hydrolysis, converting active Ras-GTP to inactive Ras-GDP and thereby negatively regulating Ras-dependent intracellular signaling. SEC14/PH-like lipid-binding modules and nuclear or synaptic contexts may modulate localization or disease biology, but the central conserved function is RasGAP-mediated signal attenuation.

Existing Annotations Review

GO Term Evidence Action Reason
GO:0005096 GTPase activator activity
IBA
GO_REF:0000033
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:1902531 regulation of intracellular signal transduction
IBA
GO_REF:0000033
MODIFY
Summary: This IBA-projected generic parent should be specialized to neurofibromin's actual role, negative regulation of RAS signal transduction via its RasGAP activity.
Reason: Generic parent; specific RasGAP child term is the correct, more informative annotation.
Propagation Review
Root cause: TERM SCOPING PROBLEM
Failure modes: GRANULARITY MISMATCH
Sources checked:
PANTHER:PTN008939999 SUPPORTS TRANSFER
Node in PTHR10194, PANTHER family name "RAS GTPASE-ACTIVATING PROTEINS", the family UniProt also assigns to the target (PTHR10194:SF142 "NEUROFIBROMIN"). Every identified seed is a RasGAP-domain protein, spanning yeast, worm, fly, rodent and human, so the target is well inside the clade and the node placement is not at issue - the shared, informative claim across the seeds is GAP-mediated damping of Ras signalling, which the generic parent understates.
MGI:MGI:97306 · mouse Nf1 (the review target itself) SUPPORTS TRANSFER
The target's own MGI record is among the IBD seeds, the expected marker that experimental grounding exists on the target itself: Nf1 carries IMP/IGI annotations at GO:0005096 GTPase activator activity (PMID:8563750, PMID:11435472, PMID:16271875, PMID:17053831) and at GO:0007265 Ras protein signal transduction (PMID:10498620, PMID:10845775), which are among the descendant evidences behind the IBD.
UniProtKB:P21359 · human NF1 (Neurofibromin) SUPPORTS TRANSFER
The 1:1 human ortholog seed; its RasGAP activity is the same function the target inherits.
FB:FBgn0015269 · Drosophila Nf1 (Neurofibromin 1) SUPPORTS TRANSFER
Invertebrate ortholog seed; places the RasGAP role deep in the bilaterian tree rather than in vertebrates alone.
MGI:MGI:1916851 · mouse Dab2ip (disabled 2 interacting protein) SUPPORTS TRANSFER
A more distant RasGAP-family seed; like the others it acts as a negative regulator of Ras, which is what makes the signed child term the family-level claim.
MGI:MGI:3039785 · mouse Syngap1 (synaptic Ras GTPase activating protein 1) SUPPORTS TRANSFER
Further RasGAP-family seed with the same direction of effect on Ras.
UniProtKB:Q5VWQ8 · human DAB2IP (Disabled homolog 2-interacting protein) SUPPORTS TRANSFER
Human counterpart of the Dab2ip seed.
UniProtKB:Q86YV0 · human RASAL3 (RAS protein activator like-3) SUPPORTS TRANSFER
Human RasGAP-family seed. GO:0046580 is a genuine descendant of GO:1902531 (via GO:0046578 and GO:0051056), so the MODIFY is a parent-to-child narrowing onto the claim the seeds actually share, not a change of claim.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0005096 GTPase activator activity
IEA
GO_REF:0000120
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0005634 nucleus
IEA
GO_REF:0000044
KEEP AS NON CORE
Summary: An NLS in the C-terminal domain permits phosphorylation-regulated nuclear localization in some contexts; the dominant functional pool is cytoplasmic/membrane-proximal.
Reason: Minor/context-dependent localization; non-core relative to membrane action.
GO:0005730 nucleolus
IEA
GO_REF:0000044
KEEP AS NON CORE
Summary: UniProt SubCell-derived nucleolar localization reflects a minor nuclear pool and is not where the RasGAP function is exerted.
Reason: Minor nuclear sub-compartment; IEA, non-core.
GO:0005737 cytoplasm
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: Neurofibromin is a large cytoplasmic protein; the cytoplasm assignment is a generic compartment broader than the membrane-proximal site where it regulates RAS.
Reason: Generic compartment; supportive but less informative than plasma-membrane localization.
GO:0005886 plasma membrane
IEA
GO_REF:0000120
ACCEPT
Summary: Membrane recruitment (aided by SPRED binding) positions neurofibromin at the plasma membrane to act on prenylated, membrane-anchored RAS where RAS signalling originates.
Reason: Site of RasGAP action on membrane-bound RAS; functionally core localization.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0008289 lipid binding
IEA
GO_REF:0000043
KEEP AS NON CORE
Summary: The CRAL-TRIO/Sec14-like domain binds glycerophospholipids, supporting membrane association and regulation but distinct from the catalytic RasGAP activity.
Reason: Real Sec14-domain property supporting localization; ancillary to core RasGAP role.
GO:0014037 Schwann cell differentiation
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: Schwann-cell differentiation depends on tightly controlled RAS signalling that neurofibromin enforces; the term is a downstream consequence of its RasGAP role.
Reason: Downstream glial differentiation phenotype (IEA).
GO:0050793 regulation of developmental process
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: This high-level developmental-regulation term reflects the many pleiotropic developmental roles downstream of neurofibromin's RAS control.
Reason: Very generic downstream developmental term; IEA.
GO:0050807 regulation of synapse organization
IEA
GO_REF:0000117
KEEP AS NON CORE
Summary: Neurofibromin influences synapse organization via its modulation of neuronal RAS/cAMP signalling; a downstream regulatory effect.
Reason: Downstream synaptic-organization role; IEA.
GO:0098793 presynapse
IEA
GO_REF:0000108
KEEP AS NON CORE
Summary: Presynaptic localization (GOC-inferred) is consistent with neurofibromin's role in neurotransmitter-secretion modulation, downstream of its signalling activity.
Reason: Synaptic compartment; pleiotropic neuronal role, non-core.
GO:0005654 nucleoplasm
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: Nucleoplasmic localization is an electronically projected refinement of the minor NLS-dependent nuclear pool of neurofibromin.
Reason: Minor nuclear sub-compartment; IEA/ISO, non-core.
GO:0008429 phosphatidylethanolamine binding
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: The CRAL-TRIO domain also binds phosphatidylethanolamine-headgroup glycerophospholipids, aiding membrane localization of neurofibromin.
Reason: Specific Sec14 lipid preference; membrane-association role, non-core.
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: Neuronal axonal localization reflects neurofibromin's distribution in neurons, consistent with its synaptic/neuronal roles but not its defining function.
Reason: Neuronal sub-cellular distribution; pleiotropic/non-core.
GO:0030425 dendrite
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: Dendritic localization is part of neurofibromin's neuronal distribution underpinning its synaptic-plasticity roles, downstream of RAS/cAMP regulation.
Reason: Neuronal distribution supporting synaptic roles; non-core.
GO:0031210 phosphatidylcholine binding
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: The Sec14-like CRAL-TRIO domain preferentially binds phosphatidylcholine-headgroup lipids, contributing to membrane targeting rather than to catalysis.
Reason: Specific Sec14 lipid preference; supports membrane association, non-core.
GO:0043535 regulation of blood vessel endothelial cell migration
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: Endothelial migration during vessel formation is modulated downstream of neurofibromin's RAS signalling control; IEA/ISO-projected.
Reason: Downstream vascular migration regulation; non-core.
GO:0045765 regulation of angiogenesis
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: Neurofibromin influences angiogenesis via its control of endothelial RAS signalling; a downstream vascular regulatory role.
Reason: Downstream angiogenesis regulation.
GO:0050890 cognition
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: Cognitive function is impaired when RAS/cAMP signalling is dysregulated by NF1 loss; a high-level behavioural phenotype downstream of the molecular defect.
Reason: Behavioural phenotype downstream of signalling dysregulation.
