RNF5

UniProt ID: Q99942
Organism: Homo sapiens
Review Status: COMPLETE
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Gene Description

RNF5 (RMA1, NG2/G16) is a small (180 aa) tail-anchored RING-type E3 ubiquitin-protein ligase (EC 2.3.2.27) embedded in the endoplasmic reticulum membrane via two C-terminal transmembrane helices, with an N-terminal cytosolic C3HC4 RING domain (catalytic Cys-42) that recruits ubiquitin-charged E2 enzymes (notably the UBE2D/UbcH5 family and UBE2N/Ubc13). RNF5 is one of the founding mammalian ER-anchored ERAD ubiquitin ligases. Together with the E2 UBE2J1/Ubc6e and Derlin-1 it recognizes folding defects in membrane proteins co-translationally and assembles K48-linked polyubiquitin chains that commit misfolded clients such as CFTR and the disease-associated CFTR-deltaF508 mutant to retrotranslocation and proteasomal degradation; it functions partly redundantly with its close paralog RNF185, with which it forms an E3 ligase module central to CFTR degradation. Beyond canonical ERAD, RNF5 has documented ligase-dependent regulatory roles that use distinct chain topologies and substrates. It builds non-degradative K63-linked chains on the ERAD adaptor JKAMP/JAMP to limit its recruitment of proteasome and p97/VCP components; it ubiquitinates and degrades the innate-immune adaptor STING1/MITA at mitochondria to dampen antiviral type I interferon responses; it controls basal autophagy by regulating the stability of a membrane pool of the cysteine protease ATG4B; and it ubiquitinates paxillin to influence cell motility. RNF5 is widely expressed, and although localized predominantly to membranes (with reported plasma-membrane and mitochondrial-membrane pools), its ER-membrane localization underlies its core ERAD ligase function.

