Kynurenine pathway / de novo NAD+ biosynthesis from tryptophan (TDO2/IDO1/AFMID/KMO/KYNU/HAAO/ACMSD/QPRT)

The kynurenine pathway is the major route of L-tryptophan catabolism and the sole de novo source of NAD+ in humans, converting tryptophan through a series of ring-opening and modification steps to quinolinate and then to nicotinate mononucleotide (NaMN), which enters the common NAD+ pathway. It also generates neuroactive branch metabolites (kynurenic acid, quinolinic acid) and is central to immune regulation. The committed first step — oxidative ring cleavage of L-tryptophan to N-formyl-L-kynurenine — is catalysed by two heme dioxygenases with distinct physiology: the hepatic, rate-limiting TDO2 (tryptophan 2,3-dioxygenase) and the broadly IFN-gamma-inducible, immunoregulatory IDO1 (indoleamine 2,3-dioxygenase). The formamidase AFMID then hydrolyses N-formyl-kynurenine to L-kynurenine. Flux toward NAD+ requires the FAD-dependent, outer-mitochondrial-membrane kynurenine 3-monooxygenase KMO to hydroxylate kynurenine to 3-hydroxykynurenine (diverting away from the kynurenic-acid branch made by the aminotransferases AADAT/GOT2), followed by the PLP-dependent kynureninase KYNU, which cleaves 3-hydroxykynurenine to 3-hydroxyanthranilate. The Fe(II)-dependent dioxygenase HAAO opens the aromatic ring of 3-hydroxyanthranilate to 2-amino-3-carboxymuconate semialdehyde (ACMS), which spontaneously cyclises to quinolinate — unless the zinc enzyme ACMSD decarboxylates ACMS instead, diverting flux away from NAD+ toward full oxidation (picolinate/ acetyl-CoA). Finally quinolinate phosphoribosyltransferase QPRT condenses quinolinate with PRPP to NaMN, completing de novo NAD+ synthesis and detoxifying excitotoxic quinolinate. Inherited HAAO and KYNU deficiencies cause a congenital NAD-deficiency malformation syndrome (niacin-preventable in models); the pathway's enzymes (IDO1, TDO2, KMO, ACMSD) are drug targets in cancer immunotherapy, neurodegeneration and metabolic disease.

MODULE:kynurenine_nad_de_novoDRAFTMetabolic Pathwaymodules/kynurenine_nad_de_novo.yaml
'de novo' NAD+ biosynthetic process from L-tryptophanGO:0034354 L-tryptophan catabolic processGO:0006569
GO:0034354
'de novo' NAD+ biosynthetic process from L-tryptophan
The pathway is the de novo NAD+ biosynthetic process from L-tryptophan (GO:0034354).
GO:0006569
L-tryptophan catabolic process
It is the major L-tryptophan catabolic process (GO:0006569), the kynurenine pathway.
file:human/TDO2/TDO2-ai-review.yaml
TDO2 gene review (human)
The hepatic tryptophan-dioxygenase step (UniProtKB:P48775, GO:0004833) matches the completed human TDO2 review.
file:human/IDO1/IDO1-ai-review.yaml
IDO1 gene review (human)
The immunoregulatory indoleamine-dioxygenase step (UniProtKB:P14902, GO:0033754) matches the completed human IDO1 review.
file:human/AFMID/AFMID-ai-review.yaml
AFMID gene review (human)
The formamidase step (UniProtKB:Q63HM1, GO:0004061) matches the completed human AFMID review.
file:human/KMO/KMO-ai-review.yaml
KMO gene review (human)
The kynurenine 3-monooxygenase step (UniProtKB:O15229, GO:0004502) matches the completed human KMO review.
file:human/KYNU/KYNU-ai-review.yaml
KYNU gene review (human)
The kynureninase step (UniProtKB:Q16719, GO:0030429) matches the completed human KYNU review.
file:human/HAAO/HAAO-ai-review.yaml
HAAO gene review (human)
The 3-hydroxyanthranilate dioxygenase step (UniProtKB:P46952, GO:0000334) matches the completed human HAAO review.
file:human/ACMSD/ACMSD-ai-review.yaml
ACMSD gene review (human)
The ACMS decarboxylase branch-point step (UniProtKB:Q8TDX5, GO:0001760) matches the completed human ACMSD review.
file:human/QPRT/QPRT-ai-review.yaml
QPRT gene review (human)
The quinolinate phosphoribosyltransferase step (UniProtKB:Q15274, GO:0004514) matches the completed human QPRT review.
4Nodes
3Parts
0Variant Sets
0Variants
8Annotons
2Connections

Derived QC

Recommended-field compliance

100.0% recommended fields populated

All recommended fields populated.