GO:0032991 protein-containing complex
ISO
GO_REF:0000096
MARK AS OVER ANNOTATED
Summary: Bare 'protein-containing complex' membership adds no functional or compositional information about neurofibromin and is an ISO-projected generic term.
Reason: Uninformative complex assignment; over-annotation.
GO:0043547 positive regulation of GTPase activity
ISO
GO_REF:0000119
ACCEPT
Summary: Direct readout of catalysis: neurofibromin accelerates the intrinsic GTPase activity of RAS, the molecular event that terminates active RAS-GTP signalling.
Reason: Proximal consequence of RasGAP catalysis; core to neurofibromin function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0001937 negative regulation of endothelial cell proliferation
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: Endothelial proliferation is restrained by neurofibromin through reduced RAS signalling, relevant to vascular phenotypes; downstream.
Reason: Downstream vascular antiproliferative phenotype.
GO:0005096 GTPase activator activity
ISO
GO_REF:0000096
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0005096 GTPase activator activity
ISO
GO_REF:0000119
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0005634 nucleus
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: An NLS in the C-terminal domain permits phosphorylation-regulated nuclear localization in some contexts; the dominant functional pool is cytoplasmic/membrane-proximal.
Reason: Minor/context-dependent localization; non-core relative to membrane action.
GO:0005654 nucleoplasm
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: Nucleoplasmic localization is an electronically projected refinement of the minor NLS-dependent nuclear pool of neurofibromin.
Reason: Minor nuclear sub-compartment; IEA/ISO, non-core.
GO:0005737 cytoplasm
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: Neurofibromin is a large cytoplasmic protein; the cytoplasm assignment is a generic compartment broader than the membrane-proximal site where it regulates RAS.
Reason: Generic compartment; supportive but less informative than plasma-membrane localization.
GO:0005886 plasma membrane
ISO
GO_REF:0000119
ACCEPT
Summary: Membrane recruitment (aided by SPRED binding) positions neurofibromin at the plasma membrane to act on prenylated, membrane-anchored RAS where RAS signalling originates.
Reason: Site of RasGAP action on membrane-bound RAS; functionally core localization.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0008429 phosphatidylethanolamine binding
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: The CRAL-TRIO domain also binds phosphatidylethanolamine-headgroup glycerophospholipids, aiding membrane localization of neurofibromin.
Reason: Specific Sec14 lipid preference; membrane-association role, non-core.
GO:0010976 positive regulation of neuron projection development
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: ISO-projected promotion of neurite outgrowth reflects neurofibromin's neuronal signalling role; downstream and electronically inferred.
Reason: Downstream neuronal morphogenesis; ISO, non-core.
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: Neuronal axonal localization reflects neurofibromin's distribution in neurons, consistent with its synaptic/neuronal roles but not its defining function.
Reason: Neuronal sub-cellular distribution; pleiotropic/non-core.
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: Neuronal axonal localization reflects neurofibromin's distribution in neurons, consistent with its synaptic/neuronal roles but not its defining function.
Reason: Neuronal sub-cellular distribution; pleiotropic/non-core.
GO:0030425 dendrite
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: Dendritic localization is part of neurofibromin's neuronal distribution underpinning its synaptic-plasticity roles, downstream of RAS/cAMP regulation.
Reason: Neuronal distribution supporting synaptic roles; non-core.
GO:0030425 dendrite
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: Dendritic localization is part of neurofibromin's neuronal distribution underpinning its synaptic-plasticity roles, downstream of RAS/cAMP regulation.
Reason: Neuronal distribution supporting synaptic roles; non-core.
GO:0031210 phosphatidylcholine binding
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: The Sec14-like CRAL-TRIO domain preferentially binds phosphatidylcholine-headgroup lipids, contributing to membrane targeting rather than to catalysis.
Reason: Specific Sec14 lipid preference; supports membrane association, non-core.
GO:0043535 regulation of blood vessel endothelial cell migration
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: Endothelial migration during vessel formation is modulated downstream of neurofibromin's RAS signalling control; IEA/ISO-projected.
Reason: Downstream vascular migration regulation; non-core.
GO:0045545 syndecan binding
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: ISO-projected syndecan binding implies a membrane/adhesion-associated partner interaction that is peripheral to the RasGAP catalytic role.
Reason: Specific partner binding, electronically projected; ancillary.
GO:0045664 regulation of neuron differentiation
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: Neuronal differentiation is modulated by RAS-pathway tone that neurofibromin sets; an indirect downstream regulatory role.
Reason: Downstream neuronal differentiation control; ISO.
GO:0045765 regulation of angiogenesis
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: Neurofibromin influences angiogenesis via its control of endothelial RAS signalling; a downstream vascular regulatory role.
Reason: Downstream angiogenesis regulation.
GO:0050890 cognition
ISO
GO_REF:0000119
KEEP AS NON CORE
Summary: Cognitive function is impaired when RAS/cAMP signalling is dysregulated by NF1 loss; a high-level behavioural phenotype downstream of the molecular defect.
Reason: Behavioural phenotype downstream of signalling dysregulation.
GO:0098926 postsynaptic signal transduction
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: Postsynaptic signal transduction involving neurofibromin reflects its synaptic localization and RAS/cAMP modulation; downstream and ISO-projected.
Reason: Downstream synaptic signalling role; ISO.
GO:0098978 glutamatergic synapse
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: SynGO localization at glutamatergic synapses supports neurofibromin's modulation of synaptic transmission/plasticity, a downstream neuronal role.
Reason: Synaptic localization tied to pleiotropic neuronal function.
GO:0099159 regulation of modification of postsynaptic structure
ISO
GO_REF:0000096
KEEP AS NON CORE
Summary: ISO-projected control of postsynaptic structural modification is part of neurofibromin's downstream synaptic-plasticity role.
Reason: Downstream postsynaptic regulation; ISO.
GO:0098978 glutamatergic synapse
IMP
PMID:22105171
Valosin-containing protein and neurofibromin interact to reg...
KEEP AS NON CORE
Summary: SynGO localization at glutamatergic synapses supports neurofibromin's modulation of synaptic transmission/plasticity, a downstream neuronal role.
Reason: Synaptic localization tied to pleiotropic neuronal function.
GO:0098978 glutamatergic synapse
IDA
PMID:22105171
Valosin-containing protein and neurofibromin interact to reg...
KEEP AS NON CORE
Summary: SynGO localization at glutamatergic synapses supports neurofibromin's modulation of synaptic transmission/plasticity, a downstream neuronal role.
Reason: Synaptic localization tied to pleiotropic neuronal function.
GO:0099175 regulation of postsynapse organization
IMP
PMID:22105171
Valosin-containing protein and neurofibromin interact to reg...
KEEP AS NON CORE
Summary: SynGO-supported regulation of postsynaptic organization reflects neurofibromin's synaptic signalling role downstream of RAS.
Reason: Synaptic-structure regulation downstream of signalling.
GO:0099175 regulation of postsynapse organization
IDA
PMID:22105171
Valosin-containing protein and neurofibromin interact to reg...
KEEP AS NON CORE
Summary: SynGO-supported regulation of postsynaptic organization reflects neurofibromin's synaptic signalling role downstream of RAS.
Reason: Synaptic-structure regulation downstream of signalling.
GO:0005096 GTPase activator activity
IMP
PMID:16271875
The HMG-CoA reductase inhibitor lovastatin reverses the lear...
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0005096 GTPase activator activity
IGI
PMID:16271875
The HMG-CoA reductase inhibitor lovastatin reverses the lear...
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0060291 long-term synaptic potentiation
IMP
PMID:16271875
The HMG-CoA reductase inhibitor lovastatin reverses the lear...
KEEP AS NON CORE
Summary: Altered LTP in Nf1 mutants arises from excess RAS/MAPK and cAMP signalling at synapses; a downstream plasticity phenotype.
Reason: Synaptic plasticity phenotype downstream of signalling control.