Existing Annotations Review

GO Term Evidence Action Reason
GO:0061630 ubiquitin protein ligase activity
IBA
GO_REF:0000033
ACCEPT
Summary: Phylogenetic assignment of RING-type ubiquitin ligase activity, the core molecular function of RNF5, conserved across the RNF5/RNF185 family.
Reason: Core molecular function; supported experimentally (EC 2.3.2.27; C42S abolishes activity) and across the family.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Membrane-bound E3 ubiquitin-protein ligase that mediates ubiquitination of target proteins
GO:0036503 ERAD pathway
IBA
GO_REF:0000033
ACCEPT
Summary: Phylogenetic assignment of involvement in ER-associated degradation, the core biological process of RNF5 as an ER-anchored ERAD ligase.
Reason: Core biological process; directly supported by IMP evidence (CFTR/CFTR-deltaF508 degradation) and conserved in the family.
Supporting Evidence:
PMID:24019521
Cystic fibrosis transmembrane conductance regulator (CFTR) is one ERAD substrate targeted to co-translational degradation by the E3 ligase RNF5/RMA1
GO:0044390 ubiquitin-like protein conjugating enzyme binding
IBA
GO_REF:0000033
KEEP AS NON CORE
Summary: RNF5 binds ubiquitin-conjugating (E2) enzymes, including the UBE2D/UbcH5 family and UBE2N/Ubc13, as part of its catalytic cycle. This is informative but ancillary to the ligase activity itself.
Reason: Accurately reflects E2 binding (UBE2D1/UBE2D2, UBE2N) required for catalysis, but is a mechanistic subsidiary of the core ubiquitin ligase activity.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
May function together with E2 ubiquitin-conjugating enzymes UBE2D1/UBCH5A and UBE2D2/UBC4
GO:0005783 endoplasmic reticulum
IEA
GO_REF:0000002
ACCEPT
Summary: InterPro-based electronic assignment of ER localization, consistent with RNF5's ER-membrane site of ERAD function.
Reason: Correct compartment; redundant with the more specific ER membrane annotations and IDA (HPA) evidence.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Endoplasmic reticulum membrane {ECO:0000269|PubMed:19285439}
GO:0005789 endoplasmic reticulum membrane
IEA
GO_REF:0000044
ACCEPT
Summary: Electronic transfer of ER membrane localization from the UniProt subcellular location; this is the core compartment for RNF5's ERAD ligase function.
Reason: Correct core localization; RNF5 is a tail-anchored ER membrane protein, supported experimentally (EXP, PMID:19285439).
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Endoplasmic reticulum membrane {ECO:0000269|PubMed:19285439}
GO:0005886 plasma membrane
IEA
GO_REF:0000044
KEEP AS NON CORE
Summary: Electronic transfer of plasma membrane localization from the original cloning study (PMID:9533025). A real but secondary localization not tied to the core ERAD function.
Reason: Reported in the early cloning paper but the functionally dominant compartment for RNF5 is the ER membrane; plasma membrane pool is peripheral.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Cell membrane {ECO:0000269|PubMed:9533025}
GO:0006511 ubiquitin-dependent protein catabolic process
IEA
GO_REF:0000002
ACCEPT
Summary: InterPro-based electronic assignment of ubiquitin-dependent protein catabolism, a parent process consistent with RNF5's ERAD role.
Reason: Correct but generic; the specific GO:0036503 (ERAD pathway) better captures the core biological role.
Supporting Evidence:
PMID:24019521
degraded by the ubiquitin-proteasome pathway through a process called ER-associated degradation (ERAD)
GO:0031966 mitochondrial membrane
IEA
GO_REF:0000044
KEEP AS NON CORE
Summary: Electronic transfer of mitochondrial membrane localization, reflecting the antiviral STING1/MITA study in which RNF5 acts at mitochondria. A real but secondary, immunity-related localization.
Reason: Supported by PMID:19285439 (MITA ubiquitination at mitochondria) but represents a secondary, context-specific role distinct from the core ER-membrane ERAD function.
Supporting Evidence:
PMID:19285439
virus-induced ubiquitination and degradation of MITA by RNF5 occurred at the mitochondria
GO:0036503 ERAD pathway
IEA
GO_REF:0000117
ACCEPT
Summary: ARBA machine-learning electronic assignment of the ERAD pathway, redundant with the experimentally supported core process.
Reason: Correct core biological process; redundant with IMP and IBA evidence.
Supporting Evidence:
PMID:24019521
Cystic fibrosis transmembrane conductance regulator (CFTR) is one ERAD substrate targeted to co-translational degradation by the E3 ligase RNF5/RMA1
GO:0044322 endoplasmic reticulum quality control compartment
IEA
GO_REF:0000108
KEEP AS NON CORE
Summary: Inter-ontology logical inference placing RNF5 in the ER quality control compartment, a plausible localization derived from its ERAD role.
Reason: Plausible localization inferred from the ERAD/ERQC link, but not directly demonstrated; the core localization annotation is ER membrane.
Supporting Evidence:
PMID:24019521
hosts a machinery called ERQC for ER quality control
GO:0061630 ubiquitin protein ligase activity
IEA
GO_REF:0000120
ACCEPT
Summary: Combined automated electronic assignment of the core RING E3 ligase activity, consistent with EC 2.3.2.27 and experimental evidence.
