Autoimmune Genetics - Greatest Hits

IN_PROGRESS BIOLOGY_DOMAIN

Species: human

Genes: PTPN22 CTLA4 IL2RA IL4 STAT4 IL13 IL23R IL7R ORMDL3 TNFAIP3 TNFRSF1A EGR2 BACH2 IRF4 STAT3 IKZF1 CD28 GATA3 SMAD3 IL10

Autoimmune Genetics - Greatest Hits

Bottom line: GWAS and functional studies have converged on a small set of
immune-regulation genes whose variants raise risk for several autoimmune
diseases at once (type 1 diabetes, rheumatoid arthritis, multiple sclerosis,
inflammatory bowel disease, lupus). We reviewed every existing GO annotation on
20 of the best-replicated of these human genes, covering T cell
co-stimulation and inhibition, cytokine receptors, Th1/Th2/Th17 transcription
factors and NF-kB control. All 20 reviews exist, have every row actioned and
validate: 2,291 annotations, with 1,464 ACCEPT, 390 KEEP_AS_NON_CORE, 142
MARK_AS_OVER_ANNOTATED, 94 MODIFY, 174 REMOVE, 11 UNDECIDED and 16 NEW. Most
removals (144 of 174) are generic protein binding IPI rows, 134 of them on
STAT3 and SMAD3; others are propagation errors such as prolactin receptor
activity on IL23R. The per-gene review files are not uniformly finalised (9
COMPLETE, 6 DRAFT, 5 IN_PROGRESS), and the supporting-text warnings listed
below remain open; the STAT3 deep-research item is stale, since
genes/human/STAT3/STAT3-deep-research-falcon.md now exists. The STATUS
section says 19 unique genes; the tables list 20.

We did this because these genes are shared across many autoimmune diseases and
are among the most heavily annotated immune genes (STAT3 456 rows, SMAD3 349,
GATA3 258), so they test whether review can find the core immune-regulatory
function under a large body of interaction and propagated annotations.

Overview

This project reviews the GO annotations for the most well-established autoimmune susceptibility genes identified through GWAS and functional studies. These genes represent the core molecular machinery of immune regulation, and variants in them confer risk for multiple autoimmune diseases including type 1 diabetes, rheumatoid arthritis, multiple sclerosis, inflammatory bowel disease, and systemic lupus erythematosus.

Model Species

Primary: Homo sapiens (human)

Gene Categories

Tier 1: "Greatest Hits" of Autoimmune Genetics

These genes harbor the most strongly replicated and functionally validated autoimmune risk variants:

Gene UniProt Key Function Associated Diseases
PTPN22 Q9Y2R2 T cell receptor signaling phosphatase T1D, RA, SLE
CTLA4 P16410 T cell co-inhibitory receptor T1D, Graves, RA
IL2RA P01589 IL-2 receptor alpha chain (CD25) T1D, MS
IL4 P05112 Th2 cytokine Asthma, atopy
STAT4 Q14765 IL-12/IFN signaling transcription factor RA, SLE
IL13 P35225 Th2 cytokine Asthma, IBD
IL23R Q5VWK5 IL-23 receptor IBD, psoriasis, AS
IL7R P16871 IL-7 receptor alpha MS, T1D
ORMDL3 Q9P0S3 ER membrane protein, sphingolipid regulation Asthma, IBD
TNFAIP3 P21580 A20, NF-kB negative regulator SLE, RA, IBD
TNFRSF1A P19438 TNF receptor 1 TRAPS, MS

Tier 2: Well-Established Autoimmune Risk Genes

Gene UniProt Key Function Associated Diseases
EGR2 P11161 Early growth response TF, T cell anergy SLE
BACH2 Q9BYV9 TF regulating B/T cell differentiation T1D, MS, celiac
IRF4 Q15306 Interferon regulatory factor SLE, RA
STAT3 P40763 JAK-STAT signaling IBD, hyper-IgE
IKZF1 Q13422 Ikaros, lymphocyte development TF SLE, T1D
CD28 P10747 T cell co-stimulatory receptor RA, MS
GATA3 P23771 Th2 lineage TF Asthma, HDR syndrome
SMAD3 P84022 TGF-beta signaling IBD, allergy
IL10 P22301 Anti-inflammatory cytokine IBD, SLE

Key Pathways

  1. T cell activation/inhibition: PTPN22, CTLA4, CD28, IL2RA, IL7R
  2. Th1/Th2 polarization: IL4, IL13, GATA3, STAT4, IRF4
  3. Th17/regulatory T cell balance: IL23R, STAT3, SMAD3, BACH2
  4. NF-kB/TNF signaling: TNFAIP3, TNFRSF1A
  5. Immune tolerance: IL10, EGR2, IKZF1
  6. ER stress/UPR (immune context): ORMDL3

Review Status

Gene Fetch Deep Research Review Validates Notes
PTPN22 DONE DONE (falcon) DONE PASS (4w)
CTLA4 DONE DONE (falcon) DONE PASS (1w)
IL2RA DONE DONE (falcon) DONE PASS (34w) Refs need supporting_text
IL4 DONE DONE (falcon) DONE PASS (14w) Inconsistencies resolved
STAT4 DONE DONE (falcon) DONE PASS (12w)
IL13 DONE DONE (falcon) DONE PASS (17w)
IL23R DONE DONE (falcon) DONE PASS (12w) core_functions + supporting_text fixed
IL7R DONE DONE (falcon) DONE PASS (2w) Inconsistencies resolved
ORMDL3 DONE DONE (falcon) DONE PASS (1w)
TNFAIP3 DONE DONE (falcon) DONE PASS (32w) Refs need supporting_text
TNFRSF1A DONE DONE (falcon) DONE PASS (13w)
EGR2 DONE DONE (falcon) DONE PASS (3w)
BACH2 DONE DONE (falcon) DONE PASS (15w)
IRF4 DONE DONE (falcon) DONE PASS (9w)
STAT3 DONE DONE (falcon) DONE PASS (0w) Clean
IKZF1 DONE DONE (falcon) DONE PASS (1w)
CD28 DONE DONE (falcon) DONE PASS (2w) Inconsistencies resolved, supporting_text added
GATA3 DONE DONE DONE PASS (0w) Clean
SMAD3 DONE DONE (falcon) DONE PASS (2w)
IL10 DONE DONE (falcon) DONE PASS (34w) Inconsistencies resolved

STATUS

All 19 unique genes (20 rows) fetched, deep-researched (falcon), reviewed, and validated. All pass with 0 errors.

NOTES

2026-02-14

2026-02-15

Slides