GO:0060291 long-term synaptic potentiation
IGI
PMID:16271875
The HMG-CoA reductase inhibitor lovastatin reverses the lear...
KEEP AS NON CORE
Summary: Altered LTP in Nf1 mutants arises from excess RAS/MAPK and cAMP signalling at synapses; a downstream plasticity phenotype.
Reason: Synaptic plasticity phenotype downstream of signalling control.
GO:0070372 regulation of ERK1 and ERK2 cascade
IMP
PMID:16271875
The HMG-CoA reductase inhibitor lovastatin reverses the lear...
KEEP AS NON CORE
Summary: ERK1/2 output is modulated as a downstream effect of neurofibromin lowering RAS-GTP levels; the regulation is exerted at the RAS node.
Reason: Downstream effector regulation, secondary to the RasGAP role.
GO:0070372 regulation of ERK1 and ERK2 cascade
IGI
PMID:16271875
The HMG-CoA reductase inhibitor lovastatin reverses the lear...
KEEP AS NON CORE
Summary: ERK1/2 output is modulated as a downstream effect of neurofibromin lowering RAS-GTP levels; the regulation is exerted at the RAS node.
Reason: Downstream effector regulation, secondary to the RasGAP role.
GO:0001953 negative regulation of cell-matrix adhesion
IGI
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
KEEP AS NON CORE
Summary: Cell-matrix adhesion is modulated downstream of neurofibromin's RAS/Rho signalling control; a downstream adhesion phenotype.
Reason: Downstream adhesion regulation, IGI.
GO:0030336 negative regulation of cell migration
IGI
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
KEEP AS NON CORE
Summary: Reduced cell migration with neurofibromin reflects its control of RAS/Rho-pathway-driven motility; a downstream cytoskeletal/signalling effect.
Reason: Downstream motility regulation.
GO:0045671 negative regulation of osteoclast differentiation
IGI
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
KEEP AS NON CORE
Summary: Neurofibromin restrains osteoclast differentiation via RAS signalling control, relevant to NF1 bone pathology; a downstream phenotype.
Reason: Downstream osteoclast regulation, IGI.
GO:0008625 extrinsic apoptotic signaling pathway via death domain receptors
IMP
PMID:15039234
Loss of the nf1 tumor suppressor gene decreases fas antigen ...
KEEP AS NON CORE
Summary: Involvement in death-receptor apoptotic signalling is downstream of neurofibromin's broader survival-pathway modulation.
Reason: Downstream apoptotic-signalling phenotype.
GO:0008625 extrinsic apoptotic signaling pathway via death domain receptors
IGI
PMID:15039234
Loss of the nf1 tumor suppressor gene decreases fas antigen ...
KEEP AS NON CORE
Summary: Involvement in death-receptor apoptotic signalling is downstream of neurofibromin's broader survival-pathway modulation.
Reason: Downstream apoptotic-signalling phenotype.
GO:0048169 regulation of long-term neuronal synaptic plasticity
IMP
PMID:11793011
Mechanism for the learning deficits in a mouse model of neur...
KEEP AS NON CORE
Summary: Long-term synaptic plasticity is modulated by neurofibromin via RAS/cAMP signalling; a downstream neuronal regulatory function.
Reason: Downstream synaptic-plasticity regulation.
GO:0048169 regulation of long-term neuronal synaptic plasticity
IGI
PMID:11793011
Mechanism for the learning deficits in a mouse model of neur...
KEEP AS NON CORE
Summary: Long-term synaptic plasticity is modulated by neurofibromin via RAS/cAMP signalling; a downstream neuronal regulatory function.
Reason: Downstream synaptic-plasticity regulation.
GO:0042308 negative regulation of protein import into nucleus
IMP
PMID:12469121
Nf1 has an essential role in endothelial cells.
KEEP AS NON CORE
Summary: A reported effect on nuclear protein import is a downstream/secondary role of neurofibromin and not its proximal RasGAP function.
Reason: Downstream/secondary regulatory phenotype, IMP.
GO:0048820 hair follicle maturation
IMP
PMID:25340873
Identification of genes important for cutaneous function rev...
KEEP AS NON CORE
Summary: Hair-follicle maturation is affected by NF1 loss via RAS-pathway dysregulation in skin appendages; a downstream developmental phenotype.
Reason: Downstream skin-appendage developmental phenotype.
GO:0010468 regulation of gene expression
IGI
PMID:25242307
Social learning and amygdala disruptions in Nf1 mice are res...
KEEP AS NON CORE
Summary: Effects on gene expression are distal transcriptional consequences of neurofibromin's control of RAS/MAPK signalling.
Reason: Distal downstream transcriptional effect, IGI.
GO:0021764 amygdala development
IGI
PMID:25242307
Social learning and amygdala disruptions in Nf1 mice are res...
KEEP AS NON CORE
Summary: Amygdala development is affected in Nf1 mutant mice, linking the RAS brake to limbic-circuit formation underlying behavioural phenotypes.
Reason: Region-specific developmental phenotype, IGI.
GO:0043408 regulation of MAPK cascade
IGI
PMID:25242307
Social learning and amygdala disruptions in Nf1 mice are res...
KEEP AS NON CORE
Summary: Generic regulation of the MAPK cascade reflects neurofibromin's indirect control of ERK signalling downstream of its action on RAS.
Reason: Downstream/generic effector regulation, not the proximal function.
GO:0061534 gamma-aminobutyric acid secretion, neurotransmission
IGI
PMID:25242307
Social learning and amygdala disruptions in Nf1 mice are res...
KEEP AS NON CORE
Summary: Neurofibromin modulates GABA release through RAS/cAMP-dependent control of inhibitory transmission; a downstream neuronal phenotype.
Reason: Downstream neurotransmission phenotype, IGI.
GO:0061535 glutamate secretion, neurotransmission
IGI
PMID:25242307
Social learning and amygdala disruptions in Nf1 mice are res...
KEEP AS NON CORE
Summary: Glutamate release is influenced by neurofibromin's RAS/cAMP signalling at synapses; a downstream excitatory-transmission role.
Reason: Downstream neurotransmission phenotype, IGI.
GO:0098597 observational learning
IGI
PMID:25242307
Social learning and amygdala disruptions in Nf1 mice are res...
KEEP AS NON CORE
Summary: Observational-learning deficits reflect neurofibromin's role in synaptic plasticity via RAS/cAMP signalling; a behavioural phenotype.
Reason: Behavioural learning phenotype, IGI, downstream.
GO:1900271 regulation of long-term synaptic potentiation
IGI
PMID:25242307
Social learning and amygdala disruptions in Nf1 mice are res...
KEEP AS NON CORE
Summary: Neurofibromin tunes LTP magnitude through its control of synaptic RAS/cAMP signalling, a downstream regulatory role.
Reason: Downstream plasticity regulation, IGI.
GO:0034605 cellular response to heat
IDA
PMID:20661302
Long-term potentiation in the CA1 hippocampus induced by NR2...
UNDECIDED
Summary: An IDA links neurofibromin to a cellular heat response; the mechanistic connection to its RasGAP role is unclear from the cached evidence, so the call is deferred.
Reason: Experimental annotation whose mechanism is unclear; do not remove, defer per guidelines.
GO:0008429 phosphatidylethanolamine binding
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: The CRAL-TRIO domain also binds phosphatidylethanolamine-headgroup glycerophospholipids, aiding membrane localization of neurofibromin.
Reason: Specific Sec14 lipid preference; membrane-association role, non-core.
GO:0031210 phosphatidylcholine binding
ISS
GO_REF:0000024
KEEP AS NON CORE
Summary: The Sec14-like CRAL-TRIO domain preferentially binds phosphatidylcholine-headgroup lipids, contributing to membrane targeting rather than to catalysis.
Reason: Specific Sec14 lipid preference; supports membrane association, non-core.
GO:2001241 positive regulation of extrinsic apoptotic signaling pathway in absence of ligand
IMP
PMID:15039234
Loss of the nf1 tumor suppressor gene decreases fas antigen ...