Reason: Correct core molecular function; redundant with EXP/IBA evidence.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
EC=2.3.2.27
GO:1904380 endoplasmic reticulum mannose trimming
IEA
GO_REF:0000117
REMOVE
Summary: ARBA machine-learning assignment of ER mannose trimming. RNF5 is a ubiquitin ligase and does not trim mannose; this is a pathway-adjacency over-annotation propagated from the ERAD/ERQC context.
Reason: RNF5 has no glycosidase/mannosidase activity; mannose trimming is performed by EDEM/ER mannosidases, not by the E3 ligase. This electronic inference is biologically incorrect.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Membrane-bound E3 ubiquitin-protein ligase that mediates ubiquitination of target proteins
GO:0005515 protein binding
IPI
PMID:12861019
RNF5, a RING finger protein that regulates cell motility by ...
KEEP AS NON CORE
Summary: IntAct interaction with paxillin (PXN), a functionally meaningful RNF5 substrate, but the bare protein binding term is uninformative.
Reason: Records a real substrate interaction (PXN) but bare protein binding is uninformative per curation guidelines.
Supporting Evidence:
PMID:12861019
the human homologue of RNF5 associates with the amino-terminal domain of paxillin
GO:0005515 protein binding
IPI
PMID:14667819
Analysis of a high-throughput yeast two-hybrid system and it...
KEEP AS NON CORE
Summary: High-throughput yeast two-hybrid interactions (e.g. ABHD16A, UBE2 enzymes). Bare protein binding is uninformative.
Reason: Records real IntAct interactions but bare protein binding is uninformative and not a core function.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; O95870: ABHD16A
GO:0005515 protein binding
IPI
PMID:16901789
Sequential quality-control checkpoints triage misfolded cyst...
KEEP AS NON CORE
Summary: Interaction with CFTR captured in the sequential-triage ERAD study; CFTR is a key RNF5 ERAD substrate. Bare protein binding is uninformative.
Reason: Records the functionally important RNF5-CFTR interaction, but bare protein binding is uninformative; the substrate relationship is captured by the ERAD process annotations.
Supporting Evidence:
PMID:16901789
an ER membrane-associated ubiquitin ligase complex containing the E3 RMA1, the E2 Ubc6e, and Derlin-1
GO:0005515 protein binding
IPI
PMID:19549727
Analysis of the human E2 ubiquitin conjugating enzyme protei...
KEEP AS NON CORE
Summary: E2 ubiquitin-conjugating enzyme interaction network capturing RNF5 binding to multiple UBE2D/UBE2E/UBE2W E2s. Bare protein binding is uninformative.
Reason: Real E2 interactions relevant to catalysis but bare protein binding is uninformative; E2 binding is captured by GO:0044390.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; P51668: UBE2D1
GO:0005515 protein binding
IPI
PMID:20152160
Crystal structure of UbcH5b~ubiquitin intermediate: insight ...
KEEP AS NON CORE
Summary: Interaction with the E2 UBE2D2/UbcH5b from a structural study of the E2~Ub conjugate. Bare protein binding is uninformative.
Reason: Real E2 interaction but bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; P62837: UBE2D2
GO:0005515 protein binding
IPI
PMID:25416956
A proteome-scale map of the human interactome network.
KEEP AS NON CORE
Summary: Large-scale interactome map capturing numerous RNF5 partners (including SLC transporters, RNF185, SEC22A). Bare protein binding is uninformative.
Reason: High-throughput interactome; bare protein binding is uninformative and not a core function.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q96GF1: RNF185
GO:0005515 protein binding
IPI
PMID:25759021
Regulation of glutamine carrier proteins by RNF5 determines ...
KEEP AS NON CORE
Summary: Interactions with glutamine carrier proteins (SLC1A5, SLC38A2) relevant to RNF5's role in breast cancer ER-stress response. Bare protein binding is uninformative.
Reason: Records real substrate/carrier interactions but bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q15758: SLC1A5
GO:0005515 protein binding
IPI
PMID:26618866
βˆ†F508 CFTR interactome remodelling promotes rescue of cystic...
KEEP AS NON CORE
Summary: Interaction with CFTR from a deltaF508 CFTR interactome-remodeling study. Bare protein binding is uninformative.
Reason: Real CFTR interaction relevant to ERAD but bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; P13569: CFTR
GO:0005515 protein binding
IPI
PMID:31515488
Extensive disruption of protein interactions by genetic vari...
KEEP AS NON CORE
Summary: Interaction captured in a study of variant-driven interactome disruption. Bare protein binding is uninformative.
Reason: High-throughput interaction; bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q969T4: UBE2E3
GO:0005515 protein binding
IPI
PMID:32296183
A reference map of the human binary protein interactome.
KEEP AS NON CORE
Summary: Binary interactome reference map capturing many RNF5 membrane-protein partners. Bare protein binding is uninformative.
Reason: High-throughput interactome; bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q9Y5U4: INSIG2
GO:0005515 protein binding
IPI
PMID:32814053
Interactome Mapping Provides a Network of Neurodegenerative ...
KEEP AS NON CORE
Summary: Interactions (e.g. OPTN, UBE2K) from a neurodegenerative-disease interactome study. Bare protein binding is uninformative.