Module deep research

✗ none found

No MODULE:kynurenine_nad_de_novo deep-research report alongside the module YAML.

Leaf nodes lacking representative members

every leaf node grounds to a representative protein.

Template conformance

every declared conforms_to bundle matches its template motif.

Gene-review completeness (8/8 grounded genes reviewed)

8 complete review(s) · 0 with deep research · 0 missing review · 8 reviewed but lacking deep research

Gene Review Complete Deep research
ACMSD Q8TDX5
AFMID Q63HM1
HAAO P46952
IDO1 P14902
KMO O15229
KYNU Q16719
QPRT Q15274
TDO2 P48775

Details

Context
cytosolGO:0005829 mitochondrial outer membraneGO:0005741
Kynurenine pathway / de novo NAD+ biosynthesis from tryptophanMetabolic Pathwaykynurenine_nad_de_novo
'de novo' NAD+ biosynthetic process from L-tryptophanGO:0034354 L-tryptophan catabolic processGO:0006569
Context
cytosolGO:0005829 mitochondrial outer membraneGO:0005741

The kynurenine pathway / de novo NAD+ biosynthesis from L-tryptophan (GO:0034354; GO:0006569), grounded to the completed human gene reviews: TDO2 (P48775, GO:0004833 + heme, hepatic rate- limiting) and IDO1 (P14902, GO:0033754 + heme, immunoregulatory) catalyse the same first step; AFMID (Q63HM1, GO:0004061) makes kynurenine; KMO (O15229, GO:0004502 + FAD, outer mitochondrial membrane) and KYNU (Q16719, GO:0030429 + PLP) make 3-hydroxyanthranilate; HAAO (P46952, GO:0000334 + Fe2+) makes ACMS -> quinolinate; ACMSD (Q8TDX5, GO:0001760 + Zn) diverts ACMS away from NAD+; and QPRT (Q15274, GO:0004514) converts quinolinate to NaMN. The kynurenic-acid branch is made by AADAT/GOT2 (aminotransferases; AADAT curated in the lysine module). GO term ids/labels verified against the local go.db (note GO:0004833 is the TDO term, GO:0033754 the IDO term — distinct; GO:0019441 tryptophan-to-kynurenine BP and GO:0047611 for ACMSD are obsolete, replaced by GO:0006569 and GO:0001760). NaMN enters the common NAD+ salvage/biosynthesis pathway (NMNAT/NADSYN). Disorders: HAAO/KYNU deficiency — congenital NAD-deficiency malformation syndrome (VCRL, niacin-preventable); IDO1/TDO2/KMO/ACMSD are drug targets in cancer immunotherapy, neurodegeneration and NAD+-related metabolic disease.

Connections

trp_to_kynurenine -> kynurenine_to_3haa Provides Input For
L-kynurenine from the dioxygenase/formamidase step is hydroxylated (KMO) and cleaved (KYNU) to 3-hydroxyanthranilate.
kynurenine_to_3haa -> three_haa_to_nad Provides Input For
3-hydroxyanthranilate is opened by HAAO to ACMS -> quinolinate, which QPRT converts to NaMN for NAD+ (ACMSD diverts a fraction away).
Part 1: tryptophan ring cleavage and formamide hydrolysis (-> kynurenine)
Tryptophan -> L-kynurenine (TDO2/IDO1, AFMID)Reactiontrp_to_kynurenine

Annotons

TDO2: tryptophan 2,3-dioxygenase (hepatic, rate-limiting)
tdo2_activity
Participant: Family: TDO2 / tryptophan 2,3-dioxygenase family
Family:
TDO2 / tryptophan 2,3-dioxygenase familyPANTHER:PTHR10138
Representative Members: TDO2 (human)UniProtKB:P48775

Function

L-tryptophan 2,3-dioxygenase activityGO:0004833
Substrates: L-tryptophan O2 (heme cofactor)
Products: N-formyl-L-kynurenine

Locations

cytosolGO:0005829

Rate-limiting heme dioxygenase; opens the tryptophan ring (hepatic).

IDO1: indoleamine 2,3-dioxygenase (immunoregulatory)
ido1_activity
Participant: Family: IDO / indoleamine 2,3-dioxygenase family
Family:
IDO / indoleamine 2,3-dioxygenase familyPANTHER:PTHR28657
Representative Members: IDO1 (human)UniProtKB:P14902

Function

indoleamine 2,3-dioxygenase activityGO:0033754
Substrates: L-tryptophan / indoleamines O2 (heme cofactor)
Products: N-formyl-L-kynurenine

Locations

cytosolGO:0005829

Inducible immunoregulatory heme dioxygenase (alternative first step).