KEEP AS NON CORE
Summary: Sensitization to ligand-independent extrinsic apoptosis reflects altered survival signalling when RAS output changes; downstream.
Reason: Downstream apoptotic-signalling phenotype, IMP.
GO:0005096 GTPase activator activity
IGI
PMID:15665300
Glioma formation in neurofibromatosis 1 reflects preferentia...
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0048147 negative regulation of fibroblast proliferation
IMP
PMID:20154697
An oncogene-tumor suppressor cascade drives metastatic prost...
KEEP AS NON CORE
Summary: Fibroblast proliferation is curbed by neurofibromin lowering RAS-GTP; a downstream antiproliferative readout in mesenchymal cells.
Reason: Downstream antiproliferative phenotype (experimental IMP; downgraded, not removed).
GO:0008542 visual learning
IMP
PMID:11279521
Learning deficits, but normal development and tumor predispo...
KEEP AS NON CORE
Summary: Visual-learning deficits in Nf1+/- mice trace to excess RAS/cAMP-dependent synaptic signalling, a downstream behavioural readout.
Reason: Behavioural learning phenotype downstream of RAS/cAMP.
GO:0001649 osteoblast differentiation
IMP
PMID:16893911
Neurofibromin plays a critical role in modulating osteoblast...
KEEP AS NON CORE
Summary: Osteoblast differentiation is affected by NF1 loss through dysregulated RAS signalling, contributing to skeletal manifestations; downstream.
Reason: Downstream skeletal-cell differentiation phenotype.
GO:0001666 response to hypoxia
IMP
PMID:16288202
Nf1 haploinsufficiency augments angiogenesis.
KEEP AS NON CORE
Summary: Responsiveness to hypoxia in NF1 contexts is a downstream physiological phenotype connected to RAS/vascular signalling rather than a direct function.
Reason: Downstream stress-response phenotype, IMP.
GO:0001937 negative regulation of endothelial cell proliferation
ISO
GO_REF:0000008
KEEP AS NON CORE
Summary: Endothelial proliferation is restrained by neurofibromin through reduced RAS signalling, relevant to vascular phenotypes; downstream.
Reason: Downstream vascular antiproliferative phenotype.
GO:0001937 negative regulation of endothelial cell proliferation
IMP
PMID:16288202
Nf1 haploinsufficiency augments angiogenesis.
KEEP AS NON CORE
Summary: Endothelial proliferation is restrained by neurofibromin through reduced RAS signalling, relevant to vascular phenotypes; downstream.
Reason: Downstream vascular antiproliferative phenotype.
GO:0001938 positive regulation of endothelial cell proliferation
IGI
PMID:16644864
Neurofibromin is a novel regulator of RAS-induced signals in...
KEEP AS NON CORE
Summary: A context-dependent positive effect on endothelial proliferation reflects complex vascular signalling outputs of neurofibromin; downstream and IGI.
Reason: Context-dependent downstream vascular phenotype.
GO:0001952 regulation of cell-matrix adhesion
IMP
PMID:16405917
Neurofibromin binds to caveolin-1 and regulates ras, FAK, an...
KEEP AS NON CORE
Summary: General regulation of cell-matrix adhesion by neurofibromin is an indirect downstream effect of its signalling role.
Reason: Downstream adhesion regulation, IMP.
GO:0005096 GTPase activator activity
IMP
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0005515 protein binding
IPI
PMID:16405917
Neurofibromin binds to caveolin-1 and regulates ras, FAK, an...
MARK AS OVER ANNOTATED
Summary: Generic 'protein binding' conveys no functional specificity for neurofibromin; its informative partner interactions (SPRED, HTR6) are captured by dedicated terms.
Reason: Uninformative MF; over-annotation.
GO:0006469 negative regulation of protein kinase activity
IMP
PMID:16835260
Nf1+/- mast cells induce neurofibroma like phenotypes throug...
KEEP AS NON CORE
Summary: Reduced kinase (e.g. ERK) activity is an indirect downstream consequence of neurofibromin lowering RAS-GTP, not direct kinase inhibition.
Reason: Indirect downstream kinase regulation.
GO:0006469 negative regulation of protein kinase activity
IGI
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
KEEP AS NON CORE
Summary: Reduced kinase (e.g. ERK) activity is an indirect downstream consequence of neurofibromin lowering RAS-GTP, not direct kinase inhibition.
Reason: Indirect downstream kinase regulation.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:15665300
Glioma formation in neurofibromatosis 1 reflects preferentia...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:15944386
Neurofibromin regulates neural stem cell proliferation, surv...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008542 visual learning
IGI
PMID:16271875
The HMG-CoA reductase inhibitor lovastatin reverses the lear...
KEEP AS NON CORE
Summary: Visual-learning deficits in Nf1+/- mice trace to excess RAS/cAMP-dependent synaptic signalling, a downstream behavioural readout.
Reason: Behavioural learning phenotype downstream of RAS/cAMP.
GO:0016525 negative regulation of angiogenesis
IGI
PMID:16648142
Neurofibroma-associated growth factors activate a distinct s...
KEEP AS NON CORE
Summary: Neurofibromin can restrain angiogenesis by limiting endothelial RAS signalling; a downstream vascular phenotype.
Reason: Downstream antiangiogenic phenotype, IGI.
GO:0021897 forebrain astrocyte development
IMP
PMID:15944386
Neurofibromin regulates neural stem cell proliferation, surv...
KEEP AS NON CORE
Summary: Forebrain astrocyte development is perturbed when NF1 loss elevates RAS signalling; a region-specific downstream developmental phenotype.
Reason: Region-specific downstream developmental phenotype.
GO:0030036 actin cytoskeleton organization
IGI
PMID:15665300
Glioma formation in neurofibromatosis 1 reflects preferentia...
KEEP AS NON CORE
Summary: Effects on the actin cytoskeleton (via Rho/ROCK/LIMK/cofilin and PKA-Ena/VASP) are downstream of neurofibromin's signalling role rather than a direct structural function.
Reason: Downstream cytoskeletal remodeling secondary to signalling regulation.
GO:0030036 actin cytoskeleton organization
IMP
PMID:16405917
Neurofibromin binds to caveolin-1 and regulates ras, FAK, an...
KEEP AS NON CORE
Summary: Effects on the actin cytoskeleton (via Rho/ROCK/LIMK/cofilin and PKA-Ena/VASP) are downstream of neurofibromin's signalling role rather than a direct structural function.
Reason: Downstream cytoskeletal remodeling secondary to signalling regulation.
GO:0030198 extracellular matrix organization
IMP
PMID:16835260
Nf1+/- mast cells induce neurofibroma like phenotypes throug...
KEEP AS NON CORE
Summary: ECM organization is influenced by neurofibromin through its control of fibroblast RAS signalling; a downstream connective-tissue phenotype.
Reason: Downstream ECM-organization phenotype.
GO:0030336 negative regulation of cell migration
ISO
GO_REF:0000008
KEEP AS NON CORE
Summary: Reduced cell migration with neurofibromin reflects its control of RAS/Rho-pathway-driven motility; a downstream cytoskeletal/signalling effect.
Reason: Downstream motility regulation.
GO:0030336 negative regulation of cell migration
IGI
PMID:16644864
Neurofibromin is a novel regulator of RAS-induced signals in...
KEEP AS NON CORE
Summary: Reduced cell migration with neurofibromin reflects its control of RAS/Rho-pathway-driven motility; a downstream cytoskeletal/signalling effect.
Reason: Downstream motility regulation.
GO:0035021 negative regulation of Rac protein signal transduction
IGI
PMID:15665300
Glioma formation in neurofibromatosis 1 reflects preferentia...
KEEP AS NON CORE
Summary: Reduced Rac signalling is reported downstream of NF1 loss; this lies in a Rho-family arm secondary to neurofibromin's primary RAS-directed GAP function.
Reason: Downstream/secondary signalling effect, not the canonical RAS GAP activity.