Reason: High-throughput interaction; bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q96CV9: OPTN
GO:0005515 protein binding
IPI
PMID:33961781
Dual proteome-scale networks reveal cell-specific remodeling...
KEEP AS NON CORE
Summary: Cell-specific interactome capturing RNF5 partners including RNF185 and RHBDD1. Bare protein binding is uninformative.
Reason: High-throughput interactome; bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q96GF1: RNF185
GO:0005515 protein binding
IPI
PMID:36012204
Differential CFTR-Interactome Proximity Labeling Procedures ...
KEEP AS NON CORE
Summary: Proximity-labeling interaction with CFTR identifying enrichment in SLC transporters. Bare protein binding is uninformative.
Reason: Real CFTR/SLC interactions but bare protein binding is uninformative.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; P13569: CFTR
GO:0042802 identical protein binding
IPI
PMID:25416956
A proteome-scale map of the human interactome network.
KEEP AS NON CORE
Summary: RNF5 self-interaction captured in a proteome-scale interactome. Reflects homo-association seen in screens.
Reason: Documents RNF5 self-association (IntAct EBI-348482 with itself) but is peripheral to the core ligase function.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q99942: RNF5
GO:0042802 identical protein binding
IPI
PMID:32296183
A reference map of the human binary protein interactome.
KEEP AS NON CORE
Summary: RNF5 self-interaction captured in the binary interactome reference map.
Reason: Documents RNF5 self-association but is peripheral to the core ligase function.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Q99942; Q99942: RNF5
GO:0016020 membrane
IEA
GO_REF:0000107
KEEP AS NON CORE
Summary: Ortholog-based electronic assignment of generic membrane localization, a parent of the specific ER membrane localization.
Reason: Correct but generic; subsumed by the more specific ER membrane localization.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Multi-pass membrane protein
GO:0055085 transmembrane transport
TAS
Reactome:R-HSA-382556
REMOVE
Summary: Reactome pathway-level annotation (ABC-family transport). RNF5 is a ubiquitin ligase, not a transporter; this reflects pathway context (CFTR/ABC transport) bleed-through.
Reason: RNF5 does not mediate transmembrane transport; it is an E3 ligase acting on transporter substrates such as CFTR. The transport annotation is a pathway-adjacency artifact, not a direct function.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Membrane-bound E3 ubiquitin-protein ligase that mediates ubiquitination of target proteins
GO:0016567 protein ubiquitination
IEA
GO_REF:0000041
KEEP AS NON CORE
Summary: UniPathway-derived general protein ubiquitination process, a parent of the specific ERAD-associated ubiquitination RNF5 performs.
Reason: Correct but generic; the specific ERAD pathway and K48/K63 ubiquitination annotations better capture the role.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
PATHWAY: Protein modification; protein ubiquitination.
GO:0061630 ubiquitin protein ligase activity
TAS
Reactome:R-HSA-8866546
ACCEPT
Summary: Reactome curation of RNF5 (with RNF185) ubiquitinating misfolded CFTR; captures the core ligase activity.
Reason: Correct core molecular function in the CFTR ERAD reaction.
Supporting Evidence:
PMID:24019521
identify RNF185 and RNF5 as a novel E3 ligase module that is central to the control of CFTR degradation
GO:0061630 ubiquitin protein ligase activity
TAS
Reactome:R-HSA-8867288
ACCEPT
Summary: Reactome curation of the ERAD E3 ligase ubiquitinating an unfolded glycoprotein substrate; captures the core ligase activity.
Reason: Correct core molecular function.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Membrane-bound E3 ubiquitin-protein ligase that mediates ubiquitination of target proteins
GO:0005783 endoplasmic reticulum
IDA
GO_REF:0000052
ACCEPT
Summary: Direct immunofluorescence (HPA) evidence for ER localization, consistent with RNF5's ER-membrane ERAD function.
Reason: IDA-supported ER localization agrees with the documented ER-membrane site of action.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Endoplasmic reticulum membrane {ECO:0000269|PubMed:19285439}
GO:0005789 endoplasmic reticulum membrane
EXP
PMID:19285439
The ubiquitin ligase RNF5 regulates antiviral responses by m...
ACCEPT
Summary: Experimental evidence that RNF5 localizes to the ER membrane; the core compartment for its ERAD ligase activity.
Reason: Core localization with direct experimental support.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005886 plasma membrane
EXP
PMID:9533025
Cloning, expression and mapping of a novel RING-finger gene ...
KEEP AS NON CORE
Summary: Experimental localization to the plasma membrane reported in the original cloning study. A real but secondary localization.
Reason: Documented in the cloning paper but the functionally dominant compartment is the ER membrane; plasma-membrane pool is peripheral to the core ERAD role.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Predominantly located in the plasma membrane, with some localization occurring within cytoplasmic organelles
GO:0031966 mitochondrial membrane
EXP
PMID:19285439