AFMID: arylformamidase (kynurenine formamidase)
afmid_activity
Participant: Family: AFMID / kynurenine formamidase family
Family:
AFMID / kynurenine formamidase familyPANTHER:PTHR48081
Representative Members: AFMID (human)UniProtKB:Q63HM1

Function

arylformamidase activityGO:0004061
Substrates: N-formyl-L-kynurenine H2O
Products: L-kynurenine formate

Locations

cytosolGO:0005829

Hydrolyses N-formyl-L-kynurenine to L-kynurenine.

Part 2: kynurenine hydroxylation and cleavage (-> 3-hydroxyanthranilate)
Kynurenine -> 3-hydroxyanthranilate (KMO, KYNU)Reactionkynurenine_to_3haa

Annotons

KMO: kynurenine 3-monooxygenase (OMM, FAD)
kmo_activity
Participant: Family: KMO / kynurenine 3-monooxygenase family
Family:
KMO / kynurenine 3-monooxygenase familyPANTHER:PTHR46028
Representative Members: KMO (human)UniProtKB:O15229

Function

kynurenine 3-monooxygenase activityGO:0004502
Substrates: L-kynurenine NADPH + O2 (FAD cofactor)
Products: 3-hydroxy-L-kynurenine

Locations

mitochondrial outer membraneGO:0005741

Hydroxylates kynurenine to 3-hydroxykynurenine (commits toward NAD+).

KYNU: kynureninase (PLP)
kynu_activity
Participant: Family: KYNU / kynureninase family
Family:
KYNU / kynureninase familyPANTHER:PTHR14084
Representative Members: KYNU (human)UniProtKB:Q16719

Function

kynureninase activityGO:0030429
Substrates: 3-hydroxy-L-kynurenine H2O
Products: 3-hydroxyanthranilate L-alanine

Locations

cytosolGO:0005829

Cleaves 3-hydroxykynurenine to 3-hydroxyanthranilate.

Part 3: quinolinate formation, branch control and NAD+ entry
3-hydroxyanthranilate -> quinolinate -> NaMN (HAAO, ACMSD, QPRT)Reactionthree_haa_to_nad

Annotons

HAAO: 3-hydroxyanthranilate 3,4-dioxygenase (Fe)
haao_activity
Participant: Family: HAAO / 3-hydroxyanthranilate 3,4-dioxygenase family
Family:
HAAO / 3-hydroxyanthranilate 3,4-dioxygenase familyPANTHER:PTHR15497
Representative Members: HAAO (human)UniProtKB:P46952

Function

3-hydroxyanthranilate 3,4-dioxygenase activityGO:0000334
Substrates: 3-hydroxyanthranilate O2 (Fe2+ cofactor)
Products: 2-amino-3-carboxymuconate semialdehyde (ACMS) -> quinolinate (spontaneous)

Locations

cytosolGO:0005829

Opens 3-hydroxyanthranilate to ACMS (-> quinolinate).

ACMSD: ACMS decarboxylase (branch away from NAD+)
acmsd_activity
Participant: Family: ACMSD / aminocarboxymuconate-semialdehyde decarboxylase family
Family:
ACMSD / aminocarboxymuconate-semialdehyde decarboxylase familyPANTHER:PTHR21240
Representative Members: ACMSD (human)UniProtKB:Q8TDX5

Function

aminocarboxymuconate-semialdehyde decarboxylase activityGO:0001760
Substrates: 2-amino-3-carboxymuconate semialdehyde (ACMS)
Products: 2-aminomuconate semialdehyde (diverted to picolinate/acetyl-CoA, away from NAD+)

Locations

cytosolGO:0005829

Decarboxylates ACMS, diverting flux away from quinolinate/NAD+.

QPRT: quinolinate phosphoribosyltransferase (-> NaMN -> NAD+)
qprt_activity
Participant: Family: QPRT / quinolinate phosphoribosyltransferase family
Family:
QPRT / quinolinate phosphoribosyltransferase familyPANTHER:PTHR32179
Representative Members: QPRT (human)UniProtKB:Q15274

Function

nicotinate-nucleotide diphosphorylase (carboxylating) activityGO:0004514
Substrates: quinolinate 5-phospho-alpha-D-ribose 1-diphosphate (PRPP)
Products: nicotinate D-ribonucleotide (NaMN) -> NAD+ CO2

Locations

cytosolGO:0005829

Converts quinolinate to NaMN (enters the common NAD+ pathway).