GO:0043065 positive regulation of apoptotic process
IMP
PMID:15944386
Neurofibromin regulates neural stem cell proliferation, surv...
KEEP AS NON CORE
Summary: Pro-apoptotic effects of neurofibromin in some cell types are downstream of its modulation of RAS-pathway survival signalling.
Reason: Downstream apoptotic-balance phenotype.
GO:0043065 positive regulation of apoptotic process
IMP
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
KEEP AS NON CORE
Summary: Pro-apoptotic effects of neurofibromin in some cell types are downstream of its modulation of RAS-pathway survival signalling.
Reason: Downstream apoptotic-balance phenotype.
GO:0043407 negative regulation of MAP kinase activity
IMP
PMID:12409258
Glycogen stored in skeletal but not in cardiac muscle in aci...
KEEP AS NON CORE
Summary: Lowered ERK/MAPK activity results indirectly from neurofibromin reducing RAS-GTP; it acts on RAS, not directly on the MAP kinase.
Reason: Indirect downstream effect of RasGAP activity on RAS.
GO:0043407 negative regulation of MAP kinase activity
IGI
PMID:12409258
Glycogen stored in skeletal but not in cardiac muscle in aci...
KEEP AS NON CORE
Summary: Lowered ERK/MAPK activity results indirectly from neurofibromin reducing RAS-GTP; it acts on RAS, not directly on the MAP kinase.
Reason: Indirect downstream effect of RasGAP activity on RAS.
GO:0043409 negative regulation of MAPK cascade
ISO
GO_REF:0000008
KEEP AS NON CORE
Summary: Dampening of the RAF-MEK-ERK cascade follows from reduced RAS activation; neurofibromin's direct target is RAS-GTP, upstream of the cascade.
Reason: Downstream consequence of negative regulation of RAS.
GO:0043409 negative regulation of MAPK cascade
IMP
PMID:16644864
Neurofibromin is a novel regulator of RAS-induced signals in...
KEEP AS NON CORE
Summary: Dampening of the RAF-MEK-ERK cascade follows from reduced RAS activation; neurofibromin's direct target is RAS-GTP, upstream of the cascade.
Reason: Downstream consequence of negative regulation of RAS.
GO:0043547 positive regulation of GTPase activity
ISO
GO_REF:0000008
ACCEPT
Summary: Direct readout of catalysis: neurofibromin accelerates the intrinsic GTPase activity of RAS, the molecular event that terminates active RAS-GTP signalling.
Reason: Proximal consequence of RasGAP catalysis; core to neurofibromin function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0045124 regulation of bone resorption
IMP
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
KEEP AS NON CORE
Summary: Bone resorption is modulated by neurofibromin through its effects on osteoclast RAS signalling; a downstream skeletal phenotype.
Reason: Downstream bone-remodeling phenotype, IMP.
GO:0045762 positive regulation of adenylate cyclase activity
IMP
PMID:11788835
Neurofibromin regulates G protein-stimulated adenylyl cyclas...
KEEP AS NON CORE
Summary: Neurofibromin promotes cAMP production via G-protein-dependent adenylyl cyclase regulation, a distinct downstream signalling arm beyond RasGAP catalysis.
Reason: Real but distinct cAMP-modulatory role; pleiotropic/non-core.
GO:0045765 regulation of angiogenesis
IMP
PMID:16288202
Nf1 haploinsufficiency augments angiogenesis.
KEEP AS NON CORE
Summary: Neurofibromin influences angiogenesis via its control of endothelial RAS signalling; a downstream vascular regulatory role.
Reason: Downstream angiogenesis regulation.
GO:0046580 negative regulation of Ras protein signal transduction
IMP
PMID:15665300
Glioma formation in neurofibromatosis 1 reflects preferentia...
ACCEPT
Summary: By converting RAS-GTP to RAS-GDP neurofibromin is the principal brake on RAS pathway output; loss elevates RAS signalling and drives the NF1 phenotype.
Reason: Direct, proximal biological role of the RasGAP; core function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0046580 negative regulation of Ras protein signal transduction
IGI
PMID:15665300
Glioma formation in neurofibromatosis 1 reflects preferentia...
ACCEPT
Summary: By converting RAS-GTP to RAS-GDP neurofibromin is the principal brake on RAS pathway output; loss elevates RAS signalling and drives the NF1 phenotype.
Reason: Direct, proximal biological role of the RasGAP; core function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0046580 negative regulation of Ras protein signal transduction
IMP
PMID:15944386
Neurofibromin regulates neural stem cell proliferation, surv...
ACCEPT
Summary: By converting RAS-GTP to RAS-GDP neurofibromin is the principal brake on RAS pathway output; loss elevates RAS signalling and drives the NF1 phenotype.
Reason: Direct, proximal biological role of the RasGAP; core function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0046580 negative regulation of Ras protein signal transduction
IMP
PMID:16835260
Nf1+/- mast cells induce neurofibroma like phenotypes throug...
ACCEPT
Summary: By converting RAS-GTP to RAS-GDP neurofibromin is the principal brake on RAS pathway output; loss elevates RAS signalling and drives the NF1 phenotype.
Reason: Direct, proximal biological role of the RasGAP; core function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0046580 negative regulation of Ras protein signal transduction
IMP
PMID:16893911
Neurofibromin plays a critical role in modulating osteoblast...
ACCEPT
Summary: By converting RAS-GTP to RAS-GDP neurofibromin is the principal brake on RAS pathway output; loss elevates RAS signalling and drives the NF1 phenotype.
Reason: Direct, proximal biological role of the RasGAP; core function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0046580 negative regulation of Ras protein signal transduction
IGI
PMID:17053831
Hyperactivation of p21ras and PI3K cooperate to alter murine...
ACCEPT
Summary: By converting RAS-GTP to RAS-GDP neurofibromin is the principal brake on RAS pathway output; loss elevates RAS signalling and drives the NF1 phenotype.
Reason: Direct, proximal biological role of the RasGAP; core function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0046929 negative regulation of neurotransmitter secretion
IMP
PMID:16298082
Stimulus-evoked release of neuropeptides is enhanced in sens...
KEEP AS NON CORE
Summary: Neurofibromin can dampen neurotransmitter release via its synaptic signalling role; a downstream regulatory effect on transmission.
Reason: Downstream neurotransmission regulation.
GO:0046929 negative regulation of neurotransmitter secretion
IGI
PMID:16298082
Stimulus-evoked release of neuropeptides is enhanced in sens...
KEEP AS NON CORE
Summary: Neurofibromin can dampen neurotransmitter release via its synaptic signalling role; a downstream regulatory effect on transmission.
Reason: Downstream neurotransmission regulation.
GO:0048715 negative regulation of oligodendrocyte differentiation
IMP
PMID:15944386
Neurofibromin regulates neural stem cell proliferation, surv...
KEEP AS NON CORE
Summary: Oligodendrocyte differentiation is sensitive to RAS tone; neurofibromin's restraint of RAS underlies this negative-regulation phenotype.
Reason: Downstream glial differentiation control.
GO:0000165 MAPK cascade
IMP
PMID:14724565
Role of TC21/R-Ras2 in enhanced migration of neurofibromin-d...
KEEP AS NON CORE
Summary: The MAPK (RAF-MEK-ERK) cascade is the principal effector arm downstream of RAS that neurofibromin restrains; involvement here is a consequence of its RasGAP role.
Reason: Downstream effector pathway of the RAS brake; not the proximal function.
GO:0007265 Ras protein signal transduction
IMP
PMID:12469121
Nf1 has an essential role in endothelial cells.
KEEP AS NON CORE
Summary: Neurofibromin participates in RAS signalling specifically as its negative regulator; the broad 'Ras protein signal transduction' term is less precise than the negative-regulation term.
Reason: Subsumed by the more specific negative-regulation-of-Ras core term; kept as supporting context.
GO:0007507 heart development
IMP
PMID:12469121
Nf1 has an essential role in endothelial cells.