The ubiquitin ligase RNF5 regulates antiviral responses by m...
KEEP AS NON CORE
Summary: Experimental localization to the mitochondrial membrane, where RNF5 ubiquitinates STING1/MITA during antiviral responses. A real but secondary, immunity-related localization.
Reason: Directly supported (PMID:19285439) but a secondary compartment for a context-specific immune role, not the core ER ERAD function.
Supporting Evidence:
PMID:19285439
virus-induced ubiquitination and degradation of MITA by RNF5 occurred at the mitochondria
GO:0061630 ubiquitin protein ligase activity
EXP
PMID:19269966
Regulation of endoplasmic reticulum-associated degradation b...
ACCEPT
Summary: Experimental demonstration of RNF5 ubiquitin ligase activity (RING-dependent ubiquitination of JAMP). Core molecular function.
Reason: Core molecular function with direct experimental support; WT but not RING-mutant RNF5 ubiquitinates substrate.
Supporting Evidence:
PMID:19269966
Ectopically expressed JAMP was efficiently ubiquitinated in vivo by WT but not the RING mutant form of RNF5
GO:0061630 ubiquitin protein ligase activity
EXP
PMID:19285439
The ubiquitin ligase RNF5 regulates antiviral responses by m...
ACCEPT
Summary: Experimental demonstration of RNF5 ligase activity ubiquitinating STING1/MITA. Core molecular function.
Reason: Core molecular function with direct experimental support.
Supporting Evidence:
PMID:19285439
RNF5 targeted MITA at Lys150 for ubiquitination and degradation after viral infection
GO:0061630 ubiquitin protein ligase activity
EXP
PMID:23093945
Regulation of ATG4B stability by RNF5 limits basal levels of...
ACCEPT
Summary: Experimental demonstration of RNF5 ligase activity controlling ATG4B ubiquitination and stability. Core molecular function.
Reason: Core molecular function with direct experimental support.
Supporting Evidence:
PMID:23093945
the membrane-associated E3 ligase RNF5 regulates basal levels of autophagy by controlling the stability of a select pool of the cysteine protease ATG4B
GO:0006511 ubiquitin-dependent protein catabolic process
IGI
PMID:24019521
RNF185 is a novel E3 ligase of endoplasmic reticulum-associa...
ACCEPT
Summary: Genetic-interaction evidence (with RNF185) that RNF5 drives ubiquitin-dependent degradation of CFTR; redundant depletion blocks CFTR-deltaF508 turnover.
Reason: Supported by the RNF5/RNF185 co-depletion experiments; consistent with the core ERAD/proteasomal degradation role.
Supporting Evidence:
PMID:24019521
simultaneous depletion of RNF5 and RNF185 profoundly blocks CFTRΞ”F508 degradation not only during translation but also after synthesis is complete
GO:0036503 ERAD pathway
IMP
PMID:24019521
RNF185 is a novel E3 ligase of endoplasmic reticulum-associa...
ACCEPT
Summary: Mutant-phenotype evidence that RNF5 is required for ERAD of CFTR/CFTR-deltaF508. Core biological process.
Reason: Core biological process with direct experimental (IMP) support from depletion experiments.
Supporting Evidence:
PMID:24019521
simultaneous depletion of RNF5 and RNF185 profoundly blocks CFTRΞ”F508 degradation
GO:0061630 ubiquitin protein ligase activity
TAS
PMID:24019521
RNF185 is a novel E3 ligase of endoplasmic reticulum-associa...
ACCEPT
Summary: Author statement of RNF5 ubiquitin ligase activity in CFTR ERAD. Core molecular function.
Reason: Correct core molecular function.
Supporting Evidence:
PMID:24019521
targeted to co-translational degradation by the E3 ligase RNF5/RMA1
GO:1904380 endoplasmic reticulum mannose trimming
TAS
Reactome:R-HSA-901032
REMOVE
Summary: Reactome ERQC pathway annotation. RNF5 does not perform mannose trimming; this is pathway-adjacency over-annotation.
Reason: RNF5 is an E3 ligase with no mannosidase activity; ER mannose trimming is carried out by ER mannosidases/EDEMs. The annotation conflates pathway membership with direct activity.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
Membrane-bound E3 ubiquitin-protein ligase that mediates ubiquitination of target proteins
GO:0044877 protein-containing complex binding
IPI
PMID:24019521
RNF185 is a novel E3 ligase of endoplasmic reticulum-associa...
KEEP AS NON CORE
Summary: RNF5 binds a protein complex (ERAD machinery) in the CFTR degradation study. More informative than bare protein binding but still ancillary.
Reason: Reflects association with the ERAD E3 module/machinery; supportive of, but subsidiary to, the core ligase and ERAD-process annotations.
Supporting Evidence:
PMID:24019521
identify RNF185 and RNF5 as a novel E3 ligase module that is central to the control of CFTR degradation
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-8866542
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization within CFTR ERAD reactions. Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-8866546
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (RNF5/RNF185 ubiquitinate misfolded CFTR). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-8866551
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (CFTR binds ERAD machinery). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-8866854
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (CFTR F508del translocation). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-8866856