KEEP AS NON CORE
Summary: Nf1-null embryos show cardiovascular defects and mid-gestation lethality because controlled RAS/MAPK and PI3K signalling is required for cardiac morphogenesis.
Reason: Downstream organ-development phenotype (well documented in mouse).
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:11246230
Neurofibromatosis 1 (NF1) heterozygosity results in a cell-a...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:11246230
Neurofibromatosis 1 (NF1) heterozygosity results in a cell-a...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:14982883
Somatic inactivation of Nf1 in hematopoietic cells results i...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0030336 negative regulation of cell migration
IMP
PMID:14724565
Role of TC21/R-Ras2 in enhanced migration of neurofibromin-d...
KEEP AS NON CORE
Summary: Reduced cell migration with neurofibromin reflects its control of RAS/Rho-pathway-driven motility; a downstream cytoskeletal/signalling effect.
Reason: Downstream motility regulation.
GO:0030336 negative regulation of cell migration
IGI
PMID:14724565
Role of TC21/R-Ras2 in enhanced migration of neurofibromin-d...
KEEP AS NON CORE
Summary: Reduced cell migration with neurofibromin reflects its control of RAS/Rho-pathway-driven motility; a downstream cytoskeletal/signalling effect.
Reason: Downstream motility regulation.
GO:0043491 phosphatidylinositol 3-kinase/protein kinase B signal transduction
IMP
PMID:14724565
Role of TC21/R-Ras2 in enhanced migration of neurofibromin-d...
KEEP AS NON CORE
Summary: PI3K/AKT is a second major RAS effector arm engaged when neurofibromin is lost; its regulation is a downstream consequence of altered RAS-GTP.
Reason: Downstream RAS effector pathway; pleiotropic, not proximal.
GO:0043547 positive regulation of GTPase activity
IMP
PMID:11435472
Hyperactivation of p21(ras) and the hematopoietic-specific R...
ACCEPT
Summary: Direct readout of catalysis: neurofibromin accelerates the intrinsic GTPase activity of RAS, the molecular event that terminates active RAS-GTP signalling.
Reason: Proximal consequence of RasGAP catalysis; core to neurofibromin function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0043547 positive regulation of GTPase activity
IMP
PMID:8563750
Nf1 deficiency causes Ras-mediated granulocyte/macrophage co...
ACCEPT
Summary: Direct readout of catalysis: neurofibromin accelerates the intrinsic GTPase activity of RAS, the molecular event that terminates active RAS-GTP signalling.
Reason: Proximal consequence of RasGAP catalysis; core to neurofibromin function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0046580 negative regulation of Ras protein signal transduction
IMP
PMID:11246230
Neurofibromatosis 1 (NF1) heterozygosity results in a cell-a...
ACCEPT
Summary: By converting RAS-GTP to RAS-GDP neurofibromin is the principal brake on RAS pathway output; loss elevates RAS signalling and drives the NF1 phenotype.
Reason: Direct, proximal biological role of the RasGAP; core function.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0005096 GTPase activator activity
IMP
PMID:11435472
Hyperactivation of p21(ras) and the hematopoietic-specific R...
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0007265 Ras protein signal transduction
IMP
PMID:11435472
Hyperactivation of p21(ras) and the hematopoietic-specific R...
KEEP AS NON CORE
Summary: Neurofibromin participates in RAS signalling specifically as its negative regulator; the broad 'Ras protein signal transduction' term is less precise than the negative-regulation term.
Reason: Subsumed by the more specific negative-regulation-of-Ras core term; kept as supporting context.
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:11401406
Analysis of melanocyte precursors in Nf1 mutants reveals tha...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:11401406
Analysis of melanocyte precursors in Nf1 mutants reveals tha...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:11435472
Hyperactivation of p21(ras) and the hematopoietic-specific R...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008542 visual learning
IMP
PMID:11793011
Mechanism for the learning deficits in a mouse model of neur...
KEEP AS NON CORE
Summary: Visual-learning deficits in Nf1+/- mice trace to excess RAS/cAMP-dependent synaptic signalling, a downstream behavioural readout.
Reason: Behavioural learning phenotype downstream of RAS/cAMP.
GO:0008542 visual learning
IGI
PMID:11793011
Mechanism for the learning deficits in a mouse model of neur...
KEEP AS NON CORE
Summary: Visual-learning deficits in Nf1+/- mice trace to excess RAS/cAMP-dependent synaptic signalling, a downstream behavioural readout.
Reason: Behavioural learning phenotype downstream of RAS/cAMP.
GO:0032228 regulation of synaptic transmission, GABAergic
IGI
PMID:11793011
Mechanism for the learning deficits in a mouse model of neur...
KEEP AS NON CORE
Summary: GABAergic transmission is regulated by neurofibromin through RAS/cAMP signalling, contributing to learning phenotypes; downstream and pleiotropic.
Reason: Downstream inhibitory-transmission regulation, IGI.
GO:0043065 positive regulation of apoptotic process
IGI
PMID:15039234
Loss of the nf1 tumor suppressor gene decreases fas antigen ...
KEEP AS NON CORE
Summary: Pro-apoptotic effects of neurofibromin in some cell types are downstream of its modulation of RAS-pathway survival signalling.
Reason: Downstream apoptotic-balance phenotype.
GO:0007265 Ras protein signal transduction
IGI
PMID:10845775
Neurofibromin negatively regulates neurotrophin signaling th...
KEEP AS NON CORE
Summary: Neurofibromin participates in RAS signalling specifically as its negative regulator; the broad 'Ras protein signal transduction' term is less precise than the negative-regulation term.
Reason: Subsumed by the more specific negative-regulation-of-Ras core term; kept as supporting context.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:10620616
Genetic and biochemical evidence that haploinsufficiency of ...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:10973261
Nf1;Trp53 mutant mice develop glioblastoma with evidence of ...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:9001241
Nf1-deficient mouse Schwann cells are angiogenic and invasiv...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0021987 cerebral cortex development
IMP
PMID:11297510
Ablation of NF1 function in neurons induces abnormal develop...
KEEP AS NON CORE
Summary: Cortical development is impaired by RAS dysregulation in NF1-deficient mice; a region-specific downstream developmental phenotype.
Reason: Region-specific CNS developmental phenotype.
GO:0022011 myelination in peripheral nervous system
IMP
PMID:10586246
Neurofibromin, the neurofibromatosis type 1 Ras-GAP, is requ...
KEEP AS NON CORE
Summary: PNS myelination by Schwann cells is sensitive to RAS dosage controlled by neurofibromin, so myelination defects are a downstream effect of NF1 loss.
Reason: Downstream PNS phenotype of dysregulated RAS in Schwann cells.
GO:0042127 regulation of cell population proliferation
IGI
PMID:10678181
Nf1 and Gmcsf interact in myeloid leukemogenesis.
KEEP AS NON CORE
Summary: General control of proliferation by neurofibromin follows from its modulation of RAS mitogenic signalling.
Reason: Downstream/generic proliferation control, IGI.
GO:0043407 negative regulation of MAP kinase activity
IGI
PMID:10620616
Genetic and biochemical evidence that haploinsufficiency of ...
KEEP AS NON CORE
Summary: Lowered ERK/MAPK activity results indirectly from neurofibromin reducing RAS-GTP; it acts on RAS, not directly on the MAP kinase.
Reason: Indirect downstream effect of RasGAP activity on RAS.
GO:0043407 negative regulation of MAP kinase activity
IMP
PMID:11297510
Ablation of NF1 function in neurons induces abnormal develop...
KEEP AS NON CORE
Summary: Lowered ERK/MAPK activity results indirectly from neurofibromin reducing RAS-GTP; it acts on RAS, not directly on the MAP kinase.
Reason: Indirect downstream effect of RasGAP activity on RAS.
GO:0043473 pigmentation
IMP
PMID:10844550
The neurofibromatosis type 1 (Nf1) tumor suppressor is a mod...