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (RNF5/RNF185 ubiquitinate CFTR F508del). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-8866857
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (CFTR F508del binds ERAD machinery). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-8867288
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization in an ERAD ubiquitination reaction. Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-9931264
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (CD274/PD-L1 ERAD transport). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-9931298
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (ubiquitination of CD274 by ERAD complex). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005789 endoplasmic reticulum membrane
TAS
Reactome:R-HSA-9931313
ACCEPT
Summary: Reactome curation of RNF5 ER membrane localization (p-CD274 binds ERAD complex). Core compartment.
Reason: Correct core localization; redundant with experimental evidence.
Supporting Evidence:
PMID:19285439
Both MITA and RNF5 were located at the mitochondria and endoplasmic reticulum (ER)
GO:0005515 protein binding
IPI
PMID:24019521
RNF185 is a novel E3 ligase of endoplasmic reticulum-associa...
KEEP AS NON CORE
Summary: Interaction captured in the RNF185/RNF5 CFTR ERAD study. Bare protein binding is uninformative.
Reason: Real interaction within the ERAD module but bare protein binding is uninformative.
Supporting Evidence:
PMID:24019521
identify RNF185 and RNF5 as a novel E3 ligase module that is central to the control of CFTR degradation
GO:0030163 protein catabolic process
IMP
PMID:19285439
The ubiquitin ligase RNF5 regulates antiviral responses by m...
KEEP AS NON CORE
Summary: Mutant-phenotype evidence that RNF5 drives degradation of a target protein (STING1/MITA). A parent of the more specific ubiquitin-dependent catabolic/ERAD process.
Reason: Correct but generic relative to the specific ERAD and K48-ubiquitination annotations; here the catabolic target is the immune adaptor MITA.
Supporting Evidence:
PMID:19285439
RNF5 targeted MITA at Lys150 for ubiquitination and degradation after viral infection
GO:0070936 protein K48-linked ubiquitination
IDA
PMID:19285439
The ubiquitin ligase RNF5 regulates antiviral responses by m...
ACCEPT
Summary: Direct evidence that RNF5 builds K48-linked polyubiquitin chains (degradative topology) on STING1/MITA. This degradative topology is also used on CFTR.
Reason: Directly demonstrated K48-linked ubiquitination, the canonical degradative topology underlying RNF5's ERAD and MITA-degradation roles.
Supporting Evidence:
PMID:19269966
CFTR ubiquitination occurred at the canonical Lys-48 topology
GO:0004842 ubiquitin-protein transferase activity
IDA
PMID:19269966
Regulation of endoplasmic reticulum-associated degradation b...
ACCEPT
Summary: Direct evidence of ubiquitin-protein transferase activity, a parent of the specific RING-type ubiquitin ligase activity.
Reason: Correct general molecular function; the specific GO:0061630 captures the RING E3 ligase activity.
Supporting Evidence:
PMID:19269966
Ectopically expressed JAMP was efficiently ubiquitinated in vivo by WT but not the RING mutant form of RNF5
GO:0005515 protein binding
IPI
PMID:19269966
Regulation of endoplasmic reticulum-associated degradation b...
KEEP AS NON CORE
Summary: Interaction with JKAMP/JAMP, a functionally important RNF5 substrate/partner at the ER membrane. Bare protein binding is uninformative.
Reason: Records the real RNF5-JAMP interaction but bare protein binding is uninformative.
Supporting Evidence:
PMID:19269966
RNF5 associates with JAMP in the ER membrane
GO:0036503 ERAD pathway
IMP
PMID:19269966
Regulation of endoplasmic reticulum-associated degradation b...
ACCEPT
Summary: Mutant-phenotype evidence linking RNF5 to ERAD, here via regulation of the ERAD adaptor JAMP. Core biological process.
Reason: Core biological process; RNF5 modulates ERAD both by direct substrate ubiquitination and by K63-regulation of JAMP.
Supporting Evidence:
PMID:19269966
RNF5 is a ubiquitin ligase anchored to the ER membrane implicated in ERAD via ubiquitination of misfolded proteins
GO:0070534 protein K63-linked ubiquitination
IDA
PMID:19269966
Regulation of endoplasmic reticulum-associated degradation b...
ACCEPT
Summary: Direct evidence that RNF5 builds non-degradative K63-linked polyubiquitin chains on JAMP (Ubc13/UBE2N-dependent), a regulatory rather than degradative modification.
Reason: Directly demonstrated K63-linked ubiquitination, establishing RNF5's capacity for non-canonical regulatory ubiquitination distinct from K48 degradative chains.
Supporting Evidence:
PMID:19269966
These findings establish that RNF5 mediates Lys-63-based polyubiquitination of JAMP
GO:0008270 zinc ion binding
TAS
PMID:9533025
Cloning, expression and mapping of a novel RING-finger gene ...
KEEP AS NON CORE
Summary: The C3HC4 RING domain coordinates zinc as a structural requirement for the ligase fold. A structural attribute supporting, not equal to, the ligase activity.
Reason: Accurate structural feature of the RING domain (residues 27-68) but subsidiary to the informative ubiquitin ligase activity; not a standalone core function.
Supporting Evidence:
file:human/RNF5/RNF5-uniprot.txt
RING-type

Core Functions

RING-type E3 ubiquitin ligase anchored in the ER membrane that ubiquitinates misfolded membrane-protein clients (e.g. CFTR and CFTR-deltaF508) with K48-linked chains to commit them to retrotranslocation and proteasomal degradation via the ERAD pathway, acting partly redundantly with RNF185.

Directly Involved In:
Supporting Evidence:
  • PMID:16901789
    an ER membrane-associated ubiquitin ligase complex containing the E3 RMA1, the E2 Ubc6e, and Derlin-1
  • PMID:24019521
    identify RNF185 and RNF5 as a novel E3 ligase module that is central to the control of CFTR degradation

ER-membrane ubiquitin ligase that builds non-degradative K63-linked polyubiquitin chains on the ERAD adaptor JKAMP/JAMP (UBE2N/Ubc13-dependent), modulating its recruitment of proteasome and p97/VCP components and thereby regulating ERAD flux.

Supporting Evidence:
  • PMID:19269966
    These findings establish that RNF5 mediates Lys-63-based polyubiquitination of JAMP

References

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Suggested Questions for Experts

Q: What determines RNF5 substrate selectivity and chain-topology choice (K48 degradative on CFTR/MITA vs K63 regulatory on JAMP), and which E2 partner (UBE2D vs UBE2N) is decisive in each case?

Q: To what extent are RNF5's antiviral (STING1/MITA) and autophagy (ATG4B) roles separable from its core ER ERAD function, and do they require distinct subcellular pools?

Suggested Experiments

Experiment: Reconstitute ERAD ubiquitination of CFTR-deltaF508 in vitro with purified RNF5, RNF185, UBE2J1/Ubc6e and Derlin-1 to map lysine sites and ubiquitin-chain linkage on the substrate and to dissect RNF5/RNF185 redundancy.

Experiment: Generate RNF5 and RNF5/RNF185 double-knockout cells and perform quantitative ubiquitinome/proteome profiling under basal and ER-stress conditions to define the endogenous ERAD substrate repertoire and the degree of paralog redundancy.

Deep Research

Falcon

(RNF5-deep-research-falcon.md)

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πŸ“š Additional Documentation

Notes

(RNF5-notes.md)

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Pn Notes

(RNF5-pn-notes.md)

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πŸ“„ View Raw YAML

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