KEEP AS NON CORE
Summary: Pigmentation phenotypes (cafe-au-lait-like) arise because melanocyte RAS signalling, normally restrained by neurofibromin, is dysregulated on NF1 loss.
Reason: Downstream melanocyte phenotype.
GO:0043525 positive regulation of neuron apoptotic process
IGI
PMID:10845775
Neurofibromin negatively regulates neurotrophin signaling th...
KEEP AS NON CORE
Summary: Promotion of neuronal apoptosis in NF1 contexts reflects altered RAS/PI3K survival signalling; a downstream neuronal phenotype.
Reason: Downstream neuronal apoptosis phenotype.
GO:0043525 positive regulation of neuron apoptotic process
IMP
PMID:11297510
Ablation of NF1 function in neurons induces abnormal develop...
KEEP AS NON CORE
Summary: Promotion of neuronal apoptosis in NF1 contexts reflects altered RAS/PI3K survival signalling; a downstream neuronal phenotype.
Reason: Downstream neuronal apoptosis phenotype.
GO:0043525 positive regulation of neuron apoptotic process
IMP
PMID:7671302
Loss of neurofibromin results in neurotrophin-independent su...
KEEP AS NON CORE
Summary: Promotion of neuronal apoptosis in NF1 contexts reflects altered RAS/PI3K survival signalling; a downstream neuronal phenotype.
Reason: Downstream neuronal apoptosis phenotype.
GO:0048712 negative regulation of astrocyte differentiation
IMP
PMID:11297510
Ablation of NF1 function in neurons induces abnormal develop...
KEEP AS NON CORE
Summary: By limiting RAS/MAPK signalling neurofibromin restrains astrocyte fate; loss promotes astrogliogenesis, a downstream developmental effect.
Reason: Downstream gliogenesis phenotype of elevated RAS.
GO:0048853 forebrain morphogenesis
IMP
PMID:11297510
Ablation of NF1 function in neurons induces abnormal develop...
KEEP AS NON CORE
Summary: Forebrain morphogenesis depends on properly tuned RAS signalling enforced by neurofibromin; defects are a downstream developmental consequence.
Reason: Downstream forebrain morphogenesis phenotype.
GO:0007265 Ras protein signal transduction
IMP
PMID:10498620
In vitro and in vivo effects of a farnesyltransferase inhibi...
KEEP AS NON CORE
Summary: Neurofibromin participates in RAS signalling specifically as its negative regulator; the broad 'Ras protein signal transduction' term is less precise than the negative-regulation term.
Reason: Subsumed by the more specific negative-regulation-of-Ras core term; kept as supporting context.
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:10498620
In vitro and in vivo effects of a farnesyltransferase inhibi...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:10591652
Mouse models of tumor development in neurofibromatosis type ...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IGI
PMID:10591653
Mouse tumor model for neurofibromatosis type 1.
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0043473 pigmentation
IMP
PMID:10594763
Induction of melanogenic abnormalities in NF1+/- mutant mice...
KEEP AS NON CORE
Summary: Pigmentation phenotypes (cafe-au-lait-like) arise because melanocyte RAS signalling, normally restrained by neurofibromin, is dysregulated on NF1 loss.
Reason: Downstream melanocyte phenotype.
GO:0043473 pigmentation
IGI
PMID:10620616
Genetic and biochemical evidence that haploinsufficiency of ...
KEEP AS NON CORE
Summary: Pigmentation phenotypes (cafe-au-lait-like) arise because melanocyte RAS signalling, normally restrained by neurofibromin, is dysregulated on NF1 loss.
Reason: Downstream melanocyte phenotype.
GO:0007154 cell communication
IMP
PMID:10442636
Haploinsufficiency for the neurofibromatosis 1 (NF1) tumor s...
KEEP AS NON CORE
Summary: Generic 'cell communication' captures neurofibromin's signalling involvement at a very high level and is far less informative than its RasGAP terms.
Reason: Generic high-level signalling process; non-core.
GO:0007420 brain development
IMP
PMID:10419687
Neurofibromin deficiency in mice causes exencephaly and is a...
KEEP AS NON CORE
Summary: Broad brain development is affected because neurofibromin's control of RAS/MAPK is required for normal neural proliferation and patterning.
Reason: Broad downstream CNS developmental phenotype.
GO:0007422 peripheral nervous system development
IMP
PMID:10419687
Neurofibromin deficiency in mice causes exencephaly and is a...
KEEP AS NON CORE
Summary: Broad PNS development is affected via Schwann-cell and neural-crest derivatives whose RAS signalling neurofibromin restrains.
Reason: Broad downstream developmental process.
GO:0007507 heart development
IMP
PMID:10419687
Neurofibromin deficiency in mice causes exencephaly and is a...
KEEP AS NON CORE
Summary: Nf1-null embryos show cardiovascular defects and mid-gestation lethality because controlled RAS/MAPK and PI3K signalling is required for cardiac morphogenesis.
Reason: Downstream organ-development phenotype (well documented in mouse).
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:10383727
The Nf1 tumor suppressor regulates mouse skin wound healing,...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:10442636
Haploinsufficiency for the neurofibromatosis 1 (NF1) tumor s...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0021915 neural tube development
IGI
PMID:10419687
Neurofibromin deficiency in mice causes exencephaly and is a...
KEEP AS NON CORE
Summary: Neural-tube development is among the embryonic processes sensitive to RAS dosage controlled by neurofibromin.
Reason: Embryonic CNS developmental phenotype, IGI.
GO:0030199 collagen fibril organization
IMP
PMID:10383727
The Nf1 tumor suppressor regulates mouse skin wound healing,...
KEEP AS NON CORE
Summary: Altered collagen fibril organization reflects effects of NF1 loss on fibroblast/ECM behaviour downstream of RAS signalling.
Reason: Downstream ECM/connective-tissue phenotype.
GO:0042060 wound healing
IMP
PMID:10383727
The Nf1 tumor suppressor regulates mouse skin wound healing,...
KEEP AS NON CORE
Summary: Wound-healing defects reflect altered proliferation/migration/ECM behaviour downstream of neurofibromin's RAS signalling control.
Reason: Downstream integrative physiological phenotype.
GO:0048593 camera-type eye morphogenesis
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Eye morphogenesis defects in Nf1 mutants reflect the requirement for controlled RAS signalling during ocular development.
Reason: Organ-development phenotype downstream of RAS control.
GO:0048712 negative regulation of astrocyte differentiation
IMP
PMID:10442636
Haploinsufficiency for the neurofibromatosis 1 (NF1) tumor s...
KEEP AS NON CORE
Summary: By limiting RAS/MAPK signalling neurofibromin restrains astrocyte fate; loss promotes astrogliogenesis, a downstream developmental effect.
Reason: Downstream gliogenesis phenotype of elevated RAS.
GO:0048712 negative regulation of astrocyte differentiation
IMP
PMID:9878702
Region-specific astrogliosis in brains of mice heterozygous ...
KEEP AS NON CORE
Summary: By limiting RAS/MAPK signalling neurofibromin restrains astrocyte fate; loss promotes astrogliogenesis, a downstream developmental effect.
Reason: Downstream gliogenesis phenotype of elevated RAS.
GO:0001656 metanephros development
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Metanephric kidney development is affected in Nf1 mutants secondary to dysregulated RAS signalling in developing tissues.
Reason: Organ-development phenotype, IMP.
GO:0001889 liver development
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Liver development is among the organogenesis processes perturbed by NF1 loss via altered RAS signalling.
Reason: Organ-development phenotype, IMP.
GO:0005096 GTPase activator activity
IMP
PMID:8563750
Nf1 deficiency causes Ras-mediated granulocyte/macrophage co...
ACCEPT
Summary: Neurofibromin's GAP-related domain supplies an arginine finger (Arg1278) that stabilizes the RAS GTP-hydrolysis transition state; this RasGAP activity is the defining function of the protein.
Reason: Defining biochemical activity (RasGAP); strongly supported by domain architecture and IMP/IGI/ISO evidence.
Supporting Evidence:
UniProt:Q04690
Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
file:mouse/Nf1/Nf1-deep-research-falcon.md
Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.
GO:0007265 Ras protein signal transduction
IMP
PMID:8563750
Nf1 deficiency causes Ras-mediated granulocyte/macrophage co...
KEEP AS NON CORE
Summary: Neurofibromin participates in RAS signalling specifically as its negative regulator; the broad 'Ras protein signal transduction' term is less precise than the negative-regulation term.
Reason: Subsumed by the more specific negative-regulation-of-Ras core term; kept as supporting context.
GO:0007265 Ras protein signal transduction
IMP
PMID:9001241
Nf1-deficient mouse Schwann cells are angiogenic and invasiv...
KEEP AS NON CORE
Summary: Neurofibromin participates in RAS signalling specifically as its negative regulator; the broad 'Ras protein signal transduction' term is less precise than the negative-regulation term.
Reason: Subsumed by the more specific negative-regulation-of-Ras core term; kept as supporting context.
GO:0007406 negative regulation of neuroblast proliferation
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Neurofibromin limits neuroblast proliferation by restraining RAS-driven cell-cycle entry; a downstream antiproliferative role in the nervous system.
Reason: Downstream antiproliferative phenotype of the RAS brake.
GO:0007507 heart development
IMP
PMID:7920653
Tumour predisposition in mice heterozygous for a targeted mu...
KEEP AS NON CORE
Summary: Nf1-null embryos show cardiovascular defects and mid-gestation lethality because controlled RAS/MAPK and PI3K signalling is required for cardiac morphogenesis.
Reason: Downstream organ-development phenotype (well documented in mouse).
GO:0007507 heart development
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Nf1-null embryos show cardiovascular defects and mid-gestation lethality because controlled RAS/MAPK and PI3K signalling is required for cardiac morphogenesis.
Reason: Downstream organ-development phenotype (well documented in mouse).
GO:0007519 skeletal muscle tissue development
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Skeletal-muscle development is influenced by NF1 loss through altered RAS/MAPK signalling; a downstream tissue-development phenotype.
Reason: Tissue-development phenotype, IMP.
GO:0008017 microtubule binding
ISO
GO_REF:0000008
KEEP AS NON CORE
Summary: ISO-projected microtubule binding has been linked to neurofibromin in mitotic/tubulin contexts but is peripheral to its core membrane-proximal RasGAP role.
Reason: Ancillary, electronically projected binding; not core function.
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:8563750
Nf1 deficiency causes Ras-mediated granulocyte/macrophage co...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008285 negative regulation of cell population proliferation
IMP
PMID:9001241
Nf1-deficient mouse Schwann cells are angiogenic and invasiv...
KEEP AS NON CORE
Summary: Neurofibromin restrains proliferation by lowering RAS-driven mitogenic signalling; its tumour-suppressor antiproliferative output is downstream of the RasGAP step.
Reason: Downstream antiproliferative (tumour-suppressor) phenotype.
GO:0008542 visual learning
IGI
PMID:9054942
A mouse model for the learning and memory deficits associate...
KEEP AS NON CORE
Summary: Visual-learning deficits in Nf1+/- mice trace to excess RAS/cAMP-dependent synaptic signalling, a downstream behavioural readout.
Reason: Behavioural learning phenotype downstream of RAS/cAMP.
GO:0014044 Schwann cell development
IMP
PMID:9001241
Nf1-deficient mouse Schwann cells are angiogenic and invasiv...
KEEP AS NON CORE
Summary: Schwann-cell development is disrupted by NF1 loss because hyperactive RAS deregulates glial proliferation/differentiation; a downstream developmental phenotype.
Reason: Developmental phenotype downstream of the RAS brake.
GO:0048485 sympathetic nervous system development
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Sympathetic (neural-crest-derived) development is perturbed by elevated RAS in NF1-deficient cells, a downstream developmental phenotype.
Reason: Neural-crest-derived developmental phenotype.
GO:0048745 smooth muscle tissue development
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Smooth-muscle development, relevant to vascular phenotypes, is perturbed downstream of neurofibromin's RAS control.
Reason: Tissue-development phenotype, IMP.
GO:0048844 artery morphogenesis
IMP
PMID:7926784
Targeted disruption of the neurofibromatosis type-1 gene lea...
KEEP AS NON CORE
Summary: Artery morphogenesis is disrupted by NF1 loss through dysregulated RAS signalling in vascular cells; a downstream cardiovascular phenotype.
Reason: Downstream vascular developmental phenotype.
GO:0005737 cytoplasm
IDA
PMID:15133494
JCV T-antigen interacts with the neurofibromatosis type 2 ge...
KEEP AS NON CORE
Summary: Neurofibromin is a large cytoplasmic protein; the cytoplasm assignment is a generic compartment broader than the membrane-proximal site where it regulates RAS.
Reason: Generic compartment; supportive but less informative than plasma-membrane localization.
GO:0007265 Ras protein signal transduction
IMP
PMID:16906226
The neurofibromin GAP-related domain rescues endothelial but...
KEEP AS NON CORE
Summary: Neurofibromin participates in RAS signalling specifically as its negative regulator; the broad 'Ras protein signal transduction' term is less precise than the negative-regulation term.
Reason: Subsumed by the more specific negative-regulation-of-Ras core term; kept as supporting context.
GO:0007507 heart development
IMP
PMID:16906226
The neurofibromin GAP-related domain rescues endothelial but...
KEEP AS NON CORE
Summary: Nf1-null embryos show cardiovascular defects and mid-gestation lethality because controlled RAS/MAPK and PI3K signalling is required for cardiac morphogenesis.
Reason: Downstream organ-development phenotype (well documented in mouse).
GO:0021510 spinal cord development
IMP
PMID:16906226
The neurofibromin GAP-related domain rescues endothelial but...
KEEP AS NON CORE
Summary: Spinal cord development is affected by NF1 loss through dysregulated RAS signalling in neural progenitors.
Reason: Region-specific CNS developmental phenotype.
GO:0030325 adrenal gland development
IMP
PMID:16906226
The neurofibromin GAP-related domain rescues endothelial but...
KEEP AS NON CORE
Summary: Adrenal (neural-crest-derived) development is affected in Nf1 mutants through dysregulated RAS signalling; a downstream developmental phenotype.
Reason: Organ-development phenotype, IMP.
GO:0045685 regulation of glial cell differentiation
IMP
PMID:12904481
Aberrant growth and differentiation of oligodendrocyte proge...
KEEP AS NON CORE
Summary: Glial differentiation is steered by RAS-pathway tone, so its regulation is an indirect consequence of neurofibromin's RasGAP activity.
Reason: Downstream glial regulation secondary to RAS control.
GO:0048485 sympathetic nervous system development
IMP
PMID:16906226
The neurofibromin GAP-related domain rescues endothelial but...
KEEP AS NON CORE
Summary: Sympathetic (neural-crest-derived) development is perturbed by elevated RAS in NF1-deficient cells, a downstream developmental phenotype.
Reason: Neural-crest-derived developmental phenotype.

Core Functions

Functions as a RasGAP that stimulates Ras GTP hydrolysis, thereby converting active Ras-GTP to inactive Ras-GDP and attenuating Ras-dependent signaling.

Supporting Evidence:
  • UniProt:Q04690
    Stimulates the GTPase activity of Ras (By similarity). NF1 shows greater affinity for Ras GAP, but lower specific activity (By similarity). May be a regulator of Ras activity (By similarity).
  • file:mouse/Nf1/Nf1-deep-research-falcon.md
    Neurofibromin is a **RAS GTPase-activating protein** that accelerates RAS GTP hydrolysis (RAS-GTP -> RAS-GDP), thereby negatively regulating Ras signaling.

References

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Deep Research

Falcon

(Nf1-deep-research-falcon.md